OBJECTIVES: @entity1 with @entity4032 and @entity6323 palliated with a superior cavopulmonary connection or Kawashima procedure (KP) have a high incidence of developing @entity2702 . The necessity for hepatic vein redirection (HVR) and its timing remains a controversy. We aimed to assess the clinical outcome of @entity1 with @entity4032 following a KP. The main end points were @entity204 , requirement for HVR and the impact of HVR on @entity26 saturation. METHODS: Retrospective review of 21 @entity1 with a diagnosis of @entity4032 , interruption of the inferior vena cava and single-ventricle physiology managed with a KP at a single centre between January 1990 and March 2010. RESULTS: Twenty-one @entity1 had a KP, with 12 subsequently undergoing HVR. There was relatively a constant monthly decrement in the proportion of @entity1 who were free from @entity204 or HVR up until 60 months following the KP, with a dramatic increase in the hazard after this time. The Cox proportional hazards regression model demonstrated a reduced early risk for HVR or @entity204 in @entity1 who underwent pulmonary artery banding versus arterial shunt as the primary procedure (hazard ratio: 0.10; P = 0.01), and an increased risk with bilateral superior vena cavas (SVCs) (hazard ratio: 3.4; P = 0.04) and age at KP (hazard ratio: 1.02 per month increase in age at KP; P = 0.02). HVR mortality was relatively high with 3 of 12 @entity1 dying in the early postoperative period with profound @entity848 . The timing of HVR after the KP did not influence the postoperative rate of increase in @entity26 saturation. CONCLUSION: These findings confirm that the majority of @entity1 who undergo a KP will require HVR. @entity1 who are older at the time of the KP or having an initial arterial shunt or bilateral SVCs are at higher risk of HVR or @entity204 . The relatively high mortality at HVR was characterized by severe @entity86 .

Outcomes following the Kawashima procedure for single-ventricle palliation in XXXX .

@entity1 :: ('9606', 'Species') :: ['Patients', 'patients'] @entity26 :: ('MESH:D010100', 'Chemical') :: ['oxygen'] @entity2702 :: ('MESH:C562404', 'Disease') :: ['pulmonary arteriovenous malformations'] @entity86 :: ('MESH:D019106', 'Disease') :: ['postoperative cyanosis'] @entity6323 :: ('MESH:C563013', 'Disease') :: ['interrupted inferior vena cava'] @entity4032 :: ('MESH:D059446', 'Disease') :: ['left atrial isomerism'] @entity204 :: ('MESH:D003643', 'Disease') :: ['death'] @entity848 :: ('MESH:D003490', 'Disease') :: ['cyanosis']
@entity4032 :: (MESH:D059446,Disease) :: ['left atrial isomerism']
