No treatment exists for vitelliform macular dystrophy. Secondary choroidal neovascularization can be managed with direct laser treatment. Evaluation of family members is important for identification of carriers and individuals with the dystrophy. Genetic counseling is provided. Consult a low vision specialist that can provide specialized equipment to assist individuals who have significant deterioration in visual acuity in both eyes.
Occupational counseling is important for affected individuals.
Although most retain reading vision in at least 1 eye throughout life, visual deterioration can occur, particularly beyond age 40. This knowledge may influence the choice of career. Physical activity does not influence the progression of this disease. No medications are used to treat Best disease. If visual changes occur at any stage, then an earlier visit should be scheduled.