BACKGROUND: @entity465 are characterized by defective antibody production and recurrent infections. @entity1 usually present with recurrent @entity1729 with consequent chronic @entity358 and @entity4595 , which could potentially influence cardiac function. Our aim was to assess noninvasively the @entity299 due to @entity358 in @entity1 with @entity465 . METHODS: A cross-sectional series of @entity1 with @entity465 syndromes from our referral immunology center were recruited. Individuals undergoing high-resolution computed tomography (HRCT) and transthoracic echocardiography were reviewed. RESULTS: Thirty primary @entity465 @entity1 aged 5-55 years of age (21 males and 9 females) were enrolled in this study. Half of the @entity1 (50%) were found to have @entity4595 in HRCT imaging. In echocardiographic examination, 20 @entity1 (67%) had at least one abnormality; among which pulmonary @entity101 was the most common (33%). @entity1 with @entity4595 had @entity551 and HRCT @entity4595 score was strongly correlated with pulmonary artery pressure (regression R = 0.59, P value = 0.001). CONCLUSION: Echocardiographic evaluation of right ventricular function and noninvasive estimation of pulmonary artery pressure could have an important diagnostic role in the follow-up and therapeutic management of @entity1 with primary @entity3230 .

Echocardiographic abnormalities and their correlation with XXXX score in primary antibody deficiencies.

@entity1 :: ('9606', 'Species') :: ['Patients', 'patients'] @entity101 :: ('MESH:D006973', 'Disease') :: ['hypertension'] @entity3230 :: ('MESH:C565469', 'Disease') :: ['immune deficiency'] @entity465 :: ('MESH:D007153', 'Disease') :: ['immunodeficient', 'Primary antibody deficiencies', 'primary antibody deficiency'] @entity358 :: ('MESH:D008171', 'Disease') :: ['pulmonary disease', 'pulmonary damage'] @entity4595 :: ('MESH:D001987', 'Disease') :: ['bronchiectasis'] @entity1729 :: ('MESH:D012141', 'Disease') :: ['respiratory tract infections'] @entity299 :: ('MESH:D006331', 'Disease') :: ['cardiac complications'] @entity551 :: ('MESH:D007022', 'Disease') :: ['higher pulmonary artery pressures']
@entity4595 :: (MESH:D001987,Disease) :: ['bronchiectasis']
