OBJECTIVES: To analyze the anatomy features of the pulmonary circuits in the @entity1 with @entity1146 ( @entity1146 ) with @entity1757 ( @entity1757 ) and major aortopulmonary collateral arteries (MAPCA), and discuss the clinical significance. METHODS: From April 2002 to June 2010, the anatomy features of pulmonary circuits in 33 @entity1 with @entity1146 / @entity1757 /MAPCA were examined and analyzed. There were 21 male and 12 female @entity1 . The age ranged from 11 months to 29 years. The anatomic types of @entity1146 / @entity1757 included group B for 22 cases, group C for 11 cases. Thirty-one @entity1 of them underwent 33 operative procedures. The operations included aorta-pulmonary shunt in 8 cases, one stage unifocalization with @entity1757 open in 2 cases, complete repair in 23 cases. RESULTS: Twenty-nine (87.9%) @entity1 had native pulmonary arteries, 6 of them were normal size and 23 were hypoplastic size. Four @entity1 (12.1%) had no native pulmonary arteries. The postoperative @entity26 saturation of the @entity1 undergone shunt and one stage unifocalization was increased to 83% to 90%. There was one early @entity204 after complete repair because of multiorgan function failure. There were 4 cases of severe @entity998 and 3 cases of respiratory function failure. Sixteen @entity1 after complete repair were followed up more than one year. The postoperative right ventricular pressure was 41 to 99 mmHg (1 mmHg = 0.133 kPa). The ejection fraction value was more than 50% in 14 @entity1 and less than 50% in 2 @entity1 . Two @entity1 had medium @entity338 . CONCLUSIONS: An individualized approach based on the anatomy of the pulmonary circuits permits achievement in the @entity1 with @entity1146 / @entity1757 /MAPCA. The surgical strategy for @entity1146 / @entity1757 /MAPCA mainly depends on the anatomy features of native pulmonary arteries, confluent pulmonary arteries and MAPCA.

[The anatomy features and surgical significance of the pulmonary circuits of @entity1146 with XXXX and major aortopulmonary collateral arteries].

@entity1 :: ('9606', 'Species') :: ['patients'] @entity998 :: ('MESH:D002303', 'Disease') :: ['low cardiac output'] @entity26 :: ('MESH:D010100', 'Chemical') :: ['oxygen'] @entity1757 :: ('MESH:D006345', 'Disease') :: ['VSD', 'ventricular septal defect'] @entity338 :: ('MESH:D011665', 'Disease') :: ['pulmonary insufficiency'] @entity1146 :: ('MESH:D018633', 'Disease') :: ['pulmonary atresia', 'PA'] @entity204 :: ('MESH:D003643', 'Disease') :: ['death']
@entity1757 :: (MESH:D006345,Disease) :: ['ventricular septal defect']
