bluuebunny/crossref_metadata_2025_split huggingface dataset:
Survey on patients’ organisations’ knowledge and position paper on screening for&nbsp;inherited neuromuscular diseases in Europe
Authors: Lamy François , Ferlini Alessandra , Board EURO-NMD Patient Advisory , Evangelista Teresinha 
Published: December 2020

Abstract
Background: The development of new genetic testing methods and the approval of the first treatments raises questions regarding when and how to perform screening for inherited neuromuscular conditions. Screening directives and access to the different techniques is not uniform across Europe. The patient advisory board of the European reference network for rare neuromuscular diseases (NMD) conducted a qualitative study to understand the state of play of screening for inherited NMD in Europe and patients’ needs. Results: We collected answers from 30 patient organisations (POs) from 18 European countries. Fifteen acknowledge the existence of pre-implantation genetic diagnosis in their country. Regarding prenatal screening, we had 25 positive answers and 5 negative ones. Twenty-four POs mentioned that newborn screening was available in their country. We had some contradictory answers from POs from the same country and in some cases; diseases said to be part of the screening programmes were not hereditary disorders. Twenty-eight organisations were in favour of screening tests. The reasons for the two negative answers were lack of reimbursement and treatment, religious beliefs and eventual insurance constrains. Most POs (21) were in favour of systematic screening with the option to opt-out. Regarding the timing for screening, “at birth”, was the most consensual response.The main priority to perform screening for NMDs was early access to treatment, followed by shorter time to diagnostic, preventive care and genetic counselling. Conclusions: This is the first study to assess knowledge and needs of POs concerning screening for NMDs. The knowledge of POs regarding screening techniques is quite uneven. This implies that, even in communities highly motivated and knowledgeable of the conditions they advocate for, there is a need for better information. Differences in the responses to the questions “how and when to screen” shows that the screening path depends on the disease and the presence of a disease modifying treatment.The unmet need for screening inherited NMDs should follow an adaptive pathway related to the fast moving medical landscape of NMDs. International coordination leading to a common policy would certainly be a precious asset tending to harmonize the situation amongst European countries.
Prospective Associations Between Fixed-Term Contract Positions and Mental Illness Rates in Denmark’s General Workforce: Protocol for a Cohort Study
Authors: Hannerz Harald , Burr Hermann , Soll-Johanning Helle , Nielsen Martin Lindhardt , Garde Anne Helene , Flyvholm Mari-Ann 
Published: December 2020

Background
In 2018, 14% of employees in the European Union had fixed-term contracts. Fixed-term contract positions are often less secure than permanent contract positions. Perceived job insecurity has been associated with increased rates of mental ill health. However, the association between fixed-term contract positions and mental ill health is uncertain. A recent review concluded that the quality of most existing studies is low and that the results of the few studies with high quality are contradictory.

Objective
This study aims to estimate the incidence rate ratios (RRs) of psychotropic drug use and psychiatric hospital treatment. These ratios will be considered, first, in relation to the contrast fixed-term versus permanent contract and, second, to fixed-term contract versus unemployment.

Methods
Interview data with baseline information on employment status from the Danish Labor Force Surveys in the years 2001-2013 will be linked to data from national registers. Participants will be followed up for up to 5 years after the interview. Poisson regression will be used to estimate incidence RRs for psychiatric hospital treatment for mood, anxiety, or stress-related disorders and redeemed prescriptions for psychotropic drugs, as a function of employment status at baseline. The following contrasts will be considered: full-time temporary employment versus full-time permanent employment and temporary employment (regardless of weekly working hours) versus unemployment. The analyses will be controlled for a series of possible confounders. People who have received sickness benefits, have received social security cash benefits, have redeemed a prescription for psychotropic drugs, or have received psychiatric hospital treatment for a mental disorder sometime during a 1-year period preceding baseline will be excluded from the study. The study will include approximately 134,000 participants (13,000 unemployed, 106,000 with permanent contracts, and 15,000 with fixed-term contracts). We expect to find approximately 16,400 incident cases of redeemed prescriptions of psychotropic drugs and 2150 incident cases of psychiatric hospital treatment for mood, anxiety, or stress-related disorders.

