bluuebunny/crossref_metadata_2025 huggingface dataset:
Evaluation of growth and nutritional status in children and adolescents with extrahepatic portal vein obstruction and portal hypertension
Authors: MARQUES Priscila Francisco , BRANDÃO Maria Angela Bellomo , HESSEL Gabriel , ALCANTARA Roberta Vacari , FERREIRA Marcela Linden , LOMAZI Elizete Aparecida
Published: August 2017

ABSTRACT Objective: This study aims to evaluate dietary intake, nutritional status, and growth rate in children and adolescents with extrahepatic portal vein obstruction and portal hypertension. Methods: Outpatients aged 1-18 years, diagnosed with extrahepatic portal vein obstruction and portal hypertension, who had no associated diseases, and who had not been subjected to a venous shunt were included in this study. Two evaluations were carried out in this study: an initial (evaluation 1) and a final evaluation (evaluation 2), with a three-month minimum interval between them. In each evaluation, dietary intake was analyzed comparing the results with recommended energy intake using the Harris & Benedict equation and participants’ anthropometric data, such as weight, height, mid-arm muscle circumference, weight-for-age, height-for-age, and body mass index-for-age, based on the World Health Organization 2006 standards. Results: A total of 22 patients participated in this study. There was a significant improvement in weight, height, body mass index, and mid-arm muscle circumference measurements (p<0.001; p<0.001; p<0.017; p=0.0018 respectively) and in the relationship between dietary intake and energy recommended energy intake, according to the Harris & Benedict equation (p=0.0001) from the first and second evaluation. Conclusion: Extrahepatic portal vein obstruction and portal hypertension were not shown to be factors predisposing to malnourishment.
Professional practice of dietitians in the Brazilian School Feeding Program: A multiple case study
Authors: PIRES Patrícia Fernanda Ferreira , RETONDARIO Anabelle , ALMEIDA Claudia Choma Bettega , SCHMIDT Suely Teresinha , BEUX Marcia Regina , FERREIRA Sila Mary Rodrigues
Published: August 2017

ABSTRACT Objective: To assess dietician’s numerical parameters for school feeding and discuss limitations and possibilities for professional practice in the municipalities of Vale do Ivaí, in Northern Paraná, Brazil. Methods: This is a multiple case study. A semi-structured interview was administered to dietitians working at the School Feeding Program in nine cities located in Vale do Ivaí, Paraná, Brazil. Resolution nº 465/2010, from the Brazilian Federal Board of Dietitians, was used to calculate the adequacy of working hours of dietitians. The legistation of the Brazilian School Feeding Program was applied to discuss professional practice. Results: All the cities had at least one dietitian responsible for the School Feeding Program. The percentage of adequate working hours was from 20 to 66%. Some dietitians were involved in management activities, administration, procurement, and accounting, in addition to dietitian assignments for the School Feeding Program. Most dietitians worked in other sectors of the municipalities such as the health system, social assistance, and at events. This practice could compromise compliance of technical activities that must be met by the dietitians of the School Feeding Program. Conclusion: The number of dietitians in most of cities working at School Feeding Program is not sufficient to meet the number of students. The insuficient workload and excessive activities could hinder the development of dietitian’s private activities. The hiring of nutrition and dietitian technicians and administrative assistants for bureaucratic activies is recommended.
Adição de uma associação polimérica a um solo argilo-arenoso com vistas à estabilização química de materiais para pavimentos
Authors: Machado Lucas Ferreira Melo , Cavalcante Erinaldo Hilário , Albuquerque Fernando Silva , Sales Angela Teresa Costa
Published: August 2017

RESUMO Visando à redução dos custos das obras de pavimentação rodoviária, sempre se procura utilizar materiais locais, preferencialmente os solos de jazidas mais próximas da construção. Às vezes, existem várias jazidas de solos inadequados para o uso, mas que podem ter suas propriedades melhoradas, aplicando-se a técnica correta de melhoramento, como a estabilização química, na qual se enquadra o uso de polímeros ou associações poliméricas. Com este trabalho propõe-se avaliar o uso de uma associação polimérica, na melhoria do comportamento geotécnico de um solo com problemas de resistência, visando ao seu uso como material de pavimentos rodoviários de baixo volume de tráfego. Esta pesquisa está baseada nos ensaios de caracterização geotécnica, compactação, ISC, (UCS RCS e permeabilidade, executados com o solo puro e com adição de material polimérico em proporções variando entre 2% e 6%. A pesquisa revelou aumentos consideráveis nos valores de ISC e RCS. Os resultados obtidos revelaram que o uso da associação polimérica resultou em diminuição da plasticidade, aumento no teor de umidade ótimo, redução do peso específico aparente seco e da expansão do solo. Concluiu-se, dessa forma, que, à luz das especificações vigentes, a adição de 6% da associação polimérica ao solo classificado como argilo-areno-siltoso de expressiva plasticidade promoveu significativas melhorias nas propriedades geotécnicas do solo.
Atividade pozolânica de adições minerais para cimento Portland (Parte II): Índice de atividade pozolânica com cimento Portland (IAP), difração de raios-X (DRX) e termogravimetria (TG/DtG)
Authors: Hoppe Filho Juarez , Gobbi Andressa , Pereira Eduardo , Tanaka Rodrigo Satoshi , Medeiros Marcelo Henrique Farias de
Published: August 2017

