HYPOTHESIS: To investigate the @entity1504 present in @entity1 with @entity4237 ( @entity4237 ), including @entity129 , and to describe their auditory abilities. BACKGROUND: The prevalence of @entity4237 has increased with the development of high resolution magnetic resonance imaging (MRI). There are varying degrees of @entity4237 from true @entity261 . The etiology of @entity4237 remains unclear and it may be associated with @entity1504 in some instances. @entity4237 needs to be identified as early as possible to ensure prompt and adequate management of @entity393 since hearing aids and cochlear implants may not be an option. METHODS: A retrospective chart review of 56 ears of pediatric @entity1 with @entity4237 was conducted between August 2006 and November 2014 at a tertiary care pediatric hospital. RESULTS: 27.6% of @entity1 had @entity18129 and 48.9.8% had @entity394 . Five @entity1 had @entity2103 and two @entity1 had aplastic bilateral olfactory nerves. In the 27 ears with an absent nerve that were functionally tested, eight (29.6%) had partial hearing which indicates the presence of an extremely small nerve whose size is below the limits of spatial resolution of the MRI. CONCLUSION: MRI is becoming the initial imaging choice for @entity1 with @entity1274 to identify @entity4237 and other @entity75 . Concomitant vestibular and @entity18129 were observed in respectively half and one-third of the pediatric @entity1 with @entity4237 . The incidence of @entity600 suggests that balance testing should be recommended for most if not all @entity4237 @entity1 .

Cochlear Nerve @entity75 in Pediatric XXXX .

@entity1 :: ('9606', 'Species') :: ['children', 'patients'] @entity129 :: ('MESH:D003389', 'Disease') :: ['abnormalities of other cranial nerves'] @entity75 :: ('MESH:D001927', 'Disease') :: ['brain anomalies'] @entity2103 :: ('MESH:D005155', 'Disease') :: ['absent or abnormal facial nerves'] @entity1504 :: ('MESH:D002561', 'Disease') :: ['intracranial abnormalities'] @entity600 :: ('MESH:D000014', 'Disease') :: ['vestibular malformation'] @entity4237 :: ('MESH:D000160', 'Disease') :: ['cochlear nerve deficiency', 'CND'] @entity261 :: ('MESH:D007011', 'Disease') :: ['aplasia to hypoplasia'] @entity1274 :: ('MESH:D006319', 'Disease') :: ['sensorineural hearing loss'] @entity393 :: ('MESH:D034381', 'Disease') :: ['hearing loss'] @entity394 :: ('MESH:D015837', 'Disease') :: ['concomitant vestibular anomalies'] @entity18129 :: ('MESH:D015834', 'Disease') :: ['cochlear abnormalities']
@entity1 :: (9606,Species) :: ['Patients']
