PSEUDOHEMOPHILIA: REPORT OF 13 NEW CASES AND STATISTICAL REVIEW OF PREVIOUSLY REPORTED CASES
Authors: J C BUCHANAN, B S LEAVELL
Journal: Annals of Internal Medicine (1956)

Article1 February 1956PSEUDOHEMOPHILIA: REPORT OF 13 NEW CASES AND STATISTICAL REVIEW OF PREVIOUSLY REPORTED CASESJOHN C. BUCHANAN, M.D., BYRD S. LEAVELL, M.D., F.A.C.P.JOHN C. BUCHANAN, M.D.Search for more papers by this author, BYRD S. LEAVELL, M.D., F.A.C.P.Search for more papers by this authorAuthor, Article, and Disclosure Informationhttps://doi.org/10.7326/0003-4819-44-2-241 SectionsAboutPDF ToolsAdd to favoritesDownload CitationsTrack CitationsPermissions ShareFacebookTwitterLinkedInRedditEmail ExcerptPseudohemophilia is a hemorrhagic disorder which, occurring in either sex, is distinguished essentially by a bleeding tendency and by the single laboratory abnormality of a prolonged bleeding time. The clotting time, platelet count and prothrombin time are normal, and clot retraction is usually normal. The tourniquet test is positive in about half of the patients with this disease. Though often occurring sporadically, pseudohemophilia is familial in a high percentage of cases.Interest in this hemorrhagic diathesis was stimulated a quarter of a century ago by von Willebrand's reports1-3in which he described a bleeding tendency observed in 16 female and...Bibliography1. von Willebrand EA: Hereditäre pseudohemofili, Finska läk.-söllsk. handl. 68: 87, 1926. Google Scholar2. von Willebrand EA: Ueber hereditäre Pseudohämophilie, Acta med. Scandinav. 76: 21, 1931. Google Scholar3. von WillebrandJürgens EAR: Ueber eine neue Bluterkrankheit, die konstitutionelle Thrombopathie, Klin. Wchnschr. 12: 414, 1933. CrossrefGoogle Scholar4. Glanzmann E: Sporadische konstitutionelle Thrombopathie, Schweiz. med. Wchnschr. 76: 1014, 1946. MedlineGoogle Scholar5. Quattrin N: Un nuovo tipo di trombopatia costituzionale? Minerva med. 2: 523, 1946. Google Scholar6. Panoff A: Ueber einen neuen Typus der Thrombopathie, Schweiz. med. Wchnschr. 78: 206, 1948. MedlineGoogle Scholar7. 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SussmanWaldRosenthal LNNRL: A hemorrhagic diathesis due to a qualitative platelet defect, Blood 7: 1100, 1952. CrossrefMedlineGoogle Scholar57. Fonio A: Ueber die Wirkung des Hyalomers der Thrombocyten auf den Retraktionsvorgang, Acta haemat. 8: 363, 1952. CrossrefMedlineGoogle Scholar This content is PDF only. To continue reading please click on the PDF icon. Author, Article, and Disclosure InformationAffiliations: *Received for publication July 12, 1955.From the Department of Internal Medicine, University of Virginia School of Medicine, Charlottesville, Virginia. PreviousarticleNextarticle Advertisement FiguresReferencesRelatedDetails Metrics Cited byAssessing bleeding in von Willebrand disease with bleeding scoreCase Report: Recurrent Hematuria and Hematospermia Due to Prostatic Telangiectasiain Classic von Willebrand’s DiseaseSpontaneous intracranial hemorrhage secondary to von willebrand's diseaseDas v. 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LOSEKE, M.D.“Idiopathic” bematuriaThe problem of haemorrhage during anaesthesia and surgeryPrimary Capillary Haemorrhage (including von Willebrand's Disease)AngiohämophilieInherited Hemorrhagic Disorder with Antihemophilic Globulin Deficiency and Prolonged Bleeding Time (Vascular Hemophilia)BRIDGE ANTICOAGULANT IN VON WILLEBRAND'S SYNDROME�ber Pseudoh�mophilie, Angioh�mophilie, v. Willebrand-J�rgenssche Krankheit und verwandte h�morrhagische DiathesenOn an Inherited Autosomal Hemorrhagic Diathesis with Antihemophilic Globulin (AHG) Deficiency and Prolonged Bleeding Times1Exercise on a PinPSEUDOHÆMOPHILIA 1 February 1956Volume 44, Issue 2Page: 241-256KeywordsHemorrhageHemostaticsPlateletsProthrombin timeResearch laboratories ePublished: 1 December 2008 Issue Published: 1 February 1956 PDF downloadLoading ...