IDIOPATHIC RETROPERITONEAL FIBROSIS ASSOCIATED WITH A COAGULATION DEFECT (FACTOR VII DEFICIENCY): REPORT OF A CASE AND REVIEW OF THE LITERATURE
Authors: B I POPHAM, T D STEVENSON
Journal: Annals of Internal Medicine (1960)

Case Reports1 April 1960IDIOPATHIC RETROPERITONEAL FIBROSIS ASSOCIATED WITH A COAGULATION DEFECT (FACTOR VII DEFICIENCY): REPORT OF A CASE AND REVIEW OF THE LITERATUREBERNARD I. POPHAM, M.D., THOMAS D. STEVENSON, M.D.BERNARD I. POPHAM, M.D.Search for more papers by this author, THOMAS D. STEVENSON, M.D.Search for more papers by this authorAuthor, Article, and Disclosure Informationhttps://doi.org/10.7326/0003-4819-52-4-894 SectionsAboutPDF ToolsAdd to favoritesDownload CitationsTrack CitationsPermissions ShareFacebookTwitterLinkedInRedditEmail ExcerptIn 1948 Ormond1described two patients with bilateral hydronephrosis secondary to obstruction of the ureters by retroperitoneal fibrous tissue proliferation of unknown etiology. Since the original description by Ormond, 23 similar cases have been reported in the literature. The clinical manifestations are predominantly the result of ureteral obstruction, with subsequent hydronephrosis and renal infection, or insufficiency due to the involvement of the ureters in the retroperitoneal fibrous tissue reaction. The term "bilateral symmetrical periureteric fibrosis" was used by Raper9in 1955 to describe this syndrome, but subsequently this same author felt that "idiopathic retroperitoneal fibrosis" was a more suitable appellation.10...Bibliography1. Ormond JK: Bilateral ureteral obstruction due to envelopment and compression by an inflammatory retroperitoneal process, J. Urol. 59: 1072, 1948. CrossrefMedlineGoogle Scholar2. EwellBruskewitz GHHW: Bilateral ureteral obstruction due to envelopment and compression by an inflammatory retroperitoneal process, Urol. and Cutan. Rev. 56: 3, 1952. MedlineGoogle Scholar3. OppenheimerNarinoSimon GDLN: Radiotherapy in the treatment of nonspecific inflammatory stricture of the ureter, J. Urol. 67: 476, 1952. CrossrefMedlineGoogle Scholar4. MillerLipinMeiselLong JMRJHJPH: Bilateral ureteral obstruction due to compression by chronic retroperitoneal inflammation, J. Urol. 68: 447, 1952. CrossrefMedlineGoogle Scholar5. MirabileSpillane CSRJ: Bilateral ureteral compression with obstruction from a nonspecific retroperitoneal inflammatory process, J. Urol. 73: 783, 1953. CrossrefGoogle Scholar6. Bradfield EC: Bilateral ureteral obstruction due to envelopment and compression by an inflammatory retroperitoneal process, J. Urol. 69: 769, 1953. CrossrefMedlineGoogle Scholar7. MacLean JT: Unusual conditions of the ureter and kidney, Brit. J. Urol. 26: 127, 1954. CrossrefMedlineGoogle Scholar8. ChisholmHutchBalomey ERJAAA: Bilateral ureteral obstruction due to chronic inflammation of the fascia around the ureters, J. Urol. 72: 812, 1954. CrossrefMedlineGoogle Scholar9. Raper FP: Bilateral symmetrical periureteric fibrosis, Proc. Roy. Soc. Med. 48: 736, 1955. CrossrefMedlineGoogle Scholar10. Raper FP: Idiopathic retroperitoneal fibrosis involving the ureters, Brit. J. Urol. 28: 436, 1956. CrossrefMedlineGoogle Scholar11. Case records of Massachusetts General Hospital (Case 42281), New England J. Med. 255: 90, 1956. MedlineGoogle Scholar12. Case records of Massachusetts General Hospital (Case (43252), New England J. Med. 256: 1198, 1957. MedlineGoogle Scholar13. IozziMurphy LJJ: Bilateral ureteral obstruction by retroperitoneal inflammation, J. Urol. 77: 402, 1957. CrossrefMedlineGoogle Scholar14. TalbotMahoney HSEM: Obstruction of both ureters by retroperitoneal inflammation, J. Urol. 78: 738, 1957. CrossrefMedlineGoogle Scholar15. Trever RW: Reticulum cell sarcoma producing retroperitoneal and periureteric fibrosis, New England J. Med. 258: 268, 1958. CrossrefMedlineGoogle Scholar16. Case records of Massachusetts General Hospital (Case 44101), New England J. Med. 258: 493, 1958. MedlineGoogle Scholar17. Mulvaney WP: Periureteritis obliterans—a retroperitoneal inflammatory disease, J. Urol. 79: 410, 1958. CrossrefMedlineGoogle Scholar18. BiggsMacfarlane RRG: Human blood coagulation and its disorders, 1957, Charles C Thomas, Springfield, Illinois. Google Scholar19. HougieBarrowGraham CEMJB: Stuart clotting defect, J. Clin. Investigation 36: 485, 1957. CrossrefMedlineGoogle Scholar20. Ackroyd JF: The function of Factor VII, Brit. J. Haematol. 2: 397, 1956. CrossrefMedlineGoogle Scholar21. Douglas AS: Mode of action of coumarin drugs, Brit. M. Bull. 11: 39, 1955. CrossrefMedlineGoogle Scholar22. CarterWarner JRED: Correction of defects in clotting accelerator activity by administration of methionine and vitamin K and of a new sulfhydryl-substituted methylnaphthoquinone, vitamin K-S(II), J. Clin. Investigation 37: 70, 1958. CrossrefMedlineGoogle Scholar This content is PDF only. To continue reading please click on the PDF icon. Author, Article, and Disclosure InformationAffiliations: Louisville, Kentucky*Received for publication October 29, 1958.Presented at the Regional Meeting (Kentucky-Tennessee) of the American College of Physicians, Louisville, Kentucky, October 18, 1958.From the Medical Service, Veterans Administration Hospital, Louisville, Kentucky, and the Department of Medicine, University of Louisville School of Medicine.Sponsored by the Veterans Administration and published with the approval of the Chief Medical Director. The statements made and the conclusions drawn by the authors are a result of their own study and do not necessarily reflect the opinion or policy of the Veterans Administration.Requests for reprints should be addressed to Thomas D. Stevenson, M.D., 323 East Chestnut Street, Louisville 2, Kentucky. 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COMINGS, M.D., K. B. SKUBI, M.D., F.A.C.P., J. VAN EYES, PH.D., M.D., ARNO G. MOTULSKY, M.D., F.A.C.P.Digestive SystemIdiopathic Retroperitoneal Fibrosis: Diagnostic Enigma: Report of a Case Simulating Diabetes Insipidus and a Review of the LiteratureRetroperitoneal FibrosisFibrotic Disorders Associated with Methysergide Therapy for HeadacheA Review of Retroperitoneal FibrosisA case of idiopathic retroperitoneal fibrosis presenting as a systemic collagen diseaseLes infections non-spécifiques des voies urinaires supérieures et de la vessieRETROPERITONEAL VASCULITIS WITH PERIVASCULAR FIBROSISSclerosing Hodgkin’s Disease vs. Idiopathic Retroperitoneal FibrosisMedical genetics 1960 1 April 1960Volume 52, Issue 4Page: 894-906KeywordsEtiologyFibrosisHemorrhageHospital medicineMedical servicesUreter ePublished: 1 December 2008 Issue Published: 1 April 1960 PDF downloadLoading ...