A case study involving a patient with exposure keratopathy after previously unsuccessful lid surgery discusses successful treatment with a combination spectacle-mounted lid crutch and moisture chamber. Because a silicone sling is reversible, it could be a possibility for some patients. Patients with oculopharyngeal dystrophy who experience severe dysphagia may be treated with cricopharyngeal myotomy, but a gastrostomy tube often is more practical. Strabismus surgery can be helpful in carefully selected patients if diplopia occurs and the patient has had a stable deviation for several months. This dysfunction often can be managed with an artificial pacemaker.
Prognosis is guarded with a generally progressive disorder.
This is a complex disorder but should be diagnosed as early as possible. Clinical and biochemical correlations in mitochondrial myopathies treated with coenzyme Q10. Combination ptosis crutch and moisture chamber for management of progressive external ophthalmoplegia. A PCR test for progressive external ophthalmoplegia and Kearns-Sayre syndrome on DNA from blood samples. Chronic progressive external ophthalmoplegia.