INTRODUCTION: @entity2333 ( @entity2333 ) describes a narrowing segment of the abdominal aorta and the branches arising from there. This narrowing frequently involves the renal arteries, with the only clinical sign being arterial @entity101 . OBJECTIVE: To review the cases of @entity2333 diagnosed in the Paediatric Nephrology Department of the Vall D'Hebron Hospital (Barcelona). METHODS AND MATERIALS: A retrospective study was conducted on 5 @entity1 aged from 8 days to 12 years old. We analysed the onset, diagnostic examinations, treatment and outcome. RESULTS: @entity101 was the common reason behind the study. In two of the five cases, it was associated with @entity177 . The definitive diagnostic was made using angiography and angio-MR, observing, in all the cases, that the renal arteries were affected (in 3 cases unilateral). The treatment was by medication in 3 cases, 1 required surgery and 1 died at 7 months. CONCLUSIONS: @entity2333 , although uncommon, is a very important cause of AHT in infancy. Angiography is the only technique to diagnose it. It is important to rule out cerebral involvement, which could lead to a fatal outcome. @entity101 is very difficult to control through medication. Surgery is required only when the @entity101 is not controllable through medication, when there is intermittent claudication, @entity951 , and @entity8 . Ideally, it is better to opt for medication as treatment, as the narrowing is progressive up to the end of puberty, after which, the narrowing stabilises.

[ XXXX : case studies from a paediatric nephrology department].

@entity1 :: ('9606', 'Species') :: ['patients'] @entity8 :: ('MESH:D007674', 'Disease') :: ['renal hypoperfusion'] @entity101 :: ('MESH:D006973', 'Disease') :: ['hypertension', 'Hypertension'] @entity177 :: ('MESH:D051437', 'Disease') :: ['renal failure'] @entity951 :: ('MESH:D000787', 'Disease') :: ['intestinal angina'] @entity2333 :: ('MESH:D001018', 'Disease') :: ['Mid-aortic syndrome', 'MAS']
@entity2333 :: (MESH:D001018,Disease) :: ['Mid-aortic syndrome']
