DORVs are usually accompanied by one of a number of ventricular septal defects. Sometimes the baby will have other associated cardiac defects.
Symptoms tend to occur early in life, often within days of birth.
The two major symptoms are congestive heart failure and cyanosis. In some cases, cyanosis can become severe because of reduced pulmonary blood flow. The goal of the surgical treatment of DORV is a complete anatomic repair. The left ventricle is connected to the aorta, the right ventricle is connected to the pulmonary artery and the VSD is closed. Usually a complete repair is undertaken at as early an age as possible.