Document:

Exhibit 10.2

   

  Execution Version

   

  RESTRUCTURING SUPPORT AGREEMENT

   

  This Restructuring Support Agreement (as amended, restated, supplemented or otherwise modified from time to time in
    accordance with the terms set forth herein, this “Agreement”), dated as of May 20, 2019, is made by
    and among: (a) Aegerion Pharmaceuticals, Inc. (“Aegerion”) and each of its subsidiaries that are
    party hereto (collectively with Aegerion, the “Company”); (b) each of the undersigned holders
    (each, a “Consenting Lender” and, collectively, the “Consenting Lenders”, including any holders that execute a Lender Joinder (as defined below) after the date hereof) of claims (as
    defined in section 101(5) of title 11 of the United States Code (the “Bankruptcy Code”)) against the Company (the “Claims”) arising under or in connection with: (i) that certain Indenture, dated as of August 15, 2014 (as amended,
    supplemented or otherwise modified prior to the date hereof, the “Convertible Notes Indenture” and a holder of such Claims, the “Consenting Noteholders”), (ii) that certain Bridge Credit
    Agreement, dated as of November 8, 2018 (as amended, supplemented or otherwise modified prior to the date hereof, the “Bridge Credit Agreement” and a holder of such Claims, the “Consenting Bridge Lenders”), and/or (iii) that certain Amended and Restated Loan and Security Agreement, dated as of March 15, 2018 (as amended, restated,
    supplemented or otherwise modified from time to time prior to the date hereof, the “Intercompany Credit Agreement” and the holder of such Claims, presently Novelion Therapeutics Inc. (“Novelion Therapeutics”) or a wholly-owned direct or indirect subsidiary thereof (excluding Aegerion and its subsidiaries, and including Novelion Services
    USA, Inc. (“Novelion Services”), and collectively, “Novelion”)1, in its capacity as such and as a holder of other
    Claims against and equity interests in the Company (including Claims in connection with the Amended Shared Services Agreements (as defined below)), and the Intercompany Credit Agreement, together with the Convertible Notes Indenture and the Bridge
    Credit Agreement, and their respective ancillary and related documents, the “Credit Documents”);
    and (c) Amryt Pharma plc (the “Plan Investor” and collectively with the Consenting Lenders, the “Plan

      Support Parties”). The Company and each of the Plan Support Parties are each referred to herein as a “Party”, and collectively, as the “Parties”. Each of the Consenting Noteholders, the
    Consenting Bridge Lenders and Novelion, as applicable, are referred to herein as a “Consenting Class.” Capitalized terms used but not otherwise defined herein have the meanings ascribed to such terms in the Plan (as defined below).

   

  RECITALS

   

  WHEREAS, the Company has determined that it would be in its best
    interests to implement a restructuring of its indebtedness and other obligations through the prosecution of “pre-negotiated” chapter 11 cases (the “Bankruptcy Cases”) in the United States Bankruptcy Court for the Southern District of New York
    (the “Bankruptcy Court”);

   

  WHEREAS, the Parties have agreed that, in connection with the
    restructuring of the Company, the Plan Investor will acquire 100% of the equity of reorganized Aegerion in exchange for equity of the Plan Investor as set forth in, and the Parties shall otherwise consummate the transactions contemplated by, the Plan
    Funding Agreement (as defined below) and related documents, including the Plan (as defined below) and the other Definitive Documentation (as

  

   

  
  

  
  

  1 For purposes of this Agreement, Novelion shall not be deemed
    to be an Affiliate of Aegerion and Aegerion shall not be deemed to be an Affiliate of Novelion.

   

  
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  defined below) (collectively, the “Transaction”), on the terms and subject to the conditions set forth in the Plan Funding Agreement;

   

  WHEREAS, the Parties have agreed on the terms of the Transaction, which are memorialized in this Agreement and: (a)
    the proposed chapter 11 plan for the Company, substantially in the form attached hereto as Exhibit A (as may be amended, modified, or supplemented from time to time, including any schedules and exhibits attached thereto, in each case, in
    accordance with the terms hereof, the “Plan”); and (b) the Plan Funding Agreement between the Company and the Plan Investor, attached hereto as Exhibit B (as the same may be amended, modified, or supplemented from time to time, in
    accordance with the terms hereof, the “Plan Funding Agreement”), and executed concurrently
    herewith; and

   

  WHEREAS, subject to the terms hereof and, as required, appropriate approvals of the Bankruptcy Court, the following
    sets forth the agreement between the Parties concerning their respective obligations in connection with the Transaction and the Bankruptcy Cases.

   

  NOW, THEREFORE, in consideration of the foregoing, the Parties agree as follows:

   

  AGREEMENT

   

  Section 1.         Chapter 11 Plan and Definitive Documentation.

   

  		1.1	Support of Plan and Definitive Documentation.

   

  		(a)	Subject to the terms of this Agreement, including the terms set forth in the immediately following sentence, so long as the Termination Date (as defined below) has not
          occurred, the Company agrees to: (i) use reasonable best efforts to take any actions, and do or cause to be done all things, necessary, appropriate or advisable in furtherance of the Transaction and the consummation thereof as promptly as
          practicable (and, in any event, within the time frames contemplated by this Agreement); (ii) commence the Bankruptcy Cases and file and seek approval on an interim and final (to the extent applicable) basis of “first day” motions (including (x) a
          motion seeking approval of a postpetition credit facility (the “DIP Facility” or the “DIP
            Credit Agreement”), substantially in the form attached hereto as Exhibit C) as may be
          amended, modified, or supplemented from time to time in accordance with the terms hereof, as well as the other Loan Documents (as defined in the DIP Credit Agreement, (y) a motion seeking
            approval of the Company’s assumption of (A) that certain Master Service Agreement dated as of December 1, 2016, but effective as of November 29, 2016, between Novelion Therapeutics and Aegerion and (B) that certain Master Service Agreement
            dated as of December 1, 2016, but effective as of November 29, 2016, between Novelion Services and Aegerion, each as amended by that certain Amendment to Shared Services Agreements dated as of May 20, 2019, between Novelion Therapeutics,
            Novelion Services and Aegerion (collectively, the “Amended Shared Services Agreements”) and
            (z) a motion (the “PFA Approval Motion”) seeking approval of the PFA Order (as defined below)) and with respect to all other “first day” motions, in the forms of the most recent drafts distributed in writing to the Plan Support Parties
            prior to the execution and delivery of this Agreement, as the same may be amended, modified or supplemented from time to time in accordance with the terms

   

  
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  hereof (all such “first day” motions, collectively, the “First Day Motions”)); (iii) file the Plan and a related disclosure statement (as may be amended, modified or supplemented from time to time in accordance with the
    terms hereof, the “Disclosure Statement”), substantially in the form annexed hereto as Exhibit
      D, with the Bankruptcy Court and seek approval of the Disclosure Statement and confirmation of the Plan pursuant to the Confirmation Order (as defined below); (iv) act in good faith and use reasonable best efforts to support and complete
    successfully the solicitation of votes in favor of the Plan in accordance with the terms of this Agreement; (v) furnish any information reasonably requested by the Plan Investor (in the form and substance so requested) in connection with any
    application, notification or other document filed by or on behalf of the Plan Investor in connection with the Transaction, which information shall not contain any untrue statement of material fact or omit to state any material fact required to be
    stated therein or necessary in order to make the statements therein, in light of the circumstances under which they are made, not misleading and (vi) use reasonable best efforts to obtain any and all regulatory approvals and third-party approvals
    required, or otherwise reasonably requested by, any of the Plan Support Parties, to consummate or make effective the Transaction. Notwithstanding anything contained herein to the contrary, the Company is expressly permitted to take any and all actions
    contemplated by Sections 6.9 of the Plan Funding Agreement (such Sections of the Plan Funding Agreement and the actions contemplated thereby are sometimes referred to herein as the “Permitted Solicitation Activities”) and, so long as such actions are taken in accordance with the terms set forth therein, the Company shall not be deemed to be in
    breach of the terms set forth herein.

   

  		(b)	Subject to the terms of this Agreement, so long as the Termination Date has not occurred, each Consenting Lender hereby agrees that it shall: (i) subject to the receipt by
          such Consenting Lender of the Disclosure Statement and Solicitation Materials (as defined below) approved by the Bankruptcy Court, and subject to the acknowledgements set forth in Section 8 of this Agreement, timely vote its Claims, now or
          hereafter beneficially owned by such Consenting Lender or for which the Consenting Lender now or hereafter serves as the nominee, investment manager or advisor for beneficial holders or over which it otherwise has voting power, to accept the Plan
          and otherwise in support and favor of the Transaction; provided that such vote shall be immediately revoked and deemed void ab initio upon termination of this Agreement as to such Consenting Lender prior to the confirmation of the Plan
          pursuant to the terms hereof; (ii) not change or withdraw (or cause to be changed or withdrawn) any such vote, subject to the proviso in the immediately preceding clause (i) of this Section 1.1(b); (iii) not, directly or indirectly, (x) object
          to, delay, impede or take any other action to interfere with acceptance, approval, confirmation or implementation of the Plan or the Transaction (or support any other person’s efforts to do any of the foregoing), (y) except as to Novelion at the
          request of the Company in connection with Permitted Solicitation Activities, (A) initiate, solicit, encourage or facilitate any inquiries, proposals or offers from any Person other than the Plan Investor and its Affiliates (as defined in the Plan
          Funding Agreement) and its and their respective advisors, consultants, legal counsel, investment bankers, agents and other representatives (with respect to any Person, the “Representatives” thereof) that are providing services in
          connection with the Transaction, relating to,

   

  
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  or that could reasonably result in, alone or together with any other related transactions, any merger, acquisition,
    exchange, divestiture, sale of material assets or equity, business combination, recapitalization, joint venture, or other transaction directly or indirectly involving the equity, voting power or all or a material portion of the assets of Novelion or
    the Company or any of their respective subsidiaries, or any other similar transaction that would serve as an alternative to the Transaction or could reasonably be expected to impede, interfere with, prevent or delay the consummation of the Transaction
    or otherwise dilute in any material respect the benefits reasonably expected by the Plan Support Parties (any such transaction, an “Alternative Transaction”); (B) participate in discussions or negotiations with any Person regarding Novelion or
    the Company or any of their respective subsidiaries, the Plan, or the Transaction with respect to, or that would reasonably be expected to result in, an Alternative Transaction; or (C) propose, support, solicit, encourage, or participate in the
    formulation of any chapter 11 plan or any other restructuring or reorganization of the Company in the Bankruptcy Cases other than the Plan, or (z) otherwise take any action that would in any material respect interfere with, delay or postpone the
    consummation of the Transaction or otherwise dilute in any material respect the benefits reasonably expected by the Plan Support Parties; (iv) use its reasonable best efforts to take any and all necessary, appropriate or advisable actions in
    furtherance of the Transaction and the consummation thereof as promptly as practicable (and, in any event, within the time frames contemplated by this Agreement), including supporting the confirmation of the Plan and entry of the Confirmation Order;
    and supporting (and not objecting to) the First Day Motions; and (v) use reasonable best efforts to obtain any and all regulatory approvals and third-party approvals required, or otherwise reasonably requested, by the Company or any of the Plan Support
    Parties, to consummate or make effective the Transaction.

   

  		(c)	Each Consenting Lender hereby agrees that, (i) so long as the Termination Date has not occurred and (ii) in the event the Termination Date occurs pursuant to (x) Section
          2.2(a) of this Agreement, (y) Sections 2.2(c), 2.2(g) or 2.2(h) of this Agreement on or after the date the Company receives any solicited or unsolicited bona fide Company Alternative Proposal (as defined in the Plan Funding Agreement)
          that has not been withdrawn or terminated or (z) as elected by any Consenting Lender pursuant to Section 2.1 of this Agreement (other than Sections 2.1(k), 2.1(p) or 2.1(q) of this Agreement) on or after the date the Company receives any
          solicited or unsolicited bona fide Company Alternative Proposal that has not been withdrawn or terminated, each Consenting Lender shall vote against any Alternative Transaction, Company Alternative Transaction or Company Alternative
          Proposal, and any plan of reorganization that supports any of the foregoing, in the Bankruptcy Court and use reasonable best efforts to oppose the Bankruptcy Court’s approval of any such Alternative Transaction, Company Alternative Transaction or
          Company Alternative Proposal; provided, however, the foregoing obligation in the case of clause (ii) above shall lapse if, following inquiry in writing by the Consenting Lenders regarding whether the Plan Investor continues to be willing to
          consummate the Transaction in accordance with the Definitive Documentation, the Plan Investor does not agree within five (5) business days following the inquiry (subject to withdrawal at any time upon five (5) business

   

  
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  days’ notice) that it would be willing to re-execute and deliver the Definitive Documents promptly after the other parties
    thereto re-execute and deliver same and consummate the Transaction in accordance with the Definitive Documentation if re-executed by the parties thereto. Notwithstanding anything to the contrary herein or in the Plan Funding Agreement, each Consenting
    Lender’s obligations under this Section 1.1(c) shall survive the Termination Date and shall remain in full force and effect until the earlier of the consummation of the Plan, any Alternative Transaction or Company Alternative Transaction.

   

  		(d)	So long as the Termination Date has not occurred, the Plan Investor hereby agrees that it shall, and shall cause its Affiliates to, comply with the terms set forth in the
          Plan Funding Agreement until the closing of the Transaction contemplated thereby.

   

  		(e)	The Backstop Parties hereby agree to backstop the Rights Offering and in connection therewith to execute the Backstop Commitment Agreement on or prior to the date of entry
          of the Disclosure Statement Order in substantially the form attached to Exhibit E hereto.

   

  		(f)	Without limiting any other provision hereof, until the Termination Date, the Company and each of the Plan Support Parties hereby agrees to use reasonable best efforts to
          negotiate in good faith each of the definitive agreements and documents referenced in, or reasonably necessary to effectuate, the Transaction, this Agreement and the Plan, which shall consist of, among other things: (i) all amendments, exhibits
          and supplements to the Plan and to the Disclosure Statement; (ii) the PFA Order and the Rights Offering procedures and agreements; (iii) the solicitation materials in respect of the Plan (such materials, collectively, the “Solicitation
            Materials”), and the order to be entered by the Bankruptcy Court approving the Disclosure Statement and Solicitation Materials as containing, among other things, “adequate information” as required by section 1125 of the Bankruptcy Code (the
          “Disclosure Statement Order”); (iv) the order to be entered by the Bankruptcy Court confirming the Plan (the “Confirmation Order”) and pleadings in support of entry of the Confirmation Order; (v) the Interim CC Order (as defined
          below) and the Final DIP Order (as defined below) to the extent not attached as exhibits to the DIP Credit Agreement; (vi) the Amended Shared Services Agreements; and (vii) such other documents, pleadings, agreements or supplements as may be
          reasonably necessary to implement the Transaction, including, but not limited to, the new convertible notes indenture and the credit agreement for the new first lien secured credit facility in accordance with the term sheets attached hereto as Exhibits

            F and G, respectively (collectively, as may be amended, modified or supplemented from
          time to time, (and together with the Plan, the Disclosure Statement and any other definitive agreements and documents attached as exhibits hereto, the “Definitive Documentation”)), which Definitive Documentation shall be in form and
          substance consistent with the terms hereof and otherwise reasonably satisfactory to the Company and each of the Required Parties (as defined below). For the avoidance of doubt, any references herein to any document constituting Definitive
          Documentation (including, without limitation, the Plan, the Disclosure Statement, the Solicitation Materials, the Disclosure Statement Order and the Confirmation Order) shall mean such document in form and

   

  
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  substance consistent with the terms hereof and otherwise reasonably satisfactory to the Company and each of the Required
    Parties.

   

  		(g)	Subject to the terms of this Agreement, so long as the Termination Date has not occurred, the Company and each Consenting Lender hereby agrees not to: (i) file any motion,
          application, adversary proceeding or cause of action (A) challenging the validity, enforceability, perfection or priority of, or seeking avoidance or subordination of any Claims (in any capacity) of a Consenting Lender or the liens securing such
          Claims, or (B) otherwise seeking to impose liability upon or enjoin a Consenting Lender (in any capacity); or (ii) support any motion, application, adversary proceeding or cause of action referred to in the immediately preceding clause (i) filed
          by a third party, or consent to the standing of any such third party to bring such motion, application, adversary proceeding or cause of action.

   

  For the avoidance of doubt, each of the Consenting Lenders, the Plan Investor and the Company also agrees, severally with
    respect to itself and not jointly, that, unless this Agreement is terminated in accordance with the terms hereof and subject to the Permitted Solicitation Activities and the right of each of the Plan Support Parties to take any action as may be set
    forth in this Agreement, the Plan Funding Agreement (including the actions contemplated by Section 6.9 of the Plan Funding Agreement in accordance with the terms set forth therein) or any other Definitive Documentation, it shall take such steps as are
    reasonably necessary to support, achieve approval of and consummate the Transaction on the terms set forth in this Agreement, the Plan Funding Agreement and the other Definitive Documentation and it will not take any action that would be expected to,
    in any material respect, interfere with, delay, or postpone the effectuation of the Transaction.

   

  		(h)	As used herein, the following terms shall have the following meanings: “Required Consenting Lenders” shall mean, as of the applicable date of determination, (i) the Consenting Lenders that own at least 50.1% of principal indebtedness outstanding (“Obligations”)

          and held by all Consenting Lenders party hereto under the Convertible Notes Indenture, (ii) Consenting Lenders that own at least 66.7% of the Obligations held by all Consenting Lenders party hereto under the Bridge Credit Agreement, and (iii)
          Consenting Lenders that own at least 50.1% of the Obligations held by all Consenting Lenders party hereto under the Intercompany Credit Agreement. “Required Consenting Bridge Lenders/Noteholders” shall mean (i) the Consenting Lenders that
          own at least 50.1% of the Obligations held by all Consenting Lenders party hereto under the Convertible Notes Indenture, and (ii) Consenting Lenders that own at least 66.7% of the Obligations held by all Consenting Lenders party hereto under the
          Bridge Credit Agreement. “Required Consenting Intercompany Lenders” shall mean Consenting
          Lenders that own at least 50.1% of the Obligations held by all Consenting Lenders party hereto under the Intercompany Credit Agreement.

   

  Section 2.         Termination Events.

   

  		2.1	Plan Support Party Termination Events.

   

  Subject to the terms set forth in Section 2.5, the occurrence of any of the following shall be a “Plan Support Party
      Termination Event”:

   

  
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  		(a)	11:59 p.m. (prevailing Eastern Time) on the date that is one (1) business day after the date hereof unless prior thereto the Bankruptcy Cases have commenced in the
          Bankruptcy Court (the “Petition Date”);

   

  		(b)	solely in the case of the Plan Investor, one (1) business day after the Petition Date, unless prior thereto the Company has filed the PFA Approval Motion;

   

  		(c)	three (3) business days after the Petition Date, unless prior thereto the Bankruptcy Court has entered an order on an interim basis authorizing the Company to use cash
          collateral (the “Interim CC Order”);

   

  		(d)	solely in the case of the Plan Investor, twenty-one (21) calendar days after the Petition Date (subject to a seven (7) day extension if the Bankruptcy Court so requires),
          unless prior thereto the Bankruptcy Court has entered an order approving the PFA Approval Motion (the “PFA Order”);

   

  		(e)	solely in the case of Novelion, if the Company defaults in its payment obligations under the Amended Shared Services Agreements, and such default remains uncured after the
          running of any applicable cure period, or has filed a motion to reject the Amended Shared Services Agreements;

   

  		(f)	thirty-five (35) calendar days after the Petition Date, unless prior thereto the Bankruptcy Court has entered an order on a final basis authorizing the
          Company to enter into the DIP Facility (the “Final DIP Order”);

   

  		(g)	sixty (60) calendar days after the Petition Date, unless prior thereto the Bankruptcy Court has entered an order approving (i) the Disclosure Statement and authorizing the
          solicitation of votes on the Plan and (ii) the procedures with respect to the Rights Offering;

   

  		(h)	one hundred twenty (120) calendar days after the Petition Date, unless prior thereto the Bankruptcy Court has entered the Confirmation Order;

   

  		(i)	the Outside Date (as defined in the Plan Funding Agreement in the form attached as Exhibit B to this Agreement on the Petition Date), as extended pursuant to the definition
          thereof in the Plan Funding Agreement (in the form attached as Exhibit B to this Agreement on the Petition Date), unless prior thereto the effective date for the Plan has occurred;

   

  		(j)	the occurrence of (A) any material breach by the Company of any of the undertakings or covenants of the Company set forth in this Agreement, or (B) any
          breach of any representation or warranty of the Company set forth in this Agreement unless the breach of such representation or warranty does not, and would not, reasonably be expected to, individually or together with any other uncured breaches,
          result in a Company Material Adverse Effect (as defined in the Plan Funding Agreement), unless, in each case, such breach is cured or waived by the Plan Support Parties within thirty (30) days after written notice of such breach is provided to
          the Company by any Party in accordance with the terms hereof;

   

  

   

  
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  		(k)	solely in the case of the Consenting Lenders, the occurrence of any material breach by the Plan Investor of any of the undertakings or covenants, representations, or
          warranties of the Plan Investor set forth in this Agreement, unless, in each case, such breach is cured by the Plan Investor or waived by the Required Consenting Lenders within three (3) days after written notice of such breach is provided to the
          Plan Investor in accordance with the terms hereof;

   

  		(l)	solely in the case of the Plan Investor, the occurrence of any material breach by any Consenting Lender of any of the undertakings or covenants, representations, or
          warranties of any Consenting Lender set forth in this Agreement, unless, in each case, such breach is cured by such Consenting Lender or waived by the Plan Investor within three (3) days after written notice of such breach is provided to such
          Consenting Lender in accordance with the terms hereof; provided, however, that, with respect to any termination as a result of a breach by a Consenting Lender as herein provided, the Plan Support Party Termination Event arising as
          a result of such breach shall apply only to the breaching Consenting Lender (at which point, for purposes of Section 2.1(v), such breaching Consenting Lender shall cease to be deemed a Consenting Lender hereunder) and this Agreement shall
          otherwise remain in full force and effect with respect to the Company and all other remaining Parties without limiting the terms set forth in Section 2.1(v);

   

  		(m)	the filing of any pleading by the Company in the Bankruptcy Cases without the prior written consent of each of the Required Parties, that seeks to amend or modify this
          Agreement, the DIP Facility, the Backstop Commitment Agreement, the Rights Offering procedures, the Plan, the Disclosure Statement, the Plan Funding Agreement or any of the Definitive Documentation, which amendment, modification or filing is (i)
          materially inconsistent with this Agreement, the Plan, the Plan Funding Agreement and/or the Definitive Documentation, as applicable, and (ii) materially adverse to the applicable Plan Support Party(ies); and such motion or pleading has not been
          withdrawn prior to three (3) business days after the Company receives written notice from the Required Consenting Bridge Lenders/Noteholders or the Required Consenting Intercompany Lenders or the Plan Investor that such motion or pleading is (x)
          materially inconsistent with this Agreement, the Plan, the Plan Funding Agreement and/or the Definitive Documentation, and (y) materially adverse to such Plan Support Party; provided, that nothing contained in this subsection shall limit the Company’s ability to conduct the Permitted Solicitation Activities pursuant to the Plan
          Funding Agreement;

