Cholestasis with Peripheral Pulmonary Stenosis. Arteriohepatic Dysplasia, AHD, and Syndromatic Hepatic Ductular Hypoplasia are considered to be synonymous with Atagille Syndrome. Sometimes surgery is necessary during infancy to help establish the diagnosis of Alagille Syndrome by direct examination of the bile duct system. Surgical reconstruction of the bile duct system is not recommended. Occasionally liver cirrhosis advances to where the liver fails to function requiring the consideration of liver transplantation.
Genetic counseling is recommended for patients and their families.
Many adults having Alagille Syndrome lead normal lives. Resources American Liver Foundation children's Liver Foundation United Liver Foundation 998 Pomptom Avenue 14245 Ventura Blvd. You are welcome to copy and share information from any issue of the GLRS Journal. The contents of this publication are developed under a grant from the Department of Education. However those contents do not necessarily represent the policy of the Department of Education, and you should not assume endorsement by the Federal Government.