Treatment consists of operative resection of the ectasia and anastomosis of the proximal duct to the jejunum. Caroli's disease is a cystic dilatation of intrahepatic bile ducts complicated by stone formation, recurrent cholangitis, and formation of hepatic abscesses. It is rare and may be associated with cystic disease of the kidney and other organs. A syndrome of chronic abdominal pain after cholecystectomy with features of partial common duct obstruction has been attributed to dysfunction of Oddi's sphincter. Endoscopic sphincterotomy may relieve pain in patients with this syndrome.
Treatment is directed toward the primary malignant disorder.
Intractable itching and jaundice may be alleviated by transhepatic or endoscopic insertion of an endoprosthesis through the obstruction.