Patients with MSUD are at risk for metabolic decompensation during periods of increased catabolism. Dietary compliance is necessary to prevent developmental delay and neurological symptoms. Educate patients and their caregivers about the principles of dietary treatment, calculation of leucine requirement, and intake and initial management of acute episodes. The Metabolic and Molecular Bases of Inherited Disease. Medicine is a constantly changing science and not all therapies are clearly established.
New research changes drug and treatment therapies daily.
However, as medical science is constantly changing and human error is always possible , the authors, editors, and publisher or any other party involved with the publication of this text do not warrant the information in this text is accurate or complete, nor are they responsible for omissions or errors in the text or for the results of using this information. The reader should confirm the information in this text from other sources prior to use. In particular, all drug doses, indications, and contraindications should be confirmed in the package insert. Maple Syrup Urine Disease Please email us with any comments you have on our new chapter format.