bluuebunny/crossref_metadata_2025_split huggingface dataset:
Course of autosomal dominant and autosomal recessive polycystic kidney disease (ADPKD and ARPKD) wich detected in prenatal, neonatal and infant periods in children.
Authors: Andreeva E. F. , Savenkova N. D. 
Published: August 2019

THE AIM:to characterize the features of the course of autosomal dominant (ADPKD) and autosomal recessive (ARPKD) polycystic kidney disease detected in the prenatal, neonatal and thoracic periods.PATIENTS AND METHODS:ADP was diagnosed in 28 and ARPP in 12 of 40 children and adolescents. The dynamics of the diameter of renal cysts (mm), total kidney volume (TKV, cm3) by ultrasound were evaluated; Constructed trend lines for average TKV and diameter of renal cysts. The glomerular filtration rate is determined by the Schwartz formula. Liver fibrosis was detected by ultrasound / MRI / CT / biopsy.RESULTS:ADPKD was detected prenatally and during the first year of life in 19.1 %, ARPKD in 70.6 %. Stable arterial hypertension was diagnosed with an ADPKD with “very early detection” in 7 % (among adolescents), with ARPKD in 100 % (under 3 years of age). The diameter of the renal cysts increases with ADPKD. Renal cysts are multiple, bilateral since birth with ARPKD, the diameter of the cysts does not increase. TKV increased at birth in 3.6 % of children with ADPKD, in 100 % with ARPKD. The trend line of average TKV with ADPKD is exponential, with ARPKD – linear. Extrarenal location of cysts was diagnosed with ADPKD in 3.6 % (in the testes), with ARPKD in 67 % (in the liver). Liver fibrosis with portal hypertension syndrome was detected in children with ARPKD in 33.3 %; performed ligation of the veins of the esophagus. Acute kidney damage was found in newborns with ADPKD in 3.6 %, with ARPKD in 33.3 %. Fatal outcome was ascertained in 3 (25 %) children with ARPKD. In the follow-up, the outcome in HBPS3 is in 2 children with ADPKD and 3 children with ARPP, in HBPS4 in 1 child with ARPKD.CONCLUSION:features of the course of ADPKD and ARPKD revealed in the prenatal, neonatal and thoracic periods are shown.
Pengaruh Customer Perceived Value , Service Quality, Dan Physical Environment Terhadap Kepuasan Dan Kesetiaan Pelanggan
Authors: Keni Shelly Agustina Natawijaya Dan 
Published: August 2019

The aim of this study are : First, to explore the effect of customer perceived value , service quality, and physical environment on customer loyalty. Second, to explore the effect of customer perceived value , service quality, and physical environment on customer satisfaction. Third, to explore the effect of customer satisfaction towards customer loyalty. Fourth, to find out if customer satisfaction can mediate customer perceived value , service quality, and physical environment towards customer loyalty. The method of data collection is purposive sampling. The samples of this research are collected from 326 respondents, who are the customers of furniture store in Jakarta. The technique of data analysis used in this study was regression analysis and mediating test to find put the hypotheses. The results are : (a) the relationship between customer perceived value , service quality, and physical environment have a significant and positive impact toward customer loyalty; (b) the relationship between customer perceived value , service quality, and physical environment have a significant and positive impact toward customer satisfaction; (c) customer satisfaction has a positive impact on customer loyalty; (d) customer satisfaction will mediate the effect of customer perceived value , service quality, and physical environment towards customer loyalty.
Pengaruh Citra Perusahaan Dan Reputasi Terhadap Kualitas Pelayanan Dan Dampaknya Pada Kepuasan Pelanggan (Pada Nasabah Tabungan Bank Artha Graha)
Authors: Mukti Rahardjo Kevin Dan 
Published: August 2019

