INTRODUCTION: With an estimated incidence of one to two per one million @entity1 , the @entity6019 ( @entity6019 ) is a rare disease. It is subclassified into a high-grade and a prognostically better low-grade type. Evidence-based data for a standardized therapy is lacking. CASE REPORT: A 32-year-old @entity28 nulligravida presented with persistent @entity3556 after the operation of an acute adnextorsion at another hospital. The repeat gynecological ultrasound examination showed a 5.3x5.3x3.6 cm vascularized, partially inhomogeneous mass in the uterus. A fractioned curettage yielded a differential diagnosis of @entity3905 or a non-differentiated @entity1478 . For completion of the operative treatment, laparotomy with hysterectomy, adnexectomy, and pelvine lymphonodectomy were performed. The final histological report described a 7 cm non-differentiated @entity1478 with infiltration of the left ovary and 25 @entity5 -free lymph nodes. DISCUSSION: Standard therapy for resectable @entity242 is abdominal hysterectomy and bilateral adnexectomy. So far, there is little data from studies reporting radio- or chemotherapy treatment of small @entity1 numbers in an adjuvant setting. CONCLUSION: The @entity6019 is a very rare disease of the uterus. Due to missing clinical data, it remains a multidisciplinary therapeutic challenge requiring individual decisions. To receive more information on this rare disease, treatment should be performed according to international protocols.

The high-grade XXXX : a rare entity.

@entity1 :: ('9606', 'Species') :: ['women', 'patient'] @entity3556 :: ('MESH:D014592', 'Disease') :: ['vaginal bleeding'] @entity28 :: ('MESH:D009765', 'Disease') :: ['obese'] @entity242 :: ('MESH:D012509', 'Disease') :: ['sarcoma'] @entity5 :: ('MESH:D009369', 'Disease') :: ['tumor'] @entity6019 :: ('MESH:D018203', 'Disease') :: ['endometrial stromal sarcoma', 'ESS'] @entity3905 :: ('MESH:D018198', 'Disease') :: ['malignant muellerian mixed tumor'] @entity1478 :: ('MESH:D014591', 'Disease') :: ['endometrial sarcoma']
@entity1478 :: (MESH:D014591,Disease) :: ['endometrial sarcoma']
