The sites of predilection are extensors of 4 limbs, buttocks and face. Intact vesicles seldom seen since they are ruptured by self scratching. Lesions heal with no scarring. Screening for the presence of coeliac disease. After starting the treatment, symptoms should subside within 48 hours and rash should be cleared up within days.
Side effects are haemolytic anaemia, methaemoglobulinaemia.
Referring to dietician if required. Dietary restriction is not easy to follow. Prognosis Spontaneous remission rate is low. This is a extremely rare group of hereditary blistering disorders which are characterized by blisters and erosions resulting from trivial trauma. Blisters occur soon after birth and mainly concentrate on bony prominence of 4 limbs.