@entity1 with @entity1614 suffer mainly from the cardiovascular manifestations of the disease, in particular the acute dissection or @entity397 of the dilated aorta. Due to improved diagnostic and early surgical intervention the life expectancy of these @entity1 could be considerably improved. However, @entity397 is still the most frequent and dissection the second frequent cause of @entity204 . Life threatening complications of @entity1580 are @entity2294 , @entity337 , due to obstruction of aortic branches. Dissection of the ascending aorta is treated by implantation of a valved conduit with reimplantation of the coronary arteries. Some surgeons favor the complete replacement of the ascending aorta with preservation of the aortic valve, although long-term results show some development of @entity337 after this procedure. Based on the experience of the last years, most surgeons prefer the prophylactic replacement of the aorta in Marfan @entity1 , i.e. before complications have occurred. A special treatment algorithm helps to define the indication for the operative treatment in different manifestations of the disease. The low mortality of the elective replacement of the ascending aorta in contrast to replacement in emergency cases speaks in favor of the early operative treatment. For the long-term prognosis of the @entity1 a closed and continuous cardiologic surveillance is mandatory. The @entity1 should be close to a center with the necessary diagnostic tools and with sufficient experience with the medical and surgical treatment, in order to further improve the life expectancy in the future.

[Surgical treatment of cardiovascular manifestations of XXXX ].

@entity1 :: ('9606', 'Species') :: ['Patients', 'patients', 'patient'] @entity2294 :: ('MESH:D010490', 'Disease') :: ['pericardial effusion'] @entity1614 :: ('MESH:D008382', 'Disease') :: ["Marfan's syndrome"] @entity397 :: ('MESH:D012421', 'Disease') :: ['rupture'] @entity337 :: ('MESH:D001022', 'Disease') :: ['aortic insufficiency and malperfusion syndrome', 'aortic insufficiency'] @entity204 :: ('MESH:D003643', 'Disease') :: ['death'] @entity1580 :: ('MESH:C562834', 'Disease') :: ['aortic dissection']
@entity1614 :: (MESH:D008382,Disease) :: ['Marfan's syndrome']
