PURPOSE: Primary @entity2828 of the jaw is rare. The aim of this study was to describe new cases of primary @entity2828 of the jaw and investigate reported prognostic factors of @entity2828 in this series and treatment outcome. MATERIALS AND METHODS: Six @entity1 with primary @entity2828 of the jaw were treated at the Memorial Sloan Kettering Cancer Center (MSKCC) from 1992 through 2013. Clinical data, pathology reports, treatment prescribed, treatment regimens, outcome, and follow-up information were reviewed. RESULTS: Five of 6 @entity1 were female and 5 cases were in the mandible. No @entity1 presented with metastatic disease at diagnosis. All cases were positive for @entity3778 , and 3 @entity1 with genetic confirmation were positive for @entity45620 fusion or @entity12726 gene rearrangement. All @entity1 received induction multiagent chemotherapy and surgical resection and 2 @entity1 received adjuvant radiotherapy. Total (grade IV) or nearly total (grade III) @entity5 @entity39 in 3 of 5 @entity1 (60%) assessed for histologic response to chemotherapy indicated intense sensitivity. All @entity1 were @entity66 , with no history of local recurrence, at a median follow-up period of 6.5  years. CONCLUSION: @entity1 with primary @entity2828 of the jaw have a good prognosis and @entity3 is an uncommon occurrence at initial presentation.

Primary Ewing Family of XXXX of the Jaw Has a Better Prognosis Compared to @entity5 of Extragnathic Sites.

@entity1 :: ('9606', 'Species') :: ['Patients', 'patients', 'patient'] @entity2828 :: ('MESH:D012512', 'Disease') :: ['Ewing sarcoma'] @entity66 :: ('MESH:D004194', 'Disease') :: ['alive and free of disease'] @entity39 :: ('MESH:D009336', 'Disease') :: ['necrosis'] @entity5 :: ('MESH:D009369', 'Disease') :: ['tumor'] @entity3778 :: ('4267', 'Gene') :: ['CD99'] @entity45620 :: ('2130;2313', 'Gene') :: ['EWS-FLI1'] @entity3 :: ('MESH:D009362', 'Disease') :: ['metastasis'] @entity12726 :: ('2130', 'Gene') :: ['EWSR1']
@entity5 :: (MESH:D009369,Disease) :: ['Tumors']
