bluuebunny/crossref_metadata_2025_split huggingface dataset:
Clinical case of the maple syrup urine disease in the neonate
Authors: Бугун О.В. , Мартынович Н.Н. , Богоносова Г.П. , Астахова Т.А. , Рычкова Л.В. , Барыкова Д.М. , Кузнецова С.Н. , Осипова Е.Г. , Дорофеева Т.Ю. , Михельсоне Ю.В. 
Published: February 2024

Наследственные болезни обмена веществ представляют собой обширную группу заболеваний, в совокупности затрагивающих до 2-3% популяции. Такая частота, а также возможность проведения эффективной терапии ряда нозологических форм, создают предпосылки к активному изучению метаболических заболеваний. Для ряда наследственных болезней обмена веществ характерны острое и ранее начало в первые дни или месяцы жизни ребенка и агрессивное течение с высокой вероятностью развития летального исхода. Такое течение болезни требует быстрой разработки стратегии обследования и лечения пациента. В группу болезней с ранним и острым началом входит лейциноз или болезнь с запахом кленового сиропа мочи, который относится к нарушениям обмена аминокислот (аминоацидопатиям). Учитывая низкую распространенность каждой нозологической формы собрать большую выборку пациентов с конкретным заболеванием очень сложно. Поэтому описание даже отдельно взятого случая представляет клинический интерес. В данной статье приведены краткие данные о распространенности, патогенезе, клинической картине и лечении болезни с запахом кленового сиропа мочи. Также представлен клинический случай пациента с классическим течением лейциноза из собственной практики.
Inborn errors of metabolism are an extensive group of congenital diseases, collectively affecting up to 2-3 % of the population. A number of hereditary metabolic diseases is characterised by an acute and earlier beginning in the first days or months of a child’s life and an aggressive course with a high probability of mortality. This course of the disease requires a rapid development of a strategy for the examination and treatment of the patient. The article presents a clinical example of a child with maple syrup urine disease. Given the rare frequency, it is very difficult to collect and analyze a large group of patients with leucinosis. Therefore, the description of even a single case is of clinical interest and is useful for highlighting the medical audience.
Who is my Neighbour? Theological Education in the Global Village of the 21st Century (Responses)
Authors: Finch Karen , Huntly Alyson 
Published: February 2024

Chukwuemeka Anthony Atansi’s keynote address offered a series of reflections on how the Igbo theological anthropology of the neighbour can enrich theological education in diverse contexts such as Montreal. The Igbo theological anthropology of the neighbour offers a relational understanding of the neighbour, a relationality which comprises a crucial component of Karen Finch’s response, one which argues that good pastoral education in today’s polarized world strongly resembles good ecumenical formation. For Finch, ecumenical formation is about relationality and the dialogues that this relationality provokes, and she argues that, when approached with openness and transparency, such dialogues can be truly generative for pastoral education.
Alyson Huntly’s response offers a series of reflections about the state of theological education in Quebec, reflections which also highlight relationality, or, more precisely, the need for Western institutions, hitherto predominantly white, to re-evaluate and re-envision how they relate to – and thereby dialogue with and learn from – the “Others” who now represent a majority demographic in Quebec’s theological colleges, many of whom come from the Global South or formerly colonized nations. This, she argues, represents the path to renewal for theological education in twenty-first century Quebec.
KEMAMPUAN LITERASI NUMERASI MATEMATIS SISWA DALAM MEMECAHKAN MASALAH BARISAN DAN DERET ARITMATIKA
Authors: Nisa Novi Darojatun , Ramlah Ramlah 
Published: February 2024

