We report on two @entity1 with @entity795 ( @entity795 ), with emphasis on its pulmonary manifestations. The first @entity1 was a 6-year-old @entity1 diagnosed with @entity795 at 5 years of age. The @entity358 first observed at age 3 years and included streaky densities with accentuated vascular markings detected by chest radiography. The @entity1 had persistent abnormalities on follow-up chest radiographs. Chest computed tomography (CT) scans showed @entity384 . The second @entity1 was a 10-year-old @entity1 diagnosed with @entity795 at age 4 years. Chest radiography and CT scans showed patchy and streaky densities intermixed with small bullae, which were interpreted as @entity55 with post-inflammatory pneumatoceles. The @entity1 developed diffuse enlargement of air spaces of the lungs at age 10 years with severe respiratory compromise. Although pulmonary manifestations in @entity795 are uncommon, recognition of @entity358 and the presentation of enlarged air spaces in the lungs at an earlier age are important for accurate diagnosis. The plain radiograph findings of accentuated vascular markings seen in @entity1 with @entity795 may appear similar to interstitial or chronic @entity55 . This report emphasizes the features of lung involvement in @entity1 with @entity795 and suggests that specific attention be paid to pulmonary manifestations using chest CT scans.    2011 Wiley-Liss, Inc.

Pulmonary manifestations in @entity795 : pulmonary varicosities and XXXX .

@entity1 :: ('9606', 'Species') :: ['children', 'girl', 'patients', 'patient', 'boy'] @entity55 :: ('MESH:D011014', 'Disease') :: ['pneumonia'] @entity795 :: ('MESH:D016715', 'Disease') :: ['PS', 'Proteus syndrome'] @entity384 :: ('MESH:D002311', 'Disease') :: ['diffuse pulmonary venous dilatations'] @entity358 :: ('MESH:D008171', 'Disease') :: ['pulmonary abnormalities', 'pulmonary vein malformation']
@entity358 :: (MESH:D008171,Disease) :: ['bullous lung disease']
