bluuebunny/crossref_metadata_2025_split huggingface dataset:
Dorfman–Chanarin Syndrome with Renal Involvement: A Rare Case Report and Literature Review
Authors: Agrebi Ikram , Jaziri Achraf , Kanoun Houda , Dammak Najla , Boudabous Mouna , Toumi Salma , Yaich Soumaya , Tahri Nabil , Kammoun Arwa , Makni Hafedh , Kammoun Khawla , Boudawara Tahya , Hmida Mohamed Ben 
Published: November 2023

Abstract
Dorfman–Chanarin syndrome (DCS) is a rare autosomal recessive disease. It is a multisystemic disease in which renal involvement is uncommon. We report the case of a woman with nephrotic syndrome associated with DCS. A 36-year-old woman was referred to the nephrology department for edema with known history for DCS. On physical examination, she had ichthyosiform erythroderma with generalized scaly skinand ascites. The ophthalmologic examination revealed a cataract in the right eye. Abdominal ultrasound examination showed hepatomegaly and splenomegaly. Laboratory tests showed normal renal and liver function. The blood cell count showed pancytopenia. Immunologic exams showed the presence of anti-mitochondrial antibodies. Kidney biopsy showed mesangial proliferative glomerulonephritis with extensive lipid vacuoles in the tubular epithelial cells. Immunofluorescence study showed mesangial deposits of IgG, C3, kappa, and lambda. To the best of our knowledge, this is the first case of DCS with renal involvement reported in an adult.
Detecting circulating microbial cell-free DNA by next-generation sequencing in patients with Mycobacterium avium complex-lung disease: A pilot study
Authors: Tseng Yen-Han , Pan Sheng-Wei , Feng Jia-Yih , Su Wei-Juin , Huang Chi-Ying F , Chen Yuh-Min 
Published: November 2023

ABSTRACT

Objectives:
Determining a diagnosis for non-Tuberculous mycobacterium (NTM)-lung disease (LD) remains difficult. The value of circulating cell-free DNA (cfDNA) secreted from microbes has been established in the detection of pathogens in septic patients. However, it is unknown whether NTM-derived cfDNA is detectable in plasma from patients with NTM-LD and whether this is associated with the disease status of NTM-LD, especially in patients with Mycobacterium avium complex (MAC)-LD.

Materials and Methods:
In this pilot study, from 2018 to 2019, we enrolled adult patients with MAC-LD at Taipei Veterans General Hospital in Taiwan for the detection of circulating cfDNA. We performed cfDNA extraction from plasma, next-generation sequencing (NGS) for nonhuman cfDNA, and sequence matching to a microbial database and then assessed the association between pathogen cfDNA and MAC-LD.

Results:
Two (40%) plasma samples from MAC-LD patients had detectable MAC-specific cfDNA, namely one instance of DNA polymerase III alpha subunit and one instance of ATP-binding cassette transporters permease. The plasma samples from the three other MAC-LD cases and the one tuberculosis control were negative for either NTM-derived cfDNA or tuberculosis-related cfDNA. In addition to MAC-specific cfDNA, Ralstonia solanacearum, Staphylococcus aureus, and Pasteurella multocida were the most observed bacteria in our patients. The two patients with MAC-cfDNA positivity yielded higher radiographic scores (P = 0.076) and presented a higher number of nonhuman reads than those without MAC-cfDNA positivity (P = 0.083).

Conclusion:
Using NGS method, we demonstrated MAC-cfDNA was detectable in patients with MAC-LD. Further large-scale research is warranted to assess the clinical value of detecting MAC-specific cfDNA in MAC-LD patients.
10‐GHz band 2 × 2 phased‐array radio frequency receiver with 8‐bit linear phase control and 15‐dB gain control range using 65‐nm complementary metal–oxide–semiconductor technology
Authors: Han Seon‐Ho , Koo Bon‐Tae 
Published: November 2023