   

  		(n)	the Company (i) withdraws the Plan, (ii) files, propounds or otherwise supports any plan of reorganization other than the Plan, or (iii) publicly announces its intention to
          do either of (i) or (ii); provided that nothing contained in this subsection shall limit the Company’s ability to conduct the Permitted Solicitation Activities pursuant to the Plan Funding Agreement;

   

  		(o)	the Company files with the Bankruptcy Court any motion or application seeking authority to sell any material assets thereof without the prior written
          consent of the Required Parties;

   

   

  
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  		(p)	any court of competent jurisdiction or other competent governmental or regulatory authority issues a final, non-appealable law or order, making illegal or otherwise
          preventing or prohibiting the consummation of the Transaction;

   

  		(q)	any of the Bankruptcy Cases shall be dismissed or converted to a chapter 7 case, or a chapter 11 trustee with plenary powers, or a responsible officer or an examiner with
          enlarged powers relating to the operation of the businesses of the Company (powers beyond those set forth in section 1106(a)(3) and (4) of the Bankruptcy Code) shall be appointed in any of the Bankruptcy Cases or the Company shall file a motion
          or other request for such relief;

   

  		(r)	the DIP Facility is terminated in accordance with the terms of the Final DIP Order or the Company’s right to use cash collateral is terminated in accordance with the terms
          of the Interim CC Order, the Final DIP Order or any separate cash collateral order that may have been entered in the Bankruptcy Cases;

   

  		(s)	the Bankruptcy Court shall enter an order terminating, annulling, modifying or conditioning the automatic stay with respect to any material assets of the Company that would
          be reasonably likely to have a Company Material Adverse Effect (as defined in the Plan Funding Agreement), without the prior written consent of the Required Parties;

   

  		(t)	the termination of the Plan Funding Agreement in accordance with the terms thereof;

   

  		(u)	any of the orders of the Bankruptcy Court approving this Agreement, the DIP Facility (including the use of cash collateral), the Rights Offering procedures, the Plan
          Funding Agreement, the Plan or the Disclosure Statement, or the PFA Order, Confirmation Order or the Disclosure Statement Order or any other Definitive Documentation are reversed, vacated or otherwise materially modified in a manner inconsistent
          with this Agreement, the Plan Funding Agreement or the Plan and materially adverse to any of the Plan Support Parties without the written consent of the Plan Investor and written consent of the Required Consenting Bridge Lenders/Noteholders (to
          the extent Novelion is not materially adversely affected thereby), Novelion (to the extent Novelion but not any of the Consenting Bridge Lenders or Consenting Noteholders is materially adversely affected thereby) or the Required Consenting
          Lenders (if Novelion and other Consenting Lenders are materially adversely affected thereby), unless the Company promptly thereafter files a motion for reconsideration, reargument or rehearing and such reversal, vacation or other material
          modification is rescinded within thirty (30) days after the filing thereof;

   

  		(v)	the Consenting Lenders at any time own less than 66.67% of the Obligations under each of the Convertible Notes Indenture, the Bridge Credit Agreement and the Intercompany
          Credit Agreement; provided that (i) no such Consenting Lender shall have the right to terminate this Agreement pursuant to this clause (v), and (ii) if any time the Consenting Lenders do not satisfy the foregoing threshold, then a Plan
          Support Party Termination Event shall not be deemed to have occurred under this clause (v) until the date that is fifteen (15) days following the date that such

   

  
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  threshold shall have ceased to be satisfied, it being agreed that if the failure to satisfy such threshold shall have been
    cured (including by joining additional Consenting Lenders to this Agreement) on or prior to the expiration of such fifteen (15) days period, then a Plan Support Party Termination Event shall not be deemed to have occurred pursuant to this clause (v);
    and

   

  		(w)	the Company loses the exclusive right to file and solicit acceptances of a chapter 11 plan; and

   

  		(x)	(i) the Company or any Consenting Lender files any motion, application, adversary proceeding or cause of action (A) challenging the validity, enforceability, perfection or
          priority of, or seeking avoidance or subordination of any Claims (in any capacity) of a Consenting Lender or the liens securing such Claims, or (B) otherwise seeking to impose liability upon or enjoin a Consenting Lender (in any capacity); or
          (ii) the Company or any Consenting Lender supports any motion, application, adversary proceeding or cause of action referred to in the immediately preceding clause (i) filed by a third party, or consents to the standing of any such third party to
          bring such motion, application, adversary proceeding or cause of action.

   

  		2.2	Company Termination Events.

   

  Subject to the terms set forth in Section 2.5, the occurrence of any of the following shall be a “Company Termination
      Event” and together with any Plan Support Party Termination Event, a “Termination Event”:

   

  		(a)	the Company shall be entitled to terminate the Plan Funding Agreement pursuant to Section 8.1(b)(iii) thereof, subject to the terms and limitations thereof;

   

  		(b)	the occurrence of (i) any material breach by the Plan Investor of any of the material undertakings or material covenants of the Plan Investor set forth in this Agreement,
          or (ii) any breach of any representation or warranty of the Plan Investor set forth in this Agreement unless the breach of such representation or warranty would not, individually or in the aggregate, reasonably be expected to have a Plan Investor
          Material Adverse Effect (as defined in the Plan Funding Agreement), unless, in each case, such breach is cured or waived within thirty (30) days after written notice of such breach is provided to the Plan Investor in accordance with the terms
          hereof.

   

  		(c)	the occurrence of (i) any material breach by any Consenting Lender of any of the material undertakings or material covenants of such Consenting Lender set forth in this
          Agreement, or (ii) any breach of any representation or warranty of any Consenting Lender set forth in this Agreement unless the breach of such representation or warranty would not, individually or in the aggregate, reasonably be expected to have
          a material adverse effect on the ability of such Consenting Lender to consummate the Transaction as herein provided, unless, in each case, such breach is cured or waived within thirty (30) days after written notice of such breach is provided to
          such Consenting Lender in accordance with the terms hereof; provided, however, that, with respect to any termination as a result of a breach by a Consenting Lender as herein provided, the Company Termination Event arising

   

  
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  as a result of such breach shall apply only to the breaching Consenting Lender and this Agreement shall otherwise remain in
    full force and effect with respect to the Company and all other remaining Parties, without limiting the terms set forth in the immediately following clause (d);

   

  		(d)	the Consenting Lenders at any time own less than 66.67% of the Obligations under each of the Convertible Notes Indenture, the Bridge Credit Agreement and the Intercompany
          Credit Agreement, provided that if any time the Consenting Lenders do not satisfy the foregoing threshold, then a Company Termination Event shall not be deemed to have occurred under this clause (d) until the date that is thirty (30) days
          following the date that such threshold shall have ceased to be satisfied, it being agreed that if the failure to satisfy such threshold shall have been cured (including by joining additional Consenting Lenders to this Agreement) on or prior to
          the expiration of such thirty (30) days period, then a Company Termination Event shall not be deemed to have occurred pursuant to this clause (d);

   

  		(e)	any court of competent jurisdiction or other competent governmental or regulatory authority issues a final, non-appealable law or order, making illegal or otherwise
          preventing or prohibiting the consummation of the Transaction;

   

  		(f)	any of the Bankruptcy Cases shall be dismissed or converted to chapter 7;

   

  		(g)	the termination of the Plan Funding Agreement in accordance with the provisions thereof; and

   

  		(h)	the Outside Date (as defined in the Plan Funding Agreement in the form attached as Exhibit B to this Agreement on the Petition Date), as extended pursuant to the definition
          thereof in the Plan Funding Agreement (in the form attached as Exhibit B to this Agreement on the Petition Date), unless prior thereto the effective date for the Plan has occurred.

   

  Notwithstanding the foregoing, any of the dates or deadlines set forth in Sections 2.1-2.2 of this Agreement may be
    extended by the written agreement of each of the Company and the Required Parties.

   

  		2.3	Company Termination Event Procedures.

   

  Subject to the terms set forth in Section 2.5 and Section 2.7, upon the occurrence of any Company Termination Event, the
    Company may elect to terminate this Agreement by delivering written notice thereof to the other Parties; provided that if the Company exercises such right only in respect of one or more Consenting Lenders as contemplated by Section 2.2(c),
    then, subject to the terms set forth in Section 2.2(c), 2.2(d) and Section 2.7, this Agreement shall terminate only in respect of such Consenting Lender or Consenting Lenders (the date of the effectiveness of such termination, the “Company
      Termination Date”) and such Consenting Lender or Consenting Lenders shall cease to be deemed a Consenting Lender hereunder from and after such date.

   

  
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  		2.4	Plan Support Party Termination Event
            Procedures.

   

  		(a)	Subject to the terms set forth in Section 2.5 and Section 2.7, the Plan Investor shall have the right to terminate this Agreement upon the occurrence of any Plan Support
          Party Termination Event (other than the Plan Support Termination Events set forth in Sections 2.1(e) and 2.1(1)) in accordance with this Section 2.4. Subject to the terms set forth in Section 2.5 and Section 2.7, the Required Consenting Bridge
          Lenders/Noteholders shall have the right to terminate this Agreement upon the occurrence of a Plan Support Party Termination Event (other than the Plan Support Termination Events set forth in Sections 2.1(b), 2.1(d), 2.1(e) and 2.1(1)) in
          accordance with this Section 2.4. Subject to the terms set forth in Section 2.5 and Section 2.7, the Required Consenting Intercompany Lenders shall have the right to terminate this Agreement upon the occurrence of a Plan Support Party Termination
          Event (other than the Plan Support Termination Events set forth in Sections 2.1(b), 2.1(d), 2.1(k) and 2.1(1)) in accordance with this Section 2.4. Subject to the terms set forth in the immediately preceding three sentences and Section 2.5 and
          Section 2.7, upon the occurrence of a Plan Support Party Termination Event, the Plan Investor, the Required Consenting Bridge Lenders/Noteholders or the Required Consenting Intercompany Lenders, as applicable, (in such capacity, the “Terminating

            Party”), may elect to terminate this Agreement with respect to such Terminating Party by delivering written notice thereof to the other Parties; provided that if the Plan Investor exercises such right only in respect of one or more
          Consenting Lenders as contemplated by Section 2.1(1), then, subject to the terms set forth in Section 2.1(1), 2.1(v) and Section 2.7, this Agreement shall terminate only in respect of such Consenting Lender or Consenting Lenders (the date of
          effectiveness of such termination, together with the Company Termination Date, being the “Termination Date”) and such Consenting Lender or Consenting Lenders shall cease to be deemed a Consenting Lender hereunder from and after such date.
          For the avoidance of doubt, the automatic stay arising pursuant to section 362 of the Bankruptcy Code shall be deemed waived or modified for purposes of providing notice or exercising rights hereunder, and the Company agrees it shall not take any
          action to enforce the automatic stay to prevent any valid termination of this Agreement and the PFA Order shall include a waiver of the automatic stay in connection therewith for purpose of providing notice or exercising rights hereunder.

   

  		(b)	Notwithstanding anything herein to the contrary, but subject to Section 2.1(1), Section 2.1(v), Section 2.2(c) and Section 2.2(d) of this Agreement, if a Termination Date
          shall occur in respect of any Consenting Lender, such termination and Termination Date shall apply only to such Consenting Lender (and such Consenting Lender shall cease to be deemed a Consenting Lender hereunder from and after such Termination)
          and this Agreement shall otherwise remain in full force and effect with respect to the Company, the Plan Investor and all such remaining Consenting Lenders.

   

  
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  		2.5	Limitation on Termination.

   

  Except with respect to a termination pursuant to Section 2.1(t), Section 2.2(a), Section 2.2(g) or Section 3 below, no
    Party shall have the right to terminate this Agreement if the Termination Event giving rise to such termination right is the result of the action or omission of such Party or any Affiliate thereof and the taking or failing to take such action by such
    Party or the applicable Affiliate thereof constitutes a breach of this Agreement, the Plan Funding Agreement or any other Definitive Document.

   

  		2.6	Consensual Termination.

   

  In addition to any Termination Event otherwise set forth herein, this Agreement shall terminate immediately upon the
    written agreement of each of the Company, the Plan Investor, and the Required Consenting Lenders.

   

  		2.7	Effect of Termination.

   

  Upon the valid termination of this Agreement, except as otherwise set forth herein (including if such termination only
    related to one or more Consenting Lenders but not this Agreement as an entirety): (a) this Agreement shall be of no further force and effect and each Party shall be released from its commitments, undertakings and agreements under this Agreement, and
    shall have the rights and remedies that it would have had it not entered into this Agreement, and shall be entitled to take all actions, whether with respect to the Transaction or otherwise, that it would have been entitled to take had it not entered
    into this Agreement; (b) any and all votes tendered by the Parties in respect of the Plan prior to such termination shall be deemed, for all purposes, to be null and void from the first instance and shall not be considered or otherwise used in any
    manner by the Parties in connection with this Agreement, the Transaction, the Plan or otherwise; and (c) if Bankruptcy Court permission shall be required for a Consenting Lender to change or withdraw (or cause to be changed or withdrawn) its vote in
    favor of the Plan, no Party to this Agreement shall oppose any attempt by such Party to change or withdraw (or cause to be changed or withdrawn) such vote. Notwithstanding the foregoing, nothing in this section or elsewhere in this Agreement, shall
    relieve any Party from (i) liability for such Party’s breach of such Party’s representations, warranties, covenants, undertakings or obligations hereunder or under any other Definitive Document (including the liability of any Consenting Lender with
    respect to the period before any Termination Date with respect to such Consenting Lender), or (ii) obligations under this Agreement or any other Definitive Document that expressly survive termination of this Agreement, including, without limitation,
    the Company’s obligation (if any) to pay professional fees and expenses pursuant to Section 9.12 hereof that accrued on or prior to the Termination Date or the Company’s obligations (if any) to make payments to the Plan Investor under the PFA Order.
    Except with respect to the obligations under this Agreement that expressly survive termination of this Agreement (including, without limitation, the Company’s obligation (if any) to pay professional fees and expenses pursuant to Section 9.12) and this
    Section 2.7 or the Company’s obligations (if any) to make payments to the Plan Investor under the PFA Order, this Agreement shall terminate automatically without any further required action or notice upon consummation of the Plan.

   

  
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  Section 3.      Fiduciary Obligations.

   

  		3.1	The Company’s Fiduciary Obligations.

   

  Notwithstanding anything to the contrary herein, but subject in all cases to compliance with the Plan Funding Agreement in
    all respects, the board of directors, board of managers, or such similar governing body of the Company, including any properly authorized committee thereof (each, a “Board”) shall be permitted to take (or permitted to refrain from taking) any
    action with respect to the Transaction as and to the extent permitted by Section 6.9 of the Plan Funding Agreement and may take such action without incurring any liability to the Consenting Lenders or the Plan Investor under this Agreement or the Plan
    as and to the extent permitted thereby; provided that nothing herein shall limit or otherwise affect the rights or remedies of (i) the Plan Investor under the Plan Funding Agreement or the PFA Order and (ii) the Consenting Lenders under Section
    9.12 of this Agreement; provided, further, that nothing herein shall limit the rights of the Required Consenting Lender or the Plan Investor to terminate this Agreement to the extent the taking or refraining from taking any action
    pursuant to this Section 3.1 would otherwise constitute a Plan Support Party Termination Event (as determined without taking into account whether the taking or refraining from taking such action is permitted under this Section 3.1).

   

  		3.2	Consenting Lender Fiduciary Obligations.

   

  Each Consenting Lender agrees not to request that the United States Trustee appoint an official committee of creditors or
    equity holders (either or both, an “Official Committee”) in the Bankruptcy Cases. Notwithstanding
    anything herein to the contrary, if any Consenting Lender is appointed to and serves on any Official Committee in the Bankruptcy Cases, the terms of this Agreement shall not be construed so as to limit such Consenting Lender’s exercise of its fiduciary
    duties to any person arising from its service on such Official Committee, and any such exercise of such fiduciary duties shall not be deemed to constitute a breach of the terms of this Agreement; provided that nothing in this Agreement shall be
    construed as requiring any Consenting Lender to serve on any Official Committee in any such chapter 11 case.

   

  		Section 4.	Conditions Precedent to Agreement.

   

  The obligations of the Parties and the effectiveness of this Agreement are subject to satisfaction of each of the
    following (the date upon which all such conditions are satisfied, the “Effective Date”): (x) execution and delivery of signature pages for the Plan Funding Agreement and the Amended Shared Services Agreements by each of the parties thereto; and
    (y) execution and delivery of signature pages for this Agreement by each of the Company, the Plan Investor and the Consenting Lenders (who, in any event, shall hold not less than 66.67% of the Obligations under each of the Convertible Notes Indenture,
    the Bridge Credit Agreement and the Intercompany Credit Agreement).

   

  
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  		Section 5.	Effects of Exclusivity Agreement.

   

  		5.1	Retention of Advance Pending PFA Order.

   

  Reference is made to the letter agreement, dated as of April 11, 2019 (the “Exclusivity Agreement”), by and among Aegerion, the Plan Investor, Novelion, Highbridge Capital Management LLC and Athyrium Capital
    Management, LP. Within two (2) business days following the date the Bankruptcy Court enters the PFA Order, the Plan Investor shall repay the entire Advance (as defined in the Exclusivity Agreement), including any previously applied portion of the
    Advance, to Aegerion by wire transfer of immediately available funds to an account identified by Aegerion. Until such time, the Plan Investor shall be entitled to retain the Advance, notwithstanding the occurrence of a No Reimbursement Event (as
    defined in the Exclusivity Agreement) by the execution and delivery of this Agreement or any other Definitive Documentation.

   

  		5.2	Use of Advance Upon Failure to Obtain PFA Order.

   

  Upon any termination of this Agreement pursuant to Section 2.1(d) or upon any termination of this Agreement
    by any Party other than the Plan Investor at a time when the PFA Order has not been entered and the Plan Investor could have terminated this Agreement pursuant to Section 2.1(d), the Plan Investor shall be entitled to retain the Advance and use it to
    pay Expenses (as defined in the Exclusivity Agreement), notwithstanding the occurrence of a No Reimbursement Event by the execution and delivery of this Agreement or any other Definitive Documentation. The Advance and any right to payment of Expenses
    shall be treated as provided in Section 4(c) through 4(g) of the Exclusivity Agreement.

   

  		5.3	Effect on Exclusivity Agreement.

   

  Except for the provisions of Section 4 of the Exclusivity Agreement that survive the execution and delivery
    of this Agreement as contemplated by this Section 5, the terms and conditions set forth in the Exclusivity Agreement shall expire and be of no further force and effect upon the execution and delivery of this Agreement.

   

  		Section 6.	Representations, Warranties and Covenants.

   

  		6.1	Power and Authority.

   

  Each Plan Support Party, severally with respect to itself and not jointly, represents, warrants, and covenants to the
    Company, and the Company, jointly and severally, represents, warrants, and covenants to each Plan Support Party, that (a) such Party has and shall maintain all requisite corporate, partnership, limited liability company or other applicable entity power
    and authority to enter into this Agreement and the other Definitive Documentation to which it is or will become a party and to carry out the transactions contemplated by, and perform its respective obligations under, this Agreement and such other
    Definitive Documentation, and (b) the execution and delivery of this Agreement and the other Definitive Documentation to which it is or will become a party and the performance of its obligations hereunder and thereunder have been duly authorized by all
    necessary action on its part.

   

  
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  		6.2	Enforceability.

   

  Each Plan Support Party, severally with respect to itself and not jointly, represents and warrants to the Company, and the
    Company, jointly and severally, represents and warrants to each Plan Support Party, that this Agreement and each other Definitive Documentation to which it is or will become a party is (or will be) its legally valid and binding obligation, enforceable
    in accordance with its terms, except as enforcement may be limited by bankruptcy, insolvency, reorganization or other similar laws limiting creditors’ rights generally or by equitable principles relating to enforceability or ruling or approval of the
    Bankruptcy Court.

   

  		6.3	Governmental Consents.

   

  Each Plan Support Party, severally with respect to itself and not jointly, represents and warrants to the Company, and the
    Company, jointly and severally, represents and warrants to each Plan Support Party that its execution, delivery, and performance of this Agreement and the other Definitive Documentation to which it is or will become a party does not and shall not
    require any registration or filing with, consent or approval of, or notice to, or other action to, with, or by, any federal, state, or other governmental authority or regulatory body, except: (a) as may be necessary and/or required by the Securities
    and Exchange Commission or federal securities laws, rules or regulations, national securities exchange, the Financial Conduct Authority or other applicable state or provincial securities or “blue sky” laws; (b) any of the foregoing as may be necessary
    and/or required in connection with the Bankruptcy Cases, including the approval of the Disclosure Statement and confirmation of the Plan by the Bankruptcy Court; (c) in the case of the Company or the Plan Investor, (i) filings of amended articles of
    incorporation or formation or other organizational or constating documents with applicable state or other local authorities that are required to implement the Transaction as contemplated by the Plan Funding Agreement, and (ii) other registrations,
    filings, consents, approvals, notices, or other actions that are reasonably necessary to maintain permits, licenses, qualifications, and governmental approvals to carry on the business of the Company or the Plan Investor; (d) authorizations, consents,
    orders or approvals of, or registrations or declarations with, any Governmental Entity (as defined in the Plan Funding Agreement), that have been or will be obtained or made prior to or on the closing date of the Transaction (the “Closing Date”),

    a true and complete list of which is set forth on Schedule 5.3 of the Plan Funding Agreement; and (e) any other registrations, filings, consents, approvals,
    notices, or other actions, the failure of which to make, obtain or take, as applicable, would not be reasonably likely to, individually or in the aggregate, (i) in the case, of the Company, have a Company Material Adverse Effect, (ii) in the case of
    the Plan Investor, have a Plan Investor Material Adverse Effect, or (iii) in the case of any Consenting Lender, materially delay or materially impair the ability of such Consenting Lender to consummate the Transaction.

   

  		6.4	Ownership.

   

  Each Consenting Lender, severally and not jointly, represents, warrants, and covenants to the Company and the other
    Parties that, without limiting the ability of such Consenting Lender to sell, transfer or assign the Claims in accordance with and subject to the terms set forth in Section 9 of this Agreement, (a) such Party is either (i) the sole legal and beneficial
    owner of its share of the Claims and/or equity interests in the Company in the amounts indicated opposite its name on Schedule 6.4 of this Agreement, or (ii) such Consenting Lender has investment or voting discretion or control with respect to
    accounts for the holders or beneficial owners of the Claims and/or equity interests in the Company in the amounts indicated opposite its name on Schedule 6.4 of this

   

  
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  Agreement; (b) it has full power and authority to vote on and consent to all matters concerning the Claims and/or equity
    interests in the Company in the amounts indicated opposite its name on Schedule 6.4 of this Agreement and to exchange, assign and transfer such Claims and/or equity interests as contemplated by the Transaction; and (c) other than pursuant to
    this Agreement and the other Definitive Documentation, such Claims and/or equity interests are and shall continue to be free and clear of any pledge, lien, security interest, charge, claim, equity, option, proxy, voting restriction, right of first
    refusal or other limitation on disposition, or encumbrances of any kind, that would adversely affect in any way such Consenting Lender’s performance of its obligations contained in this Agreement and the other Definitive Documentation at the time such
    obligations are required to be performed and the consummation of the Transaction.