RESUMO A hierarquização de adição mineral para utilização como pozolana requer a determinação de sua reatividade, o que pode ser realizado via método indireto, por meio do ensaio de resistência à compressão de argamassa com cimento Portland (NBR 5.752). As adições minerais de alta reatividade, como a sílica de casca de arroz, a sílica ativa e o metacaulim, apresentam como característica peculiar a elevada área específica, o que potencializa a fixação de cal por atividade pozolânica e incrementa a resistência à compressão da matriz hidratada. A classificação, conforme a diretriz da norma NBR 12.653, está fundamentada na resistencia à compressão axial proporcional mínima de argamassa cimentícia pozolânica em relação à argamassa de referência. A substituição volumétrica parcial do cimento por adição mineral reduz a resistência à compressão do sistema, a ser compensada, total ou parcialmente, pelos compostos hidratados formados por atividade pozolânica. O presente artigo constitui a parte II do trabalho intitulado “Atividade pozolânica de adições minerais para cimento Portland” e contempla a avaliação da atividade pozolânica de sistemas cimento Portland - adição mineral, conforme as prerrogativas da norma NBR 5.752, além da aplicação de difratometria de raios-X e análise termogravimétrica (TG/DTG) em pastas idênticas às contidas nas argamassas para análise complementar ao método indireto. A parte I deste trabalho concluiu que há inadequabilidade na metodologia proposta na NBR 5.751 (IAP com cal) para a hierarquização de adições minerais de alta reatividade em virtude do esgotamento da reserva alcalina, embora a classificação seja admissível. Já a metodologia da NBR 5.752 (IAP com cimento Portland) permitiu a classificação e a hierarquização das adições minerais de alta reatividade (sílica de casca de arroz, sílica ativa e metacaulim) quando da realização do ensaio com cimento Portland de alta resistência inicial, apesar da extrapolação do limite máximo permissível de água de amassamento.
A escrita do desastre
Authors: Neto João Alves Rocha
Published: August 2017

Tradução de fragmentos do texto de Maurice Blanchot.
The Seafarer
Authors: Ribeiro de Oliveira Marcelo Fonseca
Published: August 2017

Ezra Pound nasceu em Idaho em 1885 e estudou línguas românicas na Universidade da Pensilvania. Funda a corrente do Imagismo, editando uma antologia em 1914. Antes, havia angariado o reconhecimento de nomes como Elliot, Henry James, Frost, Joyce e outros. O poema 'The Seafarer', tradução de Pound do anglo-saxão original, reflete suas preocupações filológicas e estilísticas com a Idade Média, e é reconhecidamente a versão moderna mais aceita.
A relação entre os Mannon e as figuras dos coros em "Electra enlutada" (1931), de Eugene O’Neill: exemplaridade, intertexto e tragicidade
Authors: Leites Jr. Pedro
Published: August 2017

Propomos neste artigo um estudo sobre a manifestação do trágico na trilogia Electra enlutada (1931), do dramaturgo estadunidense Eugene O’Neill. Em específico, buscamos entender como o elemento trágico se expressa a partir da construção e inter-relação dos Mannon, família que representa o centro da ação trágica, com personagens que dialogam com a estrutura do Coro da tragédia grega. Para tanto, consideramos a intertextualidade que a obra mantem para o mito grego de Electra e, em particular, com a Oréstia (458 a.C.), de Ésquilo. Nesse sentido, temos ainda em conta o quanto o engendramento trágico e a constituição dos personagens assumem nuances de exemplaridade, o que se manifesta de diferentes formas na obra.
Sobre os poetas neo-realistas. Exercícios de releitura: poéticas do testemunho e gesto antropológico
Authors: Gusmão Manuel
Published: August 2017

Os autores neo-realistas distinguem-se pela prática da literatura como testemunho e gesto antropológico, patente não apenas na prosa mas igualmente na poesia. É essa a linha condutora destes exercícios de leitura da poesia de Manuel da Fonseca, Mário Dionísio, Joaquim Namorado, Carlos de Oliveira e de Gaibéus de Alves Redol.
LOSA, Margarida. Do romance realista ao romance proletário. Lisboa: Campo da Comunicação, 2014. 278 p.
Authors: Pereira Patrícia Resende
Published: August 2017

Resenha do livro Do romance realista ao romance proletário.
Analisis Kriteria Pengembangan Penganggaran Elektronik Menggunakan Software Quality Function Deployment (SQFD) dari Sudut Pandang Pengguna [The Analysis of Electronic Budgeting Development Criteria Using SQSD from User Perspectives]
Authors: Jati Rahmi Kartika
Published: August 2017

