bluuebunny/crossref_metadata_2025_split huggingface dataset:
Systemic Lupus Erythematosus and Lupus Nephritis in Children: Practical Approaches to Diagnosis and Treatment
Authors: Снопков В.В. , Байко С.В. 
Published: July 2024

Системная красная волчанка (СКВ) – это редкое мультисистемное аутоиммунное воспалительное заболевание. Несмотря на потенциальное поражение различных органов и систем, наиболее часто патологические проявления отмечаются со стороны кожи, суставов, центральной нервной системы, клеток крови и почек. Поражение почек при СКВ называется люпус-нефритом и чаще представлено иммунокомплексным гломерулонефритом. Люпус-нефрит является наиболее тяжелой формой СКВ, встречается чаще и протекает тяжелее в детском возрасте, требует раннего агрессивного вмешательства и непрерывной поддерживающей терапии. Несмотря на значительное улучшение отдаленных последствий заболевания, сохраняется высокая заболеваемость и смертность. Ограничение проведения широкого спектра исследований в детском возрасте затрудняет применение новых лекарственных средств и инновационных схем терапии. Существует необходимость в разработке более специфических фармакологических препаратов для пациентов, которые были бы одинаково эффективны, менее токсичны и имели бы меньше осложнений. В данном литературном обзоре будут рассмотрены этиология, эпидемиология, клинические проявления, практические подходы к постановке диагноза СКВ и люпуснефрита, оценке активности и хронизации патологического процесса в почках, а также современные рекомендации по лечению.
Systemic lupus erythematosus (SLE) is a rare, multisystem autoimmune inflammatory disease. Despite the potential damage to various organs and systems, the most frequent pathological manifestations are observed in the skin, joints, central nervous system, blood cells and kidneys. Kidney damage in histologically confirmed SLE is called lupus nephritis and is most often represented by immune complex-mediated glomerulonephritis. Lupus nephritis is the most severe form of SLE; it occurs more frequently and progresses more severely in childhood, requiring early aggressive intervention and continuous maintenance therapy. Despite significant improvement in the disease’s long-term outcomes, high morbidity and mortality persist. Limitation of a wide range of studies in childhood makes it difficult to use new drugs and innovative treatment regimens. A need exists for elaborating more patient-specific pharmacologic agents, which would be both equally effective, less toxic, and would have fewer complications. In this literature review, the etiology, epidemiology, clinical manifestations, practical approaches to diagnosing SLE and lupus nephritis and assessing renal pathological process activity and chronicity, as well as modern treatment recommendations will be considered.
Osteoporosis in Children with Duchenne Muscular Dystrophy: Current State of the Problem
Authors: Галашевская А.А. , Почкайло А.С. , Водянова О.В. 
Published: July 2024

Мышечная дистрофия Дюшенна (МДД) – наследственное Х-сцепленное рецессивное нервно-мышечное заболевание, клинически проявляющееся у мальчиков и характеризующееся прогрессирующей мышечной слабостью, ранней утратой способности к самостоятельному передвижению, костно-суставными деформациями, развитием кардиомиопатии, сердечной и дыхательной недостаточности. В настоящее время основным методом лечения МДД являются глюкокортикостероиды (ГКС) системного действия, позволяющие замедлить прогрессирование заболевания и продлить жизнь пациентам. Однако длительное применение ГКС в сочетании с прогрессирующей миопатией и содружественно нарастающей иммобилизацией оказывает негативное влияние на состояние костной ткани вплоть до развития остеопороза. Целью данного обзора является обобщение и систематизация имеющихся на сегодняшний день данных об эпидемиологии, факторах риска, подходах к диагностике, лечению и профилактике остеопороза у детей с МДД. Особое внимание уделяется раннему выявлению ключевого проявления ГКС-остеопороза – переломов позвонков.
Duchenne muscular dystrophy (DMD) is a hereditary X-linked recessive neuromuscular disease, clinically manifested in boys and characterized by progressive muscle weakness, early loss of the ability to move independently, osteoarticular deformities, development of cardiomyopathy, as well as cardiac and respiratory failure. Currently, the main treatment method for DMD is systemic glucocorticosteroids (GCS) therapy allowing delaying the disease progression and prolonging patients’ lives. Yet prolonged GCS use in combination with progressive myopathy and concomitantly increasing immobilization negatively affects the bone tissue condition up to osteoporosis formation. The purpose of this review is to summarize and systematize currently available data on the epidemiology, risk factors, and approaches to diagnosis, treatment and prevention of osteoporosis in children with DMD. A particular attention is paid to early detection of the key manifestation of GCS-induced osteoporosis, namely vertebral fractures.
INTEGRITY AS THE MOST IMPORTANT CHARACTERISTIC OF A LAWYER'S REPUTATION
Authors: МАХМУДОВА Д.М. МАХМУДОВА Д.М. , МАЛАМАГОМЕДОВ М.А. МАЛАМАГОМЕДОВ М.А. 
Published: July 2024

