BACKGROUND: @entity4128 ( @entity4128 ) is a rare @entity296 with a high burden of @entity943 , which is an important cause of @entity1164 ( @entity1164 ). @entity737 ( @entity737 ) is believed to be the most reliable management against @entity1164 . HYPOTHESIS: @entity943 does not necessarily confer a poor prognosis in @entity4128 @entity1 with an @entity737 . METHODS: A total of 39 @entity4128 @entity1 (34 male) implanted with an @entity737 at our electrophysiology center and followed up continuously were included in this study. The mean age at diagnosis was 42.1    14.8 years. RESULTS: Thirty-three @entity1 (84.6%) had suffered @entity943 with hemodynamic compromise before @entity737 implantation. During a median follow-up of 48.6 months (interquartile range, 32.3-73.3), 3 @entity1 (7.7%) died, 1 of @entity944 , 1 of @entity712 , and 1 of @entity385 . Twenty-eight @entity1 (71.8%) experienced 540 appropriate @entity737 interventions. The first appropriate @entity737 intervention occurred more than 2 years after @entity737 in 5 @entity1 (12.8%). Twelve @entity1 (30.8%) suffered from electrical storm. The event-free period was significantly shorter in @entity1 who did not have broad precordial T wave inversion >= V1-V3 (hazard ratio = 0.39, 95% confidence interval: 0.16-0.96). No significant difference was shown in antiarrhythmic drugs and radiofrequency catheter ablation before @entity737 implantation between @entity1 with and without appropriate @entity737 therapies (P > 0.05). CONCLUSIONS: Recurrence of sustained @entity1165 / @entity2224 is frequent in high-risk @entity1 with @entity4128 . The prognosis is favorable for @entity4128 @entity1 treated with an @entity737 for prevention of @entity1164 .

Long-term follow-up of arrhythmogenic right ventricular cardiomyopathy @entity1 with an implantable cardioverter-defibrillator for prevention of XXXX .

@entity4128 :: ('MESH:D019571', 'Disease') :: ['Arrhythmogenic right ventricular cardiomyopathy', 'ARVC'] @entity1164 :: ('MESH:D016757', 'Disease') :: ['sudden cardiac death', 'SCD'] @entity1 :: ('9606', 'Species') :: ['patients'] @entity296 :: ('MESH:D009202', 'Disease') :: ['inherited cardiomyopathy'] @entity712 :: ('MESH:D006333', 'Disease') :: ['heart failure'] @entity1165 :: ('MESH:D017180', 'Disease') :: ['ventricular tachycardia'] @entity944 :: ('MESH:D003645', 'Disease') :: ['sudden death'] @entity737 :: ('MESH:D057873', 'Disease') :: ['Implantable cardioverter-defibrillator', 'initial ICD implantation', 'ICD'] @entity2224 :: ('MESH:D014693', 'Disease') :: ['ventricular fibrillation'] @entity943 :: ('MESH:D001145', 'Disease') :: ['Ventricular arrhythmia', 'ventricular arrhythmia'] @entity385 :: ('MESH:D002544', 'Disease') :: ['cerebral infarction']
@entity1164 :: (MESH:D016757,Disease) :: ['sudden cardiac death']
