CONGENITAL CYSTIC DISEASE OF THE LUNG WITH PROGRESSIVE PULMONARY FIBROSIS AND CARCINOMATOSIS
Authors: V A McKUSICK, A M FISHER
Journal: Annals of Internal Medicine (1958)

Article1 April 1958CONGENITAL CYSTIC DISEASE OF THE LUNG WITH PROGRESSIVE PULMONARY FIBROSIS AND CARCINOMATOSISVICTOR A. MCKUSICK, A. MURRAY FISHERVICTOR A. MCKUSICKSearch for more papers by this author, A. MURRAY FISHERSearch for more papers by this authorAuthor, Article, and Disclosure Informationhttps://doi.org/10.7326/0003-4819-48-4-774 SectionsAboutPDF ToolsAdd to favoritesDownload CitationsTrack CitationsPermissions ShareFacebookTwitterLinkedInRedditEmail ExcerptThe subject of this communication is a condition which probably can most appropriately be termed hereditary miliary broncho-alveolar cystic disease. However, because of the cumbersome nature of this designation, the well established terminology congenital cystic disease of the lung has been retained.The purposes of this communication are four: (1) to present evidence supporting the hereditary nature of the disorder; (2) to indicate that clubbed fingers on the basis of this disorder can exist for most of the patient's lifetime—for decades before any clinical evidences of pulmonary disease are detectable; (3) to demonstrate that the clinical picture may be that...Bibliography1. AustrianMcClementRenzettiDonaldRileyCournand RJHADKWRLA: Clinical and physiologic features of some types of pulmonary diseases with impairment of alveolar-capillary diffusion, Am. J. Med. 11: 667, 1951. CrossrefMedlineGoogle Scholar2. BargenSauerSloanGage JAWGWPRP: Development of cancer in chronic ulcerative colitis, Gastroenterology 26: 32, 1954. CrossrefMedlineGoogle Scholar3. 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D., Associate Professor of Medicine, The Johns Hopkins Hospital, Baltimore 5, Maryland. 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CATHCART, M.D.Carcinoma Arising in a Congenital Lung CystThe Differential Diagnosis of Miliary Diseases of the Lungs 1 April 1958Volume 48, Issue 4Page: 774-790KeywordsCarcinomatosisFibrosisGenetic diseasesHospital medicineLungsPulmonary diseasesPulmonary fibrosis ePublished: 1 December 2008 Issue Published: 1 April 1958 PDF downloadLoading ...