This study aims to analyze the influence of corporate image and reputation on service quality and its impact on customer satisfaction in PT. Bank Artha Graha Tbk. This research used quantitative methods. The data is the primary data obtained through the distribution of questionnaires. The population in this study was customers of Bank Artha Graha, Tbk. The number of samples was determined by using Hair et.al. (1998) sampling method that is at least 5 times the number of parameters used in the study. The number of sample collected was 215 respondents. Using multiple linear regression analysis, it was found that corporate image and company reputation to have direct and significant positive effect on service quality and customer satisfaction on Bank Tabungan Graha Bank Tabungan Graha. Corporate image and company reputation has contributed 77.1% to the quality of service. In addition, the quality of service has direct and significant positive impact on service satisfaction on the Bank Tabungan Graha Bank Tabungan Graha. Contribution of company influence, company reputation and service quality equal to 71,5% to customer satisfaction. Corporate image has indirectly affected customer satisfaction through service quality at Bank Artha Graha Tbk that is 5,5% similarly, Company Reputation has indirectly influence to customer satisfaction through service quality at Bank Artha Graha Tbk that is equal to 5,3%. To improve customer satisfaction the company must maintain the corporate image abd reputation of the company through the quality of service.
Analisis Strategi Soar Pt. Xyz Dalam Meningkatkan Penjualan Bahan Baku Kimia Untuk Industri Tekstil, Kayu, Pakaian Dan Deterjen
Authors: Chiu Calvin 
Published: August 2019

PT. XYZ is a private multinational company engaged in chemical type commodities trading with sodium sulphate, sodium carbonate and hydrogen peroxide – three of the most common chemicals used in textile, pulp & paper and detergent industry – as their main traded commodities. However, due to many opportunities available and the company’s experience as an international trader, marketing plan should not be ignored especially when the company is still relatively new as a supplier. Based on last year sales revenue alone, PT. XYZ placed third among four other companies, placing PT. XYZ as a market follower and thus needed to formulate an offensive strategy to achieve higher sales. The method used in this study is by using SOAR tool instead of SWOT analysis and translated into Treacy and Wiersema’s value disciplines. consisted of three strategies, i.e. operational excellence, customer intimacy and product leadership. The study found that there is a need for the company to use a combined strategy of operational excellence and customer intimacy.
Studi Strategi Pengembangan Kredit Pada Usaha Mikro,Kecil, Dan Menengah Oleh Bank Bumn Di Daerah Cikarang-Jawa Barat Kasus Bank Bri
Authors: Adrian Hans 
Published: August 2019

Usaha Mikro,Kecil dan Menengah (UMKM) memainkan peran penting dalam pembangunan ekonomi Indonesia sekitar 54-57% Produk Domestik Bruto Indonesia berasal dari sektor ini. Terlepas dari manfaatnya dalam mengurangi tingkat pengangguran, UMKM juga telah berhasil membuktikan kekuatannya terhadap dampak krisis moneter yang terjadi pada tahun 1998. Cikarang dikenal sebagai salah satu kawasan industri Indonesia sedangkan pelaku bisnis membangun banyak perusahaan besar dan pabrik di sana. Efisiensi organisasi besar ini dalam menjalankan bisnisnya sangat dipengaruhi oleh kemampuan UMKM sebagai pemasok untuk menyediakan bahan yang dibutuhkan, sementara kemampuan UMKM dalam mengelola bisnis mereka bergantung pada masalah permodalan. Oleh karena itu, tesis ini bertujuan untuk menganalisis strategi pengembangan Kredit Usaha Mikro Kecil dan Menengah (UMKM) di daerah Cikarang-Jawa Barat, dan strategi yang dapat diterapkan untuk meningkatkan pertumbuhan dan perkembangan Usaha Mikro Kecil Menengah (UMKM) dengan memanfaatkan bank milik negara sebagai salah satu faktor pertumbuhan ekonomi. Sebagai Agen yang memberikan kontribusi penting bagi perekonomian Indonesia.
Pengaruh Green Perceived Value, Green Perceived Risk, Green Consumer Consfusion, Green Trust, Consumer Guilt, Self Monitoring, Pride Dan Perceived Consumer Effectiveness Terhadap Green Purchase Intention (Kasus Starbucks Jakarta)
Authors: Antonius Feliks 
Published: August 2019

