Stokes-Adams Syndrome and Atrial Arrhythmias as the Presenting Symptoms of Myotonic Dystrophy, with Response to Electrocardioversion
Authors: ARTHUR H. WOLINTZ
Journal: Annals of Internal Medicine (1966)

Case Studies1 December 1966Stokes-Adams Syndrome and Atrial Arrhythmias as the Presenting Symptoms of Myotonic Dystrophy, with Response to ElectrocardioversionARTHUR H. WOLINTZ, M.D., EDMUND H. SONNENBLICK, M.D., F.A.C.P., W. KING ENGEL, M.D.ARTHUR H. WOLINTZ, M.D., EDMUND H. SONNENBLICK, M.D., F.A.C.P., W. KING ENGEL, M.D.Author, Article, and Disclosure Informationhttps://doi.org/10.7326/0003-4819-65-6-1260 SectionsAboutPDF ToolsAdd to favoritesDownload CitationsTrack CitationsPermissions ShareFacebookTwitterLinkedInRedditEmail ExcerptMyotonic dystrophy is inherited as an autosomal dominant trait and is characterized by muscle weakness and wasting, delayed muscular relaxation after contraction (myotonic phenomenon), premature frontal baldness, cataracts, gonadal atrophy, cranial hyperostosis, and cardiac disorders (1). Muscle weakness and wasting are most pronounced in the facial, pharyngeal, and masticatory muscles, as well as the sternocleidomastoid muscles, the flexors and extensors of the forearms, the hands, and the quadricepts, and dorsiflexor muscles of the feet. The myotonia is most easily elicited in the muscles of the hand, forearm, and tongue and is often slight, causing little or no disability.Cardiac involvement...References1. STEINHERT H: Myopathologische beiträge. I. Über das klinische und anatomische Bild des Muskelschwundes der myotoniker. Deutsch. Z. Nervenheilk. 37: 58, 1909. Google Scholar2. GRIFFITH TW: On myotonia. Quart. J. Med. 5: 229, 1911. Google Scholar3. EVANS W: The heart in myotonia atrophica. Brit. Heart J. 4: 41, 1944. CrossrefGoogle Scholar4. FISCH C: The heart in dystrophia myotonica. Amer. Heart J. 41: 525, 1951. CrossrefMedlineGoogle Scholar5. 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PreviousarticleNextarticle Advertisement FiguresReferencesRelatedDetails Metrics Cited ByPathology of the cardiac conduction system in myotonic dystrophy: A study of 12 casesPolymyositic Heart DiseaseÄtiologie kardialer RhythmusstörungenThe natural history of conduction system disease in myotonic muscular dystrophy as determined by serial electrophysiologic studies.Noninvasive assessment of left ventricular function in myotonic muscular dystrophy.Cardiac arrest during induction of anesthesia in Duchenne muscular dystrophyRespiratory failure and cardiac disturbances in myotonic dystrophyCardiac conduction in myotonic dystrophyCardiovascular Abnormalities in Myotonic DystrophyMyokardiopathien bei MyopathienThe Stokes-Adams syndromeHereditäre Myopathien 1 December 1966Volume 65, Issue 6Page: 1260-1266KeywordsArrhythmiaElectromyographyHeart diseasesMusclesMuscular diseasesMyocardiumMyotonic dystrophyNeurologySyncopeTongue Issue Published: 1 December 1966 PDF DownloadLoading ...