In Cincinnati, data was collected prospectively from 1966 to 1989. Levinson and Wallace in 1991, reported mortality statistics compiled from surveying 22 US and 1 Canadian pediatric rheumatology centers. Amyloidosis is rare in patients with JRA in the United States. The prevalence of amyloidosis is reported to vary between different centers. Patients with systemic JCA have the highest prevalence of amyloidosis.
Renal failure is the main cause of death in patients with amyloidosis.
The last death due to amyloidosis was reported to have been in 1983.