OBJECTIVE: Management of @entity1146 with @entity12043 (PAIVS) can be directed to either biventricular repair or univentricular palliation. The optimal management strategy has yet to be defined. METHODS: All @entity1 operated at the Royal @entity1 's Hospital, Melbourne for PAIVS between 1990 and 2006 (n = 81) were reviewed. @entity1 were retrospectively stratified into a simple three-tiered classification based on right ventricle (RV) size. Multivariate logistic regression analysis was performed to identify risk factors of mortality. RESULTS: The distribution of RV sizes was normal in 11 (14%), moderate @entity509 in 45 (56%), and severe @entity509 in 25 (31%) @entity1 . RV-to-coronary-artery connections were present in 33 (41%) and RV coronary dependence in six @entity1 (7%). Sixteen @entity1 died (20%). The end-status of the remaining @entity1 was biventricular repair in 31/81 (38%), 1  -ventricle repair in 10/81 (12%), Fontan circulation in 14/81 (17%), transplantation in 1/81 (1%), and still awaiting repair in 9/81 (11%). Ten-year survival was 80% (95% confidence interval (CI): 71-87%). Independent predictors of mortality were lower tricuspid valve (TV) annulus size Z-score and the presence of RV-to-coronary-artery connections. CONCLUSIONS: A simple three-tiered classification based on RV size may allow initial stratification into biventricular or univentricular repair for @entity1 with normal RV size and severe @entity4265 . In @entity1 with moderate @entity4265 , the presence of RV-to-coronary-artery connections or a TV Z-score<-2 should caution one against attempting biventricular repair.

Changing trends in the management of XXXX with @entity12043 : the Melbourne experience.

@entity1 :: ('9606', 'Species') :: ['Patients', 'patients', 'Children'] @entity509 :: ('MESH:C538429', 'Disease') :: ['hypoplasia'] @entity12043 :: ('MESH:C562832', 'Disease') :: ['intact ventricular septum'] @entity1146 :: ('MESH:D018633', 'Disease') :: ['pulmonary atresia'] @entity4265 :: ('MESH:C535682', 'Disease') :: ['RV hypoplasia']
@entity1146 :: (MESH:D018633,Disease) :: ['pulmonary atresia']
