Clinical and Pathological Aspects of Cystic Disease of the Renal Medulla
Authors: MAURICE B. STRAUSS
Journal: Annals of Internal Medicine (1962)

Article1 September 1962Clinical and Pathological Aspects of Cystic Disease of the Renal MedullaAn Analysis of Eighteen CasesMAURICE B. STRAUSS, M.D., F.A.C.P.MAURICE B. STRAUSS, M.D., F.A.C.P.Search for more papers by this authorAuthor, Article, and Disclosure Informationhttps://doi.org/10.7326/0003-4819-57-3-373 SectionsAboutPDF ToolsAdd to favoritesDownload CitationsTrack CitationsPermissions ShareFacebookTwitterLinkedInRedditEmail ExcerptCysts of the medullary portions of the kidney may occur in a variety of circumstances. For the most part they are either asymptomatic or present no clearly recognizable clinical syndromes, although certain types may have characteristic radiologic findings.The disorder to be discussed is characterized by the insidious onset of anemia, salt wasting, and azotemia, for the most part in the absence of urinary abnormality and without elevation of blood pressure. Bone disease may be prominent in children. The examples following are illustrative.ILLUSTRATIVE CASESSALT-WASTINGTwenty years ago a young man died almost 4 years after the first symptoms...References1. THORNKOEPFCLINTON GWGFM. Renal failure simulating adrenocortical insufficiency. New Engl. J. Med. 231: 76, 1944. CrossrefGoogle Scholar2. SMITHGRAHAM CHJB: Congenital medullary cysts of the kidneys with severe refractory anemia. Amer. J. Dis. Child. 69: 369, 1945. Google Scholar3. HOGNESSBURNELL JRJM: Medullary cysts of kidneys. Arch. Intern. Med. 93: 355, 1954. CrossrefGoogle Scholar4. MURPHYCOFFMANPRINGLEISERI RVEWBHLT: Studies of sodium and potassium metabolism in salt-losing nephritis. Arch. Intern. Med. 90: 750, 1952. CrossrefGoogle Scholar5. KNOWLESLEVITINBRIDGES HCHA: Salt-losing nephritis with fixed urinary composition. Amer. J. Med. 22: 158, 1957. CrossrefMedlineGoogle Scholar6. THORNGOLDFIENSUITERDAMMIN GWATBG: Hormonal studies in salt-losing nephritis. Med. Clin. N. Amer. 44: 1139, 1960. CrossrefMedlineGoogle Scholar7. STANBURYMAHLER SWRF: Salt-wasting renal disease. Metabolic observations on a patient with 'salt-losing nephritis.' Quart. J. Med. 28: 425, 1959. MedlineGoogle Scholar8. STRAUSS MB: Cystic disease of the renal medulla, in Diseases of the Kidneys, ed. by Strauss, M. B., and Welt, L. G., Little, Brown and Company, Boston, 1963. To be published. Google Scholar9. REILLYNEUHAUSER BJEB: Renal tubular ectasia in cystic disease of the kidneys and liver. Amer. J. Roentgenol. 84: 546, 1960. Google Scholar This content is PDF only. To continue reading please click on the PDF icon. Author, Article, and Disclosure InformationAuthors: MAURICE B. STRAUSS, M.D., F.A.C.P.Affiliations: Boston, MassachusettsFrom the Medical Service and Research Laboratory, Boston Veterans Administration Hospital, and the Departments of Medicine of Boston University and Tufts University Schools of Medicine.Presented at the Forty-third Annual Session of The American College of Physicians, Philadelphia, Pennsylvania, April 9-13, 1962.Requests for reprints should be addressed to Maurice B. Strauss, M.D., Medical Service, Vetterans Administration Hospital, 150 South Huntington Avenue, Boston 30, Massachusetts. 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