GAUCHER'S DISEASE: I. A CASE WITH HEMOLYTIC ANEMIA AND MARKED THROMBOPENIA; IMPROVEMENT AFTER REMOVAL OF SPLEEN WEIGHING 6822 GRAMS: II. LIPID ANALYSIS OF THE GAUCHER'S SPLEEN
Authors: Harry Mandelbaum, Louis Berger, Max Lederer, Albert Edward Sobel, Irving Allan Kaye
Journal: Annals of Internal Medicine (1942)

Article1 March 1942GAUCHER'S DISEASEII. LIPID ANALYSIS OF THE GAUCHER'S SPLEENHARRY MANDELBAUM, M.D., F.A.C.P., Louis BERGER, M.D., F.A.C.S., MAX LEDERER, M.D., ALBERT EDWARD SOBEL, B.S., CH.E., A.M., PH.D., IRVING ALLAN KAYE, B.A., M.SC.HARRY MANDELBAUM, M.D., F.A.C.P.Search for more papers by this author, Louis BERGER, M.D., F.A.C.S.Search for more papers by this author, MAX LEDERER, M.D.Search for more papers by this author, ALBERT EDWARD SOBEL, B.S., CH.E., A.M., PH.D.Search for more papers by this author, IRVING ALLAN KAYE, B.A., M.SC.Search for more papers by this authorAuthor, Article, and Disclosure Informationhttps://doi.org/10.7326/0003-4819-16-3-438 SectionsAboutPDF ToolsAdd to favoritesDownload CitationsTrack CitationsPermissions ShareFacebookTwitterLinkedInRedditEmail ExcerptPART I. A CASE WITH HEMOLYTIC ANEMIA AND MARKED THROMBOPENIAThe subject of Gaucher's disease continues to occupy a fairly prominent position in the medical literature of recent years. The disease is not rare, although the total number of cases reported is not large. The following case is of special interest, first, because it is another instance of Gaucher's disease recognized in the fifth decade; second, because of the presence of an active hemolytic anemia necessitating recourse to splenectomy. The spleen removed is the second largest ever to be reported, and probably the largest specimen that ever taxed the skill...References PART I PART II1. ANDERSON JP: Hereditary Gaucher's disease, Jr. Am. Med. Assoc., 1933, ci, 979-981. CrossrefGoogle Scholar2. BLOOMGROENPOSTMA TFJC: Gaucher's disease, Quart. Jr. Med., 1936, v, 517-527. Google Scholar3. CAPPEREPSTEINSCHLESS AHRA: Gaucher's disease. Report of a case with presentation of a table differentiating the lipoid disturbances, Am. Jr. Med. Sci., 1934, clxxxviii, 84-92. CrossrefGoogle Scholar4. EAGLE H: Recent advances in the blood coagulation problem, Medicine, 1937, xvi, 95-138. CrossrefGoogle Scholar5. 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(Edin.)Symptomatic and hemopathic hemolytic anemiaThe LipoidosesOsseous Gaucher's diseaseHYPERSPLENISM WITH ARTHRITISGAUCHER'S DISEASE WITHOUT SPLENOMEGALY 1 March 1942Volume 16, Issue 3 Page: 438-450 Keywords Hemolytic anemia Spleen Splenectomy ePublished: 1 December 2008 Issue Published: 1 March 1942 PDF downloadLoading ...