   

  		6.5	No Conflict; Third Party Consents.

   

  Each Plan Support Party, severally with respect to itself and not jointly, represents and warrants to the Company, and the
    Company, jointly and severally, represents and warrants, to each Plan Support Party that the execution, delivery and performance by such Party of this Agreement and the other Definitive Documentation to which it is or will become a party does not, and
    the consummation of the Transaction does not and will not (a) subject to receipt of the authorizations, consents, orders or approvals of, or registrations or declarations with, any federal, state, or other governmental authority or regulatory body that
    have been or will be obtained or made prior to or on the Closing Date with respect to the Transaction as set forth on Schedule 5.3 of the Plan Funding Agreement, violate any provision of law, rule or regulation applicable to it or its charter or bylaws (or other similar governing documents) in any material respect, (b) conflict with,
    result in a breach of or constitute (with due notice or lapse of time or both) a default under any contractual obligation to which it is a party in any material respect, except, in the case of the Company, for the filing of the Bankruptcy Cases, or (c)
    other than in respect of the Company as expressly contemplated by the Plan, require the consent or approval of, or notice to, or other action by, any creditor or shareholder of any Party or from any other Person in respect of any Party (including any
    contractual obligation of any Party), other than for any such consent, approval, notice or action, the failure of which to make or obtain, as would not reasonably be expected to be material to such Party or its ability to consummate the Transaction.

   

  		6.6	Publicity; Confidentiality.

   

  		(a)	Publicity. Concurrently

          with or as promptly as practicable following the execution of this Agreement, the Parties (other than the Consenting Noteholders or Consenting Bridge Lenders) or some of the Parties shall issue the press release or press releases substantially in
          the form(s) attached to Schedule 6.6(a) (collectively, the “Initial Press Release”). Subject to the terms set forth in the immediately following sentence, none of the Parties will make, or permit any Affiliate thereof to make, any public
          statements, including any press releases, with respect to this Agreement, the other Definitive Documentation, or the Transaction unless such press release or public statement is consistent, in all material respects, with the Initial Press Release
          or receives the prior written consent of the Company, the Plan Investor and the Required Consenting Lenders. Notwithstanding anything to the contrary contained in the foregoing, any Party (or any Affiliate thereof) may (i) make disclosures
          required by any applicable law or applicable stock exchange requirements (it being acknowledged that Novelion intends to file a Current Report

   

  
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  on Form 8-K and any equivalent filing as may be required by applicable Canadian securities laws in respect of the
    Transaction within the permitted statutory timeframe from the date of this Agreement (or in a periodic report in lieu of such Form 8-K, if timing so permits), and such filing and/or subsequent filings with the Securities and Exchange Commission may
    attach or otherwise file as exhibits this Agreement and/or other Definitive Documentation), in which case the Party required to make (or whose Affiliate is required to make) such disclosure will allow the other Parties reasonable time to comment on
    such disclosure in advance of the making or issuance thereof to the extent reasonably practicable, (ii) make disclosures that are expressly contemplated by this Agreement, the Plan Funding Agreement or the Plan, including (A) in the case of the Plan
    Investor, the filing and disclosure of the Admission Document and any other documentation in respect of the solicitation of the approval of its shareholders in respect of the Transaction, subject to compliance with the terms set forth in the Plan
    Funding Agreement, and (B) in the case of the Company, such disclosures as it is required to make in connection with the Bankruptcy Cases, including in connection with the solicitation of votes in support of the Plan, and (iii) make such disclosures as
    any Party or its Affiliates determines to be advisable or required in connection with any action or legal proceeding commenced by any Party against any other Party or any Affiliate thereof in respect of any dispute arising out of this Agreement, the
    other Definitive Documentation or the Transaction.

   

  		(b)	Confidentiality. Any confidentiality agreement executed by any Party shall survive this Agreement and shall continue in full force and effect,
          subject to the terms thereof, irrespective of the terms hereof.

   

  		(c)	Disclosure of Consenting Lender Information. Unless required by applicable law or regulation or requested by any regulatory authority, no Party
          shall disclose the amount of a Consenting Lender’s holdings of Claims without the prior written consent of such Consenting Lender; provided, however, that the Company may disclose the aggregate holdings and percentages of the
          Consenting Lenders, by Consenting Class, and, if required by the Bankruptcy Court, may disclose the amount of a Consenting Lender’s holdings of Claims without the prior written consent of such Consenting Lender. If any Party or any of its
          representatives receives a subpoena or other legal process as referred to in this Section 6.6 in connection with the Agreement, such Party shall provide the other Parties hereto with prompt written notice of any such request or requirement, to
          the fullest extent permissible and practicable under the circumstances (as advised by such Party’s internal or outside counsel), so that the other Parties may seek a protective order or other appropriate remedy or waiver of compliance with the
          provisions of this Agreement.

   

  6.7          Acquired

        Interests. Each Consenting Lender severally, and not jointly, or jointly or severally, represents and warrants to the Plan Investor that it has not acquired an interest in shares (as such term is defined in the UK City Code of Takeovers and
      Mergers) in the Plan Investor during the course of the twelve months prior to the date of this Agreement (any such acquisition, a “Disqualifying Transaction”).

   

  
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  6.8           UK Panel. Each Consenting Lender severally, and not jointly, or jointly or severally, hereby represents and warrants and undertakes to the
    Company that:

   

  		(a)	neither it nor any of its Affiliates will enter into any Disqualifying Transaction in the period from the date of this Agreement until Closing of the Transaction except in the case of Highbridge MSF International Ltd., 1992 Tactical Credit Master Fund, L.P.,
          Highbridge SCF Special Situations SPV, L.P., and Highbridge SCF Loan SPV, L.P. (the “Highbridge Funds”), the Highbridge Funds and its Affiliates may, with the consent of the UK Panel on Takeovers and Mergers (the “Panel”), purchase
          all or any portion of the shares issued by the Plan Investor pursuant to any Plan Investor Additional Equity Issuance (as defined in the Plan Funding Agreement); and

   

  		(b)	neither it nor any of its Affiliates will knowingly take any action that it or such Affiliates knows at the time of such action constitutes “acting in concert” (as such term
          is defined in Rule 9.1 of the Takeover Code) with another Consenting Lender or any other third party with a view to obtain or seek to obtain control of the Company, and, if it or any of its Affiliates has actual knowledge that it or such
          Affiliate has been “acting in concert”, then it shall, or shall cause its Affiliate(s) to, advise the Company of such actions at least five (5) business days prior to the Company seeking shareholder approval of the “Rule 9 whitewash waiver” or,
          if such acting in concert has occurred during this five (5) business day period, no later than twenty-four (24) hours after the time such acting in concert has occurred.

   

  6.9           Rule 9.1 Information. Athyrium Opportunities II Acquisition LP, Athyrium Opportunities III Acquisition LP, Highbridge MSF International Ltd.,
    1992 Tactical Credit Master Fund, L.P., Highbridge SCF Special Situations SPV, L.P., and Highbridge SCF Loan SPV, L.P., in each case severally, and not jointly, or jointly or severally, represents and warrants and undertakes to the Company that all of
    the information provided to the Panel in connection with the analysis undertaken for the purposes of Rule 9.1 is true and accurate in all material respects.

   

  	Section 7.	Remedies.

   

  It is understood and agreed by each of the Parties that any breach of this Agreement would give rise to irreparable harm for which money damages
    would not be an adequate remedy and accordingly the Parties agree that, in addition to any other remedies, each non-breaching Party shall be entitled to specific performance and injunctive or other equitable relief for any such breach without the
    posting of a bond or other security. The Parties agree to waive any defense in any action for specific performance that a remedy at law would be adequate. The Company and each of the Plan Support Parties agree that for so long as the Company and the
    Plan Support Parties have not taken any action to prejudice the enforceability of this Agreement (including without limitation, alleging in any pleading that this Agreement is unenforceable), and have taken such actions as are reasonably required or
    desirable for the enforcement hereof, then the Company and the Plan Support Parties shall have no liability for damages hereunder in the event a court determines that this Agreement is not enforceable. Each of the Parties to this Agreement acknowledges
    and agrees that, notwithstanding anything in this Agreement to the contrary, it shall have no, and agrees not to pursue any, recourse against (a) Novelion for breaches or threatened breaches hereunder by Aegerion or Aegerion’s Representatives to the
    extent such Representative

  
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  was acting in its capacity as an Aegerion Representative (and not as a Novelion Representative) at the time of the alleged breach, or (b) Aegerion for breaches or
    threatened breaches hereunder by Novelion or Novelion’s Representatives to the extent such Representative was acting in its capacity as a Novelion Representative (and not as an Aegerion Representative) at the time of the alleged breach.

   

  	Section 8.	Acknowledgement.

   

  This Agreement and the Plan and transactions contemplated herein and therein are the product of negotiations among the Parties, together with
    their respective representatives. Notwithstanding anything herein to the contrary, this Agreement is not, and shall not be deemed to be, a solicitation of votes for the acceptance of the Plan or any chapter 11 plan for the purposes of sections 1125 and
    1126 of the Bankruptcy Code or otherwise. Notwithstanding anything herein to the contrary, the Company will not solicit acceptances of the Plan from any Consenting Lender until such Consenting Lender has been provided with information required by
    section 1125 of the Bankruptcy Code.

   

  	Section 9.	Miscellaneous Terms.

   

  9.1           Assignment; Transfer Restrictions.

   

  		(a)	Each Consenting Lender agrees, severally with respect to itself and not jointly, until the earlier of the date that this Agreement is validly terminated in accordance with
          its terms and the date that the closing of the Transaction occurs, not to, directly or indirectly, sell, assign, transfer, hypothecate or otherwise dispose of (including by participation) (a “Transfer”) any Claim against the Company or any
          interest therein or voting rights in respect thereof unless (i) (A) the transferee, assignee or equivalent is a Consenting Lender that is a party to and bound by this Agreement and, as applicable, the other Definitive Documentation (including the
          execution and delivery of a Lender Joinder in accordance with Subsection 9.1(c))), provided that upon the consummation of any Transfer by any Consenting Lender of any Claims, such Claims shall be, and shall automatically be deemed to be,
          subject to the terms of this Agreement and, as applicable, the other Definitive Documentation, or (B) as a condition precedent to the effectiveness of any such Transfer, the transferee thereof shall have executed and delivered a Lender Joinder in
          accordance with Subsection 9.1(c), and (ii) the consummation of such Transfer would not be reasonably expected to have or result in a material adverse impact on, or delay or impair the consummation of the Transaction in any material respect,
          within any of the time frames contemplated by this Agreement and the Plan Funding Agreement. Thereafter, such purchaser, transferee, assignee or other relevant Person shall be deemed to be a Consenting Lender for purposes of this Agreement and
          the other applicable Definitive Documentation and shall be bound by all of the terms hereof and thereof, and the transferor Consenting Lender shall be deemed to, automatically as of the consummation of such Transfer, relinquish its rights (and be
          released from its obligations) under this Agreement solely to the extent of such transferred Claims, it being understood and agreed that no such Transfer shall impact, effect or

  
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  alter the rights and obligations of the Parties under the other Definitive Documentation except to the extent expressly set forth therein.

   

  		(b)	Any Transfer of any Claim that does not comply with the procedures set forth in Subsection 9.1(a) of this Agreement shall be deemed void ab
            initio.

   

  		(c)	Any person that seeks to receive or acquire a portion of the Claims pursuant to a Transfer of such Claims by a Consenting Lender shall be required, as a condition to the
          effectiveness of such Transfer, to be bound by all of the terms of this Agreement and, as applicable, the other Definitive Documentation (a “Joining Lender Party”) by duly executing and delivering to the Company and each other Party a
          joinder in the form of Exhibit H hereto (the “Lender Joinder”). The Joining Lender Party shall thereafter be deemed to be a “Consenting Lender” and a Party for all purposes under this Agreement and, as applicable, the other
          Definitive Documentation.

   

  		(d)	With respect to the Claims held by the Joining Lender Party upon consummation of any Transfer, the Joining Lender Party shall be deemed to have made, with respect to itself,
          the representations and warranties of a Consenting Lender set forth in Section 6 of this Agreement to the Company.

   

  		(e)	Subject to Subsection 9.1(a), this Agreement shall in no way be construed to preclude any Consenting Lender from acquiring additional Claims; provided that, any such
          Claims shall automatically be deemed to be subject to the terms of this Agreement and the other Definitive Documentation.

   

  		(f)	Notwithstanding Section 9.1(a): (i) a Consenting Lender may Transfer any right, title, or interest in its Claims to an entity that is acting in its capacity as a Qualified
          Marketmaker without the requirement that the Qualified Marketmaker be or become a Consenting Lender only if such Qualified Marketmaker has purchased such Claims with a view to immediate resale of such Claims (by purchase, sale, assignment,
          transfer, participation or otherwise) as soon as reasonably practicable, and in no event later than the earlier of (A) three (3) business days prior to any voting deadline with respect to the Plan (solely if such Qualified Marketmaker acquires
          such Claims prior to such voting deadline) and (B) ten (10) business days of its acquisition to a transferee Consenting Lender that is or becomes a Consenting Lender (by executing and delivering the Lender Joinder in accordance with Subsection
          9.1(c)); and (ii) to the extent that a Consenting Lender is acting solely in its capacity as a Qualified Marketmaker, it may Transfer any right, title, or interest in any Claims that such Consenting Lender, acting solely in its capacity as a
          Qualified Marketmaker, acquires from a holder of such Claims who is not a Consenting Lender without the requirement that the transferee be or become a Consenting Lender with respect to such Claims. Notwithstanding the foregoing, (w) if at the
          time of a proposed Transfer of any Claim to the Qualified Marketmaker in accordance with the foregoing, the date of such proposed Transfer is within three (3) business days of the voting deadline with respect to the Plan, the proposed transferor
          Consenting Lender shall first vote, and shall be deemed to have voted, such Claim in accordance with the requirements of Section 1.1(b) hereof prior to any Transfer or (x) if, after a Transfer in accordance with this Section 9.1(f), a

  
    21

    
      
 

  

   

  Qualified Marketmaker is holding a Claim on any date within three (3) business days of the voting deadline with respect to the Plan, such Qualified
    Marketmaker shall vote, and shall be deemed to have voted, such Claim in accordance with the requirements of Section 1.1(b) hereof as if it were a Consenting Lender and the definitive documentation in respect of any Transfer thereto shall require the
    foregoing, in form and substance reasonably acceptable to the Plan Investor, as a condition to any such Transfer. For these purposes, a “Qualified Marketmaker” means an entity that: (y) holds itself out to the market as standing ready in the ordinary course of its business to purchase from customers and sell to customers claims against the
    Company and its Affiliates (including debt securities or other debt) or enter into with customers long and short positions in claims against the Company and its Affiliates (including debt securities or other debt), in its capacity as a dealer or market
    maker in such claims against the Company and its Affiliates; and (z) is in fact regularly in the business of making a market in claims against issuers or borrowers (including debt securities or other debt). For avoidance of doubt, J.P. Morgan Chase
    & Co. together with its Affiliates, other than Highbridge Capital Management, LLC and its subsidiaries shall be deemed to be a Qualified Marketmaker.

   

  	9.2	Certain Additional Chapter 11 Related Matters.

   

  The Company shall provide draft copies of all motions, applications and other documents that relate in any material respect to implementation of
    the Transaction (including all “first day” and “second day” motions and orders, the Plan, the Disclosure Statement, ballots and other Solicitation Materials in respect of the Plan, any proposed amended version of the Plan and/or the Disclosure
    Statement, the Confirmation Order and any other Definitive Documentation) it intends to file with the Bankruptcy Court to counsel for the Plan Investor and each Consenting Class, at least three (3) business days prior to the date when the Company
    intends to file any such pleading or other document with the Bankruptcy Court (provided that if
    delivery of such motions, orders or materials (other than the Plan, the Disclosure Statement or Confirmation Order) at least three (3) business days in advance is not reasonably practicable, such motion, application or other document shall be delivered
    as far in advance of such date of filing as is reasonably practicable) and, in each case shall, prior to the filing thereof, consult in good faith with such counsel regarding the form and substance of any such proposed filing.

   

  	9.3	No Third Party Beneficiaries.

   

  This Agreement shall be solely for the benefit of the Company, the Plan Investor, and each Consenting Lender. No other person or entity shall be
    a third party beneficiary.

   

  	9.4	Entire Agreement.

   

  This Agreement and the other Definitive Documentation, including exhibits and annexes hereto and thereto, constitutes the entire agreement of
    the Parties with respect to the subject matter hereof and thereof, including exhibits and annexes hereto and thereto, and supersedes all other prior negotiations, agreements and understandings, whether written or oral, among the Parties with respect to
    such subject; provided, however,
    that, subject to the terms and conditions of the Plan

  
    22

    
      
 

  

   

  Funding Agreement, any confidentiality agreement executed by any Party shall survive this Agreement and shall continue in full force and effect, subject to the terms thereof.

   

  	9.5	Counterparts.

   

  This Agreement may be executed in one or more counterparts, each of which shall be deemed an original and all of which shall constitute one and
    the same agreement. Delivery of an executed signature page of this Agreement by email or facsimile transmission shall be effective as delivery of a manually executed counterpart hereof.

   

  	9.6	Settlement Discussions.

   

  This Agreement, the other Definitive Documentation and the Plan are part of a proposed settlement of disputes among certain of the Parties
    hereto. Nothing herein shall be deemed to be an admission of any kind. Pursuant to Federal Rule of Evidence 408 and any applicable state rules of evidence, this Agreement and the other Definitive Documentation and all negotiations relating hereto and
    thereto shall not be admissible into evidence in any proceeding other than a proceeding to enforce the terms of this Agreement, such other Definitive Documentation or in connection with the confirmation of the Plan.

   

  	9.7	Reservation of Rights.

   

  In the event that, (x) the Transaction is not consummated in accordance with the terms and conditions hereof, the Plan Funding Agreement and the
    other Definitive Documentation, (y) a Termination Date occurs or (z) this Agreement is otherwise validly terminated for any reason, each Party fully reserves any and all of its respective rights, remedies and interests (if any) under the Credit
    Documents, the Plan Funding Agreement, the PFA Order, applicable law and in equity.

   

  	9.8	Governing Law; Waiver of Jury Trial.

   

  		(a)	The Parties waive all rights to trial by jury in any jurisdiction in any action, suit, or proceeding brought to resolve any dispute between or among the Parties arising out
          of this Agreement, whether sounding in contract, tort or otherwise.

   

  		(b)	This Agreement shall be governed by and construed in accordance with the Bankruptcy Code and the laws of the State of New York, without regard to any conflicts of law
          provision which would require the application of the law of any other jurisdiction. By its execution and delivery of this Agreement, each Party irrevocably and unconditionally agrees for itself that, subject to Subsection 9.8(c), any legal
          action, suit or proceeding brought by or against it with respect to any matter under or arising out of or in connection with this Agreement or for recognition or enforcement of any judgment rendered in any such action, suit or proceeding, shall
          be brought exclusively in any state or federal court of competent jurisdiction in New York County, State of New York, and by execution and delivery of this Agreement, each of the Parties hereby: (i) irrevocably accepts and submits itself to the
          exclusive jurisdiction of such court, generally and unconditionally, with respect to any such action, suit or proceeding; and (ii) waives any objection to laying venue in any such action, suit or proceeding.

  
    23

    
      
 

  

  
  		(c)	Notwithstanding the foregoing, if the Bankruptcy Cases are commenced, nothing in Subsections 9.8(a)-9.8(b) shall limit the authority of the Bankruptcy Court, as applicable, to
          hear any matter related to or arising out of this Agreement, and each Party irrevocably and unconditionally consents to the jurisdiction and venue of the Bankruptcy Court, as applicable, to hear and determine such matters during the pendency of
          the Bankruptcy Cases.

     

  	9.9	Successors.

   

  This Agreement is intended to bind the Parties and inure to the benefit of the Consenting Lenders, the Plan Investor and the
    Company and each of their respective successors and permitted assigns. Except in accordance with the express terms of this Agreement, no Party shall assign this Agreement or any rights or obligations hereunder without the prior written consent of the
    Company, the Plan Investor and the Required Consenting Lenders. For the avoidance of doubt, nothing contained in this Section 9.9 shall be deemed to permit any Transfer of any Claims other than in accordance with the terms of this Agreement.  

   

  	9.10	Acknowledgment of Counsel; Interpretation.

   

  		(a)	Each of the Parties acknowledges that it is sophisticated and has been represented by counsel (or had the opportunity to and waived its right to do so) in connection with the
          negotiation and execution of this Agreement and the Transaction. Accordingly, the Parties do not intend that any rule of law or any legal decision or rules relating to the interpretation of contracts against the drafter of any particular clause
          or that would otherwise provide any Party with a defense to the enforcement of the terms of this Agreement against such Party based upon lack of legal counsel shall apply to this Agreement and each Party hereby expressly waives any such
          application or defense. Furthermore, prior drafts of this Agreement and any of the documents executed and delivered in connection herewith and the fact that any clauses have been added, deleted or otherwise modified from any prior drafts of this
          Agreement or any of the documents executed and delivered in connection herewith shall not be used as a rule of construction or otherwise constitute evidence of the intent of the Parties or the parties thereto, and no presumption or burden of
          proof shall arise favoring or disfavoring any such Party or parties by virtue of such prior drafts.

     

  		(b)	When a reference is made in this Agreement to a Section, Schedule, Annex or Exhibit, such reference will be to a Section of, or a Schedule, Annex or Exhibit to, this Agreement
          unless otherwise indicated. Whenever the words “include,” “includes” or “including” are used in this Agreement, they will be deemed to be followed by the words “without limitation.” The words “hereof,” “herein” and “hereunder” and words of
          similar import when used in this Agreement will refer to this Agreement as a whole and not to any particular provision of this Agreement. The word “or” when used in this Agreement may have a disjunctive and not alternative meaning (i.e., where
          two items or qualities are separated by the word “or”, the existence of one item or quality shall not be deemed to be exclusive of the existence of the other and, as the context may require, the word “or” may be deemed to include the word “and”).
          All terms used herein with initial capital letters have the meanings ascribed to them herein. The definitions contained in this Agreement

  
    24

    
      
 

  

  			are applicable to the singular as well as the plural forms of such terms and to the masculine as well as to the feminine and neuter genders of such term. Unless otherwise
          expressly provided herein, any agreement, instrument or statute defined or referred to herein, or in any agreement or instrument that is referred to herein, means such agreement, instrument or statute as from time to time amended, modified or
          supplemented, including (in the case of agreements or instruments) by waiver or consent and (in the case of statutes) by succession of comparable successor statutes and references to all attachments thereto and instruments incorporated therein.
          All Exhibits, Annexes and Schedules annexed hereto or referred to herein are incorporated in and made a part of this Agreement as if set forth in full herein. If any time period for giving notice or taking action hereunder expires on a day that
          is not a business day, the applicable time period shall automatically be extended to the business day immediately following such day.

