The association of @entity22301 ( @entity22301 ) and @entity1582 is extremely rare. This association has been described in only six cases. We present a 4-year-old male admitted with a history of @entity1696 and @entity490 . Investigations revealed multiple calculi in both kidneys. A right pyelolithotomy and left nephrectomy were performed. Histological examination demonstrated @entity22301 and @entity2783 . At discharge serum @entity1011 had dropped to 1.1 mg/dl but after being lost to follow up for 9 years, the @entity1 was readmitted because of @entity4 . Laboratory examination revealed a @entity1985 and serum @entity1011 of 2.3 mg/dl. Rectal biopsy showed the presence of amyloid. A treatment by @entity3812 was unsuccessful. Fifteen months later, at the age of 15 years, the @entity1 developed @entity177 (serum @entity1011 14 mg/dl).

@entity1985 and XXXX by @entity2783 secondary to @entity22301 .

@entity1 :: ('9606', 'Species') :: ['patient', 'child'] @entity1985 :: ('MESH:D009404', 'Disease') :: ['nephrotic syndrome'] @entity2783 :: ('MESH:D000686', 'Disease') :: ['amyloidosis'] @entity4 :: ('MESH:D004487', 'Disease') :: ['edema'] @entity22301 :: ('MESH:D011705', 'Disease') :: ['xanthogranulomatous pyelonephritis', 'XPN'] @entity1582 :: ('MESH:D009101', 'Disease') :: ['systemic amyloidosis'] @entity177 :: ('MESH:D051437', 'Disease') :: ['terminal renal failure'] @entity1696 :: ('MESH:D001002', 'Disease') :: ['anuria'] @entity490 :: ('MESH:D015746', 'Disease') :: ['abdominal pain'] @entity1011 :: ('MESH:D003404', 'Chemical') :: ['creatinine'] @entity3812 :: ('MESH:D003078', 'Chemical') :: ['colchicine']
@entity177 :: (MESH:D051437,Disease) :: ['chronic renal failure']
