Dr. Denise Ney, a researcher in nutritional sciences, follows over 160 patients with phenylketonuria (PKU). PKU is a genetic disorder caused by deficiency of an enzyme that converts the essential amino acid phenylalanine to tyrosine. To prevent brain damage and cognitive impairment those with PKU must follow a lifelong, low-phenylalanine diet through restriction of their diet and the use of a bitter tasting amino acid formula. Track my stack Dr. Ney provides education on the importance of nutritional management of PKU, and under the auspices of the Orphan Grants program is conducting clinical studies to establish the acceptability and safety of unique foods made with whey protein for PKU. For more information visit www.fda.gov/orphan.