Document ID: chunk:federal_register_of_legislation:F2018L00195:reg:7
Version: federal_register_of_legislation:F2018L00195
Segment Type: reg
Provision Reference: reg 7
Character Range: 1604–3977

7               Kind of injury, disease or death to which this Statement of Principles relates
(1)          This Statement of Principles is about systemic sclerosis and death from systemic sclerosis.
Meaning of systemic sclerosis
(2)          For the purposes of this Statement of Principles, systemic sclerosis (also known as scleroderma):
(a)           means an autoimmune, fibrosing connective tissue disorder characterised by deposition of collagen in skin and internal organs, and microvascular lesions, especially in the skin, lungs and kidneys; and
(b)           excludes localised sclerosis, graft versus host disease with dermal fibrosis, and scleroderma-like conditions (for example, scleromyxoedema and eosinophilic fasciitis).
             Note 1:                                                         The three main subsets of systemic sclerosis are limited cutaneous systemic sclerosis (previously referred to as CREST syndrome, comprising calcinosis cutis, Raynaud phenomenon, oesophageal dysmotility, sclerodactyly, telangiectasias), diffuse cutaneous systemic sclerosis and systemic sclerosis sine scleroderma.
             Note 2:                                           The diagnosis of systemic sclerosis is based on clinical findings, although histopathologic confirmation is sometimes needed to rule out other diseases.  Serological markers for systemic sclerosis include elevated levels of anticentromere antibodies and anti-Scl-70 antibodies.
(3)          While systemic sclerosis attracts ICD‑10‑AM code M34, in applying this Statement of Principles the meaning of systemic sclerosis is that given in subsection (2).
(4)          For subsection (3), a reference to an ICD-10-AM code is a reference to the code assigned to a particular kind of injury or disease in The International Statistical Classification of Diseases and Related Health Problems, Tenth Revision, Australian Modification (ICD-10-AM), Tenth Edition, effective date of 1 July 2017, copyrighted by the Independent Hospital Pricing Authority, ISBN 978-1-76007-296-4.
Death from systemic sclerosis
(5)          For the purposes of this Statement of Principles, systemic sclerosis, in relation to a person, includes death from a terminal event or condition that was contributed to by the person's systemic sclerosis.
Note: terminal event is defined in the Schedule 1 – Dictionary.