Pesatnya perkembangan sistem informasi menjadi pemicu dalam pengembangan aplikasi pendukung operasional organisasi. Tak terkecuali pemerintah Indonesia. Sebagai organisasi yang besar, pemerintah Indonesia memandang perlu adanya perbaikan layanan kepada masyarakat. Hal tersebut dilakukan dengan menetapkan penerapan e-government. E-government merupakan salah satu alat yang digunakan dalam perbaikan birokrasi dan tata kelola pemerintahan. Pusat Penelitian X sebagai lembaga pemerintahan melakukan perbaikan terus menerus untuk meningkatkan tata kelola organisasi. Dari beberapa area yang akan menjadi objek pengembangan e-government, pihak manajemen Pusat Penelitian X memutuskan untuk memprioritaskan perbaikan pada proses keuangan, khususnya proses penganggaran. Dalam rangka perbaikan proses anggaran tersebut, perlu kajian terkait pengembangan penganggaran elektronik. Berdasarkan hal tersebut penelitian ini bertujuan untuk pengembangan penganggaran elektronik di Pusat Penelitian X. Pengembangan dilakukan dengan menggunakan Software Quality Function Deployment (SQFD) yang merupakan pengembangan Quality Function Deployment (QFD) tradisional yang umum digunakan pada pengembangan produk manufaktur. Dari penelitian ini diperoleh hasil bahwa dalam pengembangan penganggaran elektronik di Pusat Penelitian X, programmer perlu memperhatikan delapan kriteria prioritas yang menurut pengguna perlu ada di dalam penganggaran elektronik. Dimana delapan kriteria prioritas tersebut dapat digunakan sebagai dasar pengetesan sistem untuk finalisasi pengembangan penganggaran elektronik.*****The rapid development of information system is the trigger for the developing of organization operational support applications. This is also the case of Indonesian government. As a big organization, Indonesian government sees the need of improving public services. Those can be conducted by implementing e-government, as a tool to improve the bureaucracy and governance effectively and efficiently. X Research Center as a government institution continues to improve the organization arrangement system. From many areas that will be the objects of e-government developing, the management of X Research Center decided to prioritize the improvement of financial process, especially budgeting process. On the improving of the budgeting process, the study of e-budgeting development is implemented. This study used Software Quality Function Deployment (SQFD) which is a development of Quality Function Deployment (QFD) commonly used in the traditional manufacturing product development. From this paper, we can conclude that in the development of e-budgeting in X Research Center, programmers need to pay attention to the eight priority criteria according to user requirement. Eight priority criteria can be used as a basic for system testing to finalize the development of electronics budgeting.
Status dan Perkembangan Proyek Loon Terkini [Present Status and Development of Loon Project]
Authors: Yuniarti Diah , Hamjen Hilarion
Published: August 2017

Studi ini dilakukan untuk memperoleh gambaran terkait status dan perkembangan Proyek Loon di berbagai negara saat ini dari berbagai aspek hingga awal tahun 2017. Studi ini menggunakan pendekatan kualitatif dan studi literatur. Hasil penelitian menunjukkan bahwa setelah Google melakukan trial Loon di Selandia Baru, Brazil, dan Australia, saat ini Proyek Loon masih mengusahakan uji coba dan komersialisasi di negara-negara Asia yaitu di India, Sri Langka dan Indonesia terutama negara dengan banyak penduduk di wilayah terpencil yang masih belum mendapatkan layanan telekomunikasi. Dalam perjalanannya, uji coba dan komersialisasi Proyek Loon di beberapa negara tersebut terkendala beberapa hal, terutama perizinan, baik lisensi frekuensi maupun perizinan ruang udara.  *****This study is conducted to gather illustration related to recent status and development of Project Loon in different countries viewed from various aspects by the beginning of 2017. The study is using qualitative approach and literature studies. Research result shows that after Google conducted Loon trials in New Zealand, Brazil and Australia, currently Project Loon is still exploring trial and commercialization in Asia countries which are India, Sri Langka and Indonesia, particularly in country which has many underserve population of telecommunication services in remote areas. On its way, trial and commercialization of Project Loon in those different countries are constrained by several issues, particularly in term of whether frequency license or airspace permissions.
Faktor-Faktor yang Memengaruhi Kepuasan Pelanggan terhadap Layanan Pitalebar Bergerak [Determinants of Customer Satisfaction against Mobile Broadband Service]
Authors: Ariansyah Kasmad
Published: August 2017

Laju pertumbuhan jumlah pelanggan seluler diprediksi akan mengalami perlambatan. Para penyedia layanan dituntut untuk dapat melakukan inovasi dan menyusun strategi yang tepat agar dapat tetap bertahan. Layanan data saat ini menjadi andalan para penyedia layanan untuk menjaring pelanggan baru sekaligus mempertahankan pelanggan lama. Studi ini bertujuan untuk melakukan eksplorasi terkait faktor-faktor yang memengaruhi kepuasan pelanggan terhadap layanan pitalebar pada jaringan bergerak seluler di Indonesia. Temuan dari studi ini diharapkan dapat digunakan sebagai dasar dalam menyusun strategi untuk meningkatkan loyalitas pelanggan. Pengumpulan data dilakukan melalui survei. Analisis data yang digunakan terdiri dari statistika deskriptif, Chi-Square, dan Regresi Logistik Multinomial. Hasil analisis menunjukkan dua faktor demografi (pekerjaan dan pendapatan), dua atribut perangkat (jenis dan merk), pemilihan penyedia layanan, dan aktivitas penggunaan layanan data secara signifikan mempengaruhi kepuasan pelanggan.  Kaitannya dengan kinerja teknis dan non-teknis, diperoleh hasil bahwa kesesuaian kuota,  kemampuan petugas dalam menyelesaikan masalah, dan pemberitahuan sisa kuota, memengaruhi kepuasan pelanggan pada taraf signifikansi 0,05. Disamping itu, terdapat dua parameter yang memiliki taraf signifikansi sebesar 0,1, yaitu kecepatan koneksi dan kemudahan menghubungi pusat layanan pelanggan.*****The growth rate of cellular subscribers is predicted to slow down. Service providers are required to be able to innovate and develop appropriate strategies to survive. Data services nowadays have become the mainstay of service providers to capture new customers as well as to retain the old ones. This study aims to explore related factors affecting consumer satisfaction of broadband services on mobile cellular networks in Indonesia. The findings of this study are expected to be used as a consideration in devising strategies to improve customer loyalty. Data collection is carried out through a survey. The analysis consists of descriptive statistics, Chi-Square, and Multinomial Logistic Regression. The results shows that two  demographic factors (occupation and monthly income), two device attributes (device type and brand), the selection of service providers, and the activities of the use of data services significantly effect on customer satisfaction. In relation to technical and non-technical performance, the results shows that the quota conformity, the ability of officers in solving the problem, and data packet remaining notice have significant level of 0.05. In addition, there are two parameters that significantly affect customer satisfaction toward mobile broadband service at the level of  0.1.
Processing of thermal mirror signals under continuous wave excitation
Authors:   Kemerovo State University, Kalenskii A. , Zvekov A. ,   Federal Research Center of Coal and Coal Chemistry SB RAS (Institute of coal chemistry and material science), Nurmuhametov D. ,   Federal Research Center of Coal and Coal Chemistry SB RAS (Institute of coal chemistry and material science), Bulgakova O. ,   Kemerovo State University
Published: August 2017