В статье рассмотрены этические основы профессиональной деятельности адвоката, дана характеристика понятия адвокатской этики, определен принцип добросовестности как основополагающий принцип профессиональной этики адвоката.
The article examines the ethical foundations of the professional activity of a lawyer, characterizes the concept of lawyer ethics, defines the principle of good faith as the fundamental principle of professional ethics of a lawyer.
TO THE QUESTION OF THE HISTORY OF THE EMERGENCE OF THE CATEGORIES "GOODWILL" AND "BUSINESS REPUTATION"
Authors: КАСУМОВ Р.М. КАСУМОВ Р.М. 
Published: July 2024

В статье представлено описание исторической ретроспективы возникновения терминов «гудвил» и «деловая репутация». Представлены характеристики данных показателей, определены отличия. Затронут вопрос о разнице между деловой репутацией физического и юридического лица. Подчеркнута важность формирования и поддержания положительной деловой репутации компании.
The article describes the historical retrospective of the emergence of the terms "goodwill" and "business reputation". The characteristics of these indicators are presented, differences are determined. The question of the difference between the business reputation of an individual and a legal entity is raised. The importance of forming and maintaining a positive business reputation of the company is emphasized.
ANALYSIS OF THE SOCIO-ECONOMIC PERCEPTION OF THE RESORT FEE AND ITS IMPACT ON THE ECONOMICS OF THE RECREATIONAL BUSINESS IN THE RUSSIAN FEDERATION
Authors: МАХНЕНКО С.И. МАХНЕНКО С.И. , БОГАЧЕВ Е.А. БОГАЧЕВ Е.А. 
Published: July 2024

В настоящей статье рассматривается курортный сбор, его основополагающие особенности, социальное восприятие и экономические эффекты. Анализируется предыстория современного курортного сбора в РФ, специфику НПА, регламентирующих курортный сбор. Помимо этого, производится анализ понятия современного курортного сбора в РФ в контексте присоединения Крыма и развития экономики Краснодарского края. Проводится взаимосвязь между курортным сбором и состоянием инфраструктуры курортов Краснодарского края и республики Крым, а также делаются предположения по увеличению эффективности и нормативно-правовой целесообразности курортного сбора в РФ.
This article examines the resort fee, its fundamental features, social perception and economic effects. The article analyzes the background of the modern resort fee in the Russian Federation, the specifics of the regulations governing the resort fee. In addition, the concept of a modern resort fee in the Russian Federation is analyzed in the context of the annexation of the Crimea and the development of the economy of the Krasnodar Territory. The relationship between the resort fee and the state of the infrastructure of the resorts of the Krasnodar Territory and the Republic of Crimea is carried out, and assumptions are made to increase the efficiency and regulatory expediency of the resort fee in the Russian Federation.
SOSIALISASI PENTINGNYA KIP KULIAH BAGI SISWA DARI KELUARGA DENGAN KETERBATASAN EKONOMI DI SMA TARUNA MADANI
Authors: Wahyuni Yayuk , Kuswandari Inna , Jaelani Abdulloh 
Published: July 2024