     

  	9.11	Amendments, Modifications, Waivers.

   

  		(a)	Subject to the terms set forth in this Agreement, including in Section 9.1(b), this Agreement (including, without limitation, the Plan, the Plan Funding Agreement and the
          Disclosure Statement) may only be modified, amended or supplemented, and any of the terms thereof may only be waived with (i) in the case of any such modification, amendment or supplementation, the written consent by each of (a) the Company, (b)
          the Required Consenting Lenders, and (c) the Plan Investor (each of the Required Consenting Bridge Lenders/Noteholders, the Required Consenting Intercompany Lenders and the Plan Investor a “Required Party” and shall be referred to herein collectively as the “Required Parties”), and (ii) in the case of a waiver, by the Party or Parties waiving rights pursuant to the terms of such waiver, except that any waiver by the Required Consenting Bridge
          Lenders/Noteholders or the Required Consenting Intercompany Lenders shall be binding on all Consenting Noteholders and all Consenting Bridge Lenders and any waiver by the Required Consenting Intercompany Lenders shall be binding on all lenders
          under the Intercompany Credit Agreement; provided that, if the modification, amendment, supplement or waiver at issue adversely impacts the treatment or rights of any Consenting Lender (in its capacity as a Consenting Lender) in a
          materially different and materially disproportionate manner when compared to the effect thereof on other Consenting Lenders in its Consenting Class, the agreement in writing of such Consenting Lender whose treatment or rights are so adversely
          impacted shall also be required for such modification, amendment, supplement, or waiver to be effective with respect to such Consenting Lender; provided, further, that the waiver of a Termination Event arising from the breach by a Required Party of its obligations hereunder shall not require the consent of such breaching Required Party. If
          any ruling is made by the Panel that any provision of this Agreement is not permitted by the Takeover Code, such provision shall be given no effect. The Parties shall use reasonable efforts to replace such provision with a valid and enforceable
          provision which is acceptable to the Panel and carries out, as closely as possible, the intentions of the parties.

     

  		(b)	Without prejudice to the other provisions of this Agreement, each of the Parties agrees to use its respective reasonable best efforts to take or cause to be taken, in

  
    25

    
      
 

  

  			good faith, all appropriate actions (including any amendments, modifications and supplements to this Agreement, the Plan and Disclosure Statement and the Plan Funding
          Agreement) as is reasonably necessary, appropriate and advisable to memorialize and effectuate the Transaction, including, without limitation, to obtain Bankruptcy Court confirmation of the Plan pursuant to a final order of the Bankruptcy Court;
          provided that no Party shall have any obligation to take any action or otherwise agree to any amendment, modification or supplement that (i) creates any additional material obligation on such Party or (ii) adversely affects in any material
          respect the treatment, obligations or rights of such Party (it being agreed that, for the avoidance of doubt, any change to the Plan that results in a diminution of the value of the property to be received by a Consenting Class under the Plan or
          alters the form in which such value is to be received by a Consenting Class under the Plan shall be deemed to adversely affect such Consenting Class or that results in a diminution of the value and/or increase in the liabilities of the Plan
          Investor shall be deemed to adversely affect the Plan Investor) whether such change is made directly to the treatment of a Consenting Class, the treatment of another Consenting Class, any term or provision relating to or impacting the Plan
          Investor or otherwise. Notwithstanding the foregoing, the Company may amend, modify or supplement the Plan and Disclosure Statement, from time to time, with the consent of any Required Parties (such consent not to be unreasonably withheld,
          conditioned or delayed), to cure any non-material ambiguity, defect (including any technical defect), inconsistency or clerical error; provided that any such amendment, modification or supplement does not adversely affect the rights, interests or treatment of any such Plan Support Parties under such Plan and Disclosure Statement.

     

  	9.12	Professional Fees.

   

  The Company agrees to reimburse, in addition to its own advisors, all of the reasonable and documented out-of-pocket fees
    and expenses incurred by the Consenting Noteholders and the Consenting Bridge Lenders of Latham & Watkins, LLP and Ducera Partners LLC, under their respective engagement letters as in effect on the date hereof, in connection with the Transaction
    and implementation of the Plan (including, without limitation, fees and expenses incurred after the Petition Date); provided that only those fees and expenses in respect of Ducera Partners LLC that the Company shall be required to reimburse
    shall be those incurred as a result of the services expressly contemplated by the engagement letter by and between Ducera Partners LLC and Highbridge MSF International Ltd. (f/k/a 1992 MSF International Ltd.), 1992 Tactical Credit Master Fund, L.P.,
    Athyrium Opportunities II Acquisition LP, and Athyrium Opportunities III Acquisition LP, dated as of December 7, 2018 (without giving effect to any subsequent amendment, restatement, supplement or modification thereof following such date), a true,
    complete and correct copy of which has been provided to the Company prior to the date hereof, in each case without the need to file any interim or final fee applications with the Bankruptcy Court, subject to the Company obtaining Bankruptcy Court
    approval of any postpetition payments pursuant to the Interim CC Order and the Final DIP Order; provided,
    however, that if this Agreement shall be terminated due to the breach by any Consenting Noteholder
    or Consenting Bridge Lender of its representations, warranties, covenants, undertakings or obligations hereunder or under any other Definitive Documentation, then the Company shall not be required to pay the expenses referred to in the preceding
    sentences of this Section 9.12 (except to the extent provided

  
    26

    
      
 

  

  in the Interim CC Order or the Final DIP Order, as applicable). For the avoidance of doubt, but subject to the foregoing,
    the Company’s obligation to pay professional fees and expenses pursuant to this Section 9.12 shall be unaffected by, and shall survive, termination of this Agreement; provided, however, that except as otherwise provided in the Interim CC Order or the Final DIP Order, as applicable, the Company shall only be obligated pursuant to this
    Agreement to pay such fees and expenses incurred through the Termination Date. For the avoidance of doubt, Novelion and the Plan Investor shall bear (and the Company shall have no liability in respect of other than as set forth in the Exclusivity
    Agreement) their own costs and expenses incurred in connection with the Transaction, including their respective professional fees incurred in connection with the Transaction, but without limitation of any rights of the Plan Investor to receive
    reimbursement of its costs and expenses (or a portion thereof) from the Company pursuant to the terms of the Plan Funding Agreement and, the Exclusivity Agreement. In addition, on the effective date of the Plan, the Company shall pay all outstanding
    reasonable and documented fees and expenses of the Convertible Notes Trustee (including the fees and expenses of its outside counsel and other professionals), regardless of whether such fees and expenses were incurred before or after the Petition
    Date.  

   

  	9.13	Disclosure Letter References.

   

  The Parties agree that the disclosure set forth in any particular section or subsection of the disclosure schedules provided
    in connection with this Agreement and/or the Plan Funding Agreement (the “Disclosure Schedules”) or deemed disclosed as exceptions pursuant to the terms of the Plan Funding Agreement shall be deemed to be an exception to (or, as applicable, a
    disclosure for purposes of) (a) the representations and warranties (or covenants, as applicable) of the disclosing Party that are set forth in this Agreement or the Plan Funding Agreement; and (b) any other representations and warranties (or covenants,
    as applicable) of the disclosing party that are set forth in this Agreement or the Plan Funding Agreement.  

   

  	9.14	Severability of Provisions.

   

  If any provision of this Agreement for any reason is held to be invalid, illegal or unenforceable in any respect, that
    provision shall not affect the validity, legality or enforceability of any other provision of this Agreement.  

   

  	9.15	Headings.

   

  The headings of the sections, paragraphs and subsections of this Agreement are inserted for convenience only and shall not
    affect the interpretation hereof.

   

  	9.16	Certain Limitations.

   

  Each of the Parties acknowledges and agrees that, notwithstanding anything in this Agreement to the contrary, it shall have
    no, and agrees not to pursue any, recourse against (a) Novelion for breaches or threatened breaches hereunder by the Company hereunder or thereunder, or (b) the Company for breaches or threatened breaches hereunder by Novelion hereunder or
    thereunder.  

   

  
    27

    
      
 

  

   

  	9.17	Subsidiaries Bound.

   

  

  Novelion shall cause any and all of its subsidiaries (other than Aegerion and its subsidiaries) to comply with the terms of
    this Agreement and the other Definitive Documentation as if they were a party hereto and had the obligations of Novelion hereunder, and at the request of the Company, Novelion shall cause such subsidiaries (other than Aegerion and its subsidiaries) to
    sign reasonable documentation (including joinder agreements) as may be required to effect the foregoing.  

   

  	9.18	Notices.

   

  Any notices required or elected to be given hereunder must be in writing and may be served in person or by overnight mail or
    by electronic mail upon the respective parties as follows (or to such other addresses as may hereafter be designated in accordance with the terms hereof):  

   

  if to the Company:  

   

  c/o Aegerion Pharmaceuticals, Inc. 

  245 First Street 

  Riverview II, 18th Floor 

  Cambridge, MA 02142 

  		Attention:	John R. Castellano

  		Email:	JCastellano@alixpartners.com

   

  with a copy to:  

   

  Willkie Farr & Gallagher LLP 

  787 Seventh Avenue 

  New York, NY 10019 

  		Attention:	Russell L. Leaf, Esq.; Jared Fertman, Esq.; Paul V. Shalhoub, Esq.; and

   Andrew S. Mordkoff, Esq.

  		Email:	rleaf@willkie.com; jfertman@willkie.com; pshalhoub@willkie.com;

   amordkoff@willkie.com

   

  if to the Consenting Lenders:  

   

  as set forth in each signature page

   

  with a copy to:

   

  (For Novelion) 

  Goodwin Procter LLP 

  The New York Times Building 

  620 Eighth Avenue 

  New York, NY 10018 

  		Attention:	Gregory Fox, Esq.; and Jacqueline Mercier, Esq.

  
    28

    
      
 

  

  

  		Email:	GFox@goodwinlaw.com; JMercier@goodwinlaw.com

   

  (For certain of the holders of loans under the Bridge Credit Agreement and/or the 

  Convertible Notes Indenture that are Parties as of the date hereof)

  Latham & Watkins LLP 

  330 North Wabash Avenue, Suite 2800 

  Chicago, IL 60611 

  		Attention:	Richard A. Levy, Esq.

  		Email:	Richard.Levy@lw.com

   

  and

   

  King & Spalding LLP 

  444 West Lake Street 

  Suite 1650 

  Chicago, IL 60606 

  		Attention:	Matthew L. Warren, Esq.

  		Email:	mwarren@kslaw.com

   

  if to the Plan Investor:

   

  Amryt Pharma plc 

  90 Harcourt Street 

  Dublin 2, Ireland 

  		Attention:	Joe Wiley

  		Email:	joe.wiley@ amrytpharma.com

   

  with a copy to:

   

  Gibson, Dunn & Crutcher LLP 

  200 Park Avenue 

  New York, NY 10166 

  		Attention:	George P. Stamas, Esq.; William B. Sorabella, Esq.; Matthew J. Williams,

  Esq.; and Jason Zachary Goldstein, Esq.

  		Email:	GStamas@gibsondunn.com; WSorabella@gibsondunn.com;

  MJWilliams@gibsondunn.com; JGoldstein@gibsondunn.com

   

  [Signature pages follow]

  
    29

    
      
 

  

  
  IN WITNESS WHEREOF, the parties hereto have caused this Amendment to be executed and delivered as of the date first above written.        

   

  

  	 	AEGERION PHARMACEUTICALS, INC.
	 	 	 
	 	By:	/s/ John R. Castellano
	 	 	Name:	 John R. Castellano
	 	 	Title:  	Chief Restructuring Officer

   

  

  	 	AEGERION PHARMACEUTICALS HOLDINGS, INC.
	 	 	 
	 	By:	/s/ John R. Castellano
	 	 	Name: 	John R. Castellano
	 	 	Title:  	Chief Restructuring Officer

     

  

  	 	
          NOVELION THERAPEUTICS INC. 

        
	 	 	 
	 	By:	 
	 	 	Name: 
	 	 	Title:

   

  

  	 	
          

          AMRYT PHARMA PLC

        
	 	 	 
	 	By:	 
	 	 	Name: 
	 	 	Title:

   

  [Signature Page to Restructuring Support Agreement]

  
    
      
 

  

  IN WITNESS WHEREOF, the parties hereto have caused this Agreement to be executed and delivered as of the date first above written.

   

  

  	 	AEGERION PHARMACEUTICALS, INC.
	 	 	 
	 	By:	

        
	 	 	Name:	John R. Castellano
	 	 	Title:  	Chief Restructuring Officer

   

  

  	 	AEGERION PHARMACEUTICALS HOLDINGS, INC.
	 	 	 
	 	By:	

        
	 	 	Name: 	John R. Castellano
	 	 	Title: 	Chief Restructuring Officer

   

  

  	 	
          NOVELION THERAPEUTICS INC. 

        
	 	 	 
	 	By:	/s/ Ben Harshbarger
	 	 	Name: 	
          Ben Harshbarger

        
	 	 	Title:	Interim CEO

   

  

  	 	
          

          AMRYT PHARMA PLC

        
	 	 	 
	 	By:	 
	 	 	Name: 
	 	 	Title:

  

   

  [Signature Page to Restructuring Support Agreement]

  
    
      
 

  

  IN WITNESS WHEREOF, the parties hereto have caused this Agreement to be executed and delivered as of the date first above written.

   

  	 	AEGERION PHARMACEUTICALS, INC.
	 	 	 
	 	By:	

        
	 	 	Name: 	John R. Castellano
	 	 	Title:	Chief Restructuring Officer

  

   

  

  	 	AEGERION PHARMACEUTICALS HOLDINGS, INC.
	 	 	 
	 	By:	

        
	 	 	Name: 	John R. Castellano
	 	 	Title:  	Chief Restructuring Officer

   

  

  	 	
          NOVELION THERAPEUTICS INC. 

        
	 	 	 
	 	By:	 
	 	 	Name: 
	 	 	Title:

   

  

  	 	
          

          AMRYT PHARMA PLC

        
	 	 	 
	 	By:	 /s/ Joe Wiley
	 	 	Name:	Joe Wiley
          

        
	 	 	Title: 	CEO

   

  [Signature Page to Restructuring Support Agreement]

  
    
      
 

  

  

  	 	ATHYRIUM OPPORTUNITIES II ACQUISITION LP
	 	 	 
	 	By: Athyrium Opportunities Associates II LP, its general partner
	 	 
	 	By: Athyrium GP Holdings LLC, its general partner
	 	 	 
	 	By:	
          /s/ Andrew C. Hyman 

        
	 	 	Name:	 Andrew C. Hyman 
	 	 	Title: 	Authorized Signatory

   

  

  	 	ATHYRIUM OPPORTUNITIES III ACQUISITION LP
	 	 	 
	 	By: Athyrium Opportunities Associates III LP, its general partner
	 	 
	 	By: Athyrium Opportunities Associates III GP LLC, its general partner
	 	 	 
	 	By:	
          /s/ Andrew C. Hyman 

        
	 	 	Name: 	Andrew C. Hyman 
	 	 	Title: 	Authorized Signatory

   

  [Signature Page to Restructuring Support Agreement]

  
    
      
 

  

  

  	 	
          HIGHBRIDGE MSF INTERNATIONAL LTD.

        
	 	 	 
	 	By:	
          /s/ Jonathan Segal 

        
	 	 	Name: 	Jonathan Segal
	 	 	Title:	Managing Director

   

  

  	 	
          1992 TACTICAL CREDIT MASTER FUND, L.P.

        
	 	 	 
	 	By:	
          /s/ Jonathan Segal 

        
	 	 	Name: 	Jonathan Segal
	 	 	Title:	Managing Director

   

  

  	 	
          HIGHBRIDGE SCF SPECIAL SITUATIONS SPV, L.P.

        
	 	 	 
	 	By:	
          /s/ Jonathan Segal 

        
	 	 	Name: 	Jonathan Segal
	 	 	Title:	Managing Director

   

  

  	 	
          HIGHBRIDGE SCF LOAN SPV, L.P.

        
	 	 	 
	 	By:	
          /s/ Jonathan Segal 

        
	 	 	Name:	Jonathan Segal
	 	 	Title:	Managing Director

   

  [Signature Page to Restructuring Support Agreement]

  
    
      
 

  

  

  	 	
          Whitebox Relative Value Partners, LP

        
	 	 	 
	 	By:	
          /s/ Chris Hardy 

        
	 	 	Name: 	Chris Hardy
	 	 	Title: 	Chief Compliance Officer

   

  

  	 	
          Whitebox GT Fund, LP

        
	 	 	 
	 	By:	
          /s/ Chris Hardy 

        
	 	 	Name: 	Chris Hardy
	 	 	Title:	Chief Compliance Officer

   

  

  	 	
          Whitebox Multi-Strategy Partners, LP 

        
	 	 	 
	 	By:	
          /s/ Chris Hardy 

        
	 	 	Name: 	Chris Hardy
	 	 	Title: 	Chief Compliance Officer

   

  

  	 	
          Pandora Select Partners, LP 

        
	 	 	 
	 	By:	
          /s/ Chris Hardy 

        
	 	 	Name: 	Chris Hardy
	 	 	Title: 	Chief Compliance Officer

   

  [Signature Page to Restructuring Support Agreement]

  
    
      
 

  

  

   

  

  	 	
          NINETEEN77 GLOBAL MULTI-STRATEGY ALPHA MASTER LIMITED

        
	 	 	 
	 	By:	
          UBS O’Connor LLC, its investment adviser

        
	 	 	 
	 	By:	/s/ Andrew Hollenbeck
	 	 	Name:	Andrew Hollenbeck
	 	 	Title:	Managing Director

   

  

  	 	By:	
          /s/ James Del Medico

        
	 	 	Name: 	James Del Medico
	 	 	Title:	Executive Director

   

  [Signature Page to Restructuring Support Agreement]

  
    
      
 

  

  

  	 	
          NINETEEN77 GLOBAL CONVERTIBLE BOND MASTER LIMITED

        
	 	 	 
	 	By:	UBS O’Connor LLC, its investment adviser
	 	 	 
	 	By:	
          /s/ Andrew Hollenbeck

        
	 	 	Name: 	Andrew Hollenbeck
	 	 	Title: 	Managing Director

   

  

  	 	By:	
          /s/ James Del Medico

        
	 	 	Name: 	James Del Medico
	 	 	Title:	Executive Director

  

   

  [Signature Page to Restructuring Support Agreement]

  

  
    
      
 

  

  SCHEDULE 6.4

   

  Ownership Claims and Interests

   

  	Consenting

            Lender	Claim/Interest	
          Holdings (USD$) as of May 20, 2019 

        
	Athyrium Opportunities II Acquisition LP	Convertible notes (face)	95,400,000
	Athyrium Opportunities II Acquisition LP	Roll-up (principal)	12,600,000
	Athyrium Opportunities II Acquisition LP	Secured debt (principal)	1,700,000
	Athyrium Opportunities III Acquisition LP	Convertible notes (face)	22,337,000
	Athyrium Opportunities III Acquisition LP	Roll-up (principal)	3,000,000
	Athyrium Opportunities III Acquisition LP	Secured debt (principal)	33,000,000
	Highbridge MSF International  Ltd.	Roll-up	4,333,745.23
	Highbridge MSF International  Ltd.	Convertible notes (face)	21,300,000.00
	1992 Tactical Credit Master Fund, L.P.	Roll-up	2,260,404.09
	1992 Tactical Credit Master Fund, L.P.	Convertible notes (face)	19,900,000.00
	Highbridge SCF Special Situations SPV, L.P.	Convertible notes (face)	10,900,000.00
	Highbridge SCF Loan SPV, L.P.	Secured debt	15,381,922.67
	
          Nineteen77 Global Multi-Strategy Alpha Master Limited 

        	Convertible notes (face)	25,000,000
	
          Nineteen77 Global Convertible Bond Master Limited 

        	Convertible notes (face)	1,000,000
	Whitebox Relative Value Partners, LP	Convertible notes (face)	2,880,000.00
	Whitebox GT Fund, LP	Convertible notes (face)	288,000.00
	Whitebox Multi-Strategy  Partners, LP	Convertible notes (face)	2,808,000.00
	Pandora Select Partners, LP	Convertible notes (face)	1,224,000.00

  
    
      
 

  

  
  SCHEDULE 6.6(a)

  
    
      
 

  

  
  NOT FOR RELEASE, PUBLICATION OR DISTRIBUTION, IN WHOLE OR IN PART, DIRECTLY OR INDIRECTLY, IN, INTO OR
    FROM THE UNITED STATES (INCLUDING ITS TERRITORIES AND POSSESSIONS, ANY STATE OF THE UNITED STATES OR THE DISTRICT OF COLUMBIA), AUSTRALIA, CANADA, JAPAN, THE REPUBLIC OF SOUTH AFRICA OR ANY OTHER JURISDICTION IN WHICH SUCH RELEASE, PUBLICATION OR
    DISTRIBUTION WOULD BE UNLAWFUL OR WOULD CONSTITUTE A VIOLATION OF THE RELEVANT LAWS OR REGULATIONS OF THAT JURISDICTION (“RESTRICTED JURISDICTIONS”). THIS ANNOUNCEMENT IS FOR INFORMATION PURPOSES ONLY AND DOES NOT ITSELF CONSTITUTE AN OFFER FOR SALE OR
    SUBSCRIPTION OF ANY SECURITIES IN THE COMPANY.

   

  PLEASE SEE THE IMPORTANT NOTICE AT THE END OF THIS ANNOUNCEMENT.

   

  This announcement contains inside information within the meaning of the EU Market Abuse Regulation 596/2014.

     

  
    	
            May 21 2019

              AIM:AMYT

              Euronext Growth: AYP

          	

  

   

  Amryt Pharma plc

    (“Amryt” or the “Company”)

   

  RECOMMENDED ACQUISITION OF AEGERION PHARMACEUTICALS

   

  -     Creates a rare disease business with two approved products – lomitapide (Lojuxta® I Juxtapid®) and metreleptin (Myalept® I
    Myalepta®)

   

  -     $136.5m of 2018 built-in revenues, multiple growth opportunities, and a robust pipeline for value creation

   

  -     Reunites the lomitapide franchise and transforms Amryt into a global player in the orphan disease market

   

  -     Capitalizes on Amryt management’s unique knowledge of Aegerion’s assets and European commercialization capabilities

   

  -     Presents the opportunity for meaningful expense synergies - $25m-$40m in 2020

   

  -     Pre-money implied transaction equity valuations: Amryt $120m and Aegerion $190.7m

   

  -     Contingent Value Rights (“CVRs”) will be issued to Amryt stakeholders that could result in the payment of up to an
    additional $85m (settled in cash or stock) based on certain AP101 milestones being achieved

   

  -     Amryt plans to raise $60m in equity concurrent with closing of the Transaction and certain Aegerion bondholders have
    agreed to backstop this equity raise

   

  -     Establishes an appropriate capital structure and liquidity profile to drive growth and create value

   

  -     Transaction already endorsed by 34.3% of Amryt’s shareholders and in excess of 67% of Aegerion’s bondholders

   

  -     Management will host a conference call for analysts and investors today at 1330 BST (0830 EDT) – dial-in details below

   

  Amryt, a biopharmaceutical company focused on rare and orphan diseases, today announces that it has reached agreement to acquire (the
    “Transaction”) Aegerion Pharmaceuticals (“Aegerion”), a subsidiary of Novelion Therapeutics Inc. - NASDAQ:NVLN - (“Novelion”). The Transaction has been unanimously approved and recommended by the Boards of Amryt, Aegerion and Novelion.