This research aim to describe students’ numeracy literacy skills in solving mathematics problems in the form of story problems. The students involved were class X students at one of 36 high schools in Karawang district, then selected 3 students with high, medium, and low numeracy literacy skills. The method used is a case study research method with a qualitative descriptive approach. The data collection technique usedin this survey is a two dimensional description test of arithmetic rows and rows, documentation, and interviews. The data analysis technique is in the formof an aveage percentage for each indicator of numeracy literacy ability, availability of subject to be intervewed, subject answer and conclusions. The results of the study show that the subject with high numbering numeracy literacy is capable of solving problems using symbols and numbers, able to analyze the information presented, and able to interpret the result of the analysis to draw the conclusion correctly, where as the subjects with the literacy of categorical numeration are not capable of interpreting the results of analysis, and subject with low category numerational literacy does not meet the three indicators of numerational literacy, this is because the student isnot accustomed to working on the story. It was concluded that the numerical literacy of the entire student was categorized quite well.
Competencias emocionales y su relación con el liderazgo efectivo: un acercamiento desde directoras educativas de la República Dominicana
Authors: Suriel Ana Julia , Escalante José Luis 
Published: February 2024

Las competencias emocionales en todos los ámbitos tienen un valor significativo porque favorecen la toma de mejores decisiones. En el contexto de la gestión académica estas habilidades se constituyen en variables fundamentales para una correcta dirección de los procesos pedagógicos y administrativos, así como para el desarrollo de un liderazgo efectivo. Por ello, el presente estudio se desarrolló con el objetivo de establecer la correlación existente entre competencias emocionales y liderazgo efectivo de directoras de centros educativos, a fin de implementar un programa de desarrollo basado en la inteligencia emocional que permita fortalecer las habilidades consideradas deficientes. La investigación se diseñó en un enfoque cuantitativo con un diseño cuasiexperimental, para determinar la correlación entre las variables mencionadas y la influencia del programa formativo de desarrollo de habilidades emocionales en las directoras. Se eligió una muestra estratificada e intencional, la cual estuvo conformada por 8 directoras de escuelas y 201 maestros de diferentes regiones de la República Dominicana. Para obtener los datos se elaboró un cuestionario para ser aplicado en cada tipo de población (directoras y profesores) con 91 ítems en una escala adverbial y numérica, con dos versiones del mapa de competencias emocionales de Daniel Goleman. Se realizaron 2 evaluaciones con una intervención formativa de 8 semanas para reforzar las competencias que estuvieron por debajo del rango esperado en la primera medición. Los principales resultados del estudio confirman que existe una relación lineal directa y positiva entre las competencias emocionales y el liderazgo efectivo, porque las medias de estas variables se ubican en 1.5 y 1.6 en sentido general. Igualmente, se concluye que los resultados no mostraron ningún cambio significativo de la variable competencia emocional después del programa formativo. Se enfatiza la necesidad de que las instituciones de educación superior oferten, a largo plazo, planes de estudio dirigidos al desarrollo de competencias emocionales en los líderes escolares.
Perlindungan Hukum Perikatan Pembebanan Jaminan Kebendaan Dalam Akad Murabahah Di Bank Syariah Indonesia (BSI) Yang Tidak Beretikad Baik
Authors: Mustakim Agus , BT Tolo Suriani , Munawir La Ode 
Published: February 2024

Penelitian ini bertujuan untuk mengetahui dan menganalisis perlindungan hukum perikatan pembebanan jaminan kebendaan dalam akad murabahah di bank syariah Indonesia (BSI) yang tidak beretikad baik. Metode penelitian hukum empris Jenis penelitian ini adalah penelitian lapangan (fieldresearch) yaitu penelitian yang objeknya mengenai gejala-gejala atau peristiwa-peristiwa yang terjadi. hasil penelitian Perlindungan hukum perikatan pembebanan jaminan kebendaan dalam akad murabahah di bank syariah Indonesia (BSI) yang tidak beretikat baik. Perlindungan Hukum melalui Perjanjian Pembiayaan Murabahah. Perlindungan Hukum Berdasarkan Fatwa DSN04/DSN-MUI/IV/2000 Tentang Murabahah. Kontrak baku pada pembiayaan murabahah di beberapa bank syariah telah memuat klasula yang sesuai dengan karakteristik dari pembiayaan murabahah tersebut dan telah memuat syarat minimum yang harus ada dalam akad sebagaimana ditentukan dalam Fatwa Dewan Syariah Nasional yang dirumuskan dalam Peraturan Bank Indonesia.
ANALISIS FAKTOR YANG MEMPENGARUHI PENERIMAAN PELANGGAN PLN ULP BANYUWANGI KOTA TERHADAP APLIKASI NEW PLN MOBILE
Authors: Mulyono Dwi , C. Premananto Gancar 
Published: February 2024

