UNASSIGNED: Background: @entity5683 are rare @entity5 that primarily occur in @entity1 . The use of the SEER (Surveillance, Epidemiology and End Results) database allows for the analysis of the relationship between prognostic factors and survival. Methods: We analyzed the SEER database to select pediatric @entity1 (<18 years old) with histologically confirmed diagnoses of @entity2846 ( @entity2846 ; WHO Grade 0), atypical @entity2846 (WHO Grade I) and @entity9204 ( @entity9204 ; WHO grade III). In univariate and multivariate analysis, we analyzed the relationship between demographic (age, gender, race, date of diagnosis) and treatment factors (extent of surgical resection, use of adjuvant radiation) on survival. Results: Overall, 168 pediatric subjects with @entity5683 were identified as follows: 75 cases of @entity2846 , 12 cases of atypical @entity2846 and 81 cases of @entity9204 . The median follow-up time was 3.5 years for @entity2846 and 7.7 years for @entity9204 . The median age at diagnosis was 4 years for @entity2846 (10-90th percentile 0-16 years) and 1 year for @entity9204 (10-90th percentile 0-10 years). In univariate regression analysis, @entity9204 histology (b = -3.2, 95% confidence interval, CI -4.8 to -1.5, p < 0.001) was significantly associated with younger age at diagnosis in comparison to @entity2846 . The mean @entity5 size was 3.7 cm for @entity2846 and 6.0 cm for @entity9204 (p < 0.001). A higher-grade @entity5 was associated with significantly increased mortality (hazard ratio, HR = 28.90, 95% CI 3.94-211.83, p = 0.001). Overall survival at 5 years was 98.7% for @entity2846 and 58.5% for @entity9204 (p < 0.001). Among those @entity1 with @entity9204 , gross total resection (GTR) was associated with a significantly lower mortality (HR = 0.21, 95% CI 0.07-0.66, p = 0.007). Overall survival at 5 years was 70.9% after GTR, significantly better than 35.9% after subtotal resection (p = 0.012) and 30% after no surgery (p = 0.003). Radiation treatment was not found to confer a survival benefit in @entity9204 . No demographic characteristics (age, sex, race, date of diagnosis) were significantly associated with mortality. Conclusions: Analysis of a pediatric cohort of @entity5683 in @entity1 in the SEER database shows that @entity5 grade is predictive of survival. In cases of @entity9204 , the extent of surgical resection, especially GTR, is significantly associated with increased survival. Radiation did not confer survival benefit.    2014 S. Karger AG, Basel.

@entity5683 in XXXX : A Population-Based Study.

@entity1 :: ('9606', 'Species') :: ['children', 'patients'] @entity5683 :: ('MESH:D016545', 'Disease') :: ['Choroid plexus tumors', 'choroid plexus tumors'] @entity5 :: ('MESH:D009369', 'Disease') :: ['tumor', 'neoplasms'] @entity2846 :: ('MESH:D020288', 'Disease') :: ['CPP', 'choroid plexus papillomas'] @entity9204 :: ('MESH:C562943', 'Disease') :: ['CPC', 'choroid plexus carcinomas']
@entity1 :: (9606,Species) :: ['Children']
