Survival to Adulthood in a Patient with Complete Transposition of the Great Vessels
Authors: WILLIAM C. ROBERTS
Journal: Annals of Internal Medicine (1962)

Case Studies1 November 1962Survival to Adulthood in a Patient with Complete Transposition of the Great VesselsIncluding a Note on the Association of Endocrine Tumors with Heart DiseaseWILLIAM C. ROBERTS, M.D., DEAN T. MASON, M.D., EUGENE BRAUNWALD, M.D.WILLIAM C. ROBERTS, M.D., DEAN T. MASON, M.D., EUGENE BRAUNWALD, M.D.Author, Article, and Disclosure Informationhttps://doi.org/10.7326/0003-4819-57-5-834 SectionsAboutPDF ToolsAdd to favoritesDownload CitationsTrack CitationsPermissions ShareFacebookTwitterLinkedInRedditEmail ExcerptThe majority of patients with complete transposition of the great vessels die in infancy. The subject of this paper is a man who lived for 21 years with this malformation, which was associated with several other cardiac defects. A Blalock-Taussig procedure had been performed at the age of 10 years. An adrenal cortical tumor was discovered at autopsy, and this finding provided the stimulus to review the association of endocrine tumors with heart disease.REPORT OF PATIENTA 21-year-old white man, a furniture maker, was admitted to the National Heart Institute on September 20, 1961. A heart murmur and cyanosis...References1. DORNING J: A case of transposition of the aorta and pulmonary artery, with patent foramen ovale; death at ten years of age. Trans. Amer. Pediat. Soc. 2: 46, 1890. Google Scholar2. ALEXANDERWHITE FPD: Four important congenital cardiac conditions causing cyanosis to be differentiated from the tetralogy of Fallot: tricuspid atresia, Eisenmenger's complex, transposition of the great vessels, and a single ventricle. Ann. Intern. Med. 27: 64, 1947. LinkGoogle Scholar3. PUNGGOTTSTEINHIRSCH SWKEF: Complete transposition of the great vessels in a male aged 18 years. Amer. J. Med. 18: 155, 1955. CrossrefMedlineGoogle Scholar4. KEITH A: Six specimens of abnormal heart. J. 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BARTTERLIDDLEBELLBRAUNWALDHILBISHCORNELLHICKLIN FCGWNHETGWM: Problem in differential diagnosis: clinical pathological conference at the National Institutes of Health. Ann. Intern. Med. 52: 1289, 1960. LinkGoogle Scholar18. ROSSCARPENTERGLANCY RSCCDL: Personal communication. Google Scholar This content is PDF only. To continue reading please click on the PDF icon. Author, Article, and Disclosure InformationAffiliations: Bethesda, MarylandFrom the Pathologic Anatomy Department, Clinical Center, and Cardiology Branch, National Heart Institute, National Institutes of Health, Bethesda, Maryland.Requests for reprints should be addressed to William C. Roberts, M.D., Department of Medicine, The Johns Hopkins Hospital, Baltimore 5, Maryland. PreviousarticleNextarticle Advertisement FiguresReferencesRelatedDetails Metrics Cited ByMorphological and Functional Characteristics of the Right Ventricle Functioning as a Systemic Ventricle for Decades After an Atrial Switch Procedure for Complete Transposition of the Great ArteriesTetralogy of Fallot Associated With Invasive Adrenocortical Tumor in an Adult WomanSingle Left Ventricle and PheochromocytomaCyanotic congenital heart disease with malignant paragangliomaComplete transposition of great vessels without associated defectsCyanotic Malformations of the Heart with Pheochromocytoma 1 November 1962Volume 57, Issue 5Page: 834-842KeywordsAutopsyCardiovascular therapyEndocrine tumorsHeartHeart murmursStenosis Issue Published: 1 November 1962 PDF DownloadLoading ...