Fulminating Idiopathic Hemochromatosis Presenting as Constrictive Pericarditis
Authors: AGATHA C. NODY
Journal: Annals of Internal Medicine (1975)

Letters1 September 1975Fulminating Idiopathic Hemochromatosis Presenting as Constrictive PericarditisAGATHA C. NODY, M.D., MICHAEL S. BRUNO, M.D., F.A.C.P., NICHOLAS P. DEPASQUALE, M.D., F.A.C.P., PAUL A. BIENSTOCK, M.D.AGATHA C. NODY, M.D.Search for more papers by this author, MICHAEL S. BRUNO, M.D., F.A.C.P.Search for more papers by this author, NICHOLAS P. DEPASQUALE, M.D., F.A.C.P.Search for more papers by this author, PAUL A. BIENSTOCK, M.D.Search for more papers by this authorAuthor, Article, and Disclosure Informationhttps://doi.org/10.7326/0003-4819-83-3-373 SectionsAboutPDF ToolsAdd to favoritesDownload CitationsTrack CitationsPermissions ShareFacebookTwitterLinkedInRedditEmail ExcerptCongestive heart failure is the most frequent cause of death in idiopathic hemochromatosis, but the course is usually protracted (1). We report here a patient with fulminating idiopathic hemochromatosis in whom death occurred within 1 month of the onset of symptoms. Hemodynamic findings of constrictive pericarditis are also a feature of this case.A 33-year-old white male physician was admitted to Lenox Hill Hospital in New York City. He complained of dyspnea on exertion, weakness, and anorexia. He was in good health until 10 days before admission. There was no excessive dietary or parenteral intake of iron, and the family...References1. FINCHFINCH SC: Idiopathic hemochromatosis, an iron storage disease. Medicine 34:381-430, 1955 CrossrefMedlineGoogle Scholar2. EASLEYSCHREINERYU RBP: Reversible cardiomyopathy associated with hemochromatosis. N Engl J Med 287:866-867, 1972 CrossrefMedlineGoogle Scholar3. WASSERMANRICHARDSONBAIRD AEC: Cardiac hemochromatosis simulating constrictive pericarditis. Am J Med 32:316-323, 1962 CrossrefMedlineGoogle Scholar4. BURCHDEPASQUALE GN: Heart muscle disease. DM May:3-68, 1968 Google Scholar This content is PDF only. To continue reading please click on the PDF icon. Author, Article, and Disclosure InformationAffiliations: Lenox Hill Hospital 100 East 77 Street New York, New York 10021 PreviousarticleNextarticle Advertisement FiguresReferencesRelatedDetails Metrics Cited ByCardiac Involvement in HemochromatosisLeft Ventricular Remodeling, Systolic Function, and Diastolic Function in Young Adults With β-Thalassemia IntermediaLeft ventricular diastolic Doppler characteristics in beta-thalassemia major.Restrictive diastolic abnormalities identified by Doppler echocardiography in patients with thalassemia major.Myocardial iron grading by endomyocardial biopsy. A clinico-pathologic study on iron overloaded patientsMetabolische Erkrankungen mit vorwiegend restriktiver Funktionsstörung des MyokardsMyokardbeteiligung bei weiteren Erkrankungen des Stoffwechsels, der Ernährung, des Endokriniums und des hämatologischen SystemsCardiac Abnormalities in Primary HemochromatosisThe Restrictive CardiomyopathiesSuccessful reversal by chelation therapy of congestive cardiomyopathy due to iron overloadCase Report: Refractory Biventricular Heart Failure in Secondary HemochromatosisPrimary hemochromatosis: Anatomic and physiologic characteristics of the cardiac ventricles and their response to phlebotomyCardiac hemochromatosis: Beneficial effects of iron removal therapyDiagnostic problem: Constrictive pericarditis or restrictive cardiomyopathy?Cardiac disease associated with iron overloadHemochromatosis heart disease: An unemphasized cause of potentially reversible restrictive cardiomyopathyPericardial constriction 1 September 1975Volume 83, Issue 3Page: 373-374KeywordsDyspneaHeart failureHemochromatosisHemodynamics Issue Published: 1 September 1975 PDF DownloadLoading ...