Patients with MSUD are at risk for metabolic decompensation during periods of increased catabolism. Dietary compliance is necessary to prevent developmental delay and neurological symptoms. Educate patients and their caregivers about the principles of dietary treatment, calculation of leucine requirement, and intake and initial management of acute episodes. The Metabolic and Molecular Bases of Inherited Disease. Medicine is a constantly changing science and not all therapies are clearly established.
New research changes drug and treatment therapies daily.
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