Most tumors have excellent prognosis and can be treated by surgical removal.
Grossly the tumor appears as a intrabronchial polypoid mass which measures about 3-4 cm. The tumor is highly vascular and may bleed. Microscopically, the tumor is composed of nests of small, uniform, round cells. In some instances, the tumor cells exhibit atypia, pelomorphism and mitotic figures. Presence of the neurosecretory granules can be demonstrated at the ultrastructural level or by immunostaining for chromogranin, neuron specific enolase, calcitonin, and bombesin.