PURPOSE: To assess the clinical presentation and long-term visual outcome in a series of @entity1 with craniopharyn-gioma. METHODS: Retrospective case review. RESULTS: Thirty-six @entity1 were reviewed, comprising 19 female @entity1 and 17 male @entity1 . The age range was 2-77 years with a bimodal distribution of 17 @entity1 (mean age 10 years) and 19 adults (mean age 47 years). Blurred vision was the most common visual complaint (23 cases, 64%) and @entity10 the most frequent systemic complaint (19 cases, 53%). The average duration of systemic symptoms was 45 weeks compared to 10 weeks for @entity227 . @entity227 occurred in 13 @entity1 (36%) and showed no significant change from initial presentation to final review. Sixteen @entity1 (44%) had @entity1805 on presentation and pleomorphism (change from one type of @entity227 to another) occurred in 11 @entity1 . Recurrence of @entity5 occurred in 15 @entity1 (42%) and was more likely in @entity1 (59%) than adults (26%). The mean time period to recurrence was 7 years. The average follow-up period for all cases was 10 years. CONCLUSION: @entity1 with @entity976 generally present late, and the @entity227 are often preceded by a long history of systemic symptoms. @entity1 are more likely to present with systemic symptoms than adults. Visual field pleomorphism is a feature of @entity976 and occurred in one-third of the @entity1 . Local recurrence is common. Although magnetic resonance imaging is the recommended means of follow up, regular neuro-ophthalmic review is useful in the early detection of anterior visual pathway compression by recurrent @entity5 .

XXXX : a review of long-term visual outcome.

@entity1 :: ('9606', 'Species') :: ['children', 'Patients', 'patients', 'Children'] @entity227 :: ('MESH:D014786', 'Disease') :: ['visual field defect', 'Deficits in visual acuity', 'visual symptoms'] @entity5 :: ('MESH:D009369', 'Disease') :: ['tumour'] @entity1805 :: ('MESH:D006423', 'Disease') :: ['bitemporal hemianopia'] @entity976 :: ('MESH:D003397', 'Disease') :: ['craniopharyngioma'] @entity10 :: ('MESH:D006261', 'Disease') :: ['headache']
@entity976 :: (MESH:D003397,Disease) :: ['Craniopharyngioma']
