Hyperkalemia Familial Periodic Paralysis (Adynamia Episodica Hereditaria)
Authors: FREDERICK S. ARMSTRONG
Journal: Annals of Internal Medicine (1962)

Case Studies1 September 1962Hyperkalemia Familial Periodic Paralysis (Adynamia Episodica Hereditaria)FREDERICK S. ARMSTRONG, M.D.FREDERICK S. ARMSTRONG, M.D.Search for more papers by this authorAuthor, Article, and Disclosure Informationhttps://doi.org/10.7326/0003-4819-57-3-455 SectionsAboutPDF ToolsAdd to favoritesDownload CitationsTrack CitationsPermissions ShareFacebookTwitterLinkedInRedditEmail ExcerptIn 1956 Gamstorp (1) of the University of Lund, Sweden, reported her observations of a hereditary disorder manifested by periodic paralysis with hyperkalemia rather than hypokalemia as seen in classical familial periodic paralysis. She called this conditionadynamia episodica hereditaria. Undoubtedly many patients who were thought previously to have classical familial periodic paralysis had, in reality,adynamia episodica hereditaria, orhyperkalemic familial periodic paralysis, the term we prefer to use. Several reports prior to Gamstorp's paper contained descriptions of cases with a striking clinical similarity to hyperkalemic familial periodic paralysis (2-10); indeed, 2 reports were about patients from the 2...References1. GAMSTORP I: Adynamia episodica hereditaria. Acta Paediat. (Upps.) (supp.) 108: 1, 1956. Google Scholar2. BUZZARD EF: Three cases of family periodic paralysis with a consideration of the pathology of the disease. Lancet 2: 1564, 1901. CrossrefGoogle Scholar3. KULNEFF N: Myatonia periodica. Nord. Med. Ark. 2: 1, 3: 21, 1902. Google Scholar4. SCHOENTHAL L: Family periodic paralysis, with review of literature. Amer. J. Dis. Child. 48: 799, 1934. CrossrefGoogle Scholar5. WOLF A: Effective use of thyroid in periodic paralysis. New York J. Med. 43: 1951, 1943. Google Scholar6. WYLLIEWATKINS WGAG: Periodic familial paralysis. Proc. Roy. Soc. Med. 41: 861, 1948. CrossrefGoogle Scholar7. TYLERSTEPHENSGUNNPERKOFF FHFEFDGT: Studies in disorders of muscle. VII. 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Author, Article, and Disclosure InformationAffiliations: Fort Gordon, GeorgiaFrom the United States Army Hospital, Fort Gordon, Georgia.This material has been reviewed by the Office of The Surgeon General, Department of the Army, and there is no objection to its presentation and/ or publication. This review does not imply any indorsement of the opinions advanced or any recommendation of such products as may be named.Presented at the Forty-third Annual Meeting of The American College of Physicians, April 9-13, 1962, Philadelphia, Pennsylvania.Requests for reprints should be addressed to Frederick S. Armstrong, M.D., 5150 Graves Avenue, San Jose, California. PreviousarticleNextarticle Advertisement FiguresReferencesRelatedDetails Metrics Cited ByThe Periodic ParalysesDisorders of MuscleDisorders of MuscleClinical and ultrastructural observations in a kindred with normo-hyperkalaemic periodic paralysis.Hereditäre MyopathienHyperkalemic intermittent paralysis associated with spironolactone in a patient with cardiac cirrhosisHYPERKALEMIC CHANGES DURING SPIRONOLACTONE THERAPY FOR CIRRHOSIS AND ASCITES, WITH SPECIAL REFERENCE TO HYPERKALEMIC INTERMITTENT PARALYSISAdynamie épisodique héréditaireFAMILIAL HYPERKALAEMIC PERIODIC PARALYSISMedical genetics 1962 1 September 1962Volume 57, Issue 3Page: 455-461KeywordsAttentionExcretionParalysisSurgeonsThyroid Issue Published: 1 September 1962 PDF DownloadLoading ...