The research aims to find out the relationship between green perceived value, green perceived risk, green consumer consfusion, green trust, consumer guilt, self monitoring, pride and perceived consumer effectiveness to green purchase intention in Starbucks Jakarta. The method used in sampling is non-probability sampling method with purposive sampling technique which is a sampling technique by selecting sampling unit on the basis of certain criteria. The period of questionaire taking starts in May-September 2017. The data obtained will be analyze using Structural Equation Modeling (SEM). The conclusion of this study indicates green perceived value and green perceived risk have significant influence to green trust. Consumer guilt, self monitoring and pride have significant effect to perceived consumer effectiveness on product Starbucks. Green trust and perceived consumer effectiveness as intervening variable at significance 5%. More specifically, the effect of green consumer confusion on green trust is not significant and the effect of green trust on green purchase intention is not significant too. The sum of increasing perceived consumer effectiveness then increasing green purchase intention.
Pengaruh Faktor-Faktor Fundamental Terhadap Tingkat Kelengkapan Pengungkapan Laporan Keuangan Perusahaan Manufaktur Yang Terdaftar Di Bursa Efek Indonesia Pada Tahun 2015 Dan Tahun 2016
Authors: Fitelia Kenny 
Published: August 2019

Tujuan penelitian ini adalah untuk memperoleh informasi ada atau tidaknya pengaruh rasio likuiditas, rasio leverage, rasio profitabilitas, porsi saham publik dan ukuran perusahaan terhadap kelengkapan pengungkapan laporan keuangan perusahaan manufaktur yang terdaftar di Bursa Efek Indonesia baik secara parsial maupun simultan. Besarnya pengaruh rasio likuiditas, rasio leverage, rasio profitabilitas, porsi saham publik dan ukuran perusahaan terhadap kelengkapan pengungkapan laporan keuangan perusahaan manufaktur yang terdaftar di Bursa Efek Indonesia. Populasi dalam penelitian ini adalah laporan keuangan perusahaan manufaktur yang terdaftar di Bursa Efek Indonesia (BEI) baik perusahaan berskala kecil maupun besar pada tahun 2015 dan tahun 2016. Tehnik pengambilan sampel dengan pengambilan sampel terpilih (non probability sampling) yaitu dengan purposive sampling. Penelitian ini termasuk gabungan antara penelitian time series dan cross section yaitu dengan melakukan pengamatan pada perusahaan manufaktur untuk periode selama 2 (dua) tahun, yaitu tahun 2015 dan 2016 untuk laporan keuangan perusahaan manufaktur yang terdaftar di Bursa Efek Indonesia. Pada penelitian ini didapatkan hasil bahwa likuiditas (X1) mempunyai pengaruh negatif terhadap kelengkapan pengungkapan laporan keuangan, leverage (X2) berpengaruh positif terhadap tingkat kelengkapan pengungkapan laporan keuangan, profitabilitas (X3) tidak mempengaruhi kelengkapan pengungkapan laporan keuangan, ukuran perusahaan (X4) berpengaruh positif terhadap kelengkapan pengungkapan laporan keuangan, porsi saham publik (X5) berpengaruh positif terhadap kelengkapan pengungkapan laporan keuangan.
Update to the South African Stratigraphic Code and Guidelines for Standardised Lithostratigraphic/Lithodemic Descriptions
Authors: de Beer C.H. 
Published: August 2019

