PURPOSE: To describe the ophthalmic findings of @entity82 of the orbit. METHODS: Prospective case series. Twenty-one @entity1 with @entity82 with orbital involvement underwent a complete ophthalmic examination and orbital imaging by CT. RESULTS: Four of the 21 @entity1 had @entity4262 and 1 had @entity2916 . In 17 @entity1 (81%), the disease was restricted to the craniofacial region. @entity2167 , @entity735 were detected in 62% of the @entity1 . Nasolacrimal duct obstruction and strabismus were detected in only 1 and 2 @entity1 , respectively. Of the 34 orbits affected, the roof was affected in 67.6%. The floor was the least affected wall. For most orbits, the disease was seen in more than 1 wall, and in 9 orbits (26.5%) all 4 walls were involved. Twelve orbits (35.2%) showed cysts on CT within the affected bones. In 19 orbits (55.9%), the optic canal was circumferentially narrowed. Blindness was detected in only 1 @entity1 who had undergone optic canal decompression. CONCLUSIONS: The main consequences of orbital involvement in @entity82 are eye @entity10244 and @entity5768 . @entity661 is a common feature. Optic canal narrowing does not necessarily induce @entity1018 . We believe that @entity1 with apical involvement should be carefully followed and have their apices decompressed only when their vision is clearly deteriorating. Our data do not support prophylactic optic canal decompression as a therapeutic measure.

XXXX with @entity82 : implications for vision.

@entity1 :: ('9606', 'Species') :: ['patients', 'patient'] @entity1018 :: ('MESH:D054062', 'Disease') :: ['vision loss'] @entity10244 :: ('MESH:D014849', 'Disease') :: ['dystopia'] @entity82 :: ('MESH:D005355', 'Disease') :: ['fibrous dysplasia'] @entity2167 :: ('MESH:D006311', 'Disease') :: ['Facial distortion'] @entity5768 :: ('MESH:D005094', 'Disease') :: ['proptosis'] @entity4262 :: ('MESH:D005359', 'Disease') :: ['McCune-Albright syndrome'] @entity735 :: ('MESH:D005124', 'Disease') :: ['proptosis, and eye dystopia'] @entity2916 :: ('MESH:D014402', 'Disease') :: ['tuberous sclerosis'] @entity661 :: ('MESH:D054549', 'Disease') :: ['Apical involvement']
@entity661 :: (MESH:D054549,Disease) :: ['Apical involvement']
