INTRODUCTION: @entity5043 ( @entity5043 ) and en coup de sabre (ECS) are variants of morphea. Although numerous findings on central nervous system (CNS) imaging of @entity5043 and ECS have been reported, the spectrum and frequency of CNS imaging findings and relation to cutaneous and @entity16 have not been fully characterized. METHODS: We retrospectively reviewed @entity1 younger than 50  years at our institution over a 16-year interval who had clinical diagnosis of @entity5043 and ECS by a skin or facial subspecialist. Two neuroradiologists evaluated available imaging and characterized CNS imaging findings. RESULTS: Eighty-eight @entity1 with @entity5043 or ECS were identified (62 @entity1 [70.4  %]; mean age 28.8  years). Of the 43 @entity1 with CNS imaging, 19 (44  %) had abnormal findings. The only finding in 1 of these 19 @entity1 was lateral ventricle asymmetry; of the other 18, findings were bilateral in 11 (61  %), ipsilateral to the side of facial involvement in 6 (33  %), and contralateral in 1 (6  %). Sixteen @entity1 had serial imaging examinations over an average of 632  days; 13 (81  %) had stable imaging findings, and 3 (19  %) had change over time. Of six @entity1 with progressive cutaneous findings, five (83  %) had stable imaging findings over time. Among the 23 @entity1 with clinical neurologic abnormality and imaging, 12 (52  %) had abnormal imaging findings. All seven @entity1 with @entity410 (100  %) had abnormal imaging studies. CONCLUSIONS: In @entity5043 and ECS, imaging findings often are bilateral and often do not progress, regardless of cutaneous disease activity. Findings are inconsistently associated with clinical abnormalities.

CNS imaging findings associated with @entity5043 and en coup de sabre: correlation to dermatologic and XXXX .

@entity1 :: ('9606', 'Species') :: ['women', 'patients'] @entity16 :: ('MESH:D009422', 'Disease') :: ['neurologic abnormalities'] @entity410 :: ('MESH:D012640', 'Disease') :: ['seizures'] @entity5043 :: ('MESH:D005150', 'Disease') :: ['PRS', 'Parry-Romberg syndrome']
@entity16 :: (MESH:D009422,Disease) :: ['neurologic abnormalities']
