Acute @entity5442 with severe subcutaneous @entity4 is extremely rare and has been reported in only a handful of cases. We describe two similar @entity1 presenting with this disorder and generalized @entity1910 . Unlike the five previously reported cases, the clinical and histologic features of our two @entity1 are more suggestive of @entity6017 than @entity6558 . Nevertheless, scrutinizing all seven reported @entity1 , a number of specific characteristics could be defined. All @entity1 were adult males. @entity1282 was present in four. In six @entity1 , acute @entity5442 was @entity5 was present in one. Two @entity1 died despite intensive therapy, three improved on corticosteroid treatment, and two recovered spontaneously. In all @entity1 , limb involvement with marked subcutaneous @entity4 was present, clinically mimicking @entity1150 in both our @entity1 . The presence of severe subcutaneous @entity4 may be a hallmark of a distinctive variant of acute @entity5442 . More cases are needed to discern subtypes of this general entity and to establish guidelines for treatment and prognosis.

Acute XXXX with severe subcutaneous @entity4 , a new variant? Report of two cases and review of the literature.

@entity1 :: ('9606', 'Species') :: ['patients'] @entity6017 :: ('MESH:D003882', 'Disease') :: ['dermatomyositis'] @entity5442 :: ('MESH:D009220', 'Disease') :: ['inflammatory myopathy'] @entity1910 :: ('MESH:D005076', 'Disease') :: ['rash'] @entity5 :: ('MESH:D009369', 'Disease') :: ['idiopathic while malignancy'] @entity4 :: ('MESH:D004487', 'Disease') :: ['edema'] @entity1150 :: ('MESH:D020246', 'Disease') :: ['deep vein thrombosis'] @entity1282 :: ('MESH:D003680', 'Disease') :: ['Dysphagia'] @entity6558 :: ('MESH:D017285', 'Disease') :: ['polymyositis']
@entity5442 :: (MESH:D009220,Disease) :: ['inflammatory myopathy']
