The lesions are usually unilateral but bilateral involvement may occur. Soft tissue papules, tumors, and plaques of the eyelids and bulbar conjunctiva. Soft tissue papules, tumors, and plaques. Lipomatosis of the meninges and parts of the nervous system usually co-occurs with lipomas of the skin. Associated disorders may include lipomatous lesions of the middle cranial fossa, lipoangiomatous meningeal malformations, calcification of the brain, polymicrogyria, hydrocephaly, and subarachnoid calcifications.
Seizures are a constant feature.