The main features of the photothermal mirror signals arising under the continuous wave excitation were analyzed in terms of a model that takes account of thermal, mechanical, and diffraction effects. Formulae to describe the initial slope and stationary value of the signal were derived and compared with the numerical simulation results. We suggested an approach to processing the thermal mirror signals based on exploiting the initial slope and stationary value. The method was verified using numerical simulation and experimental results. We compared the method performance with the conventional approach using thermal mirror signals excited in the luminescent glasses. It was shown that the developed technique has an essentially lower computational cost, while offering a comparable level of accuracy.
Социально-этическая основа рекламного манипулирования общественным мнением
Authors: Ипатьева Ирина Адьевна
Published: August 2017

В рамках данной статьи автор раскрывает некоторые методы психологического воздействия рекламных сообщений, рассматривает их социально-этическую основу. Основное внимание уделяется специфике психологического манипулирования сознанием человека посредством создания рекламы в целях коммерческих организаций.
Financial Misappropriation in the Nigerian Public Sector: A Determination of the Role of the Internal Auditor
Authors: Oyadonghan J. K. , Ogoun S.
Published: August 2017

The continued search for a solution to the problem of poor economic management due to financial misappropriation in the public sector, and the public’s outcry against internal auditors because of their perceived connivance necessitated the current study. Furthermore, the position canvassed by internal auditors with respect to their scope of responsibility further justified the need for this research effort. Accordingly, this study was undertaken to determine, whether or not, the internal auditor has a role to play in ensuring the proper utilization of the nation’s economic resources, bearing in mind the rules specifying the scope of the internal audit function in the public sector. Drawing from the research model of survey design, both a structured questionnaire and oral interview data collection platforms were deployed to collect primary data from audit, and another staff of selected ministries in the State and the least-square regression analysis was adopted in testing the hypotheses. From the analysis, and from personal interview, the researchers were able to find out that internal audit has a responsibility to detect and prevent financial misappropriation in the public sector. It was also found out that the internal auditors in the State Civil Service are not independent, which affects their freedom to report such acts of financial misappropriation to the legislative arm for proper action. Therefore, it is recommended that The State legislative arm should ensure that the independence of the internal auditor is guaranteed by a statute.
The Impact of SMEs Financing on Business Growth in Nigeria: A Study of Keffi and Mararaba Metropolis
Authors: Tizhe Oaya Zirra Clifford , Mambula I. Charles J.
Published: August 2017

The impact of SMEs financing on business growth in Nigeria using Keffi and Mararaba Metropolis as a case study was assessed in this work. Descriptive research designs as well t-test statistics for the test of hypotheses were utilized. Hypotheses applied for the study includes: banks credits to SMEs have no significant impact on growth of Nigeria economy as well as interest rates charged on credits has no effect on SMEs business expansion in Nigeria. Access to finance was found to be sine qua non for successful entrepreneurial development while in respect of interest rate charged on SMEs loans and advances; the entrepreneurs’ ability to borrow was not hindered. The study therefore recommends strong availability to finance for successful growth of SMEs through different channels like microfinance banks and institutions in addition to formal and informal financial institutions. In addition, the scheme could be further expanded vide various tax palliatives. It is also recommended that the government should provide suitable incentives for the growth and effective performance of SMEs. There should also be close liaison between Nigeria Stock Exchange and family business to raise cheap funds for the growth of SMEs.
Complementary and Alternative Medicine: Italian Validation of a Questionnaire on Nurses’ Personal and Professional Use, Knowledge, and Attitudes
Authors: Belletti Giada , Shorofi Seyed Afshin , Arbon Paul , Molin Alberto Dal
Published: August 2017

Background: Patients are showing an increasing interest in the use of complementary and alternative medicine (CAM). Most nurses are open to the adoption of CAM into clinical nursing practice, but they may experience a lack of knowledge about the safe and effective use of these therapies. Several studies concerning nurses’ knowledge and attitudes toward CAM have been published, but only in one, the authors (Shorofi and Arbon) used a validated questionnaire. In Italy, there are no validated questionnaires to investigate this aspect of nursing practice. Purpose: To test the psychometric properties of the Italian Shorofi and Arbon questionnaire for use with Italian nurses. Methods: A forward–backward translation method was used to translate the questionnaire from English to Italian. Content validity, face validity and reliability were established. Results and Conclusions: This study examined the potential usefulness of the Shorofi and Arbon questionnaire for the evaluation of CAM knowledge of Italian speaking nurses, which showed good content validity and good reliability.
A língua Katukína-Kanamarí
Authors: Queixalós Francesc , Anjos Zoraide dos
Published: August 2017