  
    1

    
      
 

  

  Transaction Rationale

   

  The Company has built a diversified portfolio of drugs to treat patients with rare and orphan diseases through the acquisition of its AP101 and
    AP103 product lines and through the in-licencing of the Lojuxta® product line. The Transaction is in line with the Company’s strategy to expand its product portfolio to
    enhance shareholder value.

   

  The Transaction will put Amryt on the path to creating a rare and orphan disease company with a diversified offering of multiple commercial and
    development stage assets and will provide it with scale to support further growth. The Transaction will give Amryt an expanded commercial footprint to market two US and EU approved products, lomitapide (Juxtapid® (US/ROW) I Lojuxta® (EU)) and metreleptin (Myalept® (US) I Myalepta® (EU)). Amryt’s leadership team already has a deep
    knowledge of both these products and since December 2016 has successfully commercialized Lojuxta® across Europe and the Middle East.

   

  Dr. Joe Wiley, Chief Executive Officer of Amryt, commented: “The acquisition of Aegerion accelerates our ambition to become a global leader in treating rare conditions to help improve the lives of patients where there is a high unmet medical need. By delivering two substantial revenue-generating
      products and an enhanced pipeline of promising development opportunities, this will significantly strengthen our growth in highly attractive markets globally. Amryt has a unique insight into both Aegerion and its products, through our commercial
      success with Lojuxta® and given that many of our senior management team previously worked at Aegerion.”

   

  “With this Transaction we can continue the strong growth trajectory already underway with Lojuxta® in Europe on a global scale. It also delivers metreleptin, another highly compelling commercial rare disease product alongside an established commercial footprint in the US
    and internationally. This transformational deal provides Amryt with the financial flexibility to fully execute our medium-term growth plans, and is expected to deliver significant shareholder returns.”

   

  Transaction Highlights:

   

  
    		•	
            Amryt has agreed to acquire Aegerion in an all-paper transaction

          

  

  
    		•	
            The combined group had 2018 pro-forma combined revenues of $136.5m

          

  

  
    		•	
            Pre-money implied transaction equity valuations: Amryt $120m and Aegerion $190.7m

          

  

  
    		•	
            Contingent Value Rights (“CVRs”) will be issued to Amryt stakeholders that could result in the payment of up to $85m (settled in cash or stock) based on certain AP101 milestones being achieved

          

  

  
    		•	
            Amryt plans to raise $60m in equity concurrent with closing of the Transaction and certain Aegerion bondholders have agreed to backstop this equity raise

          

  

  
    		•	
            This equity raise will be placed at a 20% discount to the implied transaction equity value

          

  

  
    		•	
            Aegerion’s balance sheet is to be restructured through a US Chapter 11 process prior to Amryt acquiring Aegerion - Aegerion will continue to operate as usual during the Chapter 11 process

          

  

  
    		•	
            New loan facilities for the combined group will be put in place, and the key terms of such facilities have been agreed - Amryt’s existing European Investment Bank facility is to be repaid

          

  

  
    		•	
            The combined group’s global HQ will be in Dublin, Ireland with its US HQ in Boston, Massachusetts

          

  

  
    		•	
            Enlarged group to be re-admitted to AIM and Euronext Growth on closing with a planned dual-listing on NASDAQ

          

  

  
    		•	
            Transaction already endorsed by 34.3% of Amryt shareholders and in excess of 67% of Aegerion’s bondholders

          

  

  
    2

    
      
 

  

  Rich Commercial Portfolio & Development Pipeline with a Global Footprint

   

  
    		•	
            Amryt will have a differentiated, diverse, global offering of multiple commercial and development stage rare disease assets, including:

          

  

  
    		•	
            Two high-value commercial assets with multiple development opportunities in complementary global markets

          

  

  
    		○	
            Lomitapide (Juxtapid®(US)/Lojuxta®(EU)) for the
              treatment of adult homozygous familial hypercholesterolemia (HoFH)

          

  

  
    		○	
            Metreleptin (Myalept®(US)IMyalepta® (EU)), a leptin hormone replacement therapy, approved in the US for Generalised Lipodystrophy (GL), and recently in Europe for GL and Partial Lipodystrophy (PL)

          

  

  
    		•	
            Additional near-term potential commercial opportunities for a broadened Amryt portfolio of products

          

  

  
    		○	
            Metreleptin as a potential treatment for partial lipodystrophy (PL) in the US

          

  

  
    		○	
            Lomitapide (Juxtapid®/Lojuxta®) as a potential
              treatment for familial chylomicronemia syndrome (FCS)

          

  

  
    		○	
            A lead development asset (AP101) for Epidermolysis Bullosa (“EB”), a >$1bn market opportunity in a pivotal Phase 3 trial, which recently reported positive unblinded interim efficacy analysis results and is
              anticipated will be fully enrolled by end of H2 2019

          

  

  
    		○	
            Novel gene therapy platform (AP103) which offers a potential treatment for patients with EB and other topical indications

          

  

   

  Value Creation

   

  
    		•	
            Enhanced scale of combined group expected to drive revenue growth and future profitability

          

  

  
    		•	
            Expected to deliver meaningful operational synergies over the medium term - the Directors believe, on the work undertaken to date, that the enlarged group can deliver operational synergies of between $25m and $40m
              in 2020, rising further in 2021

          

  

  
    		•	
            Amryt’s deep knowledge of Aegerion products is key to driving growth

          

  

  
    		•	
            Reunification of lomitapide brands provides potential to replicate success of Lojuxta® in Europe with Juxtapid® in the US

          

  

  
    		•	
            Opportunity to grow Myalepta® revenues with broader reach across EU to accelerate recent launch

          

  

  
    		•	
            Delivers a ready-made commercial US infrastructure in advance of anticipated launch of AP101

          

  

  
    		•	
            Recapitalized business well-positioned to drive pipeline value

          

  

  
    		•	
            Planned NASDAQ listing to drive liquidity and investor reach

          

  

  
    		•	
            Opportunity for corporate restructuring to drive additional value

          

  

   

  Board & Management

   

  
    		•	
            Team led by Dr Joe Wiley, CEO of Amryt

          

  

  
    		•	
            Strong international management with significant industry experience

          

  

  
    		•	
            Revised Board composition, on closing of the Transaction, consisting of CEO and six Non-Executive Directors

          

  

  
    		•	
            New Board to be appointed on closing

          

  

  
    3

    
      
 

  

  Ben Harshbarger, Novelion’s (parent company of Aegerion) Interim Chief Executive Officer,
      said, “The combination of Amryt and Aegerion will create a financially stronger and well-capitalized rare disease company with two commercial products and a
      pipeline of late stage rare disease products. Amryt’s executive management team has the depth of experience to commercialize Aegerion’s marketed products, as demonstrated by its ability to grow sales of Lojuxta® in the European market, to develop and, if approved, commercialize Amryt’s late stage product candidate, AP101, and to pursue additional potential indications for metreleptin and lomitapide.”

   

  The Transaction constitutes a reverse takeover of the Company under the Euronext Growth Rules and AIM Rules and requires
    shareholder approval and the publication of an AIM and Euronext Growth Admission Document (the “Admission Document”) with details of the Enlarged Group. Trading in Amryt’s shares will be suspended on both the AIM Market and the Euronext Growth Market
    with immediate effect until the Admission Document has been published. The Transaction is also conditional on the UK Takeover Panel waiving the obligation on certain lenders of Aegerion to make a general offer under Rule 9 of The UK Takeover Code, and
    on independent Amryt shareholder approval being obtained for such waiver and whitewash.

   

  MTS Securities, LLC is serving as financial advisor and Gibson, Dunn & Crutcher LLP is serving as legal advisor to Amryt
    in this transaction. Shore Capital is acting as financial advisor, NOMAD and Joint Broker to Amryt. Stifel Nicolaus Europe Limited are Joint Broker to Amryt. Davy is acting as Euronext Growth Advisor and Joint Broker to Amryt. Moelis & Co LLC is
    serving as financial advisor to Aegerion.

   

  Conference Call Details

   

  Management will host a conference call for analysts today at 1330 BST (0830 EDT). Dial in details:

   

  Conference ID: 3387304

  From the UK/International: +44 (0) 2071 928000 I 0800 376 7922

  From Ireland: (01) 431 9615 I 1800 936148

  From the US: +1 631 510 7495 I 1 866 966 1396

   

  A recording of the call will be available from 1830 (BST) today, please email ir@amrytpharma.com for access details. The presentation for today’s call will be available to download shortly before the call commences at https://www.amrytpharma.com/newsroom/

      

  Enquiries:

  
    	 	 
	
            Amryt Pharma plc

          	
            +353 (1) 518 0200

          
	
            Dr. Joe Wiley, CEO

          	 
	
            Rory Nealon, CFO/COO

          	 
	 	 
	
            Shore Capital

          	
            +44 (0) 20 7408 4090

          
	
            Financial Advisor, NOMAD and Joint Broker

          	 
	
            Edward Mansfield, Mark Percy, Daniel Bush

          	 
	 	 
	
            Stifel

          	
            +44 (0) 20 7710 7600

          
	
            Joint Broker

          	 
	
            Jonathan Senior, Ben Maddison

          	 
	 	 
	
            Davy

          	
            +353 (1) 679 6363

          
	
            Euronext Growth Advisor and Joint Broker

          	 
	
            John Frain, Daragh O’Reilly

          	 

  

  
    4

    
      
 

  

  
    	
            Consilium Strategic Communications

          	
            +44 (0) 20 3709 5700

          
	
            Amber Fennell, Matthew Neal, David Daley

          	 

  

   

  About Amryt

   

  Amryt is a biopharmaceutical company focused on developing and delivering innovative new treatments to help improve the lives of patients with
    rare or orphan diseases.

   

  Lojuxta® is an approved treatment for adult
    patients with the rare cholesterol disorder - Homozygous Familial Hypercholesterolaemia (“HoFH”). This disorder impairs the body’s ability to remove low density lipoprotein (“LDL”) cholesterol (“bad” cholesterol) from the blood, typically leading to
    abnormally high blood LDL cholesterol levels in the body from before birth - often ten times more than people without HoFH - and subsequent aggressive and premature narrowing and blocking of blood vessels. Lojuxta® is indicated as an adjunct to a low-fat diet and other lipid-lowering medicinal products with or without LDL apheresis in adult patients with HoFH.

   

  Amryt is the marketing authorisation holder and has an exclusive licence to sell Lojuxta® (lomitapide) across the European Economic Area, Middle East and North Africa, Switzerland, Turkey, Israel, Russia, the Commonwealth of Independent States and the non-EU Balkan states.

   

  Amryt’s lead development candidate, AP101, is a potential treatment for Epidermolysis Bullosa (“EB”), a rare and distressing
    genetic skin disorder affecting young children and adults for which there is currently no treatment. It is currently in Phase 3 clinical trials and recently reported positive unblinded interim efficacy analysis results and is anticipated will be fully
    enrolled by end of H2 2019. The European and US market opportunity for EB is estimated to be in excess of $1 billion.

   

  In March 2018, Amryt in-licenced a pre-clinical gene-therapy platform technology, AP103, which offers a potential treatment
    for patients with Recessive Dystrophic Epidermolysis Bullosa, a subset of EB, and is also potentially relevant to other genetic disorders.

   

  For more information on Amryt, please visit www.amrytpharma.com.

   

  About Novelion Therapeutics and Aegerion Pharmaceuticals

   

  Novelion, through its subsidiary Aegerion Pharmaceuticals, is a global biopharmaceutical company dedicated to developing and
    commercializing therapies that deliver new standards of care for people living with rare diseases. With a global footprint and an established commercial portfolio, including Myalept/a® (metreleptin) and Juxtapid® (lomitapide), their business is supported by differentiated treatments that treat severe and rare diseases.

   

  Description of Transaction

   

  
    	•	
            Amryt has agreed to acquire Aegerion in an all-paper transaction. On closing, the implied equity valuations of Amryt and Aegerion will be $120m and $190.7m respectively. Amryt stakeholders will also receive a
              Contingent Value Right (“CVR”) of up to $85m, in cash or stock, at the election of its board, subject to certain regulatory approval and commercialization milestones of its late-stage development product candidate, AP101.

          

  

   

  
    	•	
            Amryt plans to raise $60m in new equity concurrent with the Transaction closing at a 20% discount to the implied transaction valuations. The proceeds from this financing will be used to continue to develop the
              combined group’s pipeline, to develop potential new indications for Amryt’s late

          

  

  
    5

    
      
 

  

  stage product candidates, and to be used for general corporate purposes. Certain Aegerion bondholders have agreed to backstop
    this capital raise.

   

  
    	•	
            Amryt, Aegerion and Aegerion’s key stakeholders have entered into a “Restructuring Support Agreement” pursuant to which Aegerion has filed for Chapter 11 in the United States and seek to consummate the Transaction
              through a plan of reorganization that has garnered the support of Aegerion’s key creditors and stakeholders. Pursuant to the plan of reorganization, upon Bankruptcy Court approval, Amryt will acquire the reorganized Aegerion in exchange for
              Amryt stock, which stock will be distributed, together with other consideration in the form of new debt, to certain Aegerion secured and unsecured creditors, including Aegerion’s convertible bond holders, certain unsecured creditors and
              Novelion. As a result, Aegerion will emerge from Chapter 11 after having discharged substantial pre-transaction liabilities and with a reorganized and streamlined capital structure that materially reduces its debt obligations.

          

  

   

  
    	•	
            To facilitate a smooth entry into Chapter 11, Aegerion has arranged for financing to allow it to operate uninterrupted during the Chapter 11 process, which financing will be repaid in cash pre-closing or otherwise
              exchanged into the new $125m convertible notes referred to below. Aegerion’s bondholders have agreed to support this transaction and oppose other potential transactions to acquire Aegerion.

          

  

   

  
    	•	
            $125 million of new 5% convertible notes will be issued. The notes will mature 5.5 years from closing and be convertible into equity of Amryt at a 20% premium to the implied transaction valuation. Aegerion’s
              existing $50 million (in principal) secured loan, held by certain funds managed by Athyrium Capital Management and Highbridge Capital Management, as well as Amryt’s existing €20m (in principal) secured loan, will be converted and/or
              refinanced into new first-lien secured debt of the Amryt Group, which will have a cash interest rate of 6.5% per annum and an additional 6.5% PIK (“Payment-in-kind”) interest rate and will mature 5 years from closing.

          

  

   

  
    	•	
            In connection with the Transaction, it is proposed that a corporate reorganization of Amryt will be undertaken by way of a scheme of arrangement, pursuant to which a new Irish incorporated public company will become
              the new ultimate holding company of the combined group.

          

  

   

  Governance & Management

   

  Amryt will continue to be listed on the London Stock Exchange’s Alternative Investment Market, Euronext Growth Market in Dublin and after the
    Transaction will pursue a dual-listing on NASDAQ. Following the Transaction, Amryt’s global headquarters will be in Dublin, Ireland and its US headquarters will be in Boston, Massachusetts.

   

  Upon the closing of the Transaction, the Amryt board will consist of seven Directors including Dr. Joe Wiley (CEO). The six
    Non-Executive Directors will be proposed as follows – two by Amryt and four by Athyrium Capital Management and Highbridge Capital Management (current Aegerion bondholders). The Chairperson of the Board will be proposed by Amryt and will be unaffiliated
    with Amryt, Novelion or Aegerion. All board appointments will be made by mutual consent. Amryt will continue to be led by its executive team, which will be supplemented by certain Aegerion executives on both a transitional and permanent basis.

   

  Conditions of the Transaction - Closing of the Transaction is conditional, inter alia, on:

   

  
    		•	
            US Bankruptcy Court approval of the plan of reorganization and all conditions precedent to consummation of the plan of reorganization having been satisfied or waived;

          

  

  
    6

    
      
 

  

  
    		•	
            the receipt of all necessary regulatory approvals and confirmation of no injunction preventing consummation of the Transaction;

          

  

   

  
    		•	
            the passing of all resolutions necessary in connection with the Transaction by the shareholders of Amryt, such resolutions to be set out in the Admission Document to be published by Amryt including in relation to a
              scheme of arrangement in connection with a corporate reorganization required to be undertaken in connection with the Transaction and the issuance of the CVRs;

          

  

   

  
    		•	
            a waiver being granted by The Panel on Takeovers and Mergers of the obligations which may otherwise arise pursuant to Rule 9 of the Takeover Code for certain lenders of Aegerion to make a general offer to the
              Company’s shareholders for all the issued ordinary shares in the capital of the Company as a result of the distribution of Amryt shares to such lenders following the issuance thereof to the Company as contemplated pursuant to the Transaction,
              and such waiver being approved by the Company’s shareholders by a resolution duly passed by the requisite majority of Company’s shareholders entitled to vote on such resolution pursuant to the Takeover Code and any requirement or direction
              issued by The Panel on Takeovers and Mergers in connection therewith;

          

  

   

  
    		•	
            consummation of the backstopped equity raise of $60m;

          

  

   

  
    		•	
            the Restructuring Support Agreement not having terminated and remaining in full force and effect;

          

  

   

  
    		•	
            re-admission of the enlarged group to trading on AIM;

          

  

   

  
    		•	
            completion of the agreed new term loan financing and the issuance of certain new convertible notes by the reorganized Amryt Group; and

          

  

   

  
    		•	
            certain other customary closing conditions.

          

  

   

  Indicative Timetable

   

  
    		•	
            Announcement of Transaction - 21 May 2019

          

  

   

  
    		•	
            Publication of Admission Document - Early August 2019

          

  

   

  
    		•	
            Shareholder Meeting - Late August 2019

          

  

   

  
    		•	
            Launch of the Equity Fundraise - September 2019

          

  

   

  
    		•	
            Scheme of Arrangement Completion - September 2019

          

  

   

  
    		•	
            Closing of Aegerion’s Chapter 11 Bankruptcy - Early Q4 2019

          

  

   

  
    		•	
            Completion of the Transaction and Equity Fundraise and re-Admission - Early Q4 2019

          

  

   

  The above dates are indicative only and are subject to change

  
    7

    
      
 

  

  IMPORTANT NOTICE

   

  THIS ANNOUNCEMENT IS RESTRICTED AND IS NOT FOR PUBLICATION, RELEASE OR DISTRIBUTION, DIRECTLY OR INDIRECTLY, IN WHOLE OR IN
    PART, IN OR INTO THE UNITED STATES, AUSTRALIA, CANADA, JAPAN, THE REPUBLIC OF SOUTH AFRICA OR ANY OTHER JURISDICTION IN WHICH SUCH PUBLICATION, RELEASE OR DISTRIBUTION WOULD BE UNLAWFUL (“RESTRICTED JURISDICTIONS”).

   

  THIS ANNOUNCEMENT DOES NOT ITSELF CONSTITUTE AN OFFER FOR SALE OR SUBSCRIPTION OF ANY SECURITIES IN THE COMPANY IN ANY
    JURISDICTION INCLUDING IN THE UNITED STATES. DISTRIBUTION OF THIS ANNOUNCEMENT IN CERTAIN JURISDICTIONS MAY BE RESTRICTED OR PROHIBITED BY LAW. PERSONS DISTRIBUTING THIS ANNOUNCEMENT MUST SATISFY THEMSELVES THAT IT IS LAWFUL TO DO SO.

   

  SECURITIES MAY NOT BE OFFERED OR SOLD IN THE UNITED STATES ABSENT REGISTRATION UNDER THE UNITED STATES
    SECURITIES ACT OF 1933, AS AMENDED (THE “SECURITIES ACT”), OR AN EXEMPTION FROM, OR IN A TRANSACTION NOT SUBJECT TO, REGISTRATION. THE COMPANY HAS NOT AND DOES NOT INTEND TO REGISTER ANY SECURITIES UNDER THE SECURITIES ACT, AND DOES NOT INTEND TO OFFER
    ANY SECURITIES TO THE PUBLIC IN THE UNITED STATES UNLESS REGISTERED UNDER THE SECURITIES ACT OR AN EXEMPTION FROM SUCH REGISTRATION IS AVAILABLE. NO PUBLIC OFFERING OF SECURITIES OF THE COMPANY IS BEING MADE IN THE UNITED STATES. NO COMMUNICATION OR
    INFORMATION RELATING TO THE ISSUE AND OFFERING OF SECURITIES MAY BE DISSEMINATED TO THE PUBLIC IN JURISDICTIONS OTHER THAN THE UK WHERE PRIOR REGISTRATION OR APPROVAL IS REQUIRED FOR THAT PURPOSE. NO ACTION HAS BEEN TAKEN THAT WOULD PERMIT AN OFFER OF
    SECURITIES IN ANY JURISDICTION WHERE ACTION FOR THAT PURPOSE IS REQUIRED, OTHER THAN IN THE UK.

   

  References in this announcement and these terms and conditions to Davy refer to J&E Davy. References in these terms and
    conditions to Shore Capital refer to Shore Capital Stockbrokers Limited and/or Shore Capital and Corporate Limited as the context admits.

   

  This announcement has been issued by and is the sole responsibility of the Company. No representation or warranty, express or
    implied, is or will be made as to, or in relation to, and no responsibility or liability is or will be accepted by MTS Securities LLC (“MTS”), Shore Capital or Davy or by any of their respective affiliates or agents as to or in relation to, the
    accuracy or completeness of this Announcement or any other written or oral information made available to or publicly available to any interested party or its advisers, and any liability therefore is expressly disclaimed.

   

  The distribution of this announcement may be restricted by law in certain jurisdictions and persons into whose possession this
    announcement, or other information referred to herein, comes should inform themselves about and observe any such restriction. Any failure to comply with these restrictions may constitute a violation of the securities laws of any such jurisdiction. To
    the fullest extent permitted by applicable law, the companies and persons involved in the Transaction disclaim any responsibility or liability for the violation of such requirements by any person.

   

  This announcement has been prepared for the purposes of complying with English law, the rules of AIM and Euronext Growth and
    the information disclosed may not be the same as that which would

  
    8

    
      
 

  

  have been disclosed if this announcement had been prepared in accordance with the laws and regulations of any jurisdictions
    outside England and Wales.

   

  Statements in this announcement with respect to each of Amryt’s and Aegerion’s business, strategies,
    projected financial figures, transaction synergies, earnings guidance, financial guidance, future dividends and beliefs and with respect to the Transaction, as well as other statements that are not historical facts are forward-looking statements
    involving risks and uncertainties which could cause the actual results to differ materially from such statements. Statements containing the words “expect”, “anticipate”, “intends”, “plan”, “estimate”, “aim”, “forecast”, “project” and similar
    expressions (or their negative) identify certain of these forward-looking statements. The forward-looking statements in this Announcement are based on numerous assumptions regarding the Transaction and each of Amryt’s and Aegerion’s present and future
    business strategies and the environment in which each of Amryt and Aegerion will operate in the future. Forward-looking statements involve inherent known and unknown risks, uncertainties and contingencies because they relate to events and depend on
    circumstances that may or may not occur in the future and may cause the actual results, performance or achievements to be materially different from those expressed or implied by such forward-looking statements. These statements are not guarantees of
    future performance or the ability to identify and consummate investments. Many of these risks and uncertainties relate to factors that are beyond each of Amryt’s and Aegerion’s ability to control or estimate precisely, such as future market conditions,
    currency fluctuations, the behaviour of other market participants, the actions of regulators and other factors such as each of Amryt’s and Aegerion’s ability to obtain financing, changes in the political, social and regulatory framework in which each
    of Amryt and Aegerion operates or in economic, technological or consumer trends or conditions. Past performance should not be taken as an indication or guarantee of future results, and no representation or warranty, express or implied, is made
    regarding future performance. No person is under any obligation to update or keep current the information contained in this Announcement or to provide the recipient of it with access to any additional relevant information that may arise in connection
    with it. Such forward-looking statements reflect the directors’ current beliefs and assumptions and are based on information currently available to management.