Kegiatan pengabdian kepada masyarakat ini difokuskan pada upaya peningkatan kesadaran masyarakat akan pentingnya pendidikan bagi peningkatan kualitas hidup. Permasalahan utama mitra adalah rendahnya keterserapan lulusan SMA di Kabupaten Pasuruan di jenjang pendidikan tinggi. Penyebabnya antara lain motivasi siswa yang relatif rendah, kondisi ekonomi orang tua yang kurang mampu, dan akses informasi yang terbatas. Solusi atas permasalahan ini adalah penguatan motivasi siswa, pemetaan motivasi dan potensi siswa, serta penyebaran informasi program KIP Kuliah. Kegiatan pengabdian kepada masyarakat ini bermitra dengan dua pihak, yaitu Musyawarah Guru Bimbingan dan Konseling (MGBK) SMA/SMK Kabupaten Pasuruan dan SMA Taruna Madani Jawa Timur. Sasaran kegiatan adalah siswa dan guru Bimbingan Konseling SMA/SMK se Kabupaten Pasuruan. Skenario pelaksanaan dikemas secara daring dan luring. Berdasarkan hasil tes diperoleh bahwa adanya peningkatan pengetahun siswa sebesar 24,23 % sedangkan guru BK sebesar 15,25 % terkait pentingnya pendidikan tinggi serta kemanfaatan KIP Kuliah untuk pembiayaan pendidikan tinggi dalam menjembatani kesenjangan ekonomi masyarakat. Lebih lanjut peran pendampingan yang lebih inten dari guru BK signifikan dalam memotivasi dan memberikan rekomendasi yang tepat bagi siswa untuk menempuh kuliah di perguruan tinggi
Psychosomatic dyssomnia in patients with different forms of diffuse alopecia: variability and intensity of clinical manifestations
Authors: Chemerys Maryana , Markova Marianna 
Published: July 2024

The purpose of the work is to analyze the presence, variability and intensity of sleep disturbances in patients with diffuse alopecia, in order to create, in the future, differentiated and individualized approaches to the management of this category of patients. 153 women aged 25 to 45 with diffuse alopecia were examined. With the help of a structured interview according to the ICD-10 criteria and the use of a psychodiagnostic method, three groups were distinguished among patients: without signs of mental maladjustment (MM), numbering 45 people, with separate signs of maladjustment, numbering 73 people, and with the presence of adaptation disorders, respectively to the criteria of ICD-10, numbering 35 people. Within each of these groups, two subgroups were distinguished, taking into account the genesis of alopecia: metabolic (45 patients) or mixed (108 patients). It was established that in the structure of psychosomatic clinical manifestations of the pathological trichological process in patients with diffuse alopecia, the entire variable spectrum of clinical dyssomnia symptoms is found — early, middle, late dyssomnias, nightmares and lack of rest after waking up — the prevalence and intensity of which are associated with the genesis of dermatological pathology (metabolic or mixed forms of alopecia). Among patients with a mixed form of diffuse alopecia, psychosomatic dyssomnic manifestations have a significantly greater representation and severity than among patients with metabolic alopecia, which is confirmed by the presence of statistically significant differences.
Key words:	psychodermatology, psychosomatics, mental health disorders, alopecia, mental maladjustment, adaptation disorders, dyssomnia, sleep disorders
Approximation of boundary conditions in the analytical solution of the problem of self-balanced stresses for a cylindrical rock sample
Authors: Останин М.В. , Любимова О.Н. , Свердлов Е.А. 
Published: July 2024

Исследуется явление реверсивного характера деформаций в предразрушаюей области образца горной породы при одноосном сжатии на основе модельных представлений теории самоуравновешенных напряжений с учетом экспериментально наблюдаемой деформационной картины на поверхности образца. Экспериментальные данные получены с помощью акустико-деформационного метода. Актуальность данного исследования связана именно с развитием неклассических модельных представлений механики деформируемого твердого тела, эволюции напряженно-деформируемого состояния в массивах и образцах горных пород при разного рода силовых воздействиях. Разработан метод определения полной картины напряженно-деформированного состояния во всем объеме образца на протяжении всей истории нагружения.
The phenomenon of reversible deformat-on in the pre-destructive region of a rock specimen under uniaxial compression is investigated on the basis of model representati-ons of the theory of self-equilibrated stresses, taking into account the experimentally observed deformation pattern on the specimen surface. The experimental data were obtained using the acoustic-deformation method. The relevance of this study is related to the development of non-classical model representat-ions of mechanics of deformable solid bodies, the evolution of stress-strain state in arrays and rock samples under different kinds of force actions. A method for determining the complete stress-strain state in the entire volume of the specimen throughout the entire loading history has been developed.
On the appearance of plastic regions in a rotating disk
Authors: Артемов М.А. , Барановский Е.С. , Меджидов Р.Г. , Соломатин Д.И. 
Published: July 2024