Abstract: The purposes of this research was to analyze the effect of Technology Acceptance Management (TAM) variables to explain the factors that affect acceptance to using New PLN Mobile application on costumer of PLN ULP Banyuwangi Kota. In this research analyzed the effect of information quality, relative advantage and perceived enjoyment on perceived ease of use and perceived usefulness, the effect of perceived ease of use on perceived usefulness and attitude toward using, the effect of perceived usefulness on attitude toward using and intention to use as well as the effect attitude toward using on intention to use. This research was a quantitative research done by survey method. Data collected by distributing questionaire to 226 samples whom are the costumer of PLN ULP Banyuwangi Kota. The samples determine by purposive sampling method. Data analysis done by Structural Equation Modelling use SmartPLS software. The research result shown that information quality and perceived enjoyment have no significat effect on perceived ease of use and perceived usefulness; relative advantage have significant positive effect on perceived ease of use and perceived usefulness. Furthermore also found that perceived ease of use have significant positive effect on perceived usefulness and attitude toward using; perceived usefulness have significant positive effect on attitude toward using and intention to use; as well as attitude toward using have significant positive effect on intention to useKeyword: information quality, relative advantage, perceived enjoyment, perceived ease of use, perceived usefulness, attitude toward using, and intention to use
ANALISA GOOD CORPORATE GOVERNANCE TERHADAP KINERJA PERUSAHAAN PADA EMITEN JAKARTA ISLAMIC INDEX 70
Authors: Muzahid Mukhlisul , Lukman Lukman , Aryati Aryati , Wijaya Ismed , Isra Mauli 
Published: February 2024

This study aims to analyze the effect of Good Corporate Governance on the performance of companies listed on the Jakarta Islamic Index 70 (JII 70). Good Corporate Governance is measured using the board of commissioners, board of directors and audit committee, while company performance is measured using Return On Equity (ROE). The population of this study amounted to 70 companies. There are 22 companies that meet the criteria as research samples with the 2018-2020 period so that the data is 66. The data analysis method in this study is multiple linear regression analysis. The results of this study indicate that the board of commissioners has a significant positive effect on the company's performance, the board of directors has a significant negative effect on the company's performance and the audit committee has no effect on the company's performance. Keywords: Board of Commissioners, Board of Directors, Audit Committee, Return On Equity
PENGARUH KEMAMPUAN WIRAUSAHA, PELUANG USAHA DAN TINGKAT PENDIDIKAN TERHADAP PENDAPATAN USAHA MIKRO, KECIL DAN MENENGAH (UMKM) SEKTOR KULINER DI KECAMATAN SOMBA OPU KABUPATEN GOWA
Authors: Putri Armi Permana , Syam Agus , Rahmatullah Rahmatullah , Said Muh. Ihsan , Hasan Muhammad 
Published: February 2024

The goal of this study was to ascertain how the education level, business possibilities, and entrepreneurial skills of MSMEs in the food service industry in Somba Opu District, Gowa Regency, impacted their revenue. This study falls under the quantitative descriptive research category. Through observation, surveys, and recording, data was gathered. 48 respondents made up the 48 samples in this study, which was followed by multiple regression analysis. (1) According to the findings of partial testing, business opportunity, degree of education, and entrepreneurial aptitude all had a favorable and substantial impact on the revenue of MSMEs in the culinary sector in Somba Opu District, Gowa Regency (2) The revenue of MSMEs in the food service industry in Somba Opu District, Gowa Regency is positively and significantly impacted by entrepreneurial potential, business prospects, and educational attainment. Keywords: Entrepreneurial Ability, Business Opportunity, Education Level MSME Income
ANALISIS MUTU DOSEN DALAM PERSPEKTIF REKRUTMEN (Studi Kasus di STAI Babussalam Sula Maluku Utara)
Authors: Usia Hardiaman , Hasyim Abdul Wahab , Soleman Marwan Man 
Published: February 2024