   

  This announcement includes certain combined or pro forma financial information for Aegerion and Amryt. Such combined or pro
    forma financial information is preliminary in nature, only represents current estimates of the potential impact of the Transaction on Amryt, remains subject to change and is provided solely for illustrative purposes. No reliance should be placed on the
    combined or pro forma financial information contained in this Announcement.

   

  No statement in this announcement is intended to be a profit forecast, and no statement in this
    announcement should be interpreted to mean that earnings per share of the Company for the current or future financial years would necessarily match or exceed the historical published earnings per share of the Company.

   

  Shore Capital and Corporate Limited and Shore Capital Stockbrokers Limited are, authorised and regulated in the United Kingdom
    by the Financial Conduct Authority. Shore Capital and Corporate Limited acts as nominated adviser to the Company for the purposes of the AIM Rules. Shore Capital is acting exclusively for the Company and for no one else in connection with the
    Transaction and will not be responsible to anyone other than the Company for providing the protections afforded to clients of Shore Capital or for providing advice in relation to the Transaction, or any other matters referred to in this announcement.

   

  Davy, which is regulated in Ireland by the Central Bank of Ireland, acts as the Euronext Growth adviser
    to the Company for the purposes of the Euronext Growth Rules. Davy is acting exclusively

  
    9

    
      
 

  

  for the Company and for no one else in connection with the Transaction and will not be responsible to anyone other than the
    Company for providing the protections afforded to clients of Davy or for providing advice in relation to the Transaction, or any other matters referred to in this announcement. MTS is acting exclusively for the Company and for no one else in connection
    with the Transaction and will not be responsible to anyone other than the Company for providing the protections afforded to clients of MTS or for providing advice in relation to the Transaction, or any other matters referred to in this announcement.

   

  Save for the responsibilities and liabilities, if any, of MTS, Shore Capital and Davy under relevant laws or in respect of
    fraudulent misrepresentation, no representation or warranty, express or implied, is or will be made as to, or in relation to, and no responsibility or liability is or will be accepted by or on behalf of MTS, Shore Capital, Davy or by their respective
    affiliates, agents, directors, officers and employees as to, or in relation to, the accuracy or completeness of this announcement or any other written or oral information made available to or publicly available to any interested party or its advisers,
    and any liability therefor is expressly disclaimed.

  
    10

    
      
 

  

  
    	
            

          

  

   

  Privileged & Confidential

    Draft of 5/20/2019

   

  Updated 7:45 pm EST

   

  Novelion Therapeutics Announces Subsidiary Aegerion

    Pharmaceuticals to Recapitalize Through Court Supervised

    Process In Which Amryt Pharma Plc Will Acquire 100% of

    Reorganized Stock of Aegerion

   

  
    		•	
            Transaction is result of comprehensive capital structure and strategic review conducted independently by both Novelion’s and Aegerion’s Boards of Directors

          

  

  
    		•	
            Aegerion will continue to make available to patients its two approved therapies, JUXTAPID® and MYALEPT®

          

  

  
    		•	
            Novelion to receive approximately 10% of the equity of the combined company (subject to dilution) on account of its intercompany loan and cash payments from Aegerion related to past and future expenditures for
              shared services

          

  

   

  Vancouver, BC, and Cambridge, MA, May 20, 2019 – Novelion Therapeutics Inc.
      (NASDAQ: NVLN) (Novelion), a biopharmaceutical company dedicated to developing new standards of care for individuals living with rare diseases, announced today that its wholly-owned subsidiary Aegerion Pharmaceuticals, Inc. (Aegerion) has entered
      into a plan funding agreement (PFA) and a restructuring support agreement (RSA) that will result in Aegerion selling 100% of its reorganized stock to, and becoming a wholly-owned subsidiary of, Dublin-based Amryt Pharma Plc (Amryt).

   

  The agreements, which will result in a recapitalization of Aegerion (the Recapitalization), are the result of the previously announced capital
    structure and strategic review undertaken independently by the Boards of Directors of Novelion and Aegerion, and a broad marketing process. The Recapitalization of Aegerion pursuant to the PFA and a proposed Chapter 11 plan of reorganization (the Plan)
    has been approved by Aegerion’s board and approved and recommended by the independent restructuring committee of Aegerion’s board. Novelion’s board has approved Novelion’s entry into the RSA and support for Aegerion’s proposed Chapter 11 restructuring.

   

  In conjunction with the Recapitalization, Aegerion has entered into the RSA with many of its key stakeholders, including Novelion, the holders of
    in excess of 67% of the 2.00% convertible notes issued by Aegerion due 2019 (Existing Convertible Notes) and the holders of 100% of the principal amount under Aegerion’s other indebtedness for borrowed money.

   

  To facilitate the Recapitalization, Aegerion and its U.S. subsidiary Aegerion Pharmaceuticals Holdings, Inc. (the Debtors) have commenced cases
    in the United States Bankruptcy Court for the Southern District of New York (the Court) pursuant to Chapter 11 of the United States Code. Aegerion will

  
    
      
 

  

  
  continue to operate in the ordinary course of business during the Chapter 11 process. The non-U.S. subsidiaries of Aegerion are not part of the
    Chapter 11 proceedings.

   

  Certain Key Terms of the Recapitalization

   

  The Recapitalization ascribes an enterprise value to Aegerion and Amryt of $395 million and $146 million, respectively, excluding cash and cash
    equivalents and subject to adjustment for accrued interest and certain payments that are due to the DOJ and the SEC. The key terms of the Recapitalization (the Restructuring Transactions), which are subject to Bankruptcy Court approval and other
    customary conditions, include the following:

   

  
    		•	
            Amryt acquiring 100% of the outstanding new equity interests in recapitalized Aegerion;

          

  

  
    		•	
            Ordinary equity of Amryt representing 61.4% of the outstanding ordinary equity of Amryt, after giving effect to the Restructuring Transactions but before giving effect to equity underlying the New Convertible Notes,
              the Deal Equity Raise (each as described below), ordinary shares that may be issuable in satisfaction of the CVR (described below) if the relevant milestones are achieved, and equity that is reserved for issuance under any management equity
              compensation plan adopted by Amryt, will be distributed to certain existing creditors of Aegerion in complete or partial satisfaction of their claims, including in partial satisfaction of the claims of the holders of the Existing Convertible
              Notes and in complete satisfaction of Novelion’s approximately $36 million claims on account of the Intercompany Loan;

          

  

  
    		•	
            Pre-Recapitalization shareholders of Amryt continuing to own 38.6% of the outstanding ordinary equity of Amryt, after giving effect to the Restructuring Transactions but before giving effect to equity underlying the
              New Convertible Notes, the Deal Equity Raise, and any equity issued on account of the CVRs and under any management equity compensation plan adopted by Amryt;

          

  

  
    		•	
            The equity interests of Aegerion held by Novelion being terminated;

          

  

  
    		•	
            Aegerion issuing $125 million of new 5% convertible notes (the New Convertible Notes). The New Convertible Notes will be issued to certain existing creditors of Aegerion in satisfaction of their claims (and not for
              cash), including in satisfaction of a portion of the Existing Convertible Notes, the approximately $22 million of “Roll Up Debt” under the Aegerion’s existing bridge loan facility, and any amounts drawn down under Aegerion’s DIP Financing
              (defined below) that are not otherwise satisfied in cash at the closing of the Restructuring Transactions;

          

  

  
    		•	
            Aegerion’s existing Bridge Loan in the original principal amount of $50 million, held by certain funds managed by Athyrium Capital Management, LP (Athyrium) and Highbridge Capital Management, LLC (Highbridge), as
              well as Amryt’s existing approximately €20

          

  

   

  1 Note: The announcement will lead to suspension. Following publication of the admission document, the larger Amryt Group will be listed on the AIM market.

  
    2

    
      
 

  

  million (in principal) of secured debt, will be converted into new first-lien secured debt of Amryt and Aegerion, which will
    have a cash interest rate of 6.5% per annum and an additional 6.5% PIK (Paid in Kind) interest rate and mature five years from the closing date of the Restructuring Transactions;

  
    		•	
            Amryt shareholders prior to the consummation of the Restructuring Transactions will receive a contingent value right (CVR) entitling them to receipt of proceeds of up to $85 million upon the occurrence of certain
              milestones related to the regulatory approval and commercialization of AP 101, its late-stage development product candidate, with such payments to be made in loan notes or ordinary shares, at the election of its board;

          

  

  
    		•	
            In connection with the closing of the Restructuring Transactions, Amryt plans to raise $60 million through the issuance of new equity of Amryt (the Deal Equity Raise). The proceeds from the Deal Equity Raise will be
              used as provided in the Plan to pay certain expenses and for general corporate purposes. The new equity will be priced at a 20 percent discount to Amryt’s implied valuation pro forma to the Restructuring Transaction with $18 million of the
              new equity offered to certain Amryt investors and $42 million to certain creditors of Aegerion on a pro rata basis, including Novelion. Certain of Aegerion bondholders, including Athyrium, Highbridge, UBS and Whitebox, have agreed to purchase
              any unsubscribed portion of the new equity;

          

  

  
    		•	
            Aegerion intends to, and the Plan provides that Aegerion will, continue to fully honor all obligations to the U.S. Department of
              Justice, the U.S. Securities and Exchange Commission and other U.S. and state government agencies and courts, which obligations will not be impaired by the Restructuring Transactions;

          

  

  
    		•	
            Aegerion intends to continue to pay all trade and other ordinary operating expenses that arise during the course of the Chapter 11 cases and, upon consummation of the Restructuring Transactions, repay 100% of any
              allowed trade claims outstanding as of the Chapter 11 filing;

          

  

  
    		•	
            Under the terms of the PFA, following the approval by the Court of certain provisions of the PFA, Aegerion and its advisors will have a 55-day period to solicit alternative transactions that are superior, from a
              financial point of view, to the Restructuring Transactions. Subject to the limitations of the PFA, Aegerion is also entitled to respond to unsolicited proposals if Aegerion determines that such proposals are reasonably likely to result in a
              superior transaction. Aegerion is entitled to terminate the PFA in order to enter into a superior transaction, provided that it reimburses Amryt for costs and expenses incurred in connection with the Restructuring Transactions (with a cap of
              $4,000,000) at the time of termination and pays a termination fee of $11,850,000 upon the consummation of the superior transaction. Approximately 34.3% of
              Amryt’s existing shareholders have committed to supporting the Restructuring Transactions through written undertakings.

          

  

   

  1 Note: The announcement will lead to suspension. Following publication of the admission document, the larger Amryt Group will be listed on the AIM market.

  
    3

    
      
 

  

  
    		•	
            The Debtors expect to enter into a $20 million super-priority debtor-in-possession multi-draw term loan facility (the DIP Financing) with Athyrium and Highbridge on terms and conditions set forth in the DIP credit
              agreement and proposed DIP order filed with the Court. Upon approval by the Court and the satisfaction of the conditions set forth in the DIP credit agreement, the DIP Financing will provide the Debtors with liquidity that will be used to
              support the Restructuring Transactions. Any portion of the DIP Financing that is drawn and not repaid in cash upon the closing of the Restructuring Transactions will be converted into a portion of the $125 million of New Convertible Notes
              discussed above. The Debtors have also negotiated with their existing secured lenders the terms of consensual use of cash collateral during the pendency of the Chapter 11 cases.

          

  

   

  The Recapitalization and business combination between Aegerion and Amryt is expected to create a global rare disease company with a diversified
    commercial and clinical-stage portfolio with growing commercial assets and multiple late stage product candidates. The development pipeline includes Amryt’s AP101 product candidate currently in Phase III development for epidermolysis bullosa (EB), as
    well as additional potential indications for Aegerion’s products, including metreleptin as a potential treatment for partial lipodystrophy (PL) in the U.S., which is already approved in Europe, and lomitapide as a potential treatment for familial
    chylomicronemia syndrome (FCS).

   

  “The combination of Amryt and Aegerion will create a financially stronger and well-capitalized rare disease company with two commercial products
    and a pipeline of late stage rare disease products. Amryt’s executive management team has the depth of experience to commercialize Aegerion’s marketed products, as demonstrated by its ability to grow sales of LOJUXTA® in the European market, to develop and, if approved, commercialize Amryt’s late stage product candidate, AP101, and to pursue additional potential indications for metreleptin and lomitapide,”
    said Ben Harshbarger, Novelion’s Interim Chief Executive Officer. “With the opportunity to leverage synergies between the two companies to reduce overlap in expenses and eliminate the intercompany royalties through the existing LOJUXTA licensing
    agreement among the two companies, we believe these transactions create a compelling growth story and value creation opportunity for Aegerion and its stakeholders, including Novelion.”

   

  “The acquisition of Aegerion accelerates our ambition to become a global leader in treating rare conditions where there is a high unmet medical
    need,” commented Joe Wiley, Chief Executive Officer of Amryt. By delivering two substantial revenue-generating products and an enhanced pipeline of promising development opportunities, this will significantly strengthen our growth in highly attractive
    markets globally. Amryt has a unique insight into both Aegerion and its products, through our commercial success with LOJUXTA and given that many of our senior management team previously worked at Aegerion.”

   

  1 Note: The announcement will lead to suspension. Following publication of the admission document, the larger Amryt Group will be listed on the AIM
    market.

  
    4

    
      
 

  

  Impact on Novelion

   

  Novelion has agreed to enter into the RSA and support Aegerion’s proposed Chapter 11 plan, which Novelion believes will avoid value destructive
    potential litigation with Aegerion, its other secured lenders and the majority holders of the Existing Convertible Notes, including as it may relate to challenges to Novelion’s intercompany secured loan and the terms that Aegerion could impose or “cram
    down” on Novelion through a Chapter 11 plan that Novelion did not support. Under the proposed plan, Novelion’s existing approximately $36 million intercompany secured loan to Aegerion (the Intercompany Loan) will be allowed in full and will receive a
    distribution of equity under Aegerion’s plan of reorganization representing approximately 10.1% equity ownership of Amryt on a pro forma basis, prior to any dilution from equity to be issued in connection with Deal Equity Raise, upon conversion of the
    New Convertible Notes, ordinary shares that may be issuable in satisfaction of the CVR if the relevant milestones are achieved, and equity that is reserved for issuance under any management equity compensation plan adopted by Amryt. After taking into
    account the new Amryt equity anticipated to be issued in connection with the Deal Equity Raise, Novelion is projected to own approximately 8.1% of Amryt. Novelion’s treatment under the plan on account of its intercompany loan represents an
    approximately 84% recovery and the equity received will be freely transferable. Also, Novelion has the right to subscribe to purchase its pro rata share of the $42 million of new equity being offered to Aegerion’s creditors, which are priced at a 20
    percent discount to Amryt’s implied Recapitalization valuation. Due to Novelion’s liquidity position, however, it is unlikely that Novelion will exercise that right in full or at all.

   

  In addition, the Debtors entered into shared services agreements with Novelion and Novelion Services USA, Inc., a subsidiary of Novelion, dated
    as of December 1, 2016, but effective as of November 29, 2016 (the Shared Services Agreements), pursuant to which the Debtors provide to Novelion and Novelion provides to the Debtors, certain services, including, but not limited to administrative
    support, human resources, information technology support, accounting, finance, and legal services. In connection with the execution of the RSA and to facilitate the restructuring, the Debtors and Novelion negotiated and executed an amendment to the
    Shared Services Agreements (together, the Amended Shared Services Agreements), which modified the Shared Services Agreements to provide, among other things, for Aegerion to make certain cash payments to Novelion on account of certain services Novelion
    provided or will provide to Aegerion. Pursuant to the Amended Shared Services Agreement, Aegerion has made a payment to Novelion of approximately $3.1 million and has committed to make additional cash payments of up to approximately $2 million. Amended
    Shared Services Agreements provide Novelion with greater and more certain recoveries from Aegerion for the critical shared services Novelion provides.

   

  1 Note: The announcement will lead to suspension. Following publication of the admission document, the larger Amryt Group will be listed on the AIM
    market.

  
    5

    
      
 

  

  Novelion will retain its existing cash balances, public listing and net operating loss (NOL) carryforwards (subject to applicable tax laws). The
    value, if any, of such listing and NOL carryforwards are unknown at this time.

   

  As a result of the valuation of Aegerion and its outstanding debts, Novelion is not receiving any consideration under Aegerion’s plan on account
    of its equity in Aegerion. Those existing equity interests are being cancelled under Aegerion’s Chapter 11 plan and Aegerion is issuing new equity interests to Amryt in exchange for the consideration to be paid under the PFA. Because its equity
    interests are being cancelled for no consideration under the Chapter 11 plan, Novelion is deemed to reject the plan in its capacity as a shareholder. By operation of U.S. bankruptcy law, however, Aegerion’s plan may be confirmed and consummated
    notwithstanding the deemed rejection by Novelion as its sole equity holder.

   

  In furtherance of its duty to maximize value for its shareholders, the board of directors of Novelion, together with its management team and
    legal and financial advisors, is evaluating post-closing plans with respect to Novelion, including a potential wind-up of Novelion and a distribution of assets to shareholders, and recommendations related to same will be communicated to shareholders in
    due course.

   

  Aegerion Chapter 11 Cases

   

  As described above, to facilitate the Recapitalization, concurrent with the PFA and RSA, the Debtors filed for Chapter 11 protection. Aegerion
    will continue to operate in the ordinary course of business during the Chapter 11 cases. Novelion and non-U.S. Aegerion subsidiaries are not debtors in these Chapter 11 cases.

   

  Importantly, during the pendency of the Chapter 11 cases, Aegerion intends to:

   

  

  
    		•	
            continue to make available to patients its two approved therapies, JUXTAPID and MYALEPT;

          

  

  
    		•	
            continue to pay all trade and other ordinary course operating expenses during the course of the Chapter 11 cases and, upon consummation of the
              Recapitalization, repay 100% of any allowed trade claims; and

          

  

  
    		•	
            continue to pay and provide all ordinary course compensation and benefits to its existing employees, without any impairment, delay, adjustment
              or changes.

          

  

   

  Amryt Listing, Board of Directors and Management

   

  1 Note: The announcement will lead to suspension. Following publication of the admission document, the larger Amryt Group will be listed on the AIM market.

  
    6

    
      
 

  

  1 Amryt will continue to be listed on the AIM market of the
    London Stock Exchange. Following the Recapitalization, Amryt’s global headquarters will be in Dublin, Ireland and its U.S. headquarters will be in the Cambridge, Massachusetts area.

   

  Upon the closing of the Recapitalization, Amryt will designate three members to its board, including CEO Joe Wiley, and Athyrium and Highbridge
    will designate two members each to the board. The Chairperson of the Board will be appointed by Amryt and will be unaffiliated with Amryt, Novelion or Aegerion. Amryt will continue to be led by its executive team, which will be supplemented by certain
    Aegerion executives on both a transitional and permanent basis. Amryt executives have significant experience in the development and commercialization of rare disease products, including specific knowledge of Aegerion’s products through its licensing
    relationship for LOJUXTA® in the EU. In addition, certain Amryt executives, including Chief Medical Officer Mark Sumeray and Chief Commercial Officer David Allmond, are
    former members of Aegerion’s executive team.

   

  Closing Conditions and Timing

   

  The consummation of the Recapitalization is subject to a number of closing conditions, including approval by Amryt’s shareholders, approval of
    the independent Amryt shareholders in connection with the whitewash waiver granted by the UK Panel on Takeovers and Mergers, re-admission of Amryt’s ordinary shares for trading on AIM, confirmation of the Aegerion plan of reorganization by the
    Bankruptcy Court, and other customary closing conditions.

   

  The parties expect the transaction to close in the late third or early fourth calendar quarter of 2019.

   

  Advisors

   

  Evercore acted as financial advisor and Goodwin Procter LLP and Norton Rose Fulbright Canada LLP acted as legal advisors to Novelion. Moelis
    & Company LLC acted as financial and restructuring advisor, AP Services, LLC acted as financial advisor and chief restructuring officer, and Willkie Farr & Gallagher LLP acted as legal advisor to Aegerion. Ducera Partners LLC acted as financial
    advisor and Latham & Watkins LLP and King & Spalding LLP acted as legal advisors to the ad hoc group of convertible noteholders.

   

  Additional details, including copies of the PFA, RSA and other agreements, will be contained in Current Report on Form 8-K that Novelion intends
    to file with the Securities and Exchange Commission (www.sec.gov). Investors are encouraged to read the Current Report on Form 8-K and the agreements filed therewith, and the foregoing summary of the Recapitalization is qualified in its entirety by
    reference thereto.

  
     

    

    

  

   

  1 Note: The announcement will lead to suspension. Following publication of the admission document, the larger Amryt Group will be listed on the AIM
    market.

  
    7

    
      
 

  

  Conference Call Details

  

   

  

  Amryt Management will host a conference call for analysts today at 1330 BST (0830 EDT). Dial in details:

  Conference ID: 3387304

  From the UK/International: +44 (0) 2071 928000 I 0800 376 7922

  From Ireland: (01) 431 9615 I 1800 936148

  From the US: +1 631 510 7495 I 1 866 966 1396

   

  A recording of the call will be available from 18.30 (BST) today, please email ir@amrytpharma.com for access details.

   

  About Novelion Therapeutics

  Novelion, through its subsidiary Aegerion Pharmaceuticals, is a global biopharmaceutical company dedicated to developing and commercializing
    therapies that deliver new standards of care for people living with rare diseases. With a global footprint and an established commercial portfolio, including MYALEPT®
    (metreleptin) and JUXTAPID® (lomitapide), our business is supported by differentiated treatments that treat severe and rare diseases.

   

  About Amryt

  Amryt is a biopharmaceutical company focused on developing and delivering innovative new treatments to help improve the lives of patients with
    rare or orphan diseases.

   

  LOJUXTA® is an approved treatment for adult patients with the
    rare cholesterol disorder - Homozygous Familial Hypercholesterolaemia (“HoFH”). This disorder impairs the body’s ability to remove low density lipoprotein (“LDL”) cholesterol (“bad” cholesterol) from the blood, typically leading to abnormally high
    blood LDL cholesterol levels in the body from before birth - often ten times more than people without HoFH - and subsequent aggressive and premature narrowing and blocking of blood vessels. LOJUXTA® is indicated as an adjunct to a low-fat diet and other lipid-lowering medicinal products with or without LDL apheresis in adult patients with HoFH.

   

  Amryt is the marketing authorisation holder and has an exclusive license to sell LOJUXTA® across the European Economic Area, Middle East and North Africa, Switzerland, Turkey, Israel, Russia, the Commonwealth of Independent States and the non-EU Balkan states.

   

  Amryt’s lead development candidate, AP101, is a potential treatment for Epidermolysis Bullosa (“EB”), a rare and distressing genetic skin
    disorder affecting young children and adults for which there is currently no treatment. It is currently in Phase 3 clinical trials and recently reported positive unblinded interim efficacy analysis results and is anticipated will be fully enrolled by
    end of H2 2019. The European and US market opportunity for EB is estimated to be in excess of $1 billion.

