These tumors are typically located around the base of the skull, either in the parasellar area, cerebellopontine angle or along the convexity. Gradient echo imaging might better display the paramagnetic affect of the calcification. MRA and angiography will typically show an avascular mass. The pathology of the tumor typically shows cartilaginous cells with nuclear pleomorphism including multi-nucleated giant cells. The grade is variable.
Natural history is that of local invasion typically with local recurrence.
Treatment of this tumor is primarily surgical. RI Grossman and KR Davis. SP Myers, WL Hirsch, HD Curtin, et. E Brown, EB Hug, and AL Weber. The Pediatric Experience.