This study aims to determine the analysis of the quality of lecturers from the perspective of recruitment at STAI Babussalam Sula North Maluku, using several recruitment indicators, namely, objectives, stages, basis of determination, methods and factors, while on the quality of lecturers namely education and teaching, research and development and service to society. The type of research used is descriptive qualitative, and the data analysis used is an interactive model starting from reduction, data presentation and conclusion. The results of this study indicate that 1.) Recruitment of lecturers at STAI Babussalam Sula uses an open method, but in practice it has not fully followed the SOP. This is influenced by several factors, namely: a). STAI Babussalam Sula has not been able to enforce pure procedures, like state campuses, because all decisions are based on policies from the foundation. b). STAI Babussalam Sula is a campus at the district level and is still at the developing stage. c). Lecturer recruitment has not been based on needs analysis. 2). While the quality of lecturers in the Tridarma at STAI Babussalam Sula, namely: a). In education and teaching, there are still some non-linear lecturers who carry out the learning process for majors and study programs, and the availability of inadequate infrastructure. b). Research and community service carried out by lecturers is still minimal, this is influenced by the availability of an inadequate budget, because the financial source depends on student tuition fees. Keywords: Perspective, Lecturer Quality, Recruitment
DOMESTIC INSTITUTIONAL OWNERSHIP DAN FOREIGN INSTITUTIONAL OWNERSHIP TERHADAP LIKUIDITAS SAHAM (Studi pada Industri Manufaktur yang Terdaftar di Bursa Efek Indonesia)
Authors: Hamdani Hamdani , Maulizar Maulizar , Putri Yetty Tri , Sa’diyah Halimatus 
Published: February 2024

This research was conducted to deterime the influence of ownership structure, domestic institutional ownership and foreign institutional ownership from stock market liquidity. Control variable in this research is size measure by market capitalization. This research use a quantitative approach using statistical tools in the form of multiple linear regression. This study use secondary data from manufacture firm wich fulfill the requirement and listing in Indonesia Stock Exchange from 2009-2010. The result of this study conclude that domestic institutional ownership has a significant negative influence on stock market liquidity wich measured by depth but domestic institutional ownership wich measured by relative spread hasn’t significant influence on stock market liquidity. The second result of this study is foreign institutional ownership has a significant negative influence on stock market liquidity wich measured by depth and also has a significant positive influence on market likuidity wich measured by relative spread. Control variable has varied influence on stock market liquidity. Keywords : Domestic institutional ownership, foreign institutional ownership, size, market capitalization, stock market liquidity, depth, relative spread.
Diversity and community structure of soil microarthrophods of several moorlands in Gumukmas District, Jember Regency, East Java
Authors: Yanuwiadi Bagyo , Penatagama Zulfaidah , Leksono Amin Setyo , Rahayu Puji , Nurrofik Agus , Kurniawan Nia 
Published: February 2024

<p>The effectiveness of soil microarthropods as a bioindicator was studied to evaluate various soils in the conditions of various lands, including moorland in Gumukmas District, Jember Regency. This study focuses on data collection of the diversity and structure of soil microarthropod communities along with the assessment of their ecological parameters. Field observations were carried out in five villages in Gumukmas District from August-September 2022 using the hand sorting method. The data were analyzed using α-diversity parameters (Dominance Index, Simpson Index, Evenness, Shannon-Weiner Index, Brillouin Index, and Margalef Species Richness). Habitat similarities were presented by UPGMA multivariate analysis and the estimation of abiotic factors that influence soil microarthropod composition was estimated by Canonical Component Analysis (CCA). The observations showed a total of 24 families from 13 soil microarthropod orders that spread across Gumukmas District. The abundance of diversity based on the α-diversity is still relatively low to moderate, nevertheless, the correlation of microarthropod orders to environmental factors can reveal conditions of the soil cycle through the study site. The results of the study are expected to assist in efforts to restore the diversity of soil microarthropods to support better soil quality.</p>
THE IMPACTS OF SPEECH ACTS TO THE EFL TEACHER AND THE STUDENTS’ ACTIVENESS IN THE TEACHING LEARNING PROCESS
Authors: Amir Nursakinah 
Published: February 2024

