AIMS AND OBJECTIVES: Documentation of the oral and dental manifestations of @entity18300 . SETTING AND @entity1 : @entity18300 is a member of the family of genetic craniotubular @entity4916 . This severe progressive sclerosing @entity18299 has important orofacial manifestations and a wide geographical distribution. Comprehensive oral and dental evaluation of eight affected adults in the Afrikaner community of South Africa was undertaken. RESULTS: Gross asymmetrical hypertrophy of the mandible was present in all eight @entity1 , bilateral or unilateral @entity3541 with @entity425 due to @entity2850 was present in six. Drooling of saliva and difficulties with mastication were frequent problems in these @entity1 . The teeth were structurally and mechanically normal although there was partial @entity2651 in two @entity1 and delayed @entity203 in another. Maxillary (palatal) and mandibular tori were present in every affected @entity1 . Due to the @entity4916 of the maxilla and mandible, tooth extraction was often a very difficult matter. There were no instances of post-extraction @entity4034 of the mandible. CONCLUSIONS: Accurate differentiation of @entity18300 from the other sclerosing @entity18299 is crucial for effective dental prognostication and management.

Dental and oral manifestations of XXXX .

@entity1 :: ('9606', 'Species') :: ['patients', 'person', 'PARTICIPANTS', 'persons'] @entity18300 :: ('MESH:C537525', 'Disease') :: ['sclerosteosis', 'Sclerosteosis'] @entity4916 :: ('MESH:D015576', 'Disease') :: ['hyperostoses', 'hyperostosis'] @entity18299 :: ('MESH:D001848', 'Disease') :: ['bone dysplasias', 'bone dysplasia'] @entity2651 :: ('MESH:D000848', 'Disease') :: ['anodontia'] @entity4034 :: ('MESH:D010019', 'Disease') :: ['osteomyelitis'] @entity203 :: ('MESH:D003875', 'Disease') :: ['eruption'] @entity425 :: ('MESH:D018908', 'Disease') :: ['weakness of facial muscles'] @entity2850 :: ('MESH:D009408', 'Disease') :: ['facial nerve entrapment'] @entity3541 :: ('MESH:D005158', 'Disease') :: ['facial paralysis']
@entity18300 :: (MESH:C537525,Disease) :: ['sclerosteosis']
