bluuebunny/crossref_metadata_2025_split huggingface dataset:
Unusual Characteristics and Variable Expressivity in a Brazilian Family with Cherubism
Authors: Deconte Desirée , Correia Elisa Pacheco Estima , Haubert Géssica , de Souza Vinicius , Correia Jamile Dutra , Maahs Marcia Angelica Peter , Zen Paulo Ricardo Gazzola , Fiegenbaum Marilu , Rosa Rafael Fabiano Machado 
Published: February 2020

AbstractCherubism is a rare genetic condition characterized by a bone nonneoplastic disease. We aimed to report a 6-year-old girl with cherubism presenting similar cases in the maternal family. However, her mother and grandmother seemed to be asymptomatic. The patient had an enlarged and asymmetric jaw with multiple enlarged cervical lymph nodes that increased in size with time. Sanger sequencing revealed a heterozygous mutation in exon 9 of SH3BP2 not only in the patient but also in her mother. Thus, we observed a variable expression and a probably reduced penetrance within the family, as well as unusual characteristics of the patient (in this case, the asymmetrical involvement of the jaw).
Building a CPTED research culture in Portugal: a bibliometric and social network analysis
Authors: Saraiva Miguel , Amante Ana , Santos Hélder , Ribeiro Paula 
Published: February 2020

AbstractAlthough CPTED is recognized as an important crime deterrent for some decades, there are countries where it is still in its infancy, and knowledge and dissemination are scarce. Portugal is such an example. Only in the last decade has research specifically focused on CPTED, with little convergence between the different spheres of knowledge production, such as the academia, the police or the administration. In this paper, we argue that to build a CPTED culture, these spheres need to converge. Using the Portuguese CPTED experience as a case study, we apply methodologies of social network analysis to explore the relationships between different actors and the research time-line. Through a bibliographical analysis, we further delve on the authors and theories that most influenced Portuguese CPTED. This dual approach allows introducing the little known Portuguese CPTED experience to the international community, as well as discussing how the mechanisms of knowledge production integrate towards a more cohesive implementation.
Children’s thinking-for-speaking
Authors: Aktan-Erciyes Asli , Göksun Tilbe , Tekcan Ali İzzet , Aksu-Koç Ayhan 
Published: February 2020

AbstractThis study investigates how children lexicalize motion events in their first and second languages, L1-Turkish and L2-English. English is a satellite-framed language that conflates motion with manner expressed in the main verb and path in a non-verbal element, whereas Turkish is a verb-framed language that conflates motion with path in the main verb and expresses manner in a subordinated verb. We asked three questions: (1) Does early L2 acquisition in an L1 dominant society affect motion event lexicalization in L1? (2) Is the effect of L2 on L1 subject to change due to decline in L2 exposure? (3) Do L1 vs. L2 lexicalizations differ within the bilingual mind? One hundred and twelve 5- and 7-year-old monolingual and bilingual children watched and described video-clips depicting motion events. For L1 descriptions, 5-year-old bilinguals used more manner structures than monolinguals. No difference was found for 7-year-olds. For L2 descriptions, 7-year-old bilinguals used more manner-only constructions compared to their L1 descriptions. For 5-year-old bilinguals no difference was found. Findings suggest that early exposure to a second language had an impact on how motion events are packaged, while decline in L2 exposure dampened the effects of L2.
Documenting linguistic and cultural heritage
Authors: Patpong Pattama 
Published: February 2020

AbstractThis paper aims to illustrate the relationship between documentary linguistics and ethnographic discourse analysis and to explore how language and cultural practices are connected in order to understand the linguistic practices and Black Tai death ritual as a key site of engagement. The Black Tai death ritual is selected in order to present the determined efforts made in maintaining Black Tai ethnic identity through cultural practices.Nexus analysis is introduced and deployed in this research to present the significance of Black Tai’s key communicative activity and social actions involved. In the analysis, the Black Tai death ritual is investigated. The study shows that documentary linguistics makes a noteworthy contribution to understanding the Black Tai’s linguistic and cultural heritage. It reveals that although death rituals are practiced in much the same way as they were in the past, there have inevitably been some significant changes depending on the locations, with specific adaptations and adopted elements based on the surrounding cultures (i.e., Thai culture and religious beliefs) and socio-economic conditions. Black Tai communities are at a settled stage of their death ritual practices by integrating certain aspects of Buddhism into their rituals.In order to construct a modern Black Tai identity among generations, younger generation engagement is challenging but it is essential for the inter-transmission of death rituals. With this dynamic cultural practice, the Black Tai are a good example of an adaptive and diverse ethnic group.
Attitudes towards Belhare, Nepali and English
Authors: Rai Ichchha Purna 
Published: February 2020

