The nasal angiocentric T-cell-natural killer cell lymphoma is an aggressive @entity5 , exceptional in Tunisia, which is observed especially in Asia, Mexico and South America. We report the case of an 11-year-old @entity1 , presenting with an exuberant and @entity5 of the right nasal pit. Radiological investigation evidenced a right ethmo  do-frontal @entity5 . Evolution was characterized by the installation of @entity490 and @entity221 , the evidenciation of a mass within the head of the pancreas that compressed the extra hepatic biliary duct and Wirsung's canal and was associated to @entity12828 . Biopsy under ultrasound revealed a histiocytic nature. Nasal biopsy found histiocytic and lymphocytic cells and led to a diagnosis of @entity30558 . The absence of improvement under antibiotic treatment and the development of @entity221 with leuconeutropenia oriented towards the diagnosis of a non-Hodgkinian @entity706 . Medullary biopsy and immunohistochimic study confirmed a T/NK cells lymphoma, with medullary invasion. The @entity1 died from acute @entity649 . The authors insist on the rarity of this bipolar location, in particular in @entity1 , emphasize the difficulty of the diagnosis and review the literature.

[Nasal angiocentric T cell-natural killer cell lymphoma with pancreatic localisation in a XXXX ].

@entity1 :: ('9606', 'Species') :: ['children', 'boy', 'child'] @entity706 :: ('MESH:D008223', 'Disease') :: ['malignant lymphoma'] @entity5 :: ('MESH:D009369', 'Disease') :: ['tumor', 'ulcerative tumor'] @entity649 :: ('MESH:D012128', 'Disease') :: ['respiratory distress syndrome'] @entity30558 :: ('MESH:D012226', 'Disease') :: ['rhinoscleroma'] @entity490 :: ('MESH:D015746', 'Disease') :: ['abdominal pain'] @entity221 :: ('MESH:D005334', 'Disease') :: ['fever'] @entity12828 :: ('MESH:D034321', 'Disease') :: ['hyperamylasemia']
@entity1 :: (9606,Species) :: ['child']
