A CASE OF CYSTIC FIBROSIS OF THE PANCREAS ASSOCIATED WITH CHRONIC PULMONARY DISEASE AND CIRRHOSIS OF THE LIVER
Authors: H E PUGSLEY, P M SPENCE
Journal: Annals of Internal Medicine (1949)

Case Reports1 June 1949A CASE OF CYSTIC FIBROSIS OF THE PANCREAS ASSOCIATED WITH CHRONIC PULMONARY DISEASE AND CIRRHOSIS OF THE LIVERH. E. PUGSLEY, M.D., P. MCK. SPENCE, M.D.H. E. PUGSLEY, M.D., P. MCK. SPENCE, M.D.Author, Article, and Disclosure Informationhttps://doi.org/10.7326/0003-4819-30-6-1262 SectionsAboutPDF ToolsAdd to favoritesDownload CitationsTrack CitationsPermissions ShareFacebookTwitterLinkedInRedditEmail ExcerptINTRODUCTIONCystic fibrosis of the pancreas is a rare disease of infancy and childhood which usually has a fatal termination within the first two years of life. This case is unusual in that the age at death was 17 years.CASE REPORTA 17 year old boy was admitted to the medical service of the Toronto General Hospital, February 19, 1946, because of increasing shortness of breath, and died on March 30, 1946. His father stated that he had never been a robust child, and that since shortly after birth he had had about five daily bowel movements which were...Bibliography1. ANDERSON DH: Cystic fibrosis of the pancreas, Am. Jr. Dis. Child., 1938, lvi, 344-399. Google Scholar2. FARBER S: Pancreatic function and disease in early life, Arch. Path., 1944, xxxvii, 238-250. Google Scholar3. WIGLESWORTH FW: Fibrocystic disease of the pancreas, Am. Jr. Med. Sci., 1946, ccxii, 351-365. CrossrefGoogle Scholar4. PARMELEE AH: The pathology of steatorrhoea, Am. Jr. Dis. Child., 1935, l, 1418-1428. Google Scholar5. FARBER S: Pancreatic insufficiency and the coeliac syndrome, New Eng. Jr. Med., 1943, ccxxix, 653-657, 682-687. CrossrefGoogle Scholar6. CLARKEHADFIELD CG: Congenital pancreatic disease with infantilism, Quart. Jr. Med., 1923-1924, xvii, 358. Google Scholar7. SNELLINGERB CEIH: Cystic fibrosis of the pancreas, Arch. Dis. Child., 1943, xvii, 220-226. Google Scholar8. ALLANBOWIEMACLEODROBINSON FNJJJJWL: Behaviour of depancreatized dogs kept alive with insulin, Brit. Jr. Exper. Path., 1924, v, 75-83. Google Scholar9. FISCHER NF: Attempts to maintain life of totally pancreatectomized dogs indefinitely by insulin, Am. Jr. Physiol., 1929, lxix, 634-643. Google Scholar10. RALLIRUBINPRESENT EPSHCH: The liver lipids and fecal excretion of fat and nitrogen in dogs with ligated pancreatic ducts, Am. Jr. Physiol., 1938, cxxii, 93-97. Google Scholar11. MONTGOMERYENTENMANCHAIKOFF MLCIL: The liver lipids of dogs subjected to ligation of the external pancreatic ducts, Jr. Biol. Chem., 1939, cxxviii, 387-398. CrossrefGoogle Scholar12. HERSHEY JM: Substitution of lecithine for raw pancreas in the diet of the depancreatized dog, Am. Jr. Physiol., 1930, xciii, 657-658. Google Scholar13. BESTHUNTSMAN CHME: Effects of components of lecithine upon deposition of fat in liver, Jr. Physiol., 1932, lxxv, 405-412. CrossrefGoogle Scholar14. HIMSWORTHGLYNN HPLE: Massive hepatic necrosis and diffuse hepatic fibrosis, Clin. Sci., 1944, v, 93-123. Google Scholar15. CHAIKOFFCONNORBISKIND ILCLGR: Fatty infiltration and cirrhosis of the liver in depancreatized dogs maintained with insulin, Am. Jr. Path., 1938, ci, 101-110. Google Scholar This content is PDF only. To continue reading please click on the PDF icon. Author, Article, and Disclosure InformationAffiliations: Toronto, Ontario,*Received for publication September 15, 1947.From the Departments of Medicine and Pathology, University of Toronto, and the medical service, Toronto General Hospital. PreviousarticleNextarticle Advertisement FiguresReferencesRelatedDetails Metrics Cited byCurrent Treatment Options for Cystic Fibrosis-Related Liver DiseaseCystic fibrosis of the pancreasPortal Hypertension in Fibrocystic Disease of the PancreasDie sogenannte cystische PankreasfibroseFIBROCYSTIC DISEASE OF THE PANCREAS AFTER CHILDHOOD: CASE REPORT WITH NECROPSY AT 17 YEARS*ROBERT C. HENDRIX, M.D., DONALD M. GOOD, M.D.MucoviscidosisRadiological Findings in Congenital Cystic Pancreatic FibrosisCystic Fibrosis of the Pancreas in Patients Over Ten Years of Age�ber die Serumdiastase beim BronchialasthmaDie Krankheiten der BauchspeicheldrüseThe Pancreas: Contributions of Clinical Interest in 1949Incomplete pancreatic deficiency in cystic fibrosis of the pancreas 1 June 1949Volume 30, Issue 6Page: 1262-1272KeywordsBirthCirrhosisCystic fibrosisDyspneaHospital medicineLiver fibrosisMedical servicesPancreasPulmonary diseases ePublished: 1 December 2008 Issue Published: 1 June 1949 PDF downloadLoading ...