Hypermotility of the bowel associated with diarrhea, nausea, vomiting and abdominal cramps'. Systemic fibrosis including retroperitoneal fibrosis, thickening and steonsis of the pulmonic and tricuspid valves, and pleural plaque. Hepatomegaly due to hepatic metastasis. Five year survival is excellent. Microscopically, the tumor consists of cells arranaged as islands, or sheets of cells.
Cells are uniform and have scant, pink cytoplasm and stipled nuclei.
The stroma is fibrous.