The physical examination reveals certain characteristics of the pulse and can also reveal regurgitation of the tricuspid and pulmonary valves. The treatment of this disease is often unsatisfactory. The resistance of the pulmonary blood vessels increases dramatically on exercise, so patients are advised not to exercise or carry out any activity which demands increased physical stress. The outlook is generally not good and although some patients survive as long as ten years, many die within two to three years of diagnosis. The cause of death is usually right ventricular failure or sudden death.
Sudden death is generally a late feature of the disease.
You should call on your GP to assist you with any specific medical problems you may be experiencing. Medicine is an ever-changing science. As new research and clinical experience broadens our knowledge, changes in treatment and drug therapy are required. The authors have checked with sources believed to be reliable in their efforts to provide information that is complete and generally in accord with the standards accepted at the time of publication. Readers are encouraged to confirm the information contained herein with other sources.