Treatment for CF aims to maintain good nutritional status and body weight, to keep the airways free of excessive secretions and treat respiratory infections effectively. The discovery of the CF gene means there is hope of a treatment which could alter or reverse the genetic defect responsible for this illness. This is due to changes in antiretro-viral therapy and prophylaxis against opportunistic infections. Key points Patients with ADC have special needs which can be challenging within the context of palliative care. The aim of management is to maximise patient autonomy and independence.
Communication is the essence of best care.
This includes consistency of planning and management, and involvement of all carers, both professional and lay. As death approaches, healthcare professionals are faced with a number of ethical dilemmas. Life is fragile and unpleasant symptoms may require the use of potentially dangerous treatments. Key points There has been a great deal of media interest in the DDE over the last year. This has led to further recognition of the DDE in British law.