Results
We expect the analyses to be completed by the end of 2021 and the results to be published in mid-2022.

Conclusions
The statistical power of the study will be large enough to test the hypothesis of a prospective association between fixed-term contract positions and mental illness in the general workforce of Denmark.

International Registered Report Identifier (IRRID)
DERR1-10.2196/24392
Efecto de variación en las tasas de interés por financiamiento en los resultados de la Pymes de Costa Rica
Authors: Rodríguez Alcocer Roberto 
Published: December 2020

El objetivo es analizar la tasa de interés ofrecida por los intermediarios financieros para el financiamiento de las actividades económicas de las Pequeñas y Medianas Empresas (Pymes) en Costa Rica, mediante escenarios donde se evidencian los efectos de estas variaciones, originados por una Tasa Básica Pasiva variable, tasa de referencia, y cómo estas fluctuaciones afectan los resultados económicos y financieros de estos negocios. El diseño de esta investigación es esencialmente de carácter descriptivo y comparativo, ya que pretende contribuir con la ampliación del conocimiento sobre el efecto negativo de las tasas de interés en los resultados financieros y económicos de las Pymes en Costa Rica, específicamente aquellas que han requerido financiamientos del Sistema Financiero. Por lo tanto, se realiza un análisis de los efectos de las tasas de interés en los resultados operacionales pertenecientes a las pymes, a partir del cálculo de intereses, variación en las cuotas, flujo de caja libre, capacidad de pago y conclusiones financieras. Este análisis se situa dentro del marco de administración financiera y económica de las pymes y de su efecto en la economía productiva del país.
L'importanza dell'acqua nell’industria lattiero-casearia
Authors: Andretta Annalisa 
Published: December 2020

L’industria alimentare è uno tra i settori in rapida crescita economica.
Questo settore è caratterizzato da un’elevata domanda di risorse, in
particolare di acqua. Molti degli stabilimenti lattiero-caseari
utilizza una propria fonte d’acqua, la quale dovrebbe soddisfare i
requisiti di acqua potabile. Per questo motivo è obbligatorio il suo
trattamento. Nel presente articolo viene approfondita la gestione delle
risorse e la qualità dell’acqua di due stabilimenti lattiero-caseari
situati in Polonia. Quindi, si mettono in risalto le relazioni che
intercorrono tra il processo tecnico selezionato, le attrezzature, la
qualità dell’acqua e il suo consumo. Inoltre, attraverso la
re-immissione in circolo della quantità d’acqua consumata all’interno
dell’industria, sono state proposte soluzioni che hanno il compito di
migliorare la gestione sia dell’acqua che delle acque reflue.
LOCALITY OF FORMING WINTERING RIVERBED DEPRESSION IN IRTYSH RIVER
Authors: Chemagin Andrey Aleksandrovich 
Published: December 2020

The article describes a new locality of the formed wintering riverbed depression discovered in the erosion zone of the isthmus of conjugate meanders of the Irtysh river for the rational use and effective protection of aquatic biological resources in places of their concentration in the Irtysh river basin (Western Siberia, the Russian Federation. The morphology of the riverbed depression was mapped (relief and bathymetric maps). The maximum depths in the channel depression exceeded 27 m. The channel depression and 4 control river sections were studied. The analysis
of hydroacoustic surveys showed that in the wintering riverbed depression there is, according to the statistical data, higher fish density compared to the control areas: in the water area of the riverbed depression the average fish density made 4 524 species/ha, in the control sections 245-2091 sp./ha. The cluster analysis based on the fish density and the size-taxonomic composition of the ichthyofauna has revealed that the riverbed depression is being separated into a cluster, but at the same time goes to the control section No. 4, which is located downstream, where further erosion of the river channel is registered. In this regard, the minimum protection zone of the wintering channel depression should include the water area of the channel depression and the water area of control section No. 4. In the water areas of the riverbed depression and control sections in the spring period, cyprinids dominate - up to 65% of the total number of fish, percids are represented to a lesser extent - 36.76%, coregonids and pikes - up to 18.18, sturgeons - up to 9.31%. The given locality of the wintering riverbed depression must be included in the list of protected river sections of the Fishing Rules for the West Siberian fishery basin for developing the effective strategy for the protection, restoration and rational use of aquatic biological resources, including rare and endangered fish species of the Irtysh River and the whole Ob-Irtysh basin
Borges y la matemática
Authors: Gutiérrez Hoyos Hernando 
Published: December 2020

