Cystic fibrosis , lung infections, and bronchial tumors are some predisposing factors. Symptoms may develop gradually after an infection, and become progressively worse. Symptoms vary widely with the individual. The incidence is 1 in 10,000 people. This disease may also alter the results of a chest MRI .
Treatment is aimed at controlling infections, secretions, airway obstruction , and complications.
Regular, daily postural drainage to remove bronchial secretions is a routine part of treatment. A respiratory therapist can teach postural drainage and effective coughing exercises to affected people and their families. A well balanced diet and adequate fluid intake of at least 8 glasses of fluid a day are very important for health maintenance. Antibiotics , bronchodilators, and expectorants are often prescribed for infections. Childhood vaccinations and yearly influenza vaccine help reduce the prevalence of some infections.