It forms the basis for Sillence classification. Dentinogenesis imperfecta is absent. Dentinogenesis imperfecta is present. Kyphoscoliosis Hearing loss Premature arcus senilis Easy bruising Mild short stature Type II Dentinogenesis imperfecta Blue sclera may or may not be present. Hearing loss is not applicable to this type.
Sclera is of variable hue.
No hearing loss Half of the cases have in-utero fractures. The remaining half of cases have fractures in neonatal period. Dentinogenesis imperfecta is present. In utero fractures are rare. Fractures begin in infancy.