@entity3686 is a @entity2788 . The diseased @entity1 usually have a nonlethal degree of the @entity8 , but the prognosis for the @entity1 is worse. They often die from @entity177 before the age of 35. Most cases of @entity393 occurs in @entity1 . The @entity393 is progressive after the age of 10. Audiological tests are characteristic for a @entity18129 . The debut of the disease usually appears in the post natal period giving microscopic haematuria. It can, however, occur later with haematuria and @entity644 . The @entity393 may be the first symptom, which is an observandum to otologists. Two families with @entity3686 are described. The @entity1 have been examined concerning @entity8 , audiological and vestibular pathology. The hereditary pattern is described.

Two families with XXXX .

@entity1 :: ('9606', 'Species') :: ['women', 'patients', 'men'] @entity644 :: ('MESH:D011507', 'Disease') :: ['proteinuria'] @entity8 :: ('MESH:D007674', 'Disease') :: ['kidney disease'] @entity3686 :: ('MESH:D009394', 'Disease') :: ["Alport's syndrome"] @entity177 :: ('MESH:D051437', 'Disease') :: ['renal failure'] @entity2788 :: ('MESH:D015785', 'Disease') :: ['hereditary disease striking cochlea, eye and kidney'] @entity393 :: ('MESH:D034381', 'Disease') :: ['hearing loss'] @entity18129 :: ('MESH:D015834', 'Disease') :: ['cochlear lesion']
@entity3686 :: (MESH:D009394,Disease) :: ['Alport's syndrome']
