@entity1821 , the most common soft tissue @entity242 in adults, will rarely involve the orbit, either primarily or as a @entity3 . We describe seven primary @entity2694 , representing the largest documented series of primary @entity2694 to date. Affected @entity1 were three males and four females ranging in age from 28 to 69 years (median, 51 years). Five @entity1 presented with @entity5768 , one @entity1 had @entity158 , and no details of presenting symptoms are available in one case. The site distribution was retrobulbar (3 cases), lateral orbital wall (2 cases), medial wall (1 case), and unspecified (1 case). Radiologic impression included @entity2695 , @entity362 , and an inflammatory process. Lesional size ranged from 2.8 to 4 cm. @entity1821 were purely well-differentiated, one was dedifferentiated, and one was pleomorphic in type. The well-differentiated cases comprised the following subtypes: spindle cell (2 cases), adipocytic (2 cases), and combined adipocytic/sclerosing/inflammatory (1 case). Five @entity1 underwent orbital exenteration (one followed by radiation) and two had marginal/partial excision of their @entity5 . Follow-up was available for five @entity1 , ranging from 13 to 204 months (median 65 months). Four @entity1 showed no evidence of recurrence, including the @entity1 with @entity1821 who had a long, disease-free survival (65 months) following marginal excision. One @entity1 has had multiple recurrences following initial partial excision. One @entity1 died of an unrelated cause with no clinical evidence of recurrence. Despite the difficulty in obtaining wide surgical margins, the small @entity5 size at presentation and the apparent predominance of the well-differentiated type means that the prognosis for @entity2694 is generally good. In view of the various morphologic patterns that may occur, @entity1821 should be considered in the differential diagnosis of any histologically unusual mesenchymal lesion in the orbit.

XXXX of the orbit: a clinicopathologic study of seven cases.

@entity1 :: ('9606', 'Species') :: ['patients', 'patient'] @entity242 :: ('MESH:D012509', 'Disease') :: ['sarcoma'] @entity2695 :: ('MESH:D006391', 'Disease') :: ['hemangioma'] @entity362 :: ('MESH:D008067', 'Disease') :: ['lipoma'] @entity5 :: ('MESH:D009369', 'Disease') :: ['tumor', 'tumors'] @entity5768 :: ('MESH:D005094', 'Disease') :: ['painless proptosis'] @entity2694 :: ('MESH:D009916', 'Disease') :: ['orbital liposarcoma', 'orbital liposarcomas'] @entity3 :: ('MESH:D009362', 'Disease') :: ['metastasis'] @entity158 :: ('MESH:D010146', 'Disease') :: ['painful proptosis'] @entity1821 :: ('MESH:D008080', 'Disease') :: ['Five liposarcomas', 'liposarcoma', 'pleomorphic liposarcoma', 'Liposarcoma']
@entity1821 :: (MESH:D008080,Disease) :: ['Primary liposarcoma']