Abstract
This paper reports on a sociolinguistic study of the Belhare speech community which is a part of the Belhare language documentation project funded by the Language Commission of the government of Nepal in 2018. This article presents sociolinguistic information on Belhare, a lesser known speech community originally settled in Dhankuta, east Nepal. The main contribution of this paper is to examine domains of language use, language use among generations, attitude towards Belhare, Nepali and English, Belhare speakers as multilingual speakers, languages resources and language proficiency among children.
Towards education in children’s languages in Jharkhand, India
Authors: Pattanayak Binay 
Published: February 2020

Abstract
Jharkhand, India, is home to around 20 indigenous languages. People from around 33 indigenous communities use these
languages. Around 2010, the state used to experience children’s highest dropout from primary schools in the nation. In the
education system there was no clarity about how to address this persistent issue. In 2011, the author set up a research cell
titled M-TALL (Mother-Tongue-based Active Language Learning) akhra in the state. The center undertook a
socio-linguistic survey which revealed that around 96% children in the state did not speak in Hindi. They communicated in their
local indigenous languages at home, playground and market. The study also found out that children failed to understand their
teacher and textbooks written in Hindi. Initially the duty bearers did not pay any attention to the findings. The M-TALL
akhra researchers continued their exploration and collected a lot of learning resources from each community.
They developed bilingual picture dictionaries in 9 indigenous and regional languages for use in children’s early grades. Then
M-TALL akhra developed a pre-school education package. In 2016, the state government with help of M-TALL
akhra developed culturally sensitive new textbooks in 5 indigenous and 2 regional languages. Using these, the
state initiated a mother-tongue-based multilingual education programme in around 1000 schools.
Language revitalization and community initiatives
Authors: Bhattacharjee Bidisha 
Published: February 2020

AbstractLanguage is an integral part of the social identity and ethnicity of a community apart from being its mode of communication. Language plays a key role to preserve the history, culture and identity of a community. In this era of globalization, cultural and linguistic homogenization is a common trend. The state and dominant linguistic communities expect ‘others’ or the minority groups to assimilate into the dominant culture and language. Arguments for the maintenance and revitalization of minority and endangered languages have been made by many linguists around the world. Language rights, language planning and language documentation programmes are some steps taken by government and externally-funded organizations to protect endangered and indigenous languages. Besides the initiatives taken by the non-members of the community, the future of an endangered language and culture has been decided by the role and attitude of the community towards its community-specific linguistic and cultural identity. India is a very diverse country as far as its linguistic and cultural heritage is concerned. This project is enriched with insights from field experience in various districts of West Bengal, a state in India, where the speakers of endangered linguistic communities are aware of their linguistic rights and are highly engaged in the language and cultural revitalization, and in that their degree of progress and success is commendable. This paper aims at demonstrating the major role played by the communities themselves in language-revitalization programmes.
Sociolinguistic survey of Nepalese languages
Authors: Gautam Bhim Lal 
Published: February 2020

