However, deterioration is inevitable, leading to debility and eventually death. Nonetheless, the outlook has improved steadily over the past 25 years, mainly because treatments can now postpone some of the changes that occur in the lungs. Half of the people with cystic fibrosis live longer than 28 years. Long-term survival is somewhat better in males, people who don't have pancreatic problems, and people whose initial symptoms are restricted to the digestive system. Despite their many problems, people with cystic fibrosis usually attend school or work until shortly before death.
Gene therapy holds great promise for treating cystic fibrosis.
Treatment Therapy includes prevention and treatment of lung problems, good nutrition, physical activity, and psychologic and social support. Much of the burden of treating a child with cystic fibrosis falls on the parents. They should receive adequate information so they can understand the condition and the reasons for the treatments. The patient should have a comprehensive program of therapy directed by an experienced doctor and assisted by nurses, a dietitian, a social worker, and physical and respiratory therapists. Regularly taking drugs that draw fluid into the intestine, such as lactulose, may prevent stools from obstructing the intestinal tract.