La creación Matemática y la creación Literaria tienen más afinidades y analogías que otras actividades que comprometan al cerebro humano. Muchos de los objetos y elementos sobre los cuales trabajan algunas teorías Matemáticas son verdaderas ficciones al igual que los objetos y los seres que protagonizan un cuento o una novela. Así, por ejemplo, los Alephs introducidos por Cantor para cuantificar los Conjuntos Infinitos (estableciéndose como cardinales Transfinitos) son retomados por el ilustre literato Jorge Luis Borges para muchas de sus construcciones narrativas en las que materializa y objetiva algunos infinitos como totalidades (en acto).
El rigor que acompaña el discurrir en la construcción de las teorías Matemáticas para garantizar la coherencia y evitar las contradicciones estructurales, es similar al rigor que el literato le imprime a su obra para hacerla consistente y darle credibilidad.
Failures of lumbosacral instrumented fusions addressing degenerative lumbar disease
Authors: Helal Ahmed , Madkour Amr , Yehia Ahmed 
Published: December 2020

Background:
Here, we evaluated the failure to preserve or restore adequate spinopelvic alignment following lumbosacral instrumented fusions for degenerative disease.

Methods:
Patients undergoing lumbosacral instrumented fusions for degenerative spine disease underwent; standing lumbopelvic X-rays and lumbar MRI scans obtained both preoperatively and 1 year postoperatively. Parameters measured included lumbar lordosis (LL), L4-S1 angle, pelvic incidence (PI), and LL-PI mismatch.

Results:
Fifty patients were followed for 1 year following lumbopelvic fusion. There was a statistically significant difference in the L4-S1 angle between patients with good versus poor clinical outcomes at 1 year postoperative; the LL-PI mismatch showed a strong positive correlation with better outcome scores.

Conclusion:
Preservation of an adequate LL/other lumbosacral parameters favorably impacts patients’ outcomes following lumbosacral fusion for degenerative disease.
FEFTY SHADES OF AMBIGUITY
Authors: Голубева Ольга Васильевна 
Published: December 2020

Статья посвящена изучению маркеров смысловой неопределённости, которые являются выводимыми имплицитными компонентами значения разной степени конвенциональности. Неопределённость как универсальное свойство связано с языковыми и неязыковыми факторами, но практически всегда обусловлено позицией индивида, который выводит релевантный смысл в процессе познания и общения.
The paper covers the markers of ambiguity which are considered to be inferred conventional or non-conventional implicit meaning components. It is asserted that ambiguity as a universal property is influenced by linguistic and extra-linguistic factors but practically always is affected by relevant «internal» knowledge an individual possesses and infers in the process of cognitive and communicative activities.
LANGUAGE GAME AS A MEANS OF INFLUENCE ON VOTERS (on German campaign posters)
Authors: Денисова Евгения Павловна 
Published: December 2020

Настоящая статья посвящена описанию и анализу разнообразных языковых средств, используемых в языковой игре в немецкоязычном политическом дискурсе. Функции языковой игры рассматриваются через призму типа дискурса, частью которого они становятся.
This article is devoted to the description and analysis of various language means used for creating of a language game in the German political discourse. The functions of a language game are viewed through a prism of the type of discourse which they become a part of.
PRECEDENT TEXTS IN THE MEDIA DISCOURSE AND THEIR ROLE IN FOREGROUNDING GENDER STEREOTYPES
Authors: Копоть Лилия Владимировна 
Published: December 2020

Проанализированы прецедентные тексты, вербализирующие гендерные стереотипы в медиадискурсе. В качестве предмета исследования рассматривается гендерная специфика языковой игры в медиадискурсе.
This work analyzes precedent texts verbalizing gender stereotypes in media discourse. Gender specificity of language game in the media discourse is considered as a subject of this study.
NOMINATION OF STRUCTURAL ELEMENTS OF RUSSIAN LAWS: TRANSLATION ASPECT
Authors: Борисова Лидия Александровна 
Published: December 2020

