In the US, there are an estimated 300 new cases diagnosed each year. It is most common in women between the ages of 21 and 40. Exact causes of primary pulmonary hypertension remain unknown. Researchers believe the blood vessels are particularly sensitive to certain internal or external factors and constrict, or narrow, when exposed to these factors. There may be a genetic factor, an immune system factor, or sensitivity to drugs or other chemicals.
More severe symptoms indicate more advanced disease.
The symptoms of primary pulmonary hypertension may resemble other conditions or medical problems. Consult your doctor for a diagnosis. Pulmonary hypertension is rarely discovered in a routine medical examination, and in its later stages, the signs of the disease can be confused with other conditions affecting the heart and lungs. Some patients also require supplemental oxygen delivered through nasal prongs or a mask if breathing becomes difficult. This information is not intended to be a substitute for individual medical advice in diagnosing or treating a health problem.