Activity restrictions are not indicated. Avoid prolonged fasting of greater than 5-7 hours. Some patients cannot tolerate even a shorter fasting period of less than 5 hours. During an acute illness with decreased oral intake, maintain normoglycemia with intravenous infusion of glucose-containing solution. Educate the parents and primary physician about the administration of intravenous glucose solutions during acute illness with decreased oral intake.
Dietary teaching is suggested for children as soon as they are developmentally ready.
Glucose homeostasis in adulthood and in pregnancy in a patient with hepatic glycogen synthetase dificiency. Infantile hypoglycaemia due to inherited deficiency of glycogen synthetase in liver. Medicine is a constantly changing science and not all therapies are clearly established. New research changes drug and treatment therapies daily. However, as medical science is constantly changing and human error is always possible , the authors, editors, and publisher or any other party involved with the publication of this article do not warrant the information in this article is accurate or complete, nor are they responsible for omissions or errors in the article or for the results of using this information.