INTRODUCTION: Pontine tegmental cap @entity1141 (PTCD) is a recently described @entity75 associated with @entity129 , most commonly congenital @entity1274 . The purpose of this study is to systematically characterize the cranial nerve and temporal bone findings in a cohort of @entity1 with this rare condition. METHODS: Sixteen @entity1 with PTCD and diagnostic quality imaging were retrospectively reviewed. All @entity1 had high-resolution MR of the brain and/or internal auditory canals, and seven @entity1 had additional high-resolution CT of the temporal bones. Studies were evaluated by two pediatric neuroradiologists for cranial nerve and @entity79 . RESULTS: Fifteen of 16 @entity1 (94  %) had duplication of one or both internal auditory canals. Of the 24 total duplicated internal auditory canals, all 24 (100  %) demonstrated @entity850 or @entity1146 of the vestibulocochlear nerve canal, as well as @entity4237 . Of the non-duplicated internal auditory canals, 63  % (5/8) were @entity38887 or stenotic. Thirty-eight percent (3/8) were associated with @entity4237 , and 38  % (3/8) demonstrated isolated @entity4237 . Twenty-five percent (2/8) demonstrated normal vestibulocochlear nerves, both in the same @entity1 . Fifteen of 16 @entity1 overall (94  %) demonstrated bilateral @entity4237 . Of the 32 total temporal bones, 4 (13  %) demonstrated @entity2103 . Seventy-nine percent (22/28) of facial nerves that were present demonstrated an aberrant origin or course. CONCLUSION: @entity1 with PTCD have highly characteristic temporal bone and cranial nerve findings on both CT and MR. Recognition of these findings is important for improved diagnosis of this @entity395 , particularly by CT.

Temporal bone and cranial nerve findings in pontine tegmental cap XXXX .

@entity1 :: ('9606', 'Species') :: ['children', 'Patients', 'patients', 'patient'] @entity129 :: ('MESH:D003389', 'Disease') :: ['multiple cranial neuropathies'] @entity395 :: ('MESH:D035583', 'Disease') :: ['rare disorder'] @entity75 :: ('MESH:D001927', 'Disease') :: ['brain malformation'] @entity2103 :: ('MESH:D005155', 'Disease') :: ['facial nerve aplasia'] @entity79 :: ('MESH:D001847', 'Disease') :: ['temporal bone anomalies'] @entity4237 :: ('MESH:D000160', 'Disease') :: ['absent vestibulocochlear nerve', 'ipsilateral vestibulocochlear nerve aplasia', 'cochlear nerve aplasia'] @entity1274 :: ('MESH:D006319', 'Disease') :: ['sensorineural hearing loss'] @entity1146 :: ('MESH:D018633', 'Disease') :: ['atresia'] @entity850 :: ('MESH:D003251', 'Disease') :: ['stenosis'] @entity38887 :: ('MESH:C567865', 'Disease') :: ['atretic'] @entity1141 :: ('MESH:C535662', 'Disease') :: ['dysplasia']
@entity1141 :: (MESH:C535662,Disease) :: ['dysplasia']