This research aims at identifying (1) the kinds of speech act which are performed by the teacher in Indonesian EFL classroom in terms of locutionary, illocutionary and perlocutionary, (2) The function of speech act produced by the teacher, (3) The impacts of speech act to the teacher’s and students activeness in teaching and learning process. This research employed both qualitative and quantitative method. The data were in the form of utterances spoken by the EFL teacher when teaching in the classroom. The researcher planned, collected, analyzed and reported the research findings. The steps of collecting the data were taking video of the EFL teacher when he was teaching in the classroom, transcribing what the teacher said, selecting the data, classifying the data, transferring the data into table, analyzing and interpreting the data. The findings showed that the EFL teacher commonly uses illocutionary act in his teaching. He performs mostly directives as the illocutionary acts as he often asks the students to do some works or activities. Giving instruction or command helps him to run the EFL class. Penelitian ini bertujuan untuk mengidentifikasi (1) jenis tindak tutur yang dilakukan oleh guru di kelas EFL bahasa Indonesia ditinjau dari lokusi, ilokusi, dan perlokusi, (2) Fungsi tindak tutur yang dihasilkan oleh guru, (3) Dampaknya tindak tutur terhadap keaktifan guru dan siswa dalam proses belajar mengajar. Penelitian ini menggunakan metode kualitatif dan kuantitatif. Datanya berupa ucapan yang diucapkan oleh guru EFL saat mengajar di kelas. Peneliti merencanakan, mengumpulkan, menganalisis dan melaporkan temuan penelitian. Langkah-langkah pengumpulan data adalah mengambil video guru EFL ketika dia mengajar di kelas, menyalin apa yang dikatakan guru, memilih data, mengklasifikasikan data, mentransfer data ke dalam tabel, menganalisis dan menafsirkan data. Temuan menunjukkan bahwa guru EFL umumnya menggunakan tindak ilokusi dalam pengajarannya. Ia lebih banyak melakukan arahan sebagai tindak ilokusi karena ia sering meminta siswa melakukan suatu pekerjaan atau aktivitas. Memberikan instruksi atau perintah membantunya menjalankan kelas EFL
Analysis Of Factors Affecting Measles Rubella ( Mr ) Immunization Services For Children Aged 18-24 Months During The Pandemic At The Bumiaji Health Center In Batu City
Authors: Tri Astutik  , Ratna Wardani  
Published: February 2024

As service providers, the role of officers must be supported by knowledge, infrastructure, response and empathy so that immunization services during a pandemic can continue to run optimally. The purpose of this study was to determine the factors that influence the Measles Rubella (MR) immunization service for children aged 18-24 months during the pandemic at the Bumiaji Health Center, Batu City.The research design used was observational with a cross sectional approach with linear regression statistical tests to determine the factors that influence the Measles Rubella (MR) immunization service in children aged 18-24 months during the pandemic at the Bumiaji Health Center, Batu City. The population was 32 immunization officers at the Bumiaji Health Center with a sample of 30 respondents using simple random sampling.The research design used was observational with a cross sectional approach with linear regression statistical tests to determine the factors that influence the Measles Rubella (MR) immunization service in children aged 18-24 months during the pandemic at the Bumiaji Health Center, Batu City. The population was 32 immunization officers at the Bumiaji Health Center with a sample of 30 respondents using simple random sampling.The results of statistical tests showed that the significance results for the knowledge variable were 0.735 > 0.05, the infrastructure variable was 0.000 < 0.05 and the response and empathy variables were 0.456 > 0.05. For the variables of knowledge, response and empathy, Ho is accepted and H1 is rejected, meaning that there is no influence of knowledge or response and empathy to immunization services. While in the infrastructure variable Ho is accepted and H1 is rejected, it means that there is an effect of response and empathy of officers on immunization services.From the results of the study, it was concluded that only infrastructure had an effect on immunization services. In the simultaneous analysis of all variables when analyzed simultaneously on immunization services, there is indeed a significant effect. The Health Office is expected to continue to support increasing knowledge, equipping infrastructure, motivating response and empathy for officers so that Measles Rubella (MR) immunization services for children aged 18-24 months during a pandemic can run even better.