what is krabbe disease
Krabbe disease (also known as globoid cell leukodystrophy or galactosylceramide lipidosis) is a rare, often fatal degenerative disorder that affects the myelin sheath of the nervous system.It is a form of sphingolipidosis, as it involves dysfunctional metabolism of sphingolipids.he disease is named after the Danish neurologist Knud Haraldsen Krabbe (1885-1965). Illinois, Kentucky and Pennsylvania have laws to test for Krabbe and other diseases at birth. There is a movement in Maine and other states to adopt such regulations.