Usher Syndrome is a genetic disorder with hearing loss and a progressive loss of vision called retinitis pigmentosa.
Some individuals also have balance problems.
I Usher Syndrome have a profound hearing loss in all frequencies and are considered to be deaf from birth. These persons usually have poor speech. Persons with profound hearing loss may be candidates for cochlear implants. Individuals with Type II Usher Syndrome have a moderate hearing loss in the lower frequencies. In the higher frequencies it is severe or profound.