A língua Katukína-Kanamarí, anteriormente considerada como duas línguas diferentes, é falada por cerca de duas mil pessoas nos rios Juruá, Jutaí e Javarí e seus tributários, ao sul do rio Solimões, estado do Amazonas, Brasil. Poderia ser a única língua sobrevivente da família Katukina. Pouco se sabe sobre sua estrutura, e o artigo – resultado do trabalho de campo e da análise de ambas as variedades da língua – apresenta uma visão geral dos traços fonológicos e gramaticais, enfatizando o padrão sintaticamente ergativo da língua.
De-Anonymizing Authors of Electronic Texts: A Survey on Electronic Text Stylometry
Authors: Khonji Mahmoud , Iraqi Youssef
Published: August 2017

Electronic text stylometry is a collection of forensics methods that analyze the writing styles of input electronic texts in order to extract information about authors of the input electronic texts. Such extracted information could be the identity of the authors, or aspects of the authors, such as their gender, age group, ethnicity, etc. This survey paper presents the following contributions: 1) A description of all stylometry problems in probability terms, under a unified notation. To the best of our knowledge, this is the most comprehensive definition to date. 2) A survey of key methods, with a particular attention to data representation (or feature extraction) methods. 3) An evaluation of 23,760 feature extraction methods, which is the most comprehensive evaluation of feature extraction methods in the literature of stylometry to date. The importance of this evaluation is two fold. First, identifying the relative effectiveness of the features (since, currently, many are not evaluated jointly; e.g. syntactic n-grams are not evaluated against k-skip n-grams, and so forth). Second, thanks to our generalizations, we could evaluate novel grams, such as what we name compound grams. 4) The release of our associated Python feature extraction library, namely Fextractor. Essentially, the library generalizes all existing n-gram based feature extraction methods under the "at least l-frequent, dir-directed, k-skipped n-grams'', and allows grams to be diversely defined, including definitions that are based on high-level grammatical aspects, such as POS tags, as well as lower-level ones, such as distribution of function words, word shapes, etc. This makes the library, by far, the most extensive in this domain to date. 5) The construction, evaluation, and release of the first dataset for Emirati social media text. This evaluation represents the first evaluation of author identification against Emirati social media texts. Interestingly, we find that, when using our models and feature extraction library (Fextractor), authors could be identified significantly more accurately than what is reported with similarly sized datasets. The dataset also contains sub-datasets that represent other languages (Dutch, English, Greek and Spanish), and our findings are consistent across them.
Phyto-diversity of selected stress sites of Garhwal Forest Division of Pauri Garhwal, Uttarakhand, India.
Authors: Chandra Anup , Kewat Anil Kumar
Published: August 2017

Species richness, IVI and plant diversity indices of selected biotic stress sites of Garhwal Forest Division were studied. Total density range for the tree species (Plants 100m-2) was 6.7 to 8.1; for shrubs was 48.9 to 84.9 and for herbs was 490 to 700. Total basal cover (cm2 100m-2) ranged from 386.1 to 1571 for tree, 1466.7 to 2372.5 for shrub and from 223.9 to 622.5 for herbs at different sites. Diversity index was invariably higher for herb and shrub than tree layer. Concentration of dominance showed reverse trend. It is concluded from study that site-III is highly stressed followed by site-II and site-I. Suitable measures should be adopted to conserve the invaluable plant diversity of the area.
The Clinical and Mutational Spectrum of Turkish Patients with Cystinosis
Authors: Topaloglu Rezan , Gulhan Bora , İnözü Mihriban , Canpolat Nur , Yilmaz Alev , Noyan Aytül , Dursun İsmail , Gökçe İbrahim , Gürgöze Metin Kaya , Akinci Nurver , Baskin Esra , Serdaroğlu Erkin , Demircioğlu Kiliç Beltinge , Yüksel Selçuk , Övünç Hacihamdioğlu Duygu , Korkmaz Emine , Hayran Mutlu , Ozaltin Fatih ,   on behalf of the contributors of The Turkish Cystinosis Study Group
Published: August 2017

Background and objectives

Infantile nephropathic cystinosis is a severe disease that occurs due to mutations in the cystinosis gene, and it is characterized by progressive dysfunction of multiple organs; >100 cystinosis gene mutations have been identified in multiple populations. Our study aimed to identify the clinical characteristics and spectrum of cystinosis gene mutations in Turkish pediatric patients with cystinosis.

Design, setting, participants, & measurements

We identified the clinical characteristics and spectrum of cystinosis gene mutations in Turkish patients with cystinosis in a multicenter registry that was established for data collection. The data were extracted from this registry and analyzed.

Results

In total, 136 patients (75 men and 61 women) were enrolled in the study. The most common clinical findings were growth retardation, polyuria, and loss of appetite. None of the patients had the 57-kb deletion, but seven novel mutations were identified. The most common mutations identified were c.681G>A (p.Glu227Glu; 31%), c.1015G>A (p.Gly339Arg; 22%), and c.18_21 del (p.Thr7Phefs*7; 14%). These mutations were associated with earlier age of disease onset than the other mutations. To understand the effects of these allelic variants on clinical progression, the mutations were categorized into two major groups (missense versus deletion/duplication/splice site). Although patients with missense mutations had a better eGFR at the last follow-up visit, the difference was not significant. Patients in whom treatment began at age <2 years old had later onset of ESRD (P=0.02). Time to ESRD did not differ between the patients with group 1 and group 2 mutations.