Проблема получения непрерывных полей пластических деформаций при решении задач плоского напряженного состояния, в отличие от плоского деформированного состояния, характерна для всех моделей идеального упругопластического тела, включающих кусочно-линейные функции пластичности. Однако в ряде западных научных статей считается, что только модель идеального упругопластического тела с условием пластичности Треска неправильно прогнозирует неупругие деформации. В настоящей работе определяются границы изменения внешних параметров нагрузки, для которых диск будет находиться в упругом состоянии. Напряжения связаны с упругими деформациями законом Гука. В зависимости от значений параметров нагрузки пластическая область может зарождаться на внутренней границе диска, или на внешней границе диска, или на обеих границах одновременно. Рассматриваются разные условия пластичности. Показан вид годографа вектора напряжений.
Problem obtaining continuous fields of plastic deformations when solving problems of a plane stress state, in contrast to a plane deformed state, is characteristic of all models of an ideal elastoplastic body that include piecewise linear plasticity functions. However, only the model of an ideal elastoplastic body with the Tresca plasticity condition in a number of Western scientific articles is considered to incorrectly predict inelastic deformations. In this work, the boundaries of changes in external load parameters are determined for which the disk will be in an elastic state. Stresses are related to elastic deformations by Hooke’s law. Depending on the values of the load parameters, a plastic region can nucleate on the inner boundary of the disk, either on the outer border of the disk, or on both borders simultaneously. Various plasticity conditions are considered. The view of the stress hodograph vector is shown.
Determination of the ultimate loads of an n-layer physically nonlinear concrete rod
Authors: Немировский Ю.В. , Тихонов С.В. 
Published: July 2024

В данной работе рассматривается задача изгиба многослойного стержня поперечными нагрузками при наличии зон упругого и нелинейно-неупругого деформирования, получены соотношения для определения границы раздела упругой и нелинейно-неупругой областей деформирования стержня. Получены численные расчеты для случаев совпадения и несовпадения нейтральной линии с осью стержня. Приведены численные расчеты предельных нагрузок: первой (деформация достигает значения предельной неупругой) и второй (деформация достигает значения деформации предразрушения).
This paper considers the problem of bending a multilayer rod under transverse loads in the presence of zones of elastic and nonlinear-inelastic deformation, and relations are obtained to determine the interface between the elastic and nonlinear-inelastic deformation regions of the rod. Numerical calculations were obtained for the cases of coincidence and non-coincidence of the neutral line with the axis of the rod. Numerical calculations of the ultimate loads are presented: the first (the deformation reaches the limiting inelastic value) and the second (the deformation reaches the value of the pre-fracture strain).
Clarification of the solution to the maximum permissible deformations of hybrid polymetallic Simson trusses
Authors: Немировский Ю.В. 
Published: July 2024

Рассматривается решения предельно допустимых деформаций гибридных полиметаллических ферм Мизеса. Предполагается, что все элементы создаваемой фермы Мизеса сохраняют основные базовые характеристики материалов при производстве фермы, независимо от используемых технологических разработок.
Solutions for maximum permissible deformations of hybrid polymetallic Mises trusses are considered. It is assumed that all elements of the created Mises farm retain the basic basic characteristics of the materials used in the production of the farm, regardless of the technological developments used.
The Evaporating Massive Embedded Stellar Cluster IRS 13 Close to Sgr A*. II. Kinematic Structure
Authors: Peißker Florian , Zajaček Michal , Labaj Matúš , Thomkins Lauritz , Elbe Andreas , Eckart Andreas , Labadie Lucas , Karas Vladimír , Sabha Nadeen B. , Steiniger Lukas , Melamed Maria 
Published: July 2024

