Chris Caldarone, MD Recent reports have identified a trend towards decreasing operative mortality in surgical management of total anomalous pulmonary venous drainage. Most reports, however, cite decreasing mortality in series limited to cases without other co-existing cardiac anomalies. Surgical management of the complex cases is less frequently reported, perhaps more difficult, and associated with a higher mortality.
Most reports also note a persistent incidence of post repair pulmonary venous stenosis .
Another surgical entity which is often difficult to treat often with the relentless clinical progression to pulmonary vein stenosis. The objective of this study was to define the results of operative management of this lesion at the Hospital for Sick Children in Toronto to assess the impact of associated cardiac anomalies and to assess the efficacy of therapy for post repair pulmonary vein stenosis. A retrospective review identified all patients with total anomalous pulmonary veins in the Hospital for Sick Children database over a fourteen year period. The complex group was composed of 44 patients having any other cardiac lesion. There was a slight preponderance of males in the series.