AbstractWe propose a 10‐GHz 2 × 2 phased‐array radio frequency (RF) receiver with an 8‐bit linear phase and 15‐dB gain control range using 65‐nm complementary metal–oxide–semiconductor technology. An 8 × 8 phased‐array receiver module is implemented using 16 2 × 2 RF phased‐array integrated circuits. The receiver chip has four single‐to‐differential low‐noise amplifier and gain‐controlled phase‐shifter (GCPS) channels, four channel combiners, and a 50‐Ω driver. Using a novel complementary bias technique in a phase‐shifting core circuit and an equivalent resistance‐controlled resistor–inductor–capacitor load, the GCPS based on vector–sum structure increases the phase resolution with weighting‐factor controllability, enabling the vector–sum phase‐shifting circuit to require a low current and small area due to its small 1.2‐V supply. The 2 × 2 phased‐array RF receiver chip has a power gain of 21 dB per channel and a 5.7‐dB maximum single‐channel noise‐figure gain. The chip shows 8‐bit phase states with a 2.39° root mean‐square (RMS) phase error and a 0.4‐dB RMS gain error with a 15‐dB gain control range for a 2.5° RMS phase error over the 10 to10.5‐GHz band.
Pengaruh Motivasi dan Disiplin Kerja terhadap Kinerja Karyawan pada PT Mitra Dana Top Finance Cabang Bandung
Authors: Prayogi Muhammad Sandi , Atmawinata Maya R. 
Published: November 2023

Muhammad Sandi Prayogi1,
Program Studi S1 Manajemen, Universitas Teknologi Digital
muhammadsandiprayogi19@student.stembi.ac.id 1 ,

ABSTRACT
This study aims to determine the effect of work motivation and discipline on employee performance at PT. Mitra Dana Top Finance Branch Bandung. The method used is descriptive and quality with a quantitative approach. The population in this study were all employees of PT. Mitra Dana Top Finance Branch Bandung, while the sampling technique used the Non-Probability Sampling technique or saturated samples, amounting 40 respondents. The data collection methods used questionnaires, observation and literature studies, while data analysis methods used quality tests, classical assumption tests, and hypothesis testing using the Programs Statistics SPSS 26. The results of this study motivation have a positive and significant effect on employee performance with a tcount of 2.721 > ttable of 2.026 and sig. 0.010 < a 0.05, and work discipline also has a positive and significant effect on employee performance with a tcount of 2.707 > ttable of 2.026 and sig. 0.010 < a 0.05. The R2 value in this study was obtained at 45.2% which indicates that work motivation and discipline affect employee performance, while the remaining 54.8% is influenced by other factors that were not examined in this study.
Keywords: Motivation, Work Discipline and Employee Performance.
USING REFLECTIVE JOURNALS FOR LEARNING ENGLISH AMONG PRIMARY SCHOOL STUDENTS VIA GOOGLE DRIVE
Authors: Nguyen Huu Anh Vuong  , Nguyen Thi Khanh Le  
Published: November 2023

Reflection is an important practice where teachers construct the meanings and knowledge that guide students‟ actions in the classroom. Reflective journal is advocated as a way to enhance teaching and learning. Most studies of reflective journals focus on its potential in promoting the process of teaching and learning, and the impacts of it on students‟ outcomes or motivation. The study used both quantitative and qualitative research approaches to examine the benefits of using reflective journals in teaching English to primary school students as well as their attitudes. It employed instruments such as questionnaires, students' reflective journals, and semi-structured interviews to collect data from 45 students at a primary school in Danang, Vietnam. The findings indicate four main benefits that reflective journals bring to primary school students. In addition, the study results showed students‟ positive feelings and attitudes towards writing reflective journals.
Digitalisasi Produk UMKM Berbasis E-Katalog untuk Meningkatkan Komersialisasi Pemasaran di Lingkungan Komunitas UMKM PADUKA
Authors: Irianto Wahyu Sakti Gunawan , Widiyaningtyas Triyanna , Sujito Sujito , Habibi Muhammad Afnan , Syah Abdullah Iskandar , Abdul Hadi Afif , Fuadi Ahmad 
Published: November 2023

