Presumably the combination of regional @entity194 , @entity231 and lentodonesis is a new genetic entity. The hereditary transmission seems to be autosomal-recessive. As the first @entity227 , @entity227 is noted during the second decade of life. In these early stages patches of @entity194 are limited to the intermediate and perimacular zone. ERGs are not known from these early stages. Later on, no scotopic and only subnormal photopic reactions are registered. The @entity1 can do their work relatively well until the end of the sixth decade, when a @entity231 develops and the @entity194 gradually extends to the posterior pole. Together with the @entity231 , a lentodonesis is developing. The lentodonesis is caused by @entity2537 . Therefore, in order to escape the danger of a @entity7194 or a @entity16013 into the anterior chamber, an intracapsular extraction should be done at an early stage of lentodonesis. In spite of this, the visual prognosis is poor, since the areas of @entity194 are gradually enlarging. In these late stages the macula seems to be involved in all cases.

Tapetochoroidal degeneration combined with XXXX and lentodonesis.

@entity1 :: ('9606', 'Species') :: ['patients'] @entity227 :: ('MESH:D014786', 'Disease') :: ['hemeralopia', 'visual impairment'] @entity231 :: ('MESH:D002386', 'Disease') :: ['cataract'] @entity7194 :: ('MESH:D007906', 'Disease') :: ['lens-subluxation'] @entity2537 :: ('MESH:D020966', 'Disease') :: ['degeneration and elongation of the zonular fibres'] @entity16013 :: ('MESH:C536723', 'Disease') :: ['lens-luxation'] @entity194 :: ('MESH:D001284', 'Disease') :: ['choroidal atrophy']
@entity231 :: (MESH:D002386,Disease) :: ['cataract']
