In the meantime, radiation therapy, observation, and removal of the eye seem to be equally favored. A rare, genetically determined and life-threatening tumor called a retinoblastoma can occur in young children, usually by the second or third year of life. Since early recognition and treatment of this tumor are important to the child's survival, any abnormality or suspicion of a visual defect in a baby or young child should be promptly evaluated by an ophthalmologist. If the tumor is large or involves both eyes, it may be necessary to remove an eye, treat with radiation therapy, chemotherapy or a combination of the two. Since retinoblastoma can occur in other familial disease, examination of other family members may be necessary.
Diagnosis usually requires extensive evaluation and often includes X-rays and blood tests.
Treatment methods may include radiation therapy or surgical removal of the tumor.