BACKGROUND: @entity34926 , defined as complete or partial displacement of the heart outside the thoracic cavity, is rare. The cause and pathogenesis are unknown. The anatomy of the heart may be normal, but the presence of structural @entity299 as well as @entity600 is common. @entity1 present incidentally after birth or, more recently, the condition has been diagnosed by prenatal echocardiography. OBJECTIVE: To review the presentation, diagnostic imaging, management and outcomes of @entity1 with @entity34926 at The Hospital for Sick @entity1 , Toronto, Ontario. METHODS: The medical records of the database of the Division of Cardiology, The Hospital for Sick @entity1 , were searched; echocardiograms, and surgical and autopsy reports were further reviewed. RESULTS: Between 1978 and 1998, 10 @entity1 with @entity34926 presented to the authors' centre. Normal cardiac anatomy was noted in three, and mild to complex structural @entity299 were noted in the remainder. @entity600 were found in six cases. Six were diagnosed by prenatal ultrasound between 19 and 37 weeks of gestation. Pregnancies were electively terminated or the @entity1 died shortly after birth. Four other neonates with @entity34926 were referred to the authors' centre. All of these @entity1 subsequently died either at the time of surgery for cardiac and @entity154 or in the immediate postoperative period. CONCLUSIONS: Despite modern treatment options, the mortality remains high for @entity1 with @entity34926 , especially in the presence of structural @entity299 or other @entity600 .

Presentation and outcomes of XXXX .

@entity1 :: ('9606', 'Species') :: ['Patients', 'patients', 'Children', 'infants'] @entity154 :: ('MESH:D000013', 'Disease') :: ['noncardiac anomalies'] @entity600 :: ('MESH:D000014', 'Disease') :: ['malformations', 'noncardiac malformations', 'Associated noncardiac malformations'] @entity299 :: ('MESH:D006331', 'Disease') :: ['heart disease', 'cardiac anomalies'] @entity34926 :: ('MESH:D054083', 'Disease') :: ['ectopia cordis', 'Ectopia cordis']
@entity34926 :: (MESH:D054083,Disease) :: ['ectopia cordis']