Abstract
This paper presents a close inspection of the research conducted with a sociolinguistic survey of Nepalese
languages developed by Linguistic Survey of Nepal (LiNSuN) Project (2008–2018). The paper provides an overview of the linguistic
situation of Nepal with brief outlines of various linguistic surveys in different times. It also examines the various
sociolinguistic surveys (SLS) and their implications. Through a reflection of my personal engagement in various activities of the
surveys, e.g. Kaike (Regmi 2012), Bhojpuri and Awadhi (Thakur and Regmi 2013), Khadiya (Dahal and Yadava 2014),
Gangai (Gautam and Thakur 2014) and Thulung (Gautam
and Sapkota 2014), Aathpahariya (Regmi 2015) and Tharu (Yadav 2015), Limbu (Gautam and Thakur 2016),
and Dhuleli (Prasai and Regmi 2017) and Lohwa (Gautam 2017), and quantitative
information available in the literature, it is concluded that previous surveys have mainly focused on sociolinguistic features and
have disregarded the ethnolinguistic characteristics.
Poly(cis-1,4-isoprene)-cleavage enzymes from natural rubber-utilizing bacteria
Authors: Kasai Daisuke 
Published: February 2020

ABSTRACT
Natural rubber and synthetic poly(cis-1,4-isoprene) are used industrially in the world. Microbial utilization for the isoprene rubbers has been reported in gram-positive and gram-negative bacteria. Poly(cis-1,4-isoprene)-cleavage enzymes that are secreted by rubber-utilizing bacteria cleave the poly(cis-1,4-isoprene) chain to generate low-molecular-weight oligo(cis-1,4-isoprene) derivatives containing aldehyde and ketone groups. The resulting products are converted to the compounds including carboxyl groups, which could then be further catabolized through β-oxidation pathway. One of poly(cis-1,4-isoprene)-cleavage enzymes is latex-clearing protein (Lcp) that was found in gram-positive rubber degraders including Streptomyces, Gordonia, Rhodococcus, and Nocardia species. The other one is rubber oxygenase A and B (RoxA/RoxB) which have been identified from gram-negative rubber degraders such as Steroidobacter cummioxidans and Rhizobacter gummiphilus. Recently, the transcriptional regulation mechanisms for Lcp-coding genes in gram-positive bacteria have been characterized. Here, the current knowledge of genes and enzymes for the isoprene rubber catabolism were summarized.
Tle1 attenuates hepatic ischemia/reperfusion injury by suppressing NOD2/NF-κB signaling
Authors: Chen Wei , Zheng Daofeng , Mou Tong , Pu Junliang , Dai Jiangwen , Huang Zuotian , Luo Yunhai , Zhang Yuke , Wu Zhongjun 
Published: February 2020

ABSTRACT
Liver damage induced by ischemia/reperfusion (I/R) remains a primary issue in multiple hepatic surgeries. Innate immune-mediated inflammatory responses during the reperfusion stage aggravate the injury. Nevertheless, the detailed mechanism of hepatic I/R has not been fully clarified yet. Our research focuses on the role of Transducin-like enhancer of split-1 (Tle1) in the liver I/R injury and the relation between Tle1 and Nucleotide-binding oligomerization domain 2 (NOD2). To answer these questions, we constructed mouse models of I/R and cell models of hypoxia/reoxygenation (H/R). We found decreased Tle1 accompanied by increased NOD2 during reperfusion. Mice pro-injected with Tle1-siRNA emerged aggravated liver dysfunction. Repression of Tle1 had a significant impact on NOD2 and downstream NF-κB signaling in vitro. However, alteration of NOD2 failed to affect the expression of Tle1. To conclude, our study demonstrates that Tle1 shelters the liver from I/R injury through suppression of NOD2-dependent NF-κB activation and subsequent inflammatory responses.
Design and Analysis of Rotor Line Type for Three-lobe Roots Blower
Authors: Jian-feng Gu , kai-jun Zhou 
Published: February 2020

Abstract
In order to improve and solve the capability of small and medium enterprises to design new products, the principle of operation of the three-lobe Roots blower rotor was firstly analyzed, and the characteristics of meshing of the rotor profile were analyzed. The meshing design formula was given. Based on this, the 3L41WD involute Roots blower design was taken as an example to calculate its full line type and to analyze and determine the meshing tolerance. Finally, the field test proved the rationality of the design, and provided guidance for SMEs to rapidly design the involute Roots blower rotor.
Characteristics analyses of energy consumption for bridge crane based on the energy flow
Authors: Fei Shuai , Zhihao Ge , Yifei Tong , Xiangdong Li 
Published: February 2020

