The disorder is rare in blacks. About one-third of patients are asymptomatic. There is no consistent pulmonary function test finding, but airway obstruction is common. Treatment consists of chemotherapy. Scuba diving is contraindicated.
Pleural effusion is rare.
Findings include centrilobular opacities, cystic cavitation of small nodules, and cysts . The cysts are usually less than 10 mm in size, although cysts larger than 10 mm are found in over half the cases. The intervening lung parenchyma appears normal. In the late stage, there may be diffuse cysts, with no nodules evident, while in the early stages, only nodules may be seen. Mediastinal adenopathy has been described in some series, but is usually uncommon.