FAMILIAL RECURRING POLYSEROSITIS: A DISEASE ENTITY
Authors: R J PRIEST, R K NIXON
Journal: Annals of Internal Medicine (1959)

Article1 December 1959FAMILIAL RECURRING POLYSEROSITIS: A DISEASE ENTITYROBERT J. PRIEST, ROBERT K. NIXONROBERT J. PRIESTSearch for more papers by this author, ROBERT K. NIXONSearch for more papers by this authorAuthor, Article, and Disclosure Informationhttps://doi.org/10.7326/0003-4819-51-6-1253 SectionsAboutPDF ToolsAdd to favoritesDownload CitationsTrack CitationsPermissions ShareFacebookTwitterLinkedInRedditEmail ExcerptI. INTRODUCTIONFamilial recurring polyserositis is a unique disease entity almost entirely limited to persons of Armenian, Syrian or Jewish ethnic origin. Janeway and Mosenthal1in 1908 described a syndrome of recurrent abdominal pain in a Jewish school girl aged 16 years. All of her life she had suffered from recurring episodes of fever, leukocytosis and abdominal pain with abdominal rigidity and tenderness lasting one to two days and recurring at intervals of from one to four weeks. Siegal2, 3subsequently referred to this disease as "benign paroxysmal peritonitis," and Reimann,4in his discussion of periodic diseases, included it as...Bibliography1. JanewayMosenthal TCHO: An unusual paroxysmal syndrome, probably allied to recurrent vomiting, with a study of the nitrogen metabolism, Tr. A. Am. Physicians 23: 504, 1908. Google Scholar2. Siegal S: Benign paroxysmal peritonitis, Ann. Int. Med. 23: 1, 1945. LinkGoogle Scholar3. Siegal S: Benign paroxysmal peritonitis—second series, Gastroenterology 12: 234, 1949. CrossrefMedlineGoogle Scholar4. Reimann HA: Periodic disease: periodic fever, periodic abdominalgia, cyclic neutropenia, intermittent arthralgia, angioneurotic edema, anaphylactoid purpura and periodic paralysis, J. A. M. A. 141: 175, 1949. CrossrefMedlineGoogle Scholar5. ReimannMoadiéSemerdjianSahyoun HAJSPF: Periodic peritonitis: heredity and pathology, report of seventy-two cases, J. A. M. A. 154: 1254, 1954. CrossrefMedlineGoogle Scholar6. 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GEORGE, M.D., ROBERT E. WESTFALL, M.D.Familial paroxysmal polyserositisThe differential diagnosis of coronary artery disease and gastrointestinal disorders∗Polyserositis induced by psicofuranine in man and comparative toxicity in the rat, mouse, dog, chicken, and monkeyPeriodic Polyserositis (Periodic Disease)Recurrent polyserositis (familial mediterranean fever; Periodic disease)Electrocardiographic changes in recurrent polyserositis (“periodic disease”)Familial Mediterranean FeverPeriodic Fever with Renal AmyloidosisThe Genetic Approach to the Study of Gastrointestinal DiseaseFamilial Recurring Polyserositis Simulating Acute Surgical Condition of the AbdomenMedical genetics 1959Febbre Mediterranea Familiare (FMF) 1 December 1959Volume 51, Issue 6Page: 1253-1274KeywordsAbdominal painArthralgiaArthritisFeversHospital medicineLeukocytosisPathogenesisPeritonitisRisk managementThorax ePublished: 1 December 2008 Issue Published: 1 December 1959 PDF downloadLoading ...