BACKGROUND: Tetralogy of Fallot with unilateral absence of the @entity358 is a rare @entity4297 that still represents a surgical challenge. The purpose of this study is to summarize our experience of surgical treatment of this complex lesion. METHODS: From 1983 to 2003, 27 @entity1 with tetralogy of Fallot and unilateral absence of the left (n = 25) or right (n = 2) @entity358 underwent different surgical interventions. The age of @entity1 ranged from 40 days to 37 years (median, 5.3 years). Pulmonary arterial Nakata index and Nakata index Z-score were used for the quantitative assessment of the contralateral @entity358 . Twenty @entity1 underwent various palliative procedures, namely Blalock-Taussig or Gore-Tex shunt, transluminal balloon pulmonary valvuloplasty, and reconstruction of right ventricular outflow tract without @entity1757 closure. At a median interval of 3.6 years after palliation, 13 @entity1 underwent complete repair of tetralogy of Fallot. In the other 7 @entity1 , complete repair was performed as a primary intervention. RESULTS: Hospital mortality after palliation and after a complete repair was the same and reached 5%. Sixteen @entity1 with the Nakata index greater than 200 mm2/m2 and Z-score greater than -4 survived after a complete repair. One of 4 @entity1 with Nakata index less than 200 mm2/m2 and Z-score less than -4 died after surgery. CONCLUSIONS: Majority of @entity1 with tetralogy of Fallot and unilateral absence of the @entity358 require palliative intervention as a first step of surgical treatment. Nakata index greater than 200 mm2/m2 and Nakata index Z-score greater than -4 are criteria for a successful complete repair.

Surgical correction of tetralogy of Fallot with unilateral absence of XXXX .

@entity1 :: ('9606', 'Species') :: ['patients'] @entity358 :: ('MESH:D008171', 'Disease') :: ['pulmonary artery'] @entity1757 :: ('MESH:D006345', 'Disease') :: ['ventricular septal defect'] @entity4297 :: ('MESH:D006330', 'Disease') :: ['congenital heart defect']
@entity358 :: (MESH:D008171,Disease) :: ['pulmonary artery']
