Neurofibromatosis type 1 (NF1) is a genetic disorder that increases the risk of developing optic nerve gliomas. NF1 is characterized by the growth of noncancerous tumors along nerves, skin changes, and bone deformities. Children with NF1 are more likely to develop optic nerve gliomas, with up to 15% of these individuals developing the condition. Regular screening and monitoring are crucial for those with NF1 to manage and address optic nerve gliomas early.