Patients and families should consult their physician for details and prognosis. New surgical techniques have improved survival significantly. In the past, the prognosis for these patients was very poor and most of the children died early. Initially they are treated with positive inotropic agents such as digitalis. Prostaglandin E can be given to halt the closure of the patent ductus arteriosus.
Surgical treatment is difficult and extensive and has to be done in steps.
The best known procedure is so called Norwood operation.