Conclusions

The most common cystinosis gene mutations identified in Turkey were c.681G>A (p.Glu227Glu), c.1015G>A (p.Gly339Arg), and c.18_21 del (p.Thr7Phefs*7). Patients with less severe cystinosis gene mutations tend to have better kidney outcome.
Investigation of the stability of vitamin D in emulsion-based delivery systems
Authors: Sharifi Faezeh , Jahangiri Mansour
Published: August 2017

Vitamin D is a nutraceutical agent, which is necessary for good health. However, the sufficient amount of this vitamin needed for daily intake is not found in most foods which leads to many producers choosing to develop vitamin-enriched products. Vitamin D is sensitive to the exposure to oxygen and high temperature. To protect it against degradation during food processing, emulsion-based delivery is preferred. The more stable emulsion leads to higher protection of vitamin D. The present study investigated the effects of different factors, such as the choice of biopolymer, pH, ionic strength, and temperature, on emulsion stability. As emulsions with smaller particles are known to be more stable, the minimum concentrations of the biopolymers under study allowing the minimum size of particles were determined. The results obtained were the following: gum arabic 7 %, 468 nm; maltodextrin 2 %, 266 nm; Whey protein concentrate (WPC) 0.5 %, 190 nm; Soy protein isolate (SI) 4 %, 132 nm. Among the different biopolymers and the emulsion conditions studied, the soy protein isolate emulsion provided the highest protection of vitamin D (85 %) at 4 wt% concentration, pH 7 and 25?C. SEM analysis of the dried nanocapsules of the soy protein isolate emulsion revealed homogeneous and uniform dispersion of particles.
Gizli Emir (La orden secreta), de Melih Cevdet Anday: una novela profética con temas turcos y universales
Authors: Koelle Peter Brampton
Published: August 2017

Este artículo examina la novela turca Gizli Emir (La orden secreta), de Melih Cevdet Anday, incluida entre las Novelas del 12 de Marzo, nombre con que se conoce a las obras escritas a raíz del golpe de Estado turco de esa fecha en el año 1971, y aunque fue publicada un año antes, resultó profética en su contexto sociopolítico. Este artículo hace patente cómo el autor pudo examinar la situación turca sin necesidad de mencionar a los personajes, los partidos políticos, e incluso los topónimos del país, y cómo empleó este recurso para crear un ambiente y un atractivo universales que no se limitan a la condición de la Turquía de aquel momento.
De los lectores y el metalector en "La vorágine" de J. E. Rivera
Authors: Camarero Arribas Tomás
Published: August 2017

En este número no se incluyeron resúmenes ni palabras clave.
Marcelo: el presente sin presencia en "Respiración artificial" de Ricardo Piglia
Authors: Romano Thuesen Evelia Ana
Published: August 2017

En este número no se incluyeron resúmenes ni palabras clave.
Iris M. Zavala, La musa funambulesca. Poética de la carnavalización en Valle-Inclán. Orígenes, Madrid, 1990; 175 pp. / Iris M. Zavala, Unamuno y el pensamiento dialógico. Anthropos, Barcelona, 1991; 207 pp.
Authors: Bubnova Tatiana
Published: August 2017

Se reseñó el libro: La musa funambulesca. Poética de la carnavalización en Valle-Inclán.
La fábula burlesca de Cristo y la Magdalena, de Miguel de Barrios
Authors: Alatorre Antonio
Published: August 2017

En este número no se incluyeron resúmenes ni palabras clave.
Bernard Pottier, Teoría y análisis en lingüística. Versión española de G. Ter-Sakarian. Gredos, Madrid, 1992; 321 pp. (Biblioteca romámca-hispánica, estudios y ensayos, 378).
Authors: Lara Luis Fernando
Published: August 2017

Se reseñó el libro: Teoría y análisis en lingüística. Versión española de G. Ter-Sakarian.
Francisco Rico, Texto y contextos. Estudios sobre la poesía del siglo XV. Crítica, Barcelona, 1990; 240 pp.
Authors: Munguía Zatarain Martha Elena
Published: August 2017

Se reseñó el libro: Texto y contextos. Estudios sobre la poesía del siglo XV.
Acerca del "Primer Borges"
Authors: Corral Jorda Rose
Published: August 2017

En este número no se incluyeron resúmenes ni palabras clave.
El hospital como espacio de trabajo. Algunas claves para el análisis del conflicto sindical en salud pública
Authors: Beliera Anabel Angélica
Published: August 2017

En este artículo se analiza la trama política del conflicto sindical en salud pública, a partir del estudio de la experiencia de los trabajadores del Hospital Provincial Neuquén entre los años 2005 y 2013. A partir de una estrategia metodológica cualitativa, se realizó una investigación situada con un abordaje relacional donde se plasmó el entramado de relaciones en el que se desenvuelve el conflicto laboral. Aquí se analiza la articulación entre conflictos laborales y la disputa más general por la gestión de las políticas públicas, las regulaciones especiales que legislan el trabajo hospitalario y la presencia de la “comunidad” a quienes está orientado este servicio. Estas reflexiones llevan a dialogar con los estudios sindicales en la post-convertibilidad, realizando un aporte relativo al estudio del conflicto de trabajadores estatales y de una provincia del interior del país. Se argumenta a favor de una perspectiva relacional que entienda los conflictos sindicales y huelgas en el marco de las relaciones locales que integran los trabajadores.
Apuntes y reflexiones a partir de la Causa 17/12 Fuerza de Tareas N° 5 de la Armada Argentina. Participación de investigadores en los procesos de justicia, la noción de reparación y la reivindicación obrera
Authors: Barragán Sáez Paula Eva Ivonne
Published: August 2017