   

  1 Note: The announcement will lead to suspension. Following publication of the admission document, the larger Amryt Group will be listed on the
    AIM market.

  
    8

    
      
 

  

  In March 2018, Amryt in-licenced a pre-clinical gene-therapy platform technology, AP103, which offers a potential treatment for patients with
    Recessive Dystrophic Epidermolysis Bullosa, a subset of EB, and is also potentially relevant to other genetic disorders.

   

  For more information on Amryt, please visit www.amrytpharma.com.

   

  Forward-Looking Statements and Risk Factors

  Certain statements in this press release constitute “forward-looking statements” and “forward-looking information” within the meaning of
    applicable laws and regulations, including U.S. and Canadian securities laws. Any statements contained herein which do not describe historical facts, including, among others, statements regarding beliefs about, and expectations for, plans to undertake
    a comprehensive restructuring of Aegerion Pharmaceuticals, the proposed transaction between Aegerion Pharmaceuticals and Amryt, including the key terms, expected ownership, benefits of the proposed transaction to Novelion’s and Aegerion’s stakeholders,
    expected closing and performance of the combined company, and the RSA are forward-looking statements which involve risks and uncertainties that could cause actual results to differ materially from those discussed in such forward-looking statements.

   

  Such risks and uncertainties include, among others, Novelion’s and Aegerion’s ability to meet immediate operational needs and obligations, as
    well as long-term obligations; Novelion’s and Aegerion’s ability to continue as a going concern; the possibility that the restrictions in and other terms of Aegerion’s loan arrangements could have a negative impact on Novelion’s business and its
    shareholders (whose interests may not be aligned, and may be in conflict, with those of Aegerion’s holders of convertible notes and other lenders); whether Aegerion will be able to successfully complete the Restructuring Transactions; that Novelion
    will not realize the benefits of the Restructuring Transactions; potential adverse effects of the Chapter 11 cases; the Debtors ability to obtain timely approval by the Court with respect to motions filed in the Chapter 11 cases; objections to the
    Restructuring Transactions, DIP Financing or other pleadings filed that could protract the Chapter 11 cases; the effects of the bankruptcy petitions on Novelion and on the interest of various constituents, including holders of Novelion’s common stock;
    the Court’s ruling in the Chapter 11 cases; risks associated with third party motions in the Chapter 11 cases; and increased administrative and legal costs related to the Chapter 11 process and other litigation and inherent risks involved in a
    bankruptcy process; Novelion’s ability to maintain its listing status on Nasdaq (the failure of which would constitute an event of default under Aegerion’s loan arrangements), as well as those risks identified in Novelion’s filings with the Commission,
    including under the heading “Risk Factors” in Novelion’s Annual Report on Form 10-K for the fiscal year ended December 31, 2018, and subsequent filings with the Commission, all of which are available on the Commission’s website at www.sec.gov.

   

  We caution you not to place undue reliance on any forward-looking statements, which speak only as of the date they are made. Except as required
    by law, we undertake no obligation to update or revise the

   

  1 Note: The announcement will lead to suspension. Following publication of the admission document, the larger Amryt Group will be listed on the
    AIM market.

  
    9

    
      
 

  

  information contained in this press release, whether as a result of new information, future events or circumstances or
    otherwise. Given the uncertainties, assumptions and risk factors associated with this type of information, including those described above, investors are cautioned that the information may not be an appropriate subject of reliance for other purposes.

   

  Investors and others should note that we communicate with our investors and the public using the Novelion website
    www.novelion.com, including, but not limited to, company disclosures, investor presentations and FAQs, Commission filings, press releases, public conference call
    transcripts and webcast transcripts. The information that we post on this website could be deemed to be material information. As a result, we encourage investors, the media and others interested to review the information that we post there on a regular
    basis. The contents of our website shall not be deemed incorporated by reference in any filing under the Securities Act of 1933, as amended. 

   

  CONTACT:

  Amanda (Murphy) Cray, Director, Investor Relations & Corporate Communications

  Novelion Therapeutics Inc.

  857-242-5024

  amanda.cray@novelion.com

   

  1 Note: The announcement will lead to suspension. Following publication of the admission document, the larger Amryt Group will be listed on the
    AIM market.

  
    10

    
      
 

  

  EXHIBIT A

   

  Plan

  
    
      
 

  

  EXHIBIT B

   

  Plan Funding Agreement

  
    
      
 

  

  EXHIBIT C

   

  DIP Credit Agreement

  
    
      
 

  

  EXHIBIT D

   

  Disclosure Statement

  
    
      
 

  

  EXHIBIT E

   

  Backstop Commitment Agreement

  
    
      
 

  

  EXHIBIT F

   

  Term Sheet for New Convertible Notes Indenture

  
    
      
 

  

  EXHIBIT G

   

  Term Sheet for New First Lien Secured Credit FacilityExhibit 10.3

     

    EXECUTION VERSION

     

    	 	
            AMRYT PHARMA PLC

          	 
	 	 	 
	 	
            HIGHBRIDGE MSF INTERNATIONAL LTD.

          	 
	 	 	 
	 	
            HIGHBRIDGE SCF SPECIAL SITUATIONS SPV, L.P.

          	 
	 	 	 
	 	
            1992 TACTICAL CREDIT MASTER FUND, L.P.

          	 
	 	 	 
	 	
            ATHYRIUM OPPORTUNITIES II ACQUISITION 2 LP

          	 
	 	 	 
	 	
            ATHYRIUM OPPORTUNITIES III ACQUISITION 2 LP

          	 
	 	 	 
	 	
            WHITEBOX RELATIVE VALUE PARTNERS, LP 

             

            WHITEBOX GT FUND, LP

          	 
	 	 	 
	 	
            WHITEBOX MULTI-STRATEGY PARTNERS, LP 

             

            PANDORA SELECT PARTNERS, LP

          	 
	 	 	 
	 	
            NINETEEN77 GLOBAL MULTI-STRATEGY ALPHA MASTER LIMITED

          	 
	 	 	 
	 	
            AND

          	 
	 	 	 
	 	
            NINETEEN77 GLOBAL CONVERTIBLE BOND MASTER LIMITED

          	 
	 	 	 
	 	 	 
	 	
            BACKSTOP SUBSCRIPTION AGREEMENT

          	 
	 	 	 
	 	 	 
	 	 	 
	 	 	 
	 	 	 
	 	
            99 Bishopsgate

          	 
	 	 	 
	 	
            London

          	 
	 	 	 
	 	
            EC2M3XF

          	 
	 	 	 
	 	
            www.1w.com

          	 
	 	 	 

     

    
      
        
 

    

    TABLE OF CONTENTS

    

    

    	
            Clause

          	 	
            Page

          
	 	 	 
	
            1.

          	
            DEFINITIONS AND INTERPRETATION

          	
            5

          
	 	 	 
	
            2.

          	
            CONDITIONS

          	
            8

          
	 	 	 
	
            3.

          	
            BACKSTOP SUBSCRIPTION OBLIGATION

          	
            9

          
	 	 	 
	
            4.

          	
            FEE

          	
            10

          
	 	 	 
	
            5.

          	
            BACK STOP PARTY WARRANTIES

          	
            10

          
	 	 	 
	
            6.

          	
            COMPANY WARRANTIES

          	
            10

          
	 	 	 
	
            7.

          	
            THIRD PARTY RIGHTS

          	
            11

          
	 	 	 
	
            8.

          	
            NOTICES

          	
            11

          
	 	 	 
	
            9.

          	
            TERMINATION

          	
            13

          
	 	 	 
	
            10.

          	
            MISCELLANEOUS

          	
            13

          
	 	 	 
	
            11.

          	
            ENTIRE AGREEMENT

          	
            14

          
	 	 	 
	
            12.

          	
            APPLICABLE LAW

          	
            14

          

     

    
      
        
 

    

    This Agreement (the “Agreement”) is made on July 10, 2019

     

    BETWEEN

     

    
      	(1)	
              AMRYT PHARMA PLC, a company incorporated in England and Wales with the registered number 05316808 and registered address at Dept 920a 196 High Road, Wood Green, London, England, N22 8HH (the “Company”);

            

    

     

    
      	(2)	
              HIGHBRIDGE MSF INTERNATIONAL LTD., an exempted company incorporated under the laws of the Cayman Islands with registered office at c/o Maples Corporate Services Limited, PO Box 309, Ugland House,
                Grand Cayman, KY1-1101, Cayman Islands (“MSF”);

            

    

     

    
      	(3)	
              HIGHBRIDGE SCF SPECIAL SITUATIONS SPV, L.P., an exempted limited partnership formed under the laws of the Cayman Islands and registered office at c/o Maples Corporate Services Limited, PO Box 309,
                Ugland House, Grand Cayman, KY1-1101, Cayman Islands (“SCF”);

            

    

     

    
      	(4)	
              1992 TACTICAL CREDIT MASTER FUND, L.P., an exempted limited partnership organized under the laws of the Cayman Islands and registered office at c/o Maples Corporate Services Limited, PO Box 309,
                Ugland House, Grand Cayman, KY1-1101, Cayman Islands (“TCF”, and together
                with MSF and SCF, “Highbridge”);

            

    

     

    
      	(5)	
              ATHYRIUM OPPORTUNITIES II ACQUISITION 2 LP, a limited partnership whose registered address is at 251 Little Falls Drive Wilmington, DE 19808-1674 (“Athyrium II”);

            

    

     

    
      	(6)	
              ATHYRIUM OPPORTUNITIES III ACQUISITION 2 LP, a limited partnership whose registered address is at 251 Little Falls Drive Wilmington, DE 19808-1674 (“Athyrium III”, and together with Athyrium III, “Athyrium”);

            

    

     

    
      	(7)	
              WHITEBOX RELATIVE VALUE PARTNERS, LP, a limited partnership whose registered address is at Jayla Place, Wickhams Cay 1, Road Town, Tortola, British Virgin Islands VG1110 (“Whitebox Relative”);

            

    

     

    
      	(8)	
              WIDTEBOX GT FUND, LP, a limited partnership whose registered address is at 251 Little Falls Drive, Wilmington, DE 19808 (“Whitebox GT”);

            

    

     

    
      	(9)	
              WHITEBOX MULTI-STRATEGY PARTNERS, LP, a limited partnership whose registered address is at Jayla Place, Wickhams Cay 1, Road Town, Tortola, British Virgin Islands VG1110 (“Whitebox Multi-Strategy”);

            

    

     

    
      	(10)	
              PANDORA SELECT PARTNERS, LP, a limited partnership whose registered address is at Jayla Place, Wickhams Cay 1, Road Town, Tortola, British Virgin Islands VG1110 (“Pandora”, and together with Whitebox Relative, Whitebox GT and Whitebox Multi-Strategy, “Whitebox”);

            

    

     

    
      	(11)	
              NINETEEN77 GLOBAL MULTI-STRATEGY ALPHA MASTER LIMITED, an exempted company incorporated under the laws of the Cayman Islands whose registered office address is at c/o Maples Corporate Services
                Limited, Ugland House, PO Box 309, Grand Cayman, KY1-1104, Cayman Islands (“Nineteen Multi-Strategy”); and

            

    

     

    
      	(12)	
              NINETEEN77 GLOBAL CONVERTIBLE BOND MASTER LIMITED, an exempted company incorporated under the laws of the Cayman Islands whose registered office address is at c/o Maples Corporate Services Limited,
                Ugland House, PO Box 309, Grand Cayman, KY1-1104, Cayman Islands (“Nineteen Bond,” and together with Nineteen
                Multi-Strategy, “O’Connor”).

            

    

     

    
      
        
 

    

    WHEREAS

     

    
      	(A)	
              The Company was incorporated on 20 December 2004 and its shares are admitted to trading on AIM, a market operated by the London Stock Exchange plc (“AIM”) and the Euronext Growth Market, a market operated by Euronext Dublin (“Euronext”).

            

    

     

    
      	(B)	
              The Company has entered into a restructuring support agreement (the “RSA”) and a plan funding agreement (the “Plan Funding Agreement”) pursuant to which, among others, it proposes to acquire the entire share capital of Aegerion Pharmaceuticals, Inc. (“Aegerion”).

            

    

     

    
      	(C)	
              The Company proposes to effect a scheme of arrangement under Part 26 of the Companies Act pursuant to which the holders of Ordinary Shares (the “Company Shareholders”) and the holders of options
                or warrants over Ordinary Shares (the “Company Options”) (and the holders of the Company Options, the “Company Optionholders”) will exchange the Ordinary Shares held by such Company Shareholders (and the Company Options held by such Company Optionholders) for new ordinary
                shares (or new options or warrants over such ordinary shares) issued by a newly incorporated company (“New Amryt TopCo”), together with one (1) CVR security for each Company Share (or Company Option), whereupon the Company shall procure that the rights and obligations
                of the Company under this Agreement shall be assumed by New Amryt TopCo (such scheme of arrangement, the “Scheme”).

            

    

     

    
      	(D)	
              In accordance with the RSA and subject to the terms and conditions set out in this Agreement, the Company proposes to raise $60 million (the “Capital Raise Amount”) by way of an offer of Ordinary Shares to Investors and Creditors at the Placing Price (the “Capital Raise”).

            

    

     

    
      	(E)	
              Pursuant to the terms of the Capital Raise:

            

    

     

    
      		(i)	
              the Creditor Placing Shares will be offered by the Company to the Creditors for an aggregate subscription price of $42 million at the Placing Price, and each Creditor will have the right, but not the obligation, to subscribe, for its pro rata share of the Creditor Placing Shares. To the extent that any Creditor Placing Shares remain unsubscribed, first, each Investor as determined by the Company may elect to subscribe for any
                unsubscribed Creditor Placing Shares and thereafter, to the extent that any Creditor Placing Shares remain unsubscribed, each Creditor who has previously subscribed for the Creditor Placing Shares will have the right, but not the
                obligation, to subscribe, for its pro rata share of the remaining Creditor Placing Shares (the “Creditor Placing”). To the extent that a subscription for
                Creditor Placing Shares by a Creditor is, or is deemed to be, an offer to purchase such Creditor Placing Shares and not an acceptance of an offer by the Company to purchase such Creditor Placing Shares, the Company agrees (1) to not
                unreasonably reject such offer/subscription and, in any event, (2) to treat each Creditor that offers to purchase Creditor Placing Shares, and each offer/subscription therefor, equally in all material respects; and

            

    

     

    
      		(ii)	
              the Investor Placing Shares will be offered by the Company to the Investors for an aggregate subscription price of $18 million at the Placing Price (the “Investor Placing”).

            

    

     

    
      	(F)	
              Each Back Stop Party will subscribe for, and the Company will allot and issue to each Back Stop Party, any Remaining Shares, if:

            

    

     

    
      		(i)	
              the Creditor Placing has not been fully subscribed (as described in Recital (E)(i)); and

            

    

     

    
      		(ii)	
              the Investor Placing has not been fully subscribed (as described in Recital (E)(ii)),

            

    

     

    on such terms, in such proportions, and in such manner, as prescribed in this Agreement.

     

    
      
        
 

    

    
      	(G)	
              An application will be made by the Company for all of the Placing Shares to be admitted to trading on AIM and Euronext.

            

    

     

    IT IS AGREED THAT:

     

    
      	1.	
              DEFINITIONS AND INTERPRETATION

            

    

     

    
      	1.1	
              In this Agreement (including the Recitals hereto), in addition to expressions already defined, the following expressions shall have the meanings set out below.

            

    

     

    “Accredited Investors” has the meaning specified in Rule 501(a) of Regulation D under the Securities Act;

     

    “Admission” means the admission of the Placing Shares to trading on AIM and Euronext becoming effective as provided under the AIM Rules and the Euronext Rules
      respectively;

     

    “Affiliate” has the meaning specified in Rule 501(b) of Regulation D under the Securities Act;

     

    “AIM” has the meaning set out in Recital (A);

     

    “AIM Rules” means the rules and guidance notes for AIM Companies issued by the LSE from time to time related to AIM traded securities and the operation of AIM;

     

    “Applications” means the applications made by (or on behalf of) the Company for Admission in the form prescribed by the LSE and the Euronext;

     

    “Articles of Association” means the articles of association of the Company from time to time;

     

    “Average USD to GBP Exchange Rate” means the average closing USD to GBP exchange rate as derived from the Bloomberg Composite Rate (taken each day as at 4 pm
      London time) over the five (5) Business Days falling immediately prior to the date of this Agreement;

     

    “Back Stop Party” means each of MSF, TCF, Athyrium II, Athyrium III, Whitebox Relative, Whitebox GT, Whitebox Multi-Strategy, Pandora, Nineteen77
      Multi-Strategy and Nineteen Bond, and collectively, the “Back Stop Parties”;

     

    “Board” means the board of directors of the Company from time to time;

     

    “Business Day” means any day other than a Saturday, Sunday or bank or public holiday in New York, London or Dublin;

     

    “Capital Raise” has the meaning set out in Recital (D);

     

    “Capital Raise Amount” has the meaning set out in Recital (D);

     

    “Companies Act” means the Companies Act 2006;

     

    “Company Options / Warrants” means any options or warrants
      issued by the Company which entitle the holder thereof to require the issuance of any Ordinary Shares by the Company on exercise of such options or warrants by the holder in accordance with the terms thereof;

     

    “Company Warranties” means the warranties given by the Company pursuant to Clause 6;

     

    

    “Conditions” has the meaning given in Clause 2.1; 

     

    
      
        
 

    

     

    “Creditors” means the publicly traded ultimate parent of Aegerion and, subject to all applicable regulatory restrictions and securities laws in any applicable
      jurisdiction, certain unsecured creditors of Aegerion;

     

    “Creditor Placing” has the meaning set out in Recital (E)(i);

     

    “Creditor Placing Shares” means Ordinary Shares offered pursuant to the Creditor Placing for an aggregate subscription price of $42 million;

     

    “CREST” means the system for the paperless settlement of trades in securities and the holding of securities in uncertificated form of which Euroclear is the
      Operator (as defined in the CREST Regulations);

     

    “CREST Regulations” means the Uncertificated Securities Regulations 2001 (SI 2001 No 3755), as amended;

     

    “CVR Instrument” means the deed poll in the agreed form to be entered into by New Amryt TopCo constituting the CVR securities to be issued to the Company
      Shareholders and the Company Optionholders;

     

    “Employee Share Option Plan” means the Company’s Employee Share Option Plan, as adopted 18 April 2016 and as amended 25 May 2017;

     

    “Encumbrance” means any pledge, charge, lien, mortgage, debenture, hypothecation, security interest, pre-emption right, option, claim, equitable right, power
      of sale, pledge, retention of title, right of first refusal or other third party right or security interest of any kind or an agreement, arrangement or obligation to create any of the above;

     

    “Euronext Rules” means the Euronext Growth Rules for Companies published by Euronext Dublin from time to time;

     

    “FSMA” means the Financial Services and Markets Act 2000;

     

    “Group” means in relation to each of the Back Stop Parties or the Company, as the context requires, any legal entity or person which from time to time
      controls, is controlled by or is under common control with that party, and “control”, in relation to a legal entity, means the power of a person to secure that the affairs of the legal entity are conducted in
      accordance with the wishes of that person (i) by means of the holding of shares, or the possession of voting power, in or in relation to that or any other legal entity; (ii) by means of the ability to direct the business of such legal entity (whether
      through its board or otherwise); or (iii) by virtue of any powers conferred by the constitutional or corporate documents, or any other document, regulating that or any other legal entity.

     

    “Investor Placing” has the meaning set out in Recital (E)(ii);

     

    “Investor Placing Shares” means Ordinary Shares offered pursuant to the Investor Placing for an aggregate subscription price of $18 million;

     

    “Investors” means such persons (whether existing Company Shareholders or otherwise) as the Company may procure for the purposes of subscribing for the
      Investor Placing Shares or the unsubscribed portion of the Creditor Placing;

     

    “Long-Stop Date” means the Outside Date as defined in the Plan Funding Agreement or any such later date as may be agreed between the parties in writing;

     

    
      
        
 

    

    “LSE” means the London Stock Exchange plc;

     

    “Notification Form” has the meaning set out in Clause 3.2;

     

    “Ordinary Shares” means the ordinary shares in the capital of the Company in issue from time to time;

     

    “Payment Amount” has the meaning given in Clause 3.3;

     

    “Placing Price” means the placing price at which Placing Shares will be offered for subscription calculated in accordance with the following formula:

    

    

    	 	
            $60,000,000

          	
             x A

          
	 	
            Placing Shares

          

     

    where:

     

    “A” means the Average USD to GBP Exchange Rate;

     

    “Closing Shares” has the meaning given in the Plan Funding Agreement;

     

    “Placing Shares” means such number of Ordinary Shares to be allotted and issued pursuant to the Capital Raise, calculated in accordance with the following
      formula:

     

    	
            Capital Raise Ownership Percentage x  

          	
            Pre – Money Shares

          
	
            (1 – Capital Raise Ownership Percentage)

          

     

    where:

     

    “Capital Raise Ownership Percentage” is calculated using the following formula:

    

    

    	 	
            $60,000,000

          	 
	 	
            (($190,700,000 + $120,000,000) X 0. 8 + $60,000,000)

          	 

     

    “Pre-Money Shares” means the number of Ordinary Shares and Company Options and Warrants (other than Company Options issued pursuant to the Employee Share
      Option Plan) in issue immediately prior to the issue of the Placing Shares, including the Closing Shares;

     

    where, for the avoidance of doubt, the number of Placing Shares shall be equal to the Capital Raise Ownership Percentage (which is approximately 19.4452%) of the sum of: (i) the Pre-Money Shares; and
      (ii) the Placing Shares.

     

    “Regulation S” means Regulation S under the Securities Act;

     

    “Relevant Percentage” means in the case of MSF, 10.5 per cent., in the case of TCF, 9.8 per cent., in the case of SCF, 5.4 per cent., in the case of Athyrium
      II, 47 per cent., in the case of Athyrium III, 11 per cent, in the case of Whitebox Relative 1.4 per cent., in the case of Whitebox GT 0.1 per cent., in the case of Whitebox Multi-Strategy 1.4 per cent., in the case of Pandora 0.6 per cent., in the
      case of Nineteen Multi-Strategy 12.3 per cent., and in the case of Nineteen Bond, 0.5 per cent.;

     

    “Remaining Creditor Placing Shares” means such number of Creditor Placing Shares that have not been subscribed for pursuant to the Creditor Placing;

     

    
      
        
 

    

    
      “Remaining Investor Placing Shares” means such number of Investor Placing Shares that have not been subscribed for pursuant to the Investor Placing;

    

     

    “Remaining Shares” means the Remaining Investor Placing Shares and the Remaining Creditor Placing Shares;

     

    “Scheme Document” means the document to be sent to the Company Shareholders containing, amongst other things, the Scheme and the notices convening the
      meetings of the the Company Shareholders to consider and, if thought fit, approve the Scheme;

     

    “Securities Act” means the United States Securities Act of 1933, as amended;

     

    “Subscription Date” means the date given for the allotment and issue of the Remaining Shares as notified to each Back Stop Party by the Company in the
      Notification Form, provided that this date shall be no earlier than two (2) Business Days following the date of the Notification Form; and

     

    “Takeover Code” means the UK City Code on Takeovers and Mergers;

     

    “United States” has the meaning assigned thereto in Regulation S under the Securities Act.

