1 Schwannomas of other cranial and spinal nerves are often present, as well as meningiomas.
Patients typically have hearing loss in the second or third decade of life.
Among the many ophthalmic signs that have been described in NF2, 1-4 papilledema has not been highlighted. We report 2 cases in which the dire consequences of sustained elevated intracranial pressures were not recognized in time to prevent visual loss. Bilateral sensorineural hearing was documented. Results of a neurological examination were otherwise normal. These findings were considered diagnostic of sporadic NF2.