@entity16663 ( @entity16663 ) are rare in childhood. Determination of malignant potential is difficult. To assess the presentation, clinical behaviour, and histology of these @entity5 in our center, the records of nine @entity1 with ACTs between 1989 and 2000 were analyzed. The age, sex, clinical presentation, investigations, treatment, follow-up data, and current status were determined. The pathological features were reanalyzed by our pathologist. The endocrine profile of the @entity5 was also retrieved from the records. There were two males and seven females; the median age at referral was 2.5 years. Two @entity1 (one male, one female) presented with clinical features of @entity699 with @entity101 . Four @entity1 had features of @entity699 with associated virilization. One 11-year-old @entity1 presented with @entity101 , @entity1371 , and pseudoparalysis due to an @entity1369 -secreting @entity5 . One @entity1 presented with precocious pubic hair and clitoromegaly. One male had evidence of true precocious puberty. The endocrine profile was available in eight cases: @entity701 levels were raised in four, @entity251 in four, and @entity1369 in one. One @entity1 had pubertal levels of follicle-stimulating hormone and @entity251 . Surgery was the only modality of therapy used. Histopathology showed capsular invasion in four @entity1 and vascular invasion in two. The median @entity5 weight was 80 g (15-550 g) and the size ranged from 1.5 x 1.5 to 12 x 12 cm. Five @entity1 are alive without @entity5 recurrence at a median follow-up time of 2 years. @entity5 recurrence was seen in two @entity1 , one with capsular rupture during surgery and another with a @entity5 weight of 16 g with associated capsular and vascular invasion. Atypical modes of presentation like pseudoparalysis must be kept in mind. Histologic criteria for @entity5 in @entity16663 are unreliable. @entity5 weight may not always be accurate in predicting @entity5 behaviour. Complete surgical excision remains the only effective and potentially curative treatment.

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@entity1 :: ('9606', 'Species') :: ['girl', 'patients', 'girls', 'boy'] @entity251 :: ('MESH:D013739', 'Chemical') :: ['testosterone'] @entity1369 :: ('MESH:D000450', 'Chemical') :: ['aldosterone'] @entity101 :: ('MESH:D006973', 'Disease') :: ['hypertension'] @entity5 :: ('MESH:D009369', 'Disease') :: ['tumor', 'Tumor', 'malignancy', 'tumors'] @entity699 :: ('MESH:D003480', 'Disease') :: ["Cushing's syndrome"] @entity16663 :: ('MESH:D000306', 'Disease') :: ['ACT', 'Adrenocortical tumors'] @entity701 :: ('MESH:D006854', 'Chemical') :: ['cortisol'] @entity1371 :: ('MESH:D007008', 'Disease') :: ['hypokalemia']
@entity16663 :: (MESH:D000306,Disease) :: ['Adrenocortical tumors']
