The main differential diagnosis is obstructive uropathy. All of these cases are associated with severe oligohydramnios. Prune belly occurs predominantly in males, is commonly due to posterior urethral valves and has a low recurrence risk. Mild webbing of the neck and intra-abdominal testis have also been associated with this syndrome 14 08D0C9EA79F9BACE118C8200AA004BA90B02000000080000000E0000005F005200650066003400350033003100340031003100340031000000 . An intrauterine death has been described 12 08D0C9EA79F9BACE118C8200AA004BA90B02000000080000000E0000005F005200650066003400350033003900390033003800300032000000 .
Intestinal dysfunction is the cause of death despite hyperalimentation.
There are no reported cases of long term survivors. The prognosis is poor and treatment has been shown to be ineffective. Recommendations for surgical management include palliative surgery. Hyperalimentation is required. Parasympathomimetics, synthetic gastrointestinal stimulants, adrenergic blockers, and multiple gastrointestinal hormones have not been effective in inducting adequate bowel function.