A Case of Bicuspid Aorta with Stanford Type a Aortic Dissection
Authors:   Department of Clinical Cardiology. Department of Clinical Cardiology. IMSS UMAE Specialty Hospital 14 National Medical Center ̈Adolfo Ruiz Cortines ̈, Veracruz, Mexico, Ordóñez Fabiola Zarate , García Aranda Marcos ,   Department of Internal Medicine. High Specialty Regional Hospital of Veracruz SESVER, Mexico, Olarte García Josué Isaac ,   Department of Internal Medicine. High Specialty Regional Hospital of Veracruz SESVER, Mexico, Cruz Ruiz José Martín Santa ,   Department of Clinical Cardiology. Department of Clinical Cardiology. IMSS UMAE Specialty Hospital 14 National Medical Center ̈Adolfo Ruiz Cortines ̈, Veracruz, Mexico, Jiménez Yoloxóchitl García ,   Department of Clinical Cardiology. Department of Clinical Cardiology. IMSS UMAE Specialty Hospital 14 National Medical Center ̈Adolfo Ruiz Cortines ̈, Veracruz, Mexico, Hernandez Mejia Kenia ,   Department of Internal Medicine. High Specialty Regional Hospital of Veracruz SESVER, Mexico, Navarrete Jessica Ariatna Carreto ,   Department of Internal Medicine. High Specialty Regional Hospital of Veracruz SESVER, Mexico, Gómez Mayorquín Tania Dennis ,   Department of Internal Medicine. High Specialty Regional Hospital of Veracruz SESVER, Mexico, Sarmiento Sosa Yunelly Paola ,   Department of Internal Medicine. High Specialty Regional Hospital of Veracruz SESVER, Mexico, González Palmira Villegas ,   Department of Internal Medicine. High Specialty Regional Hospital of Veracruz SESVER, Mexico, Rodríguez Ibarra Moisés ,   Department of Internal Medicine. High Specialty Regional Hospital of Veracruz SESVER, Mexico, Galindo Meza Karla Ruth ,   Department of Internal Medicine. High Specialty Regional Hospital of Veracruz SESVER, Mexico, villalobos Rolando Castellanos ,   Department of Internal Medicine. High Specialty Regional Hospital of Veracruz SESVER, Mexico, Aranda Héctor García ,   Department of Internal Medicine. High Specialty Regional Hospital of Veracruz SESVER, Mexico, Dueñas Roberto Lazcano ,   Department of Internal Medicine. High Specialty Regional Hospital of Veracruz SESVER, Mexico, Antonio Calixto Estanislao ,   Department of Clinical Cardiology. National Institute of Cardiology "Ignacio Chávez", Mexico City, Mexico
Published: September 2023

Bicuspid aortic valve disease (BAV) is a congenital disease that frequently produces complications during adulthood, and is considered not only a problem of valvulogenesis, but also a more complex genetic alteration that involves the development of the heart and the aorta, which entails a high morbidity and mortality in these patients. In 50% of adults with this pathology, non-valvular anomalies are observed, with dilation of the ascending aorta being the most common. Genes such as NOTCH1, UFDL1, ACTA2, eNOS, among others, have been identified as responsible for the appearance of aneurysms, which increases the risk in these patients of complications such as aortic dissection and its subsequent rupture. Painless aortic dissection may be seen in less than 5% of patients and may have an atypical clinical presentation. A case and review of the literature is presented in which we can observe the great complexity of this pathology, in the case of a patient with BAV, annulo-ectatic dilation of the aortic root and ascending aorta who developed heart failure, syncope and presented as a complication Stanford type A aortic dissection, requiring highly specialized surgical treatment.