UNASSIGNED: @entity715 ( @entity715 ) is a frequent complication of @entity1575 , but it can also occur as a primary @entity455 amid @entity409 . Extrahepatic @entity6315 (EHPVO) refers to the obstruction of the extrahepatic portal vein with or without involvement of the intrahepatic portal vein branches, splenic and/or superior mesenteric vein. It is a distinct disorder that excludes @entity715 occurring in concurrence with @entity1575 or @entity157 . The term "EHPVO" implies chronicity and is principally reserved for a long-standing condition characterized by cavernous transformation of the portal vein. The most characteristic imaging manifestation is the formation of portoportal collaterals (via the venous plexi of Petren and Saint) that allow hepatopetal flow. However, this collateral circulation is insufficient resulting in clinically significant pre-hepatic portal @entity101 , wherein the liver function and structure remain preserved until late. Although the long-term (more than 10   years) survival with controlled variceal bleeding is up to 100%, affected individuals have an impaired quality of life owing to portal cavernoma cholangiopathy, @entity6118 , @entity149 and @entity851 . Imaging diagnosis is not always straightforward as the collaterals can also present as a @entity5 -like solid mass that can be inadvertently biopsied. Moreover, EHPVO has its implications for the biliary tree, arterial circulation, liver/splenic volumes and stiffness, which merit proper understanding but have not been so well described in literature. In this review, we present the complete spectrum of the vascular, biliary and visceral changes with a particular emphasis on what our medical/surgical hepatology colleagues need to know from us in the pre-operative and post-operative settings.

Multimodality imaging of primary extrahepatic XXXX (EHPVO): what every radiologist should know.

@entity455 :: ('MESH:D014652', 'Disease') :: ['vascular disorder'] @entity851 :: ('MESH:D006130', 'Disease') :: ['growth retardation'] @entity101 :: ('MESH:D006973', 'Disease') :: ['hypertension'] @entity5 :: ('MESH:D009369', 'Disease') :: ['tumour'] @entity409 :: ('MESH:D008107', 'Disease') :: ['absent liver disease'] @entity149 :: ('MESH:D002493', 'Disease') :: ['neurocognitive dysfunction'] @entity157 :: ('MESH:D006528', 'Disease') :: ['hepatocellular carcinoma'] @entity6118 :: ('MESH:D006971', 'Disease') :: ['hypersplenism'] @entity1575 :: ('MESH:D008103', 'Disease') :: ['liver cirrhosis'] @entity715 :: ('MESH:D013927', 'Disease') :: ['Portal vein thrombosis', 'PVT'] @entity6315 :: ('MESH:C563407', 'Disease') :: ['portal vein obstruction']
@entity6315 :: (MESH:C563407,Disease) :: ['portal vein obstruction']
