However, microtia is a distinguishing feature of the syndrome. In campomelic dysplasia the ribs are normally ossified but the fetus may be missing a pair of rib. The scapulas are very small and the pelvis and spine show changes. The inferior part of the scapula is hypoplastic. Cleft palate, micrognathia, flat face, and hypertelorism are also features.
Most patients die in the neonatal period of respiratory distress.
Yet, survival has extended to adulthood. Intensive care for respiratory distress, feeding difficulty and infection. Cleft palate repair, special education and hearing aids for hearing loss. Maxillo-mandibular development in cerebrocostomandibular syndrome.