Abstract
Aiming at the problems of energy consumption disorder and energy waste of bridge crane, based on the characteristics analysis of working condition and energy consumption, the power balance equation is established combining with the energy transmission process of bridge crane, which provides an important theoretical basis for the evaluation of crane energy consumption.
Penetration resistance of concrete reinforced by hybrid fibre subjected to multiple projectile impacts
Authors: Ma Jiajun , Yan Luhui , Xu Mohan 
Published: February 2020

Abstract
Penetration resistance of steel-ultrahigh molecular weight polyethylene (S-UHMWPE) hybrid-fibre-reinforced concrete under multiple projectile impacts are investigated. In this paper, 16 sets of hybrids with various hybridizations were designed and prepared considering 0%-1.5% steel fibre volume and 0%-0.3% UHMWPE fibre volume. Each hybrid-fibre concrete target was stroke triple times sequentially under 12.7mm armor-piercing projectile. The projectile impact locations are among the middle of the target in equilateral triangle shape. After each penetration, depth of penetration (DOP) and crater area were investigated. Results show that hybrid-fibre concrete performs much better than steel or UHMWPE fibre reinforced concrete with less crater area and lower DOP for hybrid-fibre concrete combines the reinforcement and toughening effect of UHMWPE fibre on concrete’s tensile strength and strengthening effect of steel fibre on concrete’s compressive strength. Besides, the crater area caused by each impact decreased with the number of strikes increases.
Evaluation of the curvature ductility ratio of a circular cross-section of concrete reinforced with GFRP bars
Authors: Pichardo C , Tovar W , Fernandez-Davila V I 
Published: February 2020

Abstract
The present study deals with the use of fiberglass reinforced polymer bars (GFRP) as a replacement for the common steel of a reinforced concrete circular pile, in order to avoid the corrosion of durability of reinforcing bars and thus improve them. The comparative analysis was carried out between a pile reinforced with GFRP and another with steel, where the ductility was evaluated by obtaining moment-curvature diagram. As a result, said idealized moment-curvature diagrams and ductility indices are presented, concluding the ductility of the section reinforced with GFRP in 20% more than that of steel.
Study on ZnO Varistors Doped with Y2O3 by Microwave Two-step Sintering
Authors: Peng Yongjing , Fang Zhen , Wang Bowen , Hu Jianping , Xie Pengkang 
Published: February 2020

Abstract
The zinc oxide varistor prepared in this paper is mainly composed of submicron zinc oxide powder and dopants, and is prepared by two-step sintering method, which is in contrast with traditional sintering method and ordinary microwave sintering method. The effects of microwave sintering temperature and holding time on the microstructure and electrical properties of ZnO varistors were investigated. The results show that the potential gradient of microwave sintering is higher than that of traditional sintering, but the leakage current also increases. Compared with ordinary microwave sintering, the two-step sintering can further effectively reduce the grain size, enhance densification, not only improve the potential gradient, but also reduce leakage current. In two-step sintering, increasing sintering temperature can effectively reduce leakage current and non-linear coefficient, but the potential gradient is also greatly reduced. When the holding time is more than 1 hour, there is little difference in electrical performance. When the holding time is too small, its electrical performance is weak overall.
Application and Development of the Super-large Diameter Column Foundation of Bridge
Authors: Qiaodan Ye , Junjie Wang , Changjiang Wang 
Published: February 2020

Abstract
With the increase of span, the structural form of bridge foundation is seeking for development. The super-large diameter column foundation has become one of the best alternatives for bridge substructures. With the development of bridge foundation, the application status of the super-large diameter column foundation is combed. Its construction methods are briefly summarized, such as artificial digging, embedding prestressed pipe and super-large diameter bored pile, which promote the application of single column foundation. In the future, engineers can also get inspiration from the offshore wind turbine and seek new development ideas. Combined with the application of super-large diameter column foundation in the cross-sea bridge at home and abroad, the unique advantages and the problems needed to be solved in the practical application of the super-large diameter column foundation of bridge are pointed out, and its development is prospected.
Properties of AlN-MWCNTs/epoxy Nanocomposites
Authors: Xie Fang , Diao Guiqiang , Qiang Na , Xiao Dingshu 
Published: February 2020