В статье предпринимается попытка установить англоязычные переводные эквиваленты номинативным единицам, маркирующим структуру документов российского законодательства. На материале переводов Конституции РФ, кодексов и федеральных законов автором выстраивается иерархия переводных эквивалентов в английском языке. Делается вывод о допустимости разных переводческих решений в связи с выполнением переводом функции информирования, а не нормативного регулирования.
The paper considers the issue of translating legislative texts from Russian into English. Special attention is paid to the structural elements of laws. By analyzing the translations of the Russian Constitution, some Russian codes and federal laws the author presents a hierarchy of English translation equivalents. The translation equivalents may differ since the translation itself performs informative rather than normative function.
KRITIK SOSIAL DALAM TIGA CERPEN DI KORAN MANUNTUNG TAHUN 1980-AN DI KALIMANTAN TIMUR
Authors: Hariyanto Dwi 
Published: December 2020

AbstrakPengkajian ini memaparkan gambaran kritik sosial dalam tiga cerpen yang dimuat dalam koran di Kalimantan Timur pada tahun 1980-an, yaitu “Nomer”, “Suatu Sore di Pinggiran Desa”, dan “Tatkala Takbir Menggema”. Fenomena sosial di masyarakat dalam cerpen yang dimuat dalam media cetak berbentuk koran ini layak diungkapkan. Pengungkapan fenomena sosial dalam tiga cerpen tersebut sangat diperlukan untuk melihat kondisi sosial masyarakat di tahun 1980-an karena pada tahun-tahun tersebut dapat dikatakan sebagai awal kemunculan karya sastra berbentuk cerpen dalam media cetak berbentuk koran di Kalimantan Timur. Metode kualitatif digunakan penulis untuk mengungkapkan gambaran sosial yang terjadi pada tahun 1980-an di Kalimantan Timur. Pendekatan sosiologi sastra digunakan sebagai alat untuk mengungkapkan masalah sosial dalam tiga cerpen ini. Namun, sebagai pijakan awal, penulis akan memanfaatkan struktural untuk mengungkapkan salah satu unsur intrinsik yang terdapat dalam karya cerpen yang dibahas. Gambaran masalah sosial yang terdapat dalam tiga cerpen di atas adalah masalah kemiskinan, disorganisasi dalam keluarga, disorganisasi keluarga, generasi muda dalam masyarakat modern, pelanggaran terhadap norma masyarakat, kependudukan, lingkungan hidup, dan birokrasi. Kata kunci: kaltim, kritik sosial, koran, cerpen Abstract This study presents a picture of social criticism in three short stories published in newspapers in East Kalimantan in the 1980s, namely "Nomer", "Suatu Sore di Pinggiran Desa", and "Tatkala Takbir Menggema". Social phenomena in the society in those short stories are worth disclosing. It is necessary to see the social conditions in the society in the 1980s. It can be considered to be the beginning of literary works in the form of short stories in print media of newspapers in East Kalimantan. The author uses qualitative methods to reveal the social picture in the 1980s in East Kalimantan. It also uses the sociological approaches to literature to show social problems in these three short stories. However, as a starting point, the writer will use the structure to reveal one of the intrinsic elements in the short stories. Social problems in those short stories are poverty, disorganization in the family, family disorganization, young people in modern society, violations of social norms, demography, environment, and bureaucracy. Keywords: East Kalimantan, social criticism, newspaper, short stories
Assessing the Mediating Role of Organization Learning Capability between the Relationship of Green Intellectual Capital and Business Sustainability
Authors: Muhammad Rizwan Sabir  , Muqqadas Rehman  , Waheed Asghar  
Published: December 2020

