@entity409 , commonly associated with @entity8 , can result in massive @entity382 and debilitating symptoms. Surgical intervention for symptomatic @entity409 has been associated with significant morbidity and inconsistent long-term palliation; it is more appropriate in @entity1 with a single dominant cyst or cysts which is/are confined to one lobe. At our institution, nine @entity1 have undergone orthotopic liver transplantation for symptomatic @entity99 with excellent long-term results and minimal morbidity and mortality. Surgical candidates were selected based on severe limitations in daily activities and on sequelae of hepatic cystic involvement. Other factors considered were the extent and pattern of hepatic @entity8 , and prior surgical intervention. Three @entity1 (33%) required combined liver and kidney transplantation because of renal cystic involvement with @entity177 . The one-year survival rate was 89% with excellent symptomatic relief and improved quality of life in all the surviving @entity1 . One @entity204 occurred in a significantly malnourished 62-year-old female. Complications included one case each of @entity715 requiring retransplantation, biliary leak necessitating biliary reconstruction, and @entity86 requiring re-exploration. The mean hospital stay was 23 days and the mean intraoperative blood transfusion requirement was 18 units. Our experience demonstrates that appropriately selected @entity1 with extensive @entity99 with adult @entity409 can have an excellent outcome with transplantation, with morbidity comparable with other surgical options.

Liver transplantation for adult XXXX .

@entity1 :: ('9606', 'Species') :: ['patients'] @entity8 :: ('MESH:D007674', 'Disease') :: ['polycystic kidney disease', 'cystic disease, the degree of hepatic and renal dysfunction'] @entity409 :: ('MESH:D008107', 'Disease') :: ['Polycystic liver disease', 'polycystic liver disease'] @entity177 :: ('MESH:D051437', 'Disease') :: ['renal insufficiency'] @entity86 :: ('MESH:D019106', 'Disease') :: ['postoperative bleeding'] @entity382 :: ('MESH:D006529', 'Disease') :: ['hepatomegaly'] @entity715 :: ('MESH:D013927', 'Disease') :: ['hepatic artery thrombosis'] @entity99 :: ('MESH:D056486', 'Disease') :: ['hepatic cysts', 'hepatic involvement'] @entity204 :: ('MESH:D003643', 'Disease') :: ['death']
@entity409 :: (MESH:D008107,Disease) :: ['polycystic liver disease']
