AIM OF STUDY: In the final stages of @entity2720 of the knee joint, the preservation of walking ability is only possible by joint replacement. Fibrotic ancylosis and @entity85 , being mostly bilaterally, make the joint reconstruction difficult and impair the results. The purpose of this study was to evaluate the results of total knee replacement (TKR) in @entity447 . METHODS: From 1990 to 1998, 14 TKR in 7 @entity1 with severe @entity447 were performed. The mean age at operation was 47.3 years (range, 27-62 years). The mean follow-up period was 3.7 years (range, 1-7 years). The TKR was performed bilaterally at the same time in 6 cases. In 1 case, the bilateral TKR was done one after another with 6 months interval. In 10 knee joints, an unconstrained or semi-constrained surface replacement system was used. In 4 joints, a hinged prosthesis was required. RESULTS: The range of motion (extension-flexion) was improved from 0-23-69 degrees preoperatively to 0-4-88 degrees at follow-up. The mean HSS Score increased from 34.5 points preoperatively to 77.9 points at follow-up. Perioperatively, no @entity548 or early infections were observed. In 1 case, 6 years postoperatively a late infection of the hinged knee prosthesis occurred. A two-stage-exchange of the prosthesis was performed. Aseptic loosenings of prosthetic components were not observed. CONCLUSION: The TKR in @entity447 is technically demanding and requires a consequent perioperative F-VIII or F-IX substitution. A bilateral simultaneous implantation is useful. The indication for TKR has to be strict because of the higher risks and requires a close cooperation with the haemostaseologist.

[Knee endoprosthesis implantation in XXXX : results, problems and complications].

@entity1 :: ('9606', 'Species') :: ['patients'] @entity548 :: ('MESH:D006470', 'Disease') :: ['haemorrhages'] @entity447 :: ('MESH:D006467', 'Disease') :: ['haemophilia'] @entity2720 :: ('MESH:D007592', 'Disease') :: ['haemophilic arthropathy'] @entity85 :: ('MESH:D009140', 'Disease') :: ['severe deformities']
@entity2720 :: (MESH:D007592,Disease) :: ['hemophiliac arthropathy']
