Document ID: chunk:federal_register_of_legislation:F2021L01171:reg:7
Version: federal_register_of_legislation:F2021L01171
Segment Type: reg
Provision Reference: reg 7
Character Range: 1655–3911

7               Kind of injury, disease or death to which this Statement of Principles relates
(1)          This Statement of Principles is about polycythaemia vera and death from polycythaemia vera.
Meaning of polycythaemia vera
(2)          For the purposes of this Statement of Principles, polycythaemia vera:
(a)          means a chronic Philadelphia-chromosome negative myeloproliferative neoplasm characterised by proliferation of bone marrow cells of all types, resulting in elevated red cell production and increased haematocrit, haemoglobin or red blood cell mass, and usually an excess of platelets and white blood cells; and
(b)          includes masked, or bled down polycythaemia vera; and
(c)          excludes:
(i)            relative polycythaemia;
(ii)          familial and congenital polycythaemia; and
(iii)        secondary polycythaemia from hypoxaemia or increased erythropoietin.
Note 1: Polycythaemia vera is also known as polycythaemia rubra vera.
             Note 2: Typical clinical manifestations of polycythaemia vera include formation of blood clots, bleeding, fatigue, night sweats, visual disturbances, headache, nausea and abdominal pain. Patients can be asymptomatic.
             Note 3: The clinical course is usually indolent, but transformation to bone marrow failure, myelofibrosis and acute leukaemia may occur.
(3)          While polycythaemia vera attracts ICD‑10‑AM code D45, in applying this Statement of Principles the meaning of polycythaemia vera is that given in subsection (2).
(4)          For subsection (3), a reference to an ICD-10-AM code is a reference to the code assigned to a particular kind of injury or disease in The International Statistical Classification of Diseases and Related Health Problems, Tenth Revision, Australian Modification (ICD-10-AM), Tenth Edition, effective date of 1 July 2017, copyrighted by the Independent Hospital Pricing Authority, ISBN 978-1-76007-296-4.
Death from polycythaemia vera
(5)          For the purposes of this Statement of Principles, polycythaemia vera, in relation to a person, includes death from a terminal event or condition that was contributed to by the person's polycythaemia vera.
Note: terminal event is defined in the Schedule 1 - Dictionary.