BACKGROUND AND IMPORTANCE: his is the first case report of clipping a @entity438 in a @entity1 with @entity17578 ( @entity17578 ). @entity17578 is a newly described autosomal dominant connective tissue disease with systemic vascular involvement. Unique to this syndrome is the development of @entity439 at a young age with the propensity of dissection or @entity397 at a stage that is earlier than when surgical intervention is typically indicated. We describe the nuances in intraoperative and postoperative management. CLINICAL PRESENTATION: A 31-year-old @entity1 who recently received a diagnosis of with @entity17578 type II presented to neurosurgical attention for management of an unruptured right ophthalmic @entity438 . The @entity1 underwent a right pterional craniotomy for clipping of the @entity439 , with lumbar drain placement before the procedure. @entity3302 had to be used several times to counteract @entity2553 of the vessels during arachnoid dissection. Because of vascular reactivity, temporary clipping was not used, and the @entity439 was clipped successfully. CONCLUSION: @entity17578 is a newly described disorder that warrants awareness in the neurosurgical community because of its association with @entity439 as well as @entity91 (19%), @entity1635 (20%), cervical spine instability (7%), @entity1276 , and @entity1645 . When clipping @entity439 in these @entity1 , the surgeon should be aware of the potential for severe vascular reactivity during dissection and avoid temporary clipping when possible. Avoidance of lumbar drainage intraoperatively reduces the risk of @entity551 after removal.

Clipping of a XXXX in a @entity1 with @entity17578 : case report.

@entity1 :: ('9606', 'Species') :: ['woman', 'patients', 'patient'] @entity1276 :: ('MESH:D006849', 'Disease') :: ['hydrocephalus'] @entity1645 :: ('MESH:D001139', 'Disease') :: ['Arnold-Chiari malformation'] @entity17578 :: ('MESH:D055947', 'Disease') :: ['Loeys-Dietz syndrome', 'LDS'] @entity1635 :: ('MESH:D012600', 'Disease') :: ['scoliosis'] @entity397 :: ('MESH:D012421', 'Disease') :: ['rupture'] @entity439 :: ('MESH:D000783', 'Disease') :: ['aneurysms', 'intracerebral aneurysms', 'aneurysm'] @entity3302 :: ('MESH:D010208', 'Chemical') :: ['Papaverine'] @entity91 :: ('MESH:D003398', 'Disease') :: ['craniosynostosis'] @entity2553 :: ('MESH:D020301', 'Disease') :: ['vasospasm'] @entity551 :: ('MESH:D007022', 'Disease') :: ['intracranial hypotension'] @entity438 :: ('MESH:D002532', 'Disease') :: ['artery aneurysm', 'cerebral aneurysm']
@entity438 :: (MESH:D002532,Disease) :: ['cerebral aneurysm']
