Little is known about the incidence and management of @entity241 ( @entity241 ) in @entity1 . We conducted a retrospective review of all @entity1 younger than 18 years of age treated for @entity241 over a period of 11  years (2000-2011) in Madrid, Spain. The sample consisted of 13 @entity1 . The average annual incidence of @entity241 in the pediatric population corresponded to 1.02 cases per million @entity1 -years (95% confidence interval  0.55, 1.73). Sites of involvement were diverse, with 15.3% of @entity5 found in acral locations. The median @entity5 size was 3.5 cm * 3  cm and the median time from apparent onset to diagnosis was 36  months. Histopathologic examination revealed conventional (77.0%), pigmented (15.4%), and myxoid (7.6%) variants. The mitotic index was consistently <5 per 10 high-power fields. All lesions were removed using surgical excision. One @entity1 developed a local recurrence because of initial affected margins; none developed @entity3 . The median duration of clinical follow-up was 70.5  months. This study estimated the average annual incidence rate of @entity241 in a population of @entity1 younger than 18 years and reviewed the experience of several hospitals in the management of this @entity5 .

Pediatric XXXX in Madrid, Spain: Multi-institutional Outcomes.

@entity1 :: ('9606', 'Species') :: ['children', 'patients', 'patient', 'person'] @entity241 :: ('MESH:D018223', 'Disease') :: ['dermatofibrosarcoma protuberans', 'DFSP'] @entity5 :: ('MESH:D009369', 'Disease') :: ['tumor', 'tumors'] @entity3 :: ('MESH:D009362', 'Disease') :: ['metastases']
@entity241 :: (MESH:D018223,Disease) :: ['Dermatofibrosarcoma Protuberans']
