REPORT OF A CASE OF PURPURA ANNULARIS TELANGIECTODES (MAJOCCHI'S DISEASE) AND ITS TREATMENT WITH CORTISONE
Authors: I KASS, P SNEID, M SLAVIN
Journal: Annals of Internal Medicine (1954)

Case Reports1 August 1954REPORT OF A CASE OF PURPURA ANNULARIS TELANGIECTODES (MAJOCCHI'S DISEASE) AND ITS TREATMENT WITH CORTISONEIRVING KASS, M.D., PHILIP SNEID, M.D., MANUEL SLAVIN, M.D.IRVING KASS, M.D.Search for more papers by this author, PHILIP SNEID, M.D.Search for more papers by this author, MANUEL SLAVIN, M.D.Search for more papers by this authorAuthor, Article, and Disclosure Informationhttps://doi.org/10.7326/0003-4819-41-2-349 SectionsAboutPDF ToolsAdd to favoritesDownload CitationsTrack CitationsPermissions ShareFacebookTwitterLinkedInRedditEmail ExcerptIn 1896 Domenico Majocchi1observed the unusual hemorrhagic eruption which now bears his name. He first noted this slowly progressing eruption on the lower part of the legs of a 21 year old man. He called this disorder "purpura annularis telangiectodes." The disorder was characterized by cutaneous hemorrhages or hemorrhagic puncta which coalesced to form purpuric and pigmented macules and rings of 2 to 20 mm. in diameter. These did not fade on pressure. The centers of many of the annular figures were smooth, depigmented and atrophic. Associated with the eruption were rheumatoid pains in the legs. The first record...Bibliography1. Majocchi D: Sopra una dermatosi telangiectode non ancora descritta "purpura annularis," Gior. ital. d. mal. ven. Milano 31: 263-264, 1896. Google Scholar2. Brandweiner A: Purpura annularis telangiectodes, Wien. dermat. Gesellsch. Arch. f. Dermat. u. Syph. 77: 122, 1905. Google Scholar3. MacKee GM: Purpura annularis telangiectodes, J. Cutan. Dis. 33: 129-141 (Feb.); 186-208 (Mar.); 280-311 (Apr.) 1915. Google Scholar4. SulzbergerLeider MBM: A case of diagnosis; angioma serpiginosum (Hutchinson's infectious angioma?) or purpura annularis telangiectodes (Majocchi?), Arch. Dermat. and Syph. 64: 794, 1951. Google Scholar5. Gross P: Purpura annularis telangiectodes? Radiodermatitis? Hemostasis dermatitis? Arch. Dermat. and Syph. 60: 800, 1949. (Part I.) Google Scholar6. 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PreviousarticleNextarticle Advertisement FiguresReferencesRelatedDetails Metrics Cited byAcrally distributed dermatoses: Vascular dermatoses (purpura and vasculitis)WITHDRAWN: ACRALLY DISTRIBUTED DERMATOSES Vascular dermatoses (purpura and vasculitis)Purpura annularis telangiectodes of Majocchi: case report and review of the literature 1 August 1954Volume 41, Issue 2Page: 349-357KeywordsHemorrhageLesionsPainRheumatic pain ePublished: 1 December 2008 Issue Published: 1 August 1954 PDF downloadLoading ...