The Indonesian economy has traditionally relied heavily on the vital contributions of Micro, Small, and Medium Enterprises (MSMEs) to support economic growth and national development. MSMEs not only create jobs but also drive economic growth, especially after economic crises. This community engagement focuses on the Kasembon Subdistrict in Malang Regency and involves the PADUKA MSME Community. In this program, the introduction of an E-Catalog is presented as a solution to improve the marketing of MSME products. The results show that the implementation of the E-Catalog has enhanced the efficiency of product marketing, facilitated access to product information, and provided benefits to consumers. However, challenges related to technology adaptation and diverse understandings need to be addressed. Continuous support and capacity-building in the form of training and mentoring are necessary to ensure the sustainability of this program. This initiative underscores the significant potential of technology in advancing MSMEs and emphasizes the need for a sustainable approach to drive local economic growth.
Keywords: E-Catalog, Community Engagement, Economic Growth, Product Digitalization
SMOLENSK OBLAST – THE «JUDICIAL REVOLUTION»
Authors: ГУСЕЙНОВА-ВАДИШ Севиль Гасановна 
Published: November 2023

статье на примере Смоленской области рассматривается актуальный вопрос, связанный с «судебной революцией». Проводится анализ современного состояния и последних преобразований некоторых институтов судебной системы, в частности, затрагивающих порядок функционирования судов общей юрисдик- ции на уровне кассационного и апелляционного производства, с учетом внесения изменений в действующее законодательство. В завершение автор приходит к выводу о том, что дальнейшие изменения судебной системы должны быть направлены на проработку ряда вопросов: введение новой меры дисциплинарной ответствен- ности судей; определение критериев разграничения судебной ошибки и дисциплинарного проступка судей; введение автоматизированных систем распределения дел между судьями; технологическая модернизация правосудия; введение в уголовное законодательство понятия уголовного проступка; сопровождение судебной реформы соответствующими мерами по модернизации «смежных» структур.
This article examines the topical issue related to the judicial revolution on the example of the Smolensk region. This article analyses the current state and recent transformations of some institutions of the judicial system particularly those affecting the procedure of functioning of courts of general jurisdiction at the level of cassation and appeal proceedings taking into account amendments in the current legislation. In conclusion, the author concludes that further changes in the judicial system should focus on a number of issues: the introduction of a new measure of disciplinary responsibility of judges; definition of criteria for distinguishing judicial error and disciplinary misconduct of judges; introduction of automated systems for distribution of cases among judges; technological modernization of justice; introduction into criminal law the concept of criminal misconduct; accompanying judicial reform with appropriate measures to modernize «related» structures.
LEGAL SOVEREIGNTY: AN ATTEMPT TO JUSTIFY
Authors: ПОДОСИННИКОВА Л.А. 
Published: November 2023

Цель работы – выявить и дать оценку наиболее важным свойствам явления под названием «правовой суверенитет». Использовались метод системного анализа, историко-философский метод, формаль- но-юридический метод, философский метод идеализма. В статье исследованы представления некоторых оте- чественных и зарубежных авторов относительно данного явления, до сих пор не нашедшего достойного места в юридической науке. Особенно это касается современной политико-правовой практики, которая диктует свой понятийно-смысловой дискурс. В юридической науке категория «правовой суверенитет» должна быть напол- нена собственным смысловым содержанием как сложное политико-правовое свойство власти и государства, выражающееся в многообразии общественных отношений между государством и гражданами, государством и обществом, государством и государством на международной арене, государством и народом в связи с реализа- цией государственной власти. Выявлены общие свойства данного феномена. Значимость работы заключается в том, что в ней сформулированы теоретические положения, направленные на формирование полноценных представлений о правовом суверенитете и развитие данного свойства государствами в современных условиях.
The purpose of the work is to identify and evaluate the most important properties of the phenomenon under consideration called «legal sovereignty». The method of system analysis, the historical-philosophical method, the formal-legal method, the philosophical method of idealism were used. The article examines the views of some domestic and foreign authors regarding this phenomenon, which has not yet found its rightful place in legal science. This is especially true of modern political and legal practice, which dictates its own conceptual and semantic discourse. In legal science, the category of «legal sovereignty» should be filled with its own semantic content as a complex political and legal property of the government and the state, expressed in the diversity of public relations between the state and citizens, the state and society, the state and the state in the international arena, the state and the people in connection with the implementation of state power. The general properties of this phenomenon are revealed. The significance of the work lies in the fact that it formulates theoretical provisions aimed at forming full-fledged ideas about legal sovereignty and the development of this property by states in modern conditions.
SUBSURFACE GEOECOLOGY OF THE VERHNEKAMSK POTASSIUM SALT DEPOSIT
Authors: PHILATOV V. , VANDYSHEVA K. 
Published: November 2023