AbstractSynergistic effect of AlN in combination with MWCNTs in AlN-MWCNTs/epoxy nanocomposites was found. Thermal conductivity of AlN-MWCNTs/epoxy nanocomposites increased obviously with the increase of AlN content. The added AlN can be filled in the networks of MWCNTs to form a more dense three-dimensional thermal conductivity network and provide more thermal conductivity channels. In addition to that, mechanical and flame-retardant properties of the nanocomposites were improved also. AlN-MWCNTs/epoxy nanocomposites presented optimum mechanical properties with the addition of 5∼7.5%wt AlN powder. With the addition of AlN powder in AlN-MWCNTs/epoxy nanocomposites, its LOI value is increased from 30.8% to 43.4% and UL 94 test achieves V-0 ranking.
Microstructure and mechanical characterization of high strength low alloy steel welded joint by hybrid laser arc welding
Authors: Bao Liang Liang , Wang Yong , Han Tao 
Published: February 2020

Abstract
Hybrid laser arc welding was developed to joint EQ70 steels. Welds with no visible defects were obtained. Investigations on microstructure and mechanical properties showed that: the welded metal (WM) consisted of acicular ferrite (AF), granular bainite (GB) and M-A constituents. The arc zone and laser zone possessed semblable HAZ microstructures. Coarse grained heat affected zone (CGHAZ) and fine grained HAZ (FGHAZ) were both composed of lath martensite (LM), GB and polygonal ferrite (PF). The intercritically HAZ (ICHAZ) consisted of martensite and M-A constituents. The microstructure of the subcritically HAZ (SCHAZ) was tempered sorbite. Partly cracked blocky M-A constituents were found at the grain boundary of intercritically reheated CGHAZ (ICCGHAZ). Some M-A constituents was slender and distributed in the grain of ICCGHAZ. The arc zone and laser zone had similar hardness and micro-shear strength distributions. The highest hardness and micro-shear strength of the backing and double-pass welded joints appeared near CGHAZs, reheated WM and ICCGHAZ. Slightly soften showed up at the SCHAZs. SCHAZ, CGHAZ and ICCGHAZ showed a reduction of micro-shear toughness. -40°C sub-size Charpy impact testing showed that FL specimens possessed the lowest impact values. The coarse CGHAZs and cracked blocky M-A constituents of ICCGHAZ may be the reason caused the toughness deterioration.
Mathematical modeling and analysis of energy conversion efficiency of particle jet accelerating nozzle
Authors: Fang Tiancheng , Ren Fushen , Cheng Xiaoze , Hu Qing , Tong Tiexin 
Published: February 2020

Abstract
The impact kinetic energy of particle jet determines rock-breaking effect and velocity, and as acceleration device of particle jet, the energy conversion efficiency of nozzle determines rock-breaking efficiency. According to three different types of nozzles of the straight-taper nozzle, the pressure drop model and energy conversion efficiency of particle jet was established, and the energy conversion efficiency under different type nozzles was studied. And then, the acceleration ability of different nozzles for was analyzed with simulation. The results of model calculation and simulation show that constant-acceleration nozzle has the best acceleration ability and energy conversion efficiency. The rock-breaking experiment was carried out with the adopted nozzle, and comparison analysis between experimental results and numerical calculation prove that the applicability of mathematical model.
Stabilization of a Subgrade Composed by Low Plasticity Clay with Rice Husk Ash
Authors: Ormeño E , Rivas N , Duran G , Soto M 
Published: February 2020

Abstract
The construction of road works in the world has always been a challenge for engineering, especially in areas where the conditions and types of soil are not adequate for the execution of this type of projects. The present investigation has as main objective to determine the influence that has the rice husk ash (RHA) to stabilize the subgrade layer of a pavement, composed of a low resistance clayey soil. RHA is a waste and pollutant material for the environment; therefore that its use can be considered as an economic and ecological alternative. Thus, several tests were carried out where it proved the value of CBR increased from 4.30% to 20.70%, by adding a 20% RHA dosage, achieving its optimum value to be considered a very good subgrade. In this way, it is possible to affirm that the addition of RHA improves the geotechnical properties of the soil.