AIM: To investigate behavior and cognitive performances of teenage @entity1 with @entity3148 ( @entity3148 ). METHODS: We enrolled 20 teenage @entity1 (12 females and 8 males) with @entity3148 , followed in the @entity1 Neurology Unit of the Catholic University (Rome). @entity1 underwent a full clinical examination including behavioral and cognitive assessments (respectively, CBCL and Wechsler scales). RESULTS: All @entity1 showed @entity146 and @entity1032 , mild in six cases, moderate in seven and severe in the remaining seven. Among @entity1032 @entity1 visual function, particularly visuo-motor abilities resulted mostly impaired in Wechsler subtests, whereas verbal skills were relatively preserved. In contrast, a general @entity73 was observed in moderately and @entity1032 @entity1 . CONCLUSIONS: Our teenage @entity1 with @entity3148 compared with other series at different ages (young childhood, adulthood) suggest a progressivity of neurological and neuropsychological signs. A visuomotor default and a relative preservation of verbal skills, like what has been found in previous reports of younger @entity1 , are still evident in mildly impaired cases. Therefore, the progression over time of these cases toward a generalized impairment may be suggested, but only longitudinal studies can confirm it. There was a possible responsibility of some @entity302 in worsening the neuropsychological outcome (early @entity410 and atypical absences, as well as persistent EEG background slowness in the last 3years).

Cognitive-behavioral profiles in teenagers with XXXX .

@entity1 :: ('9606', 'Species') :: ['Child', 'Patients', 'patients'] @entity1032 :: ('MESH:D008607', 'Disease') :: ['severely retarded', 'mental retardation', 'mildly retarded'] @entity410 :: ('MESH:D012640', 'Disease') :: ['myoclonic seizures'] @entity146 :: ('MESH:D001523', 'Disease') :: ['behavior disorders'] @entity73 :: ('MESH:D003072', 'Disease') :: ['cognitive impairment'] @entity302 :: ('MESH:D004827', 'Disease') :: ['epileptic disorders'] @entity3148 :: ('MESH:D004831', 'Disease') :: ['Dravet syndrome', 'DS']
@entity3148 :: (MESH:D004831,Disease) :: ['Dravet syndrome']