The geological environment experiences a significant transformation in any type of economic activity in the form of changes in its structure, properties and state. The exploitation of deposits is accompanied by the extraction and movement of huge masses of rock and captures areas of tens and hundreds of square kilometers. Therefore, the problem of safe field operation is geoecologically relevant.
This work summarizes the experience of studying the complex of geological and geophysical methods of tectonic structure and dynamic events that occurred at the Verkhnekamsk deposit of potassium salts in the Perm Urals, and also the criteria for their prediction are substantiated.
Investors’ Biases & Stock Return Volatility: A Systematic Literature Review
Authors: Anam Qamar  , Dr. Afaq Ahmed Kazi  
Published: November 2023

Purpose:
Literature is scarce on the possible relationship between investors’ biases, risk tolerance attitude, and stock return volatility. The researcher investigated what are the investor biases, and how they contribute to the risk-averse and risk-seeking attitudes and developed a taxonomy model of investors’ biases in the form of a causal framework that impacts stock return volatility.
Methodology:
The study employs a systematic literature review approach. The analysis of literature includes 65 articles from impact factor journals including three seminal papers in the fields of traditional and behavioral finance. The time frame ranges from 2008 to 2022.
Findings:
The findings suggest that investors encounter certain biases such as cognitive, emotional, cultural, religious, financial, macroeconomic, demographic, etc. Literature has identified positive, negative, and mixed impacts of investors' biases on stock return volatility. The systematic analysis of literature helps in identifying recently evolving biases such as individualism, uncertainty avoidance, a religious adherence, investor mood, weather bias, fear sentiments, sports sentiments, power distance, masculinity, social media sentiments so on and so forth.
Conclusion:
The study has proposed an integrated taxonomy model comprised of possible investors’ biases as independent variables along with mediating, controlling, and moderating variables that impact stock return volatility. Moreover, investors’ risk tolerance profile is also constructed which indicates the role of behavioral biases in shaping investors’ attitudes as risk seekers and risk-averse.
Signficant Femoral Version Abnormalities and Patient-Reported Quality of Life
Authors: Greenstein Michael D. , Ellsworth Bridget K. , Sheridan Gerard A. , Fragomen Austin T. , Rozbruch S. Robert 
Published: November 2023

Introduction:
The purpose of this study was to determine how the Limb Deformity–Modified Scoliosis Research Society (LD-SRS) and Patient-Reported Outcomes Measurement Information System (PROMIS) questionnaire scores differ between patients with femoral version abnormalities and healthy control subjects.

Methods:
A retrospective database review identified patients with femoral version abnormalities between December 2018 and September 2022. A total of 21 adult patients scheduled for femoral derotational osteotomy and 33 control subjects were included. All individuals completed the LD-SRS and PROMIS questionnaires.

Results:
Patients with femoral version abnormalities reported significantly worse scores than control subjects on all LD-SRS and PROMIS domains: LD-SRS (Total [3.46 ± 0.66 vs. 4.58 ± 0.37, P < 0.001]; Function/Activity [3.48 ± 0.83 vs. 4.44 ± 0.4, P < 0.001]; Mental Health [3.41 ± 0.96 vs. 4.3 ± 0.73, P < 0.001]; Pain [3.55 ± 0.9 vs. 4.81 ± 0.31, P < 0.001]; and Self-Image/Appearance [3.37 ± 0.79 vs. 4.75 ± 0.43, P < 0.001]) and PROMIS (Function [41.6 ± 7.58 vs. 60.0 ± 7.28, P < 0.001]; Pain Intensity [45.85 ± 8.04 vs. 33.7 ± 4.89, P < 0.001]; Pain Interference [56.78 ± 9.63 vs. 42.8 ± 6.6, P < 0.001]; Global Mental Health [47.97 ± 9.68 vs. 55.3 ± 7.81, P = 0.004]; and Global Physical Health [45.23 ± 7.49 vs. 58.2 ± 7.07, P < 0.001]).

