BACKGROUND: @entity10970 ( @entity10970 ) is chronic and benign disease belonging to the heterogeneous spectrum of @entity66 . It is characterised by flask, superficial, aseptic pustules, mainly involving the trunk, axilla and inguinal folds, favourably responsive to @entity59110 . AIM: We report an original case with an atypical clinical presentation and course. CASE REPORT: A 25-year old @entity1 presented with an @entity203 that had appeared one week before. Similar flare-ups were reported for 3 years. No drug intake history nor recent infection were reported. Physical examination showed superficial pustules mainly located on the face and limbs, lying on an erythematous skin and sometimes grouped in large plaques with a serpiginous disposition having a characteristic aspect of hypopyon pustule. A specimen taken from the pustules did not show @entity2348 . Histological examination of a biopsy specimen showed subcorneal pustules with a dermal peri-capillary neutrophilic infiltrate. Direct immuno-fluorescence was negative. No associated diseases were found. The @entity1 was resistant to a 1 month treatment with @entity3761 (100 mg/day). Improvement was obtained with @entity14028 (25 mg/day) within 3 months. CONCLUSION: Our case has some specificities: cephalic involvement, resistance to @entity3761 and favourable outcome to a low dose of @entity14028 .

[ XXXX : an atypical case pustular].

@entity1 :: ('9606', 'Species') :: ['woman', 'patient'] @entity3761 :: ('MESH:D003622', 'Chemical') :: ['dapsone'] @entity14028 :: ('MESH:D017255', 'Chemical') :: ['acitretin'] @entity59110 :: ('MESH:D013450', 'Chemical') :: ['sulfones'] @entity66 :: ('MESH:D004194', 'Disease') :: ['neutrophilic diseases'] @entity10970 :: ('MESH:D012872', 'Disease') :: ['Sneddon-Wilkinson disease', 'SW'] @entity203 :: ('MESH:D003875', 'Disease') :: ['erythematous pustular eruption'] @entity2348 :: ('MESH:D001424', 'Disease') :: ['bacterial or fungal infection']
@entity10970 :: (MESH:D012872,Disease) :: ['Sneddon-Wilkinson's subcorneal dermatosis']