Esta intervención tiene como objetivo problematizar y proponer algunas reflexiones sobre las implicancias, aportes y resultados de las participaciones de tesistas e investigadores en el sistema judicial, específicamente, en los juicios por crímenes de lesa humanidad. Buscamos aportar a problematizar, reconocer las voces y los objetivos de los distintos actores presentes en una escena judicial específica, el proceso oral y público y la condena la Fuerza de Tareas 5 de la Armada Argentina por las violaciones a los derechos humanos cometidas por durante la última dictadura militar (1976-1983) en el cordón industrial de las localidades bonaerenses de Berisso y Ensenada y en la región del Río Santiago. Intentaremos reflexionar sobre como en dicha oportunidad el ámbito judicial fue receptivo y sirvió a la materialización de una reivindicación colectiva y de clase al componer una forma ampliada de reparación, económica, simbólica y moral, para un colectivo de trabajadores.
EL FIN DE LA TIERRA CONOCIDA. APROPIACIONES CONCEPTUALES DEL MUNDO CULTURAL: ENTREVISTA AL DR. ÁNGEL JOSÉ GARFÍAS FRÍAS.
Authors: Aldegani Emiliano
Published: August 2017

Doctor en ciencias políticas y sociales, Magister en comunicación y Licenciado en ciencias de la comunicación por la Facultad de Ciencias Políticas y Sociales de la UNAM. Profesor asociado de tiempo completo en la misma institución. Ha sido profesor de otras universidades como el SAE y la Universidad de Claustro de Sor Juana. Coordina la comunidad de Investigación La Finisterra en la Facultad de Ciencias Políticas y Sociales de la UNAM, cuyas líneas de investigación son: Videojuegos, Tecnologías para la comunicación audiovisual, Comics, Animación y Lucha libre.
Estudio del tratamiento del enlace químico en los libros de texto españoles
Authors: Gonzalez-Felipe Maria Esther , Aguirre-Perez Constancio , Cortes-Simarro José Manuel , Fernandez Cezar Raquel , Vázquez Moliní Ana María
Published: August 2017

En este trabajo se presenta un análisis del tratamiento del concepto de enlace químico en los libros de texto de Educación Secundaria en España. Se ha realizado un estudio de caso comparativo de tres de las editoriales más utilizadas con mayor frecuencia, para ello se elaboró una rúbrica con seis categorías: secuenciación de los contenidos, causa de la formación del enlace, terminología utilizada, clasificación de las sustancias según tipo de enlace, modelos de enlace y estudio de las fuerzas intermoleculares. Se concluye que entre las editoriales no hay diferencias en cuatro de los seis puntos, pero sí en: terminología empleada y el tratamiento de las fuerzas intermoleculares. Se aconseja al profesorado hacer uso de la rúbrica diseñada para analizar el tratamiento del enlace químico en los libros de texto y decidir cuál utilizar en sus clases.
Pautas para la aplicación de métodos de enseñanza musical desde un enfoque constructivista
Authors: Navarro Solís José Luis
Published: August 2017

Muchos músicos se han dedicado a dar clases, lo que dio origen a la educación musical; sin embargo, en varias escuelas de música la formación pedagógica dada a los escolares es elemental o nula y se va aprendiendo por medio del método ensayo-error. Parte del problema con la didáctica es la utilización de un método de enseñanza, pues no existe una correlación demostrable entre el docente y el éxito que pueda tener un método en cada uno de los contextos. Este artículo ofrece una revisión teórica de conceptos pedagógicos de autores representativos, seguidos de una serie de recomendaciones para desarrollar o implementar métodos de enseñanza musical en diversos entornos educativos con el apoyo de algunas teorías derivadas del constructivismo.
PERLINDUNGAN HUKUM BAGI PEMEGANG SERTIFIKAT HAK MILIK ATAS TANAH DALAM KETENTUAN PASAL 32 AYAT (2) PP No. 24 TAHUN 1997
Authors: Martana Putu Ade Harriestha
Published: August 2017

The title of this study is “legal protection for land ownership right certificate holder according to Article 32 clause (2) Government Regulation Number 24 Year 1997”. There is a contradiction between the negative publication system which is adopted in Indonesian land registration system and the indefeasable title that is given after the certificate is published for more than five years according to Article 32 clause (2) Government Regulation Number 24 Year 1997 about Land Registration. Therefore some issues are occured, which is the legal certainty and legal protection of the land ownership right certificate holder after the five years period according to Article 32 clause (2) Government Regulation Number 24 Year 1997. The research method used in this study is normative legal research focusing on investigation of legislature as the primary legal material and supported with the legal doctrine as secondary legal material. The approaching methods used is legal concepts approach and statute approach. From the legal material research can be concluded that in normative basis the aim of article 32 clause (2) Government Regulation Number 24 year 1997 is to give a legal protection and legal certainty, but in the process the article  is contradictory to the negative publication system and the clauses in the article itself is contradictory, therefore it does not give adequate legal protection and legal certainty for the holder of the land ownership right certificate after the five years period.
KONSEP WANPRESTASI DALAM HUKUM PERJANJIAN DAN KONSEP UTANG DALAM HUKUM KEPAILITAN (STUDI KOMPARATIF DALAM PERSPEKTIF HUKUM PERJANJIAN DAN KEPAILITAN)
Authors: Kurniawan Nyoman Samuel
Published: August 2017

Based on the assumption default is debt, the settlement of default case in contract law by using mechanisms of the law of Bankruptcy’s has become a new phenomenon in Indonesian business world. Though it is not infrequently the defendant of bankruptcy intentionally default to reply the counterparty that had already  been  in  default  (exceptio  inadimpleti  contractus  situation).  So  the research problem of this thesis is: Is the concept of default on the law of treaties can be fully applied to the concept of debt in bankruptcy law? This research used normative legal research methods by using statue approach, case-based approach, comparative approach and the conceptual approach. Analysis of legal materials is done with a qualitative approach to the exploratory nature of interpretive techniques, systematic, evaluative, constructive and argumentative. The results showed that not all defaults can be expressed as a debt in bankruptcy Law, except if the intended achievement is an achievement in the field of business activity (accounts payable). Default is determined from the agreement, regardless of whether there has been an exchange of rights and obligations or not, while the concept of debt has to be determined from the exchange between the rights and obligations which just happens sided (unilateral halt) though it is not preceded by a written agreement. Beside that, in contract law, tort only accountable to the creditors who have made a covenant only, but in bankruptcy law, the settlement will involve and affect a whole other creditors as well.
PENGATURAN PERADILAN ADAT DALAM AWIG-AWIG DESA PAKRAMAN: STUDI PENDAHULUAN TENTANG EKSISTENSI PERADILAN ADAT DALAM KESATUAN MASYARAKAT HUKUM ADAT DESA PAKRAMAN
Authors: Sudantra I Ketut
Published: August 2017

This study aims to determine the regulation on customary justice in the traditionalrules of awig-awig of  pakraman village, the rules made by the customarycommunity unit of Pakraman village in Bali. This study focused on structure,competency, mechanism, and principle of customary justice. The result shows thatstructure and competency of customary justice have been regulated clearly onawig-awig of pakraman village, but the mechanism of customary justice doesn’tregulated clearly. Awig-awig of desa pakraman only regulates initial mechanism,namely the process of filing a case, but does not regulate mechanisms after thecase was subsequently processed by the customary justice. It can be identifiedsome principles in awig awig of pakraman village to be a guidance for thecustomary courts in resolving cases that occur on it’s jurisdiction
PELAKSANAAN PERATURAN DAERAH PROVINSI BALI NOMOR 9 TAHUN 2009 TERKAIT DENGAN POGRAM WAJIB BELAJAR 12 TAHUN
Authors: Sentana Ni Nyoman Budi
Published: August 2017

The local government of Bali Province issued a policy that was formulated in The Local Regulation of Bali Province Number 9 of 2009. In appendix of The Local Regulation Number 9 of 2009 is described a 12-year compulsory education. This study discusses the effectiveness of The Local Regulation of Bali Province Number 9 of 2009 related to the implementation of 12-years compulsory education in Bali Province and the factors that influence the effectiveness of the implementation of The Local Regulation Number 9 of 2009 related to the implementation of 12-years compulsory education in Bali Province. This research is empirical legal research. The nature of research is descriptive. The data in this study include primary data that was collected through interview techniques and secondary data that was collected through the study of literature. The research location is in Bali Province with sample in Denpasar and Bangli regency. The data collected was analyzed qualitatively and descriptively presented analytically. Effectiveness of The Local Regulation of Bali Province Number 9 of 2009 related to the implementation of 12-years compulsory education in Bali Province is not optimal in some areas. The factors that influence the effectiveness of the implementation of The Local Regulation Number 9 of 2009 related to the implementation of 12-years compulsory education in Bali Province are legal factors, law enforcement factor, means and facilities in law enforcement factor, community factors and cultural factors
FUNGSI JAKSA DALAM MENUNTUT TERDAKWA KORUPSI UNTUK PENGEMBALIAN KERUGIAN KEUANGAN NEGARA PERSPEKTIF SISTEM PERADILAN PIDANA INDONESIA
Authors: Sinaryati Ni Wayan
Published: August 2017

This thesis of prosecutor function in the implementation of the court decision related to return of financial loss caused by corruption. In addition, this study also aims to determine and assets the constraints in the implementation of court decisions related to the return of financial loss. It is invecitable that at current time, corruption is one of the remarkable (extra ordinary crime) that endanger the stability and security as well as economic development in Indonesia. Corruption in Indonesia has been so severed and widespread in the community and very alarming, its development continues to increase from year to year, both in number of cases and the amonut of state financial losses and in terms of quality. These cirminal offenses commit more systematic and scope into all aspects of life. Starting from lower level of the dominant and state officials or law enforcement. Judge in imposing sanctions not only imprisonment and also fined an additional punishment, including the return of financial loss to the state by state corruption. The method used in this research is the method of normative juridical legal research of the research using primary and secondary data sources by document. This approact to use the statute approach, the analifical and conseptual approach, case approach and comparative approach legal, basic of corruption in the judicial process is ussed act No. 8 of 1981 (KUHAP), Act No. 31 of 1999, Act No. 20 of 2001 and Act No. 16 of 2004 The constraints in the implementation of the court decision related to the return of states losses, is convicted assets and property that has been transfered, multiple population administration and duration of the judicial proceses of implementation is not effective.
KEBERADAAN PEMEGANG SAHAM DALAM RUPS DENGAN SISTEM TELECONFERENCE TERKAIT JARINGAN BERMASALAH DALAM PERSPEKTIF CYBER LAW
Authors: Dharmawan Ni Ketut Supasti
Published: August 2017

In Indonesia, the General meeting of Shareholder through teleconference mechanism can be conducted under the provision of Article 77 of Law No. 40 of 2007 concerning Limited Liability Company. This teleconferencing mechanism allows all participants to see and to hear each other as well as  to participate in the teleconference meeting. There is legal vacuum with regard to position of shareholders in the General Meeting by teleconference mechanism, especially in the case of network problems. However, by analogy with the legal construct of the provisions of Article 90 of the Company Law can be stated that the position of shareholders continues to be recognized as a legal subject who has legal right and has valid votes counted even if the minutes of the meeting have not been signed electronically because internet network problem as long as treatise or the minute of General Meeting of shareholders is made by notarial deed and shall be signed by the Notary who made the deed.