@entity1725 (P.P.) is characterised by the presence in the peritoneal cavity of 3 elements--mucinous neoplasic cells, mucinous @entity843 and diffuses mucinous implants. We analysed the @entity1 treated in our service and we made a literature review. The study is a retrospective analysis on the 1984-2000 period. 6 @entity1 were diagnosed with P.P., 2 females and 4 @entity1 , with medial age 63 years (53-75). Clinical findings and biologic analysis were not specific and the imagistic explorers didn't permit the preoperative diagnosis. The @entity1 were submitted to variate surgical procedures, based on the benign (4 cases) or malignant (2 cases) character of the disease and on the origin of the lesions: @entity9296 of the appendix with secondary @entity5 of the ovary (the 2 females) and, respectively, @entity9296 and cytsadenocarcinoma of the appendix, mucinous paraenteric cyst with @entity1725 , mucinous @entity5 (the 4 @entity1 ). We practiced intraperitoneal chemotherapy with Thio-Tepa in 5 cases (intraoperative in 4 cases) and systemic, with @entity1487 and mytomicine, in one case. The operative morbidity and mortality were null. All the @entity1 were follow-up (average 4.2 years). The global 5-year survival rate was 60% (100% in the benign disease and 0% in the malignant form). CONCLUSION: P.P. is a @entity395 , still poorly understood. The origin of the disease is the appendix (70-80%) and less frequently the ovary. It was divided in two distinct forms: disseminated peritoneal adenomucinosis and @entity298 . The treatment associates radical surgery and intraperitoneal chemohyperthermia, in specialised centres, but the prognosis still remains poor (50-70% 5-year global survival rate).

[Pseudomyxoma peritonei ( XXXX )].

@entity1 :: ('9606', 'Species') :: ['patients', 'men'] @entity5 :: ('MESH:D009369', 'Disease') :: ['recto-sigmoidian neoplasm', 'tumours'] @entity843 :: ('MESH:D001201', 'Disease') :: ['ascites'] @entity1725 :: ('MESH:D011553', 'Disease') :: ['pseudomyxoma retroperitonei', 'Pseudomyxoma peritonei'] @entity395 :: ('MESH:D035583', 'Disease') :: ['rare disease'] @entity9296 :: ('MESH:D003537', 'Disease') :: ['cystadenoma'] @entity298 :: ('MESH:D010538', 'Disease') :: ['peritoneal mucinous carcinomatosis'] @entity1487 :: ('MESH:D005472', 'Chemical') :: ['5-FU']
@entity298 :: (MESH:D010538,Disease) :: ['gelatinous peritonitis']