Summary
The South African Committee for Stratigraphy (SACS) is the official body in South Africa which regulates the nomenclature and definition of lithostratigraphic and lithodemic rock units, unconsolidated deposits and soils. The robust framework set in the existing stratigraphic code and guide for publication by the Council for Geoscience (CGS) have for many years provided leadership in this field, but there are a number of aspects in need of reconsideration. One example is the non-compliance of our nomenclature for high-grade supracrustal rocks with international (and South African) stratigraphic codes and another is manuscript format changes necessitated by publishing SACS descriptions in the SAJG. Any stratigraphic code is a living document that should be able to accommodate changing views and circumstances. This review provides a consensus opinion from experts on how to deal with changing needs.
Human capital for digital economy modernization
Authors: Afanasyev V. Y. , Grabchak E. P. , Korytny M. A. , Mishcheryakov S. V. , Cherezov A. V. 
Published: August 2019

The article outlines the scientific approaches to the formation of digital technologies of the ecosystem of professional education and management of the formation of human capital for the real sector of the Russian economy. It has been proposed to highlight specific competences as training units (quantums), digitize them, create a level classifier and build an ordering system, a system of choice used for order fulfillment, a continuous (from general education to professional education for a given position) professional education system based on individual educational trajectories with well-defined (digitized) parameters and focused investments in human capital. Using the formed systems, it has been proposed to provide digital modernization of the main didactic processes with guaranteed achievement of specific diagnosed learning outcomes in accordance with the order.For new competencies it is possible to develop ontological models of employee professional activities. Herewith it is planned to solve several important tasks, including the development and adoption of a general concept of continuous professional education, the selection and classification of didactic units for specific professions, the development and introduction of a classification system for educational organizations according to their levels of competence, the development and introduction of a system for qualifying teachers, formation of a system of educational trajectories (necessary competencies) for business, development of pedagogical technologies standards that guarantee the achievement of results (the right people - in the right place - at the right time). It has been offered to select several branches of the real sector of the economy for the implementation of pilot projects with the subsequent dissemination of experience throughout the Russian economy.
Management of organizational culture in the conditions of enterprises digitalization
Authors: Groshev I. V. , Zheregelya A. V. , Shkolnyi D. V. 
Published: August 2019

Global digitalization processes are transcontinental and trans-industry in nature. There is no sphere vital activity, that does not feel the influence of digital institutions. Economic activity of agents is most sensitive to digital innovations and market shifts.The process of integrating digital innovations into the activities of large foreign companies, based on the study of foreign sources, has been considered. The dignities, advantages and disadvantages of this practice have been adduced. The consequences of the ill-conceived unbalanced policies of companies in the context of following fashion trends, happening in the digital environment, have been analyzed separately. The conclusion about the need to customize Russian companies to the modern requirements of the global digital market has been made. It is noted, that the domestic practice lags behind not so much in the mechanism of implementation of modern digital practices, but in the efficiency of their use and qualitative growth of the organizational structure due to the synergetic effect of digitalization of production and all related procedures and processes.The authors have concluded, that the management of a modern company should be based on the interaction of all stakeholders, and not due to the dominance of processes and hierarchy, which in turn, will require changes in the management of organizational culture. At the center of this interaction there are digital social tools, the useful functions of which are obvious, on the one hand, determining the dynamics of interaction (openness, sincerity, human communication), on the other - expanding the area of awareness of participants in the interaction. Herewith it has been noted, that the use of modern information products is necessary in a certain balance with standard offline work tools.
Competitive strategies of internationalization, searching and creating markets
Authors: Mickhailov O. V. 
Published: August 2019