     

    
      	1.2	
              References in this Agreement to any act, statute or statutory provision include references to any such provision as amended, re-enacted or replaced from time to time and any former statutory provision replaced (with or without
                modification) by the provision referred to.

            

    

     

    
      	1.3	
              References in this Agreement to the singular include references to the plural and vice versa and references to any gender shall include references to all other genders.

            

    

     

    
      	1.4	
              Headings in this Agreement are inserted for convenience only and shall not affect the interpretation of this Agreement or any part thereof.

            

    

     

    
      	1.5	
              The expressions “subsidiary” shall have the meaning given by the Companies Act and the expression “subsidiary” shall be deemed to include “subsidiary undertakings” as defined by the Companies Act.

            

    

     

    
      	1.6	
              References to “$” or “US Dollars” are to the lawful currency of the United States.

            

    

     

    
      	1.7	
              References to “£” are to the lawful currency of the United Kingdom.

            

    

     

    
      	2.	
              CONDITIONS

            

    

     

    
      	2.1	
              The obligations of each Back Stop Party under this Agreement are in all respects conditional on the satisfaction (or waiver, as the case may be) of the following (the “Conditions”):

            

    

     

    
      		(a)	
              the Applications and all other documents required to be submitted with the Applications, being delivered to the LSE and Euronext Dublin respectively, no later than 8.00 am (London time) two (2) Business Days prior to the Subscription
                Date;

            

    

     

    
      		(b)	
              Admission becoming effective by no later than 8.00 a.m. (London time) on the Subscription Date;

            

    

     

    
      		(c)	
              the rights attaching to the Ordinary Shares under the articles of association of the Company as at the date of execution of the RSA not having been altered in any respect;

            

    

     

    
      
        
 

    

    
      		(d)	
              the approval of the “Rule 9 whitewash waiver” shareholder resolution (the “whitewash Resolution”) by the independent Company Shareholders for the purposes
                of the Takeover Code;

            

    

     

    
      		(e)	
              resolutions of the Company’s shareholders having been passed to authorise and approve the issue and allotment of the Placing Shares pursuant to the terms of this Agreement;

            

    

     

    
      		(f)	
              the Company having fully performed its material obligations under this Agreement in all respects to the extent that such obligations are to be performed prior to Admission;

            

    

     

    
      		(g)	
              none of the Company Warranties being untrue or inaccurate or misleading in any respect at any time between the date of this Agreement and Admission and no fact or circumstance having arisen which would render any of the Company
                Warranties untrue or inaccurate or misleading if repeated as at Admission;

            

    

     

    
      		(h)	
              with respect to the Chapter 11 bankruptcy case for Aegerion, there having been entered a final order confirming the plan of reorganisation filed in such case (the “Plan”),
                in form and substance reasonably satisfactory to the Back Stop Parties and to the Company (in each case acting in good faith) and the “Effective Date”, as set forth in the Plan, having
                occurred, and all conditions precedent to the occurrence of such Effective Date having been satisfied (or waived by the Backstop Parties).

            

    

     

    
      	2.2	
              The Back Stop Parties, acting unanimously and in their sole discretion, may waive in whole or in part all or any of the Conditions by notice in writing given to the Company.

            

    

     

    
      	2.3	
              If any of the Conditions is not fulfilled or waived on or before the Long-Stop Date, the Back Stop Parties shall be entitled to treat this Agreement as terminated on the basis set out in Clause 9.

            

    

     

    3.          BACKSTOP SUBSCRIPTION OBLIGATION

     

    
      	3.1	
              Each Back Stop Party hereby severally, and neither jointly, nor jointly and severally, undertakes to the Company to subscribe for itself (in its own name or as it may direct, provided that the subscription is compliant with the Whitewash
                Resolution) its Relevant Percentage of: (a) the Remaining Creditor Placing Shares; and (b) the Remaining Investor Placing Shares, in each case, at the Placing Price.

            

    

     

    
      	3.2	
              The Company shall notify each Back Stop Party of the number of Remaining Shares that they are required to subscribe for and the Subscription Date by giving notice in writing to the Back Stop Parties in the form appended hereto in the
                Schedule (the “Notification Form”), such Notification Form to be served not later than two (2) Business Days prior to the Subscription Date, and each Back
                Stop Party shall subscribe for such number of Securities in accordance with Clause 3.4.

            

    

     

    
      	3.3	
              Subject to Clause 4.2, if the Company requires the Back Stop Parties to subscribe for any Remaining Shares and delivers a Notification Form in accordance with Clause 3.2, each Back Stop Party shall pay to the Company an amount equal to
                the Placing Price multiplied by the number of Remaining Shares subscribed by such Back Stop Party in accordance with Clause 3.4 (the “Payment Amount”).

            

    

     

    
      	3.4	
              On the Subscription Date, each Back Stop Party shall subscribe for, and the Company shall allot and issue to the Back Stop Party with such rights as set out in the Articles of Association, fully paid, such number of Remaining Shares as
                is notified in the Notification Form, provided that the maximum number of Remaining Shares to be subscribed for by each Back Stop Party shall be subject to the limits set out in Clause 3.1.

            

    

     

    
      
        
 

    

    
      	3.5	
              Subject to clause 4.2, on the Subscription Date: (a) the Company shall procure that the Remaining Shares subscribed by each Back Stop Party are credited to the CREST stock accounts (or depositary accounts) notified by the Back Stop
                Parties in writing to the Company no later than one (1) Business Day prior to the Subscription Date; and (b) each Back Stop Party undertakes to pay in cash to the Company their respective Payment Amount.

            

    

     

    
      	3.6	
              Settlement of the issue of the Remaining Shares shall be performed on a delivery versus payment (DVP) basis.

            

    

     

    
      	4.	
              FEE

            

    

     

    
      	4.1	
              In consideration of the undertakings given herein by the Back Stop Patties and conditional upon the subscription for the Placing Shares occurring on the Subscription Date, the Company shall pay to the Back Stop Parties by way of
                commission a fee equal to five (5) per cent. of the Capital Raise in an aggregate amount of $3,000,000 (the “Fee”). The Fee payable under this Clause 4.1 shall be paid in cash in same day available
                funds on or before the Subscription Date or, if there are no Remaining Shares, the Effective Date (as defined in the Plan Funding Agreement). The Fee shall be allocated and paid by the Company to each of the Back Stop Parties in accordance
                with each Back Stop Party’s Relevant Percentage.

            

    

     

    
      	4.2	
              Without prejudice to their right to receive the Fee directly from the Company, the Back Stop Parties shall be entitled and are authorised to deduct some or all of the amounts due and payable pursuant to Clause 4.1 from the Payment Amount
                payable under Clause 3.3, if the Company has not paid such amounts prior to the date on which each Back Stop Party is required to make such payment.

            

    

     

    
      	5.	
              BACK STOP PARTY WARRANTIES

            

    

     

    
      	5.1	
              Each Back Stop Party severally, and not jointly, or jointly and severally, hereby warrants and undertakes to the Company on the date of this Agreement and on the Subscription Date that:

            

    

     

    
      		(a)	
              it is an Accredited Investor;

            

    

     

    
      		(b)	
              this Agreement has been duly authorised, executed and delivered by the Back Stop Party and constitutes a valid and legally binding agreement of the Back Stop Party enforceable against the Back Stop Patty in accordance with its terms; and

            

    

     

    
      		(c)	
              it is authorised and entitled to subscribe for the Remaining Shares under the laws of all relevant jurisdictions that apply to it, has complied and will fully comply with all such laws, and has obtained all applicable consents which may
                be required, in relation to the subscription of the Remaining Shares.

            

    

     

    
      	6.	
              COMPANY WARRANTIES

            

    

     

    
      	6.1	
              The Company hereby warrants and undertakes to the Back Stop Patties on the date of this Agreement and on the Subscription Date that:

            

    

     

    
      		(a)	
              the Company is a company duly incorporated and validly existing under the laws of England and Wales;

            

    

     

    
      		(b)	
              this Agreement has been duly authorised, executed and delivered by the Company and constitutes a valid and legally binding agreement of the Company enforceable against the Company in accordance with its terms;

            

    

     

    
      		(c)	
              save for the Conditions referred to at Clauses 2.1(a) to (e), the execution, delivery and performance by the Company of its obligations under this Agreement will not require the Company to obtain any consent, waiver or approval of, or
                give any notice to or make

            

    

     

    
      
        
 

    

    any registration or filing with, any governmental, regulatory, other authority or other person which has not been obtained or made at the date of this Agreement on a basis both unconditional and
      which cannot be revoked;

     

    
      		(d)	
              the Remaining Shares will, when issued, have been validly authorised and issued, and, following payment of the Payment Amount (less any amounts deducted under Clause 4.2), be fully paid up and no further amounts will be payable to the
                Company in respect of their issue; and

            

    

     

    
      		(e)	
              when issued, there will be no Encumbrance on, over or affecting any of the Remaining Shares nor will there be any commitment by it to give or create any such Encumbrance, and, so far as the Company is aware, no person has claimed to be
                entitled to any such Encumbrance.

            

    

     

    
      	6.2	
              Any warranties and representations given by the Company to the Investors and/or the Creditors as part of the Capital Raise shall also be deemed given to the Back Stop Parties mutatis mutandis in
                relation to the subscription of the Remaining Shares on the date of this Agreement and on the Subscription Date.

            

    

     

    
      	7.	
              THIRD PARTY RIGHTS

            

    

     

    
      	7.1	
              Any person who is not a party to this Agreement shall have no right under the Contracts (Rights of Third Parties) Act 1999 to enforce any terms of this Agreement, but this does not affect any right or remedy of a third party which exists
                or is available apart from that act.

            

    

     

    
      	8.	
              NOTICES

            

    

     

    
      	8.1	
              All notices given hereunder shall be in writing and signed by or on behalf of the party giving it and shall be served by delivering it by hand or sending it by pre-paid envelope by recorded delivery or registered post or by email to the
                party due to receive it, at its address or email address set out in this Agreement or to such other address or email address as are last notified in writing to the parties.

            

    

     

    The Companv:

     

    Amryt Pharma plc

      90 Harcourt Street

      Dublin 2

      Ireland

     

    For attention of: Joe Wiley

     

    Email: joe.wiley@amrytpharma.com

     

    With a copy to:

     

    Gibson, Dunn & Crutcher LLP

      200 Park Avenue

      New York

      NY 10166

     

    For the attention of: George P.Stamas, Esq.; William B. Sorabella, Esq.; Robert Klyman, Esq.; and Mathhew J. Williams, Esq.

     

    
      
        
 

    

    Email: GStamas@gibsondunn.com; WSorabella@gibsondunn.com;

      RKlyman@gibsondunn.com; and MJWilliams@gibsondunn.com

     

    Highbridge

     

    Highbridge Capital Management LLC

      40 W 57th St # E

      New York, NY 10019

      United States of America

     

    For attention of: Damon Meyer and Jonathan Segal

      Email: Damon.Meyer@highbridge.com; and Jonathan.Segal@highbridge.com

     

    Athyrium

     

    Athyrium Capital Management, LP

      530 5th Ave,

      New York, NY 10036

     

    For attention of: Hondo Sen and Samuel Helfaer

      Email: hsen@,athyrium.com; and SHelfaer@athyrium.com

     

    Whitebox

     

    Whitebox Advisors LLC

      3033 Excelsior Boulevard, Suite 300

      Minneapolis, MN 55416

     

    For attention of: Ruth Andrews Scott Specken

      Email: Aruth@whiteboxadvisors.com; and SSpecken@whiteboxadvisors.com

     

    O’Connor

     

    UBS O’Connor LLC

      UBS Tower

      1 North Wacker Drive, 32nd Floor

      Chicago, IL 60606

     

    For attention of: Andy Martin and Andrew Hollenbeck

      Email: andy.martin@ubs.com; and andrew.hollenbeck@ubs.com

     

    
      	8.2	
              Such notice shall be deemed served, if delivered by hand, at the time of delivery, in the case of recorded delivery or registered post, two Business Days after posting, or if sent by email, at the time of transmission, provided in each
                case that the time of deemed service shall be a Business Day failing which the time of deemed service shall be the commencement of the next Business Day.

            

    

     

    
      	8.3	
              In proving service of any notice it shall be sufficient to prove:

            

    

     

    
      		(a)	
              in the case of a letter, that the letter was delivered by hand or was properly stamped and addressed and sent by recorded delivery or registered post; and

            

    

     

    
      		(b)	
              in the case of an email, that it was duly transmitted provided the sender obtains confirmation of transmission.

            

    

     

    
      
        
 

    

    
      	9.	
              TERMINATION

            

    

     

    
      	9.1	
              This Agreement will terminate upon the earlier of:

            

    

     

    
      		(a)	
              if the Conditions have not been fulfilled (or waived, as the case may be) by the Long-Stop Date, by either the Company or the Back Stop Parties giving notice in writing to the other parties on or after the Long-Stop Date;

            

    

     

    
      		(b)	
              the termination of the RSA, other than any termination solely on account of the action or inaction of the Back Stop Parties in violation of the RSA; and

            

    

     

    
      		(c)	
              the mutual written agreement between the Company, Highbridge, Athyrium, Whitebox, and O’Connor,

            

    

     

    subject to the rights of the parties accrued at the date of such termination, which rights shall remain in force; provided, however, that the provisions of Clauses 6.2, 8, 9, 11, and 12 shall survive
      the termination of this Agreement.

     

    
      	9.2	
              In the event of termination under this Clause 9, all offers to subscribe any Remaining Shares shall be cancelled, and the Company shall have no obligation to issue and deliver, and the Back Stop Parties shall have no obligation to
                subscribe for, any Remaining Shares.

            

    

     

    
      	9.3	
              No party shall have any right to rescind this Agreement and the only termination rights shall be those set out in Clause 9.1.

            

    

     

    
      	10.	
              MISCELLANEOUS

            

    

     

    
      	10.1	
              Time shall be of the essence of this Agreement with respect to all dates and time periods set forth or referred to in this Agreement.

            

    

     

    
      	10.2	
              No party to this Agreement may assign any of their respective rights under this Agreement to a party which is not a member of its Group without the prior written consent of the other parties. This Agreement shall be binding on and enure
                for the benefit of each parties’ successors in title. No provision of this Agreement may be varied without the prior written consent of all parties to this Agreement.

            

    

     

    
      	10.3	
              At any time after the date of this Agreement, each party shall, and shall use reasonable endeavours to procure that any necessary third party shall at the cost of that party, execute all such documents and do all such acts and things as
                the other party may reasonably require for the purpose of giving full effect to the provisions of this Agreement.

            

    

     

    
      	10.4	
              All payments by the Company under this Agreement shall be paid without set-off or counterclaim, and free and clear of and without deduction or withholding for or on account of, any present or future taxes.

            

    

     

    
      	10.5	
              All of the obligations of the Back Stop Parties under this Agreement are several and not joint or joint and several and none of the Back Stop Parties shall have any obligation or liability to any Party or any other person as a result of
                any failure or breach of the obligations of any other such person under this Agreement.

            

    

     

    
      	10.6	
              The Back Stop Parties irrevocably appoint GLAS Agency of 45 Ludgate Hill, London EC4M 7JU (Attention: Paul Cattennole, TES@glas.agency, +44 20 3597 2940) as their agent to receive on their behalf in England or Wales service of any
                proceedings under Clause 12.2. Such service shall be deemed completed on delivery to such agent (whether or not it is forwarded to and received by the Back Stop Parties) and shall be valid until such time as New Amryt Topco has received
                prior written notice that such agent has ceased to act as agent. If for any reason such

            

    

     

    
      
        
 

    

    agent ceases to be able to act as agent or no longer has an address in England or Wales, the Back Stop Parties shall forthwith appoint a substitute acceptable to the Back Stop Parties and deliver to
      New Amryt Topco the new agent’s name and address within England and Wales.

     

    
      	10.7	
              The parties acknowledge and agree that on and from the effectiveness of the Scheme, New Amryt TopCo shall assume all rights and obligations of the Company hereunder, and shall be substituted for the Company as a party to this Agreement
                for all purposes hereunder, mutatis mutandis. The parties shall, and the Company shall procure that New Amryt TopCo shall, enter into all such agreements and execute all such further contracts as are required to give effect to this Clause
                10.7. Any references in this Agreement to the Company Shareholders, the Company and its corporate details or place of incorporation shall be construed accordingly.

            

    

     

    
      	10.8	
              If any ruling is made by the UK Panel on Takeovers and Mergers (the “Panel”) that any provision of this Agreement is not permitted by the Takeover Code,
                such provision shall be given no effect. The parties shall use reasonable efforts to replace such provision with a valid and enforceable provision which is acceptable to the Panel and carries out, as closely as possible, the intentions of
                the patties.

            

    

     

    
      	11.	
              ENTIRE AGREEMENT

            

    

     

    
      	11.1	
              This Agreement, and any other agreement entered into in connection with this Agreement, constitute the entire and only agreements between the parties relating to the subject matter of this Agreement.

            

    

     

    
      	11.2	
              If any provision of this Agreement shall be held to be illegal, invalid or unenforceable, in whole or in part, such provision or relevant part shall be deemed not to form part of this Agreement but the legality, validity and
                enforceability of the remainder of this Agreement shall not be affected.

            

    

     

    
      	12.	
              APPLICABLE LAW

            

    

     

    
      	12.1	
              This Agreement shall be governed by and construed in accordance with English law.

            

    

     

    
      	12.2	
              Each of the parties hereby submits to the non-exclusive jurisdiction of the courts of England and Wales in relation to any matters arising out of this Agreement. This Clause 12 shall be without prejudice to the right of any patty to
                bring proceedings in any other jurisdiction for the purpose of enforcement or execution of any judgment or other settlement in any other court.

            

    

     

    
      	12.3	
              Notwithstanding Clause 12.2, each Back Stop Party shall retain the right to join the Company to proceedings in connection with the Capital Raise, the transactions contemplated by this Agreement or any dispute, to which such Back Stop
                Party is a party, in any other court (or courts) of competent jurisdiction.

            

    

     

    
      
        
 

    

    IN WITNESS of which the parties have signed this Agreement on the date set out above.

     

    AMRYT PHARMA PLC

     

    	
            By:

          	/s/ Rory Nealon 	 
	
            Name: Rory Nealon

          	 
	
            Title: Director

          	 

     

    
      
        
 

    

    ATHYRIUM OPPORTUNITIES II ACQUISTION 2 LP

     

    By: Athyrium Opportunities Associates II LP, its general partner

     

    By: Athyrium GP Holdings LLC, its general partner

     

    	
            By:

          	
            /s/ Andrew C. Hyman

          	 
	
            Name:

          	
            Andrew C. Hyman

          	 
	
            Title:

          	
            Authorized Signatory

          	 

     

    
      
        
 

    

    ATHYRIUM OPPORTUNITIES III ACQUISTION 2 LP

     

    By: Athyrium Opportunities Associates III LP, its general partner

     

    By: Athyrium Opportunities Associates III GP LLC, its general partner

     

    	
            By:

          	
            /s/ Andrew C. Hyman

          	 
	
            Name:

          	
            Andrew C. Hyman

          	 
	
            Title:

          	
            Authorized Signatory

          	 

     

    
      
        
 

    

    HIGHBRIDGE MSF INTERNATIONAL LTD.

     

    	
            By:

          	
            /s/ Jonathan Segal

          	 
	
            Name: Jonathan Segal

          	 
	
            Title: Managing Director

          	 

     

    
      
        
 

    

    1992 TACTICAL CREDIT MASTER FUND, L.P.

     

    	
            By:

          	
            /s/ Jonathan Segal

          	 
	
            Name: Jonathan Segal

          	 
	
            Title: Managing Director

          	 

     

    HIGHBRIDGE SCF SPECIAL SITUATIONS SPV, L.P.

     

    	
            By:

          	
            /s/ Jonathan Segal

          	 
	
            Name: Jonathan Segal

          	 
	
            Title: Managing Director

          	 

     

    
      
        
 

    

    NINETEEN77 GLOBAL MULTI-STRATEGY ALPHA MASTER LIMITED

     

    By: UBS O’Connor LLC, its investment adviser

     

    

    	
            By:

          	
            /s/ James Del Medico

          	 
	
            Name: James Del Medico

          	 
	
            Title: Executive Director

          	 

     

    	
            By:

          	
            /s/ Connor Burke

          	 
	
            Name: Connor Burke

          	 
	
            Title: Director

          	 

     

    
      
        
 

    

    NINETEEN77 GLOBAL CONVERTIBLE BOND MASTER LIMITED

     

    By: UBS O’Connor LLC, its investment adviser

     

    	
            By:

          	
            /s/ James Del Medico

          	 
	
            Name: James Del Medico

          	 
	
            Title: Executive Director

          	 

     

    	
            By:

          	
            /s/ Connor Burke

          	 
	
            Name: Connor Burke

          	 
	
            Title: Director

          	 

     

    
      
        
 

    

    WHITEBOX RELATIVE VALUE PARTNERS, LP

      By: Whitebox Advisors LLC its investment manager

     

    	
            By:

          	
            /s/ Luke Harris

          	 
	
            Name: Luke Harris

          	 
	
            Title: Deputy General Counsel

          	 

     

    
      
        
 

    

    WHITEBOX GT FUND, LP

      By: Whitebox Advisors LLC its investment manager

     

    	
            By:

          	
            /s/ Luke Harris

          	 
	
            Name: Luke Harris

          	 
	
            Title: Deputy General Counsel

          	 

     

    
      
        
 

    

    WHITEBOX MULTI-STRATEGY PARTNERS, LP

      By: Whitebox Advisors LLC its investment manager

     

    	
            By:

          	
            /s/ Luke Harris

          	 
	
            Name: Luke Harris

          	 
	
            Title: Deputy General Counsel

          	 

     

    
      
        
 

    

    PANDORA SELECT PARTNERS, LP

      By: Whitebox Advisors LL its investment manager

     

    	
            By:

          	
            /s/ Luke Harris

          	 
	
            Name: Luke Harris

          	 
	
            Title: Deputy General Counsel

          	 

     

    
      
        
 

    

    SCHEDULE

      FORM OF NOTIFICATION FORM

     

    [Back Stop Party]

      [Address]

     

    (the “Back Stop Party”, “you”)

     

    [l]

     

    Dear Sirs

     

    We refer to the backstop subscription agreement dated [l] 2019, and any valid amendments thereto, between, inter alia, Amryt Pharma PLC and the Back Stop Party (the “Agreement”).

     

    The Company hereby declares and undertakes in favour of the Back Stop Party that all of the Conditions have been satisfied or validly waived in accordance with the terms of the Agreement.

     

    In accordance with the Agreement, we hereby notify you that you are required to subscribe for [l] Remaining Shares for an aggregate subscription price of
      $[l], and such Remaining Shares shall be issued to you on [l] (the “Subscription Date”).

     

    Payment for, and the allotment and issue of, the [l] Remaining Shares will be effected in accordance with the provisions of Clauses 3 and 4.2 to the
      Agreement.

     

    Defined terms used in this letter have the same meaning as set out in the Agreement unless defined herein.

     

    Yours faithfully,

     

    For and on behalf of

      AMRYT PHARMA PLC

     

    By:

      Name:

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