There has been a lot of debate on intellectual capital and its dimensions, except green intellectual capital (GIC). The economic benefit of business not only eliminates the neediness of the region but also invigorate the prosperity in the area; however, the heat of financial interest among business competitor causes social inequality and destruction of the environment. This paper is novel conception due to the lack in prior studies as many did not focus on the relationship between green intellectual capital (green human capital, green structural capital and green relational capital) and business sustainability (BS) in the context of a developing country; Pakistan to assess the mediating role organization learning capability (OLC) between the relationship of GIC and BS. The current study tried to link two theories, natural resource-based view and intellectual capital-based view (NRBV& ICBV), to conceptualize the intangible resources that lead to business sustainability by assimilating the "green" into conventional intellectual capital namely green intellectual capital. Data were collected from 154 SME manufacturing companies in Lahore, Pakistan. The simple random sampling technique used for data collection. SPSS and AMOS software is used for data analysis. The results show that all three dimensions of green intellectual capital effect on business sustainability. While discussing the mediation role of organizational learning capability, OLC mediates the relationship between human capital and business sustainability. Furthermore, OLC does not play a mediation role between structural capital, relational capital, and business sustainability. Finally, this study described limitations as well as future directions
Correction of the aortic arch hypoplasia in newborn babies, suffering complete form of atrio-ventricular septal defect
Authors: Тruba Ya. P. , Dovhaliuk А. А. , Dzyurii І. V. , Danchenko P. А. , Golovenko О. S. , Lazoryshynets V. V. 
Published: December 2020

Objective. Tactics of treatment and results of the hypoplasia of the aortic arch correction in newborn babies with complete form of atrio-ventricular septal defect were studied.
Маterials and methods. During period from 2011 tо 2019 yrs in 21 patients correction of hypoplasia of aortic arch and atrio-ventricular septal defect were performed. The investigated group consisted of patients with a two-ventricular physiology. The patients, suffering imbalanced form of atrio-ventricular septal defect and with variants of hypoplasia in left parts of the heart, were excluded from the investigation. There were 9 (42.9%) boys and 12 (57.1%) girls. Average age of the patients have constituted (2.3 ± 1.1) mo (from 0.06 до 7.7 mo). Average body mass of the patients have constituted (3.8 ± 1.0) kg (from 2.0 до 5.9 kg). The aortic arch segment was considered a hypoplastic one if a Z-score (Standard Score - standard estimation) shift have constituted lesser than 2.0.
Results. Hospital lethality have constituted 14.2%. Three newborn babies died: 2 - after first stage of correction, and 1 - after second stage of correction. All the patients, to whom a one-staged correction was done, have survived. The causes of lethality were not connected with method of the aortic arch reconstruction. While performance of echocardiography before discharge from the hospital the pressure gradient on place of the aortic arch plasty have constituted (13.6 ± 6.8) mm Hg at average. Average follow-up period have constituted (2.6 ± 2.1) yrs (from 2 mo tо 8.1 yr). In late follow-up period lethality was absent. In 2 (9.5%) patients in postoperative period reoperations on aortic arch and mitral valve were performed. Tracheal compression as well as the main bronchi compression, neurological complications in late follow-up period were absent.
Conclusion. For the patients, suffering complete form of atrio-ventricular septal defect in conjunction with hypoplasia of aortic arch the staged correction constitutes a more favorable option, owing good immediate and late results. A staged approach in the treatment is indicated for newborn babies, suffering hypoplasia of distal aortic arch and competent atrio-venticular valves or with small regurgitation. Оne-stage correction is indicated in hypoplasia of aortic arch, pronounced regurgitation on common atrio-ventricular valve and pronounced heart failure.
The Factors That Affect Diet Compliance in Patients with Diabetes Mellitus at Nganjuk Hospital
Authors: Cahyono Sony Wahyu tri 
Published: December 2020

Abstract

Patients with diabetes mellitus must follow a strict diet to control blood sugar levels to keep them within normal limits. If it is not controlled, it will cause various diseases which will be caused by visual disturbances, cataracts, heart problems, impaired kidney function, sexual impotence, difficulty in healing wounds or even rot/gangrene, lung infections, vascular disorders, and strokes. The purpose of this study was to determine the factors that affect dietary compliance in diabetes mellitus sufferers. This study uses a qualitative method with a phenomenological approach. This study explores the experiences of people with diabetes mellitus when they are on a diet. The participants in this study were 10 people. The technique of collecting data was by conducting in-depth interviews so that the results were 3 themes, namely lack of knowledge about diet, lack of family support, and difficulty in adhering to a diet. The importance of support and motivation from family and health workers for diabetes mellitus sufferers to always adhere to a diet to avoid various complications.
Keywords : Diabetes Mellitus, and Diet Compliance