Risk factors are related to the causes. The incidence is 2 out of 1000 people.
Prevention is related to the causes.
A barium swallow shows narrowing of the esophagus. An endoscopy shows narrowing of the esophagus. Dilation of the esophagus is the preferred treatment. Repeated dilation may be necessary to prevent the recurrence of the narrowing. If dilation is unsuccessful, surgical replacement of the esophagus with a segment of the stomach or large intestine may be attempted.