BACKGROUND: @entity4888 ( @entity4888 ) is a rare variant of @entity3217 fungoides with clinical peculiarities, refractoriness to conventional treatments, and worse prognosis when compared to classic @entity3217 fungoides. OBJECTIVE: To evaluate the clinical and epidemiological characteristics of @entity4888 @entity1 in a single center in Brazil. METHODS: Data were retrospectively collected from @entity1 with @entity4888 who attended the @entity706 Clinic, University of S  o Paulo Medical School, between 1987 and 2013. RESULTS: Thirty-three @entity1 were included (median age 46 years old at diagnosis; 20 male; 27 white). The median disease duration before diagnosis was 3 years. Regarding stage at diagnosis, 61% had advanced stage disