UNASSIGNED: Congenital @entity5630 is an @entity74 of @entity1003 with wide genotypic and phenotypic variations. The clinical presentation can vary from asymptomatic @entity1 to @entity1 with major bleedings in severe @entity942 (factor VII <1%). Investigations show prolonged PT and low factor VII. Treatment modalities include FFP and repeated recombinant factor VII infusions. We hereby report the first successful LRLT for @entity5630 in an @entity1 , the first-ever youngest baby reported worldwide. A six-month-old male @entity1 presented with easy bruisability, ecchymotic patches, @entity811 , and @entity410 . CT of the head showed @entity548 , which was treated conservatively. He had markedly increased PT (120  s) with normal platelets, and aPTT with factor VII level <1%. Despite the treatment by rFVIIa administration weekly, which was very expensive, he still had repeated life-threatening @entity548 episodes. LRLT was performed with mother as the donor, whose factor VII level was 57%. A factor VII infusion plan for pre-, intra- and postoperative periods was formulated and @entity17792 followed. Postoperatively, his factor VII started increasing from third day and was 38% on 24th day with PT <14  s. He had uneventful intraoperative and postoperative courses. LT is a safe and definite cure for @entity5630 .

First living-related liver transplant to cure XXXX .

@entity1 :: ('9606', 'Species') :: ['child', 'patients', 'infant'] @entity410 :: ('MESH:D012640', 'Disease') :: ['convulsions'] @entity548 :: ('MESH:D006470', 'Disease') :: ['bleeding', 'subdural hemorrhage'] @entity5630 :: ('MESH:D005168', 'Disease') :: ['factor VII deficiency'] @entity1003 :: ('MESH:D001778', 'Disease') :: ['blood coagulation'] @entity17792 :: ('CHEBI:44926', 'Chemical') :: ['TEG'] @entity74 :: ('MESH:D030342', 'Disease') :: ['autosomal recessive serious disorder'] @entity811 :: ('MESH:D006417', 'Disease') :: ['hematuria'] @entity942 :: ('MESH:D003677', 'Disease') :: ['deficiency']
@entity5630 :: (MESH:D005168,Disease) :: ['factor VII deficiency']
