French National Registry of Rare Peritoneal Surface Malignancies

Study Overview
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Brief Summary
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Despite advances in the management of and changes in clinical practice, little is known about the epidemiology, patterns of care and outcomes of rare peritoneal surface malignancies patients in France. In order to better understand the characteristics of rare peritoneal surface malignancies and to evaluate treatment strategies, the RENAPE registry aims at the collection of data from patients presenting with a rare peritoneal surface malignancy in France. Data will be entered prospectively in a specifically designed and secured web database. All RENAPE's centres and physicians are invited to register patients with a rare peritoneal surface malignancy diagnosis and to participate to the registry. Data will be evaluated within regular time frames, focusing on types of rare peritoneal surface malignancies, treatment modalities and patient outcomes (e.g. survival, recurrence), thereby contributing to the better understanding of these rare cancers.

Official Title
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French National Registry of Rare Peritoneal Surface Malignancies (RENAPE Registry)

Conditions
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Rare Peritoneal Surface Malignancies, Pseudomyxoma Peritonei, Peritoneal Mesothelioma, Desmoplastic Small Round Cell Tumor, Psammocarcinoma, Primary Peritoneal Serous Carcinoma, Diffuse Peritoneal Leiomyomatosis, Appendiceal Mucinous Neoplasms

Intervention / Treatment
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* Other: Non interventional


Participation Criteria
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Eligibility Criteria
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Inclusion Criteria: Patients are eligible if they have a histologically proven rare peritoneal surface malignancy. Exclusion Criteria: Histological diagnostic of peritoneal surface malignancy not confirmed Expected clinical follow up data not available
Sexes Eligible for Study
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All

Accepts Healthy Volunteers
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No

Study Plan
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How is the study designed?
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Arms and Interventions

| Participant Group/Arm | Intervention/Treatment |
| --- | --- |
| pseudomyxoma peritonei<br>Data from pseudomyxoma peritonei cases will be used to generate descriptive statistics on demographics, clinical characteristics including prevalence and incidence of co-morbidities, treatment patterns, and patient outcomes (resulting from treatment or disease). | Other: Non interventional<br>* Data collection<br>|
| peritoneal mesothelioma<br>Data from peritoneal mesothelioma cases will be used to generate descriptive statistics on demographics, clinical characteristics including prevalence and incidence of co-morbidities, treatment patterns, and patient outcomes (resulting from treatment or disease). | Other: Non interventional<br>* Data collection<br>|
| desmoplastic small round cell tumor<br>Data from desmoplastic small round cell tumor cases will be used to generate descriptive statistics on demographics, clinical characteristics including prevalence and incidence of co-morbidities, treatment patterns, and patient outcomes (resulting from treatment or disease). | Other: Non interventional<br>* Data collection<br>|
| psammocarcinoma<br>Data from primary peritoneal serous carcinoma cases will be used to generate descriptive statistics on demographics, clinical characteristics including prevalence and incidence of co-morbidities, treatment patterns, and patient outcomes (resulting from treatment or disease). | Other: Non interventional<br>* Data collection<br>|
| primary peritoneal serous carcinoma<br>Data from primary peritoneal serous carcinoma cases will be used to generate descriptive statistics on demographics, clinical characteristics including prevalence and incidence of co-morbidities, treatment patterns, and patient outcomes (resulting from treatment or disease). | Other: Non interventional<br>* Data collection<br>|
| diffuse peritoneal leiomyomatosis<br>Data from diffuse peritoneal leiomyomatosis cases will be used to generate descriptive statistics on demographics, clinical characteristics including prevalence and incidence of co-morbidities, treatment patterns, and patient outcomes (resulting from treatment or disease). | Other: Non interventional<br>* Data collection<br>|
| appendiceal mucinous neoplasms<br>Data from appendiceal mucinous neoplasms cases will be used to generate descriptive statistics on demographics, clinical characteristics including prevalence and incidence of co-morbidities, treatment patterns, and patient outcomes (resulting from treatment or disease). | Other: Non interventional<br>* Data collection<br>|

What is the study measuring?
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Primary Outcome Measures

| Outcome Measure | Measure Description | Time Frame |
| --- | --- | --- |
| Incidence of rare peritoneal surface malignancies | Collect detailed clinical and histological diagnosis for estimating annual incidence rate | year 5 | 

Secondary Outcome Measures

| Outcome Measure | Measure Description | Time Frame |
| --- | --- | --- |
| Impact of specific treatment strategies | Collect detailed therapeutic strategies (surgical procedure, chemotherapy, etc.) on patients with rare peritoneal surface malignancies | year 5 | 

 Terms related to the study
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Keywords Provided by Centre Hospitalier Valida
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Rare peritoneal surface malignancies, pseudomyxoma peritonei, peritoneal mesothelioma, desmoplastic small round cell tumor, psammocarcinoma, primary peritoneal serous carcinoma, diffuse peritoneal leiomyomatosis, appendiceal mucinous neoplasms, registry, population-based database