Kidney Polycystic Disease in Adult Congenital Hepatic Fibrosis
Authors: JEAN-LOUIS DUPOND
Journal: Annals of Internal Medicine (1978)

Brief Reports1 April 1978Kidney Polycystic Disease in Adult Congenital Hepatic FibrosisJEAN-LOUIS DUPOND, M.D., JEAN-PHILIPPE MIGUET, M.D., JEAN-PIERRE CARBILLET, M.D., YVES SAINT-HILLIER, M.D., CLAUDE PEROL, M.D., ROBERT LeCONTE-des-FLORIS, M.D.JEAN-LOUIS DUPOND, M.D.Search for more papers by this author, JEAN-PHILIPPE MIGUET, M.D.Search for more papers by this author, JEAN-PIERRE CARBILLET, M.D.Search for more papers by this author, YVES SAINT-HILLIER, M.D.Search for more papers by this author, CLAUDE PEROL, M.D.Search for more papers by this author, ROBERT LeCONTE-des-FLORIS, M.D.Search for more papers by this authorAuthor, Article, and Disclosure Informationhttps://doi.org/10.7326/0003-4819-88-4-514 SectionsAboutPDF ToolsAdd to favoritesDownload CitationsTrack CitationsPermissions ShareFacebookTwitterLinkedInRedditEmail ExcerptCongenital hepatic fibrosis and the adult type of polycystic disease of liver and kidneys are regarded as different entities (1). [a] Congenital hepatic fibrosis is characterized by fibrous thickening of the portal tracts and an excess of small bile ducts. The cysts of congenital hepatic fibrosis, which are in fact dilated bile ducts, are small, generally microscopic, and communicate with the bile ducts. The hepatic cysts in polycystic disease are large and do not communicate with the biliary passages. [b] In congenital hepatic fibrosis, dilatation of the collecting tubules is considered as the most common associated renal lesion (1). Multiple...References1. FAUVERT R and BENHAMOU J: Congenital hepatic fibrosis, in The Liver and Its Diseases, edited by SCHAFFNER F, SHERLOCK S, LEEVY CM. Stuttgart, Georg Thieme, 1974, p. 283 Google Scholar2. PARKER R: Fibrosis of the liver as a congenital anomaly. J Pathol 71:359-368, 1956 CrossrefGoogle Scholar3. KANH L, SAUNDERS S, and HICKMAN R: Congenital hepatic fibrosis: a case report and family study. S Afr Med J 580-583, 1969 MedlineGoogle Scholar4. CLERMONT R, MAILLARD J, BENHAMOU J, and FAUVERT R: Fibrose hépatique congénitale. Can Med Assoc J 97:1272-1278, 1967 MedlineGoogle Scholar5. Case records of the Massachusetts General Hospital. N Engl J Med 290:676-683, 1974 CrossrefMedlineGoogle Scholar This content is PDF only. To continue reading please click on the PDF icon. Author, Article, and Disclosure InformationAuthors: JEAN-LOUIS DUPOND, M.D.; JEAN-PHILIPPE MIGUET, M.D.; JEAN-PIERRE CARBILLET, M.D.; YVES SAINT-HILLIER, M.D.; CLAUDE PEROL, M.D.; ROBERT LeCONTE-des-FLORIS, M.D.Affiliations: Hôpital Saint Jacques Besancon France PreviousarticleNextarticle Advertisement FiguresReferencesRelatedDetails Metrics Cited byCongenital abnormalities of the biliary tractNonparasitic Cystic Diseases of the Liver and Intrahepatic Biliary TreeLésions kystiques congénitales des voies biliaires intra et extra-hépatiquesCongenital Hepatic FibrosisThree Cases of Congenital Hepatic Fibrosis with Caroli`s Disease in Three SiblingsAutosomal Recessive Polycystic Kidney DiseaseCongenital hepatic fibrosisCongenital hepatic fibrosis and adult-type autosomal dominant polycystic kidney disease in a childNon-cirrhotic Intrahepatic Portal Hypertension in AdultsThe Renal Lesion of Congenital Hepatic Fibrosis: Pathologic and Morphometry Analysis, with Comparison to the Renal Lesion of Infantile Polycystic DiseaseCaroli's disease in congenital hepatic fibrosis and infantile polycystic diseasePolycystic kidney diseaseCongenital hepatic fibrosis in children 1 April 1978Volume 88, Issue 4Page: 514-515KeywordsBile ductsFibrosisKidneysLesionsLiver diseasesLiver fibrosisPolycystic kidney disease ePublished: 1 December 2008 Issue Published: 1 April 1978 PDF downloadLoading ...