Discussion:
Patients with femoral version abnormalities reported markedly worse quality of life as measured on the LD-SRS and PROMIS scores compared with healthy control subjects. The combination of these two surveys effectively captures the multifaceted quality-of-life–deficit individuals with excessive femoral version may experience.
Use of prebriefing in simulation-based experience for nursing education: a scoping review
Authors: Chan Hoi Man , Wong Suet Lai , Yau Sui Yu , Chan Shi Hang 
Published: November 2023

Embracing innovative pedagogies and structured pre-simulation activities in healthcare simulation enhances learning and clinical performance. The Society for Simulation in Healthcare (SSH) and the International Nursing Association for Clinical Simulation and Learning (INACSL) propose a three-phase approach of prebriefing, simulation-based experiences and debriefing. This scoping review explored the impact of prebriefing pedagogies, aiming to enhance nursing students’ chances of success in simulation-based learning experiences.
This scoping review encompassed the existing literature on simulation in nursing education, specifically focusing on prebriefing strategies.
The existing literature revealed variations in the contexts, educational concepts, prebriefing pedagogy and outcome measures employed in simulation-based experiences. None of the studies established a correlation between dependent variables and prebriefing pedagogy strategies. Instead, most studies utilized a combination of dependent variables to measure the correlated aspects of prebriefing, namely personal development and engagement.
The recognized prebriefing strategies serve as valuable resources for nurse educators when designing the prebriefing phase of a simulation-based experience.
Inkling: Thinking about Ink
Authors: Balfour Barbara 
Published: November 2023

Something about the haptic and visual qualities of ink.
Something about ink moving from matrix to substrate.
Something about how printmakers are drawn to ink.
It’s an inkling I have…
I want to focus on a crucial yet often overlooked aspect of printmaking, namely ink. Returning to the studios after months of remote learning, students in one of my print media courses were struck by the physical presence of ink on paper. Drawn to actually touch the printed ink film, they wanted to confirm the physical and sensuous qualities they perceived through sight.
The fact of ink on paper might seem too obvious to mention, yet I have an inkling that it is worth revisiting and re-examining ink’s haptic qualities and materiality in addition to, or even apart from, its visual presence. I believe an examination and articulation of the physicality, tactility, and malleability of ink – its inkiness, even its sheer messiness – is worthy of study.
Between the Pen and the Line: Digital Drawing and the Feeling of Alienation and Distance
Authors: Schrøder Tiril 
Published: November 2023

As an artist I work mainly with digital drawing tools, but I also have this feeling of alienation towards digital drawing: As an artist educated around the 80s/90s, the classic analog drawing is the basis for my understanding of both analogue anddigital drawing, and my experience with the digital drawing tools is filtered through this early training.

In my research I have been testing various digital hardware and software to see how they work, and what kind of results they make. In my presentation I will look at the different quality of lines various hardware and software makes, show some of my line tests from different digital technology and reflect on my own drawing process. I will also reflect on my experience when working with digital tools and the experience I get from the finished works. The presentation will be illustrated with my own digital drawings made specially as part of my research.
Drawing is an act traditionally done with a drawing tool held in the hand to make a line on a surface. Basically, the physical action - the gesture itself - is the same, whether I draw analog or digital: I hold the pen in the same way, move my hand and arm in the same way. But what exists between the hands gesture, the tip of the pen and the resulting line, is different in analog and digital drawing, and the line itself is also different. The digital drawing tools add their own qualities to the lines and the drawings.

I will look at some of the differences I experience between digital and analog drawing: I see digital drawing both as a sort of drawing among many others, and at the same time as something completely different, it adds something other than traditional drawing tools.