The clinical, electrophysiological, and pathological findings, and the therapeutic characteristics in ten @entity1 with @entity2646 ( @entity2646 ), whose onset age was less than 16 years, were evaluated. The clinical progression pattern of the initial phase divided the @entity1 into two groups. One group (six @entity1 ) showed a subacute progression for up to 2 months after onset and a subsided progression over 3 months. Three @entity1 in this group had a preceding febrile episode. The other group (four @entity1 ) showed a chronic insidious progression for more than 3 months. The former group of @entity1 revealed a favourable response to corticosteroid therapy as compared with the latter group. However, other clinical and laboratory features at the peak impairment were not distinguishable between these two groups. Motor dominant @entity16 was common to all @entity1 , and only three cases showed @entity132 on the distal limbs. No cases revealed @entity129 . Motor and sensory nerve conduction and sural nerve biopsy studies revealed the demyelinating nature of the @entity16 . These clinicopathological features suggest that the subacute progression form frequently associated with prodromal episode and rather favourable corticosteroid response is characteristic in childhood @entity2646 , while the chronic insidious progression form is indistinguishable from the common adult @entity2646 .

Clinicopathological features of XXXX in childhood.

@entity1 :: ('9606', 'Species') :: ['children', 'patients'] @entity129 :: ('MESH:D003389', 'Disease') :: ['cranial nerve involvement'] @entity132 :: ('MESH:D010468', 'Disease') :: ['sensory disturbance'] @entity16 :: ('MESH:D009422', 'Disease') :: ['neuropathy'] @entity2646 :: ('MESH:D020277', 'Disease') :: ['CIDP', 'chronic inflammatory demyelinating polyradiculoneuropathy']
@entity2646 :: (MESH:D020277,Disease) :: ['chronic inflammatory demyelinating polyradiculoneuropathy']
