It is seldom seen before a child is 10 years old. It may also develop in the skull or the flat bones of the trunk. This type of tumor is almost never seen in black children.
Clinical symptoms are few.
The most common is pain and occasionally swelling at the site of the tumor. Fever may also be present and is considered an unfavorable prognostic sign. Metastasis is present in approximately one-third of the children at the time of diagnosis. There is no known prevention for this disorder. This tumor is frequently fata.