OBJECTIVE: To evaluate @entity1 presenting with Tetralogy of @entity215 with @entity338 to a tertiary care hospital and their surgical management. METHODS: The retrospective study was conducted at Congenital Cardiac Services, Aga Khan University Hospital, Karachi, Pakistan, and comprised data of Tetralogy of @entity215 @entity1 between April 2007 and June 2012. Data was analysed together with follow-up echocardiography. Variables assessed included demographics, imaging, operative technique, complications, post-operative recovery and follow-up echocardiography. SPSS 17 was used for statistical analysis. RESULTS: Of the 204 @entity1 , 6 (3%) had undergone surgical correction for Tetralogy of @entity215 with @entity338 . All 6(100%) @entity1 underwent complete repair. Median age for surgery was 8.5 years (range: 0.5-29 years). Of the different surgical strategies used, Contegra and Bioprosthetic valve placement had satisfactory outcome with minimal gradient at Right Ventricular Outflow Tract, good ventricular function and mild @entity340 . One (16.6%) @entity1 with Trans Annular Patch developed post-operative Right Ventricle Outflow Tract gradient of 80mmHg with moderate @entity338 . One (16.6%) @entity1 with monocusp valve developed free @entity338 at 6 months. The other 4(66.6%) @entity1 are currently free from any complications or re-intervention. CONCLUSIONS: Early surgery is preferred in symptomatic @entity1 . The repair depends upon achieving integrity of pulmonary circulation which is best achieved by using right ventricle to pulmonary artery conduit or inserting a pulmonary valve.

Tetralogy of XXXX with @entity338 ; appropriate surgical strategies.

@entity1 :: ('9606', 'Species') :: ['patients', 'patient'] @entity215 :: ('MESH:D013771', 'Disease') :: ['Fallot'] @entity338 :: ('MESH:D011665', 'Disease') :: ['pulmonary regurgitation', 'absent pulmonary valve syndrome'] @entity340 :: ('MESH:D006349', 'Disease') :: ['valvular regurgitation']
@entity215 :: (MESH:D013771,Disease) :: ['Fallot']
