@entity980 is the most common soft tissue @entity242 in adolescence and childhood, which manifests by the locally destructive growth of the @entity5 or its metastases. We report on a 29-year-old @entity1 with an @entity3943 presenting with an unusual @entity1778 -like picture. On admission, the @entity1 suffered from diffuse @entity158 and @entity177 . Peripheral blood analysis showed @entity417 , thrombocythaemia and blast-like cells. A bone marrow aspirate revealed extensive infiltration by atypical blast-like cells which were interpreted as @entity981 . Although confirmation of this diagnosis by immunophenotyping did not succeed chemotherapy was started immediately and led to partial remission. Histologic analysis of a bone marrow biopsy from the iliac crest, however, revealed an extensive @entity5 with @entity133 , lined by primitive round cells with positive PAS-reaction in the cytoplasm. Immunostaining demonstrated a positive reaction of the @entity5 cells for @entity2283 and in a few @entity5 cells for smooth-muscle-actin. Chromosomal analysis showed a t(2;13) translocation typical for @entity3943 . Although multiple @entity75 of the skeletal system became evident during the further clinical course, the site of origin of the @entity5 could not be defined retrospectively. In conclusion, @entity980 should be included in the differential diagnosis of @entity262 with extensive @entity236 by @entity5 cells that could otherwise be misinterpreted as a @entity5 .

[ XXXX presenting as acute leukemia].

@entity1 :: ('9606', 'Species') :: ['patient', 'man'] @entity981 :: ('MESH:D054198', 'Disease') :: ['acute lymphoblastic leukemia'] @entity2283 :: ('1674', 'Gene') :: ['desmin'] @entity417 :: ('MESH:D000740', 'Disease') :: ['anaemia'] @entity242 :: ('MESH:D012509', 'Disease') :: ['sarcoma'] @entity5 :: ('MESH:D009369', 'Disease') :: ['tumor', 'haematologic malignancy', 'solid tumor', 'primary tumor'] @entity75 :: ('MESH:D001927', 'Disease') :: ['lytic lesions'] @entity262 :: ('MESH:D034721', 'Disease') :: ['systemic diseases'] @entity133 :: ('MESH:D002282', 'Disease') :: ['alveolar spaces'] @entity177 :: ('MESH:D051437', 'Disease') :: ['renal insufficiency'] @entity1778 :: ('MESH:D007938', 'Disease') :: ['leukemia'] @entity158 :: ('MESH:D010146', 'Disease') :: ['bone pain'] @entity980 :: ('MESH:D012208', 'Disease') :: ['Rhabdomyosarcoma', 'rhabdomyosarcoma'] @entity236 :: ('MESH:D001855', 'Disease') :: ['bone marrow infiltration'] @entity3943 :: ('MESH:D018232', 'Disease') :: ['alveolar rhabdomyosarcoma']
@entity3943 :: (MESH:D018232,Disease) :: ['Alveolar rhabdomyosarcoma']
