INTRODUCTION: Primary @entity10064 (PCG) is a rare and sight threatening condition. Few large epidemiological studies are available in the literature concerning this condition. The purpose of the study was to evaluate the epidemiological and clinical characteristics of @entity1 affected by PCG. @entity1 AND METHOD: @entity1 affected by PCG, from 1day to 3years old at the time of diagnosis were retrospectively included between 1999  and 2014. The analysis concerned the pregnancy, family history, initial referral, clinical presentation with description of the classic findings in this condition, mean age at first consultation, duration of follow-up and presence of a delay in treatment, defined as a delay of over one month from the appearance of clinical signs until diagnosis. Two groups were defined according to age at appearance of the clinical signs: "early" group prior to 2months old and "late" group beyond 2months up until 3years old. RESULTS: One hundred and forty-one eyes of 71 @entity1 were included, with 49.3% @entity1 (n=35 @entity1 ) and 50.7% @entity1 (n=36 @entity1 ) for a male:female ratio of 1.02. The "early" group included 50 @entity1 i.e. 70.3% of the population; the "late" group 21 @entity1 or 29.7% of the population. A first-degree family history of @entity10064 existed in 28% of cases (n=19). The average age at first consultation was 13.1months for the entire population, and the mean duration of follow-up was 56.6months. Involvement was bilateral in 99.3% of cases (n=70 @entity1 ) and the most frequent clinical sign was buphthalmos in 64.5% of eyes (n=91eyes). Treatment was delayed in 35.3% of cases (n=25 @entity1 ). DISCUSSION AND CONCLUSION: This study is of particular relevance because it was performed over a long period and on a large population, considering the rare prevalence of the pathology, and has found epidemiological and clinical data comparable with those available in the literature for similar populations.

[Epidemiology and clinical characteristics of primary XXXX ].

@entity1 :: ('9606', 'Species') :: ['children', 'Children', 'PATIENTS', 'girls', 'boys'] @entity10064 :: ('MESH:C565547', 'Disease') :: ['congenital glaucoma']
@entity10064 :: (MESH:C565547,Disease) :: ['congenital glaucoma']