Abstract
The existence of two distinct and apparently unrelated populations of dusty stellar objects in the Nuclear Stellar Cluster of the Milky Way, namely IRS 13 and the S-cluster, are potentially prone to a general process describing the star formation history in the Galactic center (GC). The former cluster is thought to be entangled in the clockwise and counterclockwise disks, a large-scale stellar distribution revealed by the analysis of stars at different distances from Sgr A*, the supermassive black hole in the GC. Recently, this large-scale distribution was reported to exhibit a multidisk structure with at least four components. Motivated by this finding, we revisit the anisotropic IRS 13 cluster and find strong evidence for a disk-like structure. An examination of about 50 individual stellar orbits reveals a new structure that does not follow any trend known in the literature. Furthermore, we investigate the possibility of an inspiral cluster undergoing star formation processes, as proposed by several authors. Using a simplified N-body simulation to reproduce our observational results, we conclude that, under certain conditions, a massive cluster can migrate from the Circum Nuclear Disk toward the inner parsec. Based on this classification, we revisit the large-scale NACO Very Large Telescope (VLT) observations of IRS 13 and find evidence for a separation of the cluster into a gravitationally stable core remnant and a dissipating part. With the velocity-resolved H30α line and the broadband spectral energy distribution of IRS 13 E3, we provide tentative support for the existence of an intermediate-mass black hole of ∼3 × 104
M
⊙ surrounded by a hot gaseous stream.
Applications of Fast Magnetic Reconnection Models to the Atmospheres of the Sun and Protoplanetary Disks
Authors: Pucci Fulvia , Singh K. Alkendra P. , Gorti Uma , Turner Neal J. , Velli Marco , Varshney Disha , Innocenti Maria Elena 
Published: July 2024

Abstract
Partially ionized plasmas consist of charged and neutral particles whose mutual collisions modify magnetic reconnection compared with the fully ionized case. The collisions alter the rate and locations of the magnetic dissipation heating and the distribution of energies among the particles accelerated into the nonthermal tail. We examine the collisional regimes for the onset of fast reconnection in two environments: the partially ionized layers of the solar atmosphere, and the protoplanetary disks that are the birthplaces for planets around young stars. In both these environments, magnetic nulls readily develop into resistive current sheets in the regime where the charged and neutral particles are fully coupled by collisions, but the current sheets quickly break down under the ideal tearing instability. The current sheets collapse repeatedly, forming magnetic islands at successively smaller scales, until they enter a collisionally decoupled regime where the magnetic energy is rapidly turned into heat and charged-particle kinetic energy. Small-scale, decoupled fast reconnection in the solar atmosphere may lead to preferential heating and energization of ions and electrons that escape into the corona. In protoplanetary disks such reconnection causes localized heating in the atmospheric layers that produce much of the infrared atomic and molecular line emission observed with the Spitzer and James Webb Space Telescopes.
Discovery and Follow-up of a Quasiperiodically Nulling and Subpulse Drifting Pulsar with the Murchison Widefield Array
Authors: Grover Garvit , Bhat N. D. Ramesh , McSweeney Samuel J. , Lee Christopher P. , Meyers Bradley W. , Tan Chia Min , Kudale Sanjay S. 
Published: July 2024

Abstract
The phenomenon of pulsar nulling, where pulsars temporarily and stochastically cease their radio emission, is thought to be indicative of a “dying” pulsar, where radio emission ceases entirely. Here we report the discovery of a long-period pulsar, PSR J0452−3418, from the ongoing Southern-sky MWA Rapid Two-meter pulsar survey. The pulsar has a rotation period of ∼1.67 s and a dispersion measure of 19.8 pc cm−3, and it exhibits both quasiperiodic nulling and subpulse drifting. Periodic nulling is uncommon, reported in only <1% of the pulsar population, with even a smaller fraction showing periodic nulling and subpulse drifting. We describe the discovery and follow-up of the pulsar, including a positional determination using high-resolution imaging with the upgraded Giant Metrewave Radio Telescope (uGMRT), initial timing analysis using the combination of Murchison Widefield Array (MWA) and uGMRT data, and detailed characterization of the nulling and drifting properties in the MWA’s frequency band (140–170 MHz). Our analysis suggests a nulling fraction of 34% ± 6% and a nulling periodicity of

42

−
1.3

+
1.5

pulses. We measure the phase (P
2) and time modulation (P
3) caused by the subpulse drifting, with an average P
2 of 7.1

−
3.1

+
26.3

degrees and a P
3 of 4.8

−
0.9

+
1.5

pulses. We compare and contrast the observed properties with those of other pulsars that exhibit subpulse drifting and quasiperiodic nulling phenomena, and find that the majority of these objects tend to be in the “death valley” in the period–period derivative (P–

P

̇

) diagram. We also discuss some broader implications for pulsar emission physics and the detectability of similar objects using next-generation pulsar surveys.