BACKGROUND: Type B interrupted aortic arch with @entity1757 is @entity4297 that may have associated @entity3585 . Surgical management has evolved from a two-stage approach to the currently favored single-stage approach. The following data summarize our experience with the two-stage approach over a 15-year period. METHODS: Between 1980 and 1995, 27 consecutive @entity1 with @entity1892 interrupted aortic arch and @entity1757 underwent surgical management using the two-stage approach. There were 15 @entity1 and 12 @entity1 ; 21 @entity1 had the @entity2418 . RESULTS: Stage I was performed at a median age of 4 days. Twenty-six (96%) of 27 @entity1 survived first-stage palliation. One @entity1 survived stage I palliation but died before undergoing stage II. Twenty-five @entity1 underwent second-stage repair at a median age of 6 weeks (range, 1 to 46 weeks). There were 2 early deaths and 1 late @entity204 . Actuarial analysis demonstrates 1- and 5-year survival rates of 85% and 81%, respectively. Twenty-two survivors have been followed up for an average of 8 +/- 2 years. Freedom from reoperation for arch graft enlargement has been 86% at 3 years and 55% at 5 years. Freedom from reoperation for @entity3585 has been 82% at both 3 and 5 years. CONCLUSIONS: The two-stage approach can achieve good mid- to long-term palliation of @entity1 with @entity1892 interrupted aortic arch and @entity1757 . These results should provide a reference from which to gauge the long-term success of the single-stage approach.

Mid- to long-term results of the two-stage approach for @entity1892 interrupted aortic arch and XXXX .

@entity1 :: ('9606', 'Species') :: ['patients', 'patient', 'girls', 'boys'] @entity3585 :: ('MESH:D014694', 'Disease') :: ['left ventricular outflow tract obstruction'] @entity1757 :: ('MESH:D006345', 'Disease') :: ['ventricular septal defect'] @entity1892 :: ('MESH:D016393', 'Disease') :: ['type B'] @entity2418 :: ('MESH:D004062', 'Disease') :: ['DiGeorge syndrome'] @entity204 :: ('MESH:D003643', 'Disease') :: ['death'] @entity4297 :: ('MESH:D006330', 'Disease') :: ['a complex congenital heart defect']
@entity1757 :: (MESH:D006345,Disease) :: ['ventricular septal defect']