Actuality, content and advantages of strategies of the business internationalization, detecting and creating new markets are often remaining underestimating and ignoring of many subjects of the world economy. During formation of strategies and competitive advantages are missed the problems and possibilities of the world market and competition for the accelerated and outstriped self-developing of the business subjects. The gap is increased between traditional approaches to the strategies and real needs of the world, between temporary advantages and stable competitiveness, between competitive leaders and majority subjects of the world and national economies. The existing barriers for business internationalization are determined mainly by the traditional mental-goal oriented arrangements. Considering strategies are connected with ensure of the leadership on the world markets, that means more than the largest market share or quantitative its changes.The modern leadership in the world includes the superiority in innovation ability unique technologies, key competencies, setting up perspective directions of progress, new standards and game rules for the competitors. The psychological leadership often precedes the market leadership, it is its cause and foundation. The world market champions are highlighted by psychology superiority and intellectual leadership, implying desire to appoint the tendencies on the market not only go after them. The hidden champions became leaders, because they offered entire world their best and incessant improved products/services to all world clients. The combination of specialization (concerning products and know-how) and global broadening of the market/niche has diversity advantages, including of economies on scale, experience curve and temporal monopolization of the market niche.The strategy of revealing and creating new markets and market niches can form and create not only big companies, but middle and small enterprises, having unusually initiatives, invention initiatives, creation capabilities in finding and creating the new markets/niches. Transnational expanding the business can be calling out by the different motives, but it should start as early as possible and realise as quickly as possible. The leaders of the world economy create their products, possibly more distinctive and not accept еру definition and the boundaries of the market, given by their competitors, instead, they determine their market themselves.
Prospects for cooperation between the financial corporation and companies, working in the field of digital technologies
Authors: Efremov V. S. , Pilishvili A. S. 
Published: August 2019

The problems, associated with the development of new digital technologies, which, in turn, have an impact on the activities of large financial institutions of the Russian Federation, have been examined in the article. The aim of the study is to analyze the current situation in the economy, related to the growth of the market for digital products, their integration into the existing model of providing financial services to clients, as well as finding solutions to the joint activities of financial corporations and financial and technological companies. The definitions and main activities of financial corporations and fintech startups have been given in the article. The advantages and disadvantages of a large financial corporation and developing companies, operating in the field of digital technologies, as well as the positive results of combining their resources, have been highlighted. Positive examples of world experience in cooperation between the two types of these organizations and the attitude of the main regulator of the Central Bank of Russia to the development and implementation of financial technologies in the country’s economy have been adduced.The problems and opportunities of high competition in the struggle for the modern consumer, which lead to the rapid development of the entire financial industry market, have been analyzed. The results of the study have showed, that every day, worldwide, fintech companies test a significant number of digital products, various open architecture tools, methods of transferring information through blockchain technologies, and optimize and integrate into the existing systems new client base programs, that completely change the main business processes of large enterprises and have a significant impact on the main consumer - a person. This indicates the need for further research aimed at studying and analyzing the integration of financial corporations with technology companies, changing the existing business model, finding new approaches to the modern consumer and creating a new organization development strategy in the digital economy of the country.
Macroeconomic model of safe functioning of the national economy of Azerbaijan in the long-term period
Authors: Ayyubov M. R. 
Published: August 2019

In the 90s of the twentieth century, due to the formation of new independent states in the post-Soviet space, as well as a change in the constitutional foundations of Eastern European countries, the governments of the countries were faced with the task of ensuring economic security of the countries.In the scientific literature, there are three main paradigms for solving the problem of the country’s economic security: the paradigm of the country’s national interests; the paradigm of independent and independent development of the national economy; paradigm of sustainable development of the national economy. The economic system of the country, with its characteristic mechanism, operates in a cyclical mode, consisting of four stages: development, slowdown in development and stagnation (crisis), recession and depression, stabilization. It is necessary to have a toolkit (methodology), allowing one to foresee the onset and completion of all stages of the functioning cycle, the lead-time of more than 30 years. The structural and conjuncture equation of the country’s economy functioning cycle in the long-term period, with a leadtime of more than 30 years, can be used to determine the time of occurrence of economic threats in the national economy. The basis of the macroeconomic model of safe functional organization of the national economy of the country has been laid the equation of the cyclic functioning of the national economy, as a dynamic system, developed by the author, the equation of the cyclic functioning of the national economy of the country on the long-term period. Based on the equation of the cyclical functioning of the national economy of Azerbaijan, the time of the beginning of the slowing down rate of development of the national economy of the Republic has been determined. Three basic conditions for the safe functioning of the national economy have been offered. Based on the method, developed by the author, the basic conditions for the safe functioning of the national economy of Azerbaijan have been determined.