Sehschärfe
The syndrome is frequently noticed first in children around six months of age by their photophobic activity or their nystagmus. The nystagmus becomes less noticeable with age but the other symptoms of the syndrome become more relevant as school age approaches. Visual acuity and stability of the eye motions generally improve during the first six to seven years of life – but remain near 20/200. The congenital forms of the condition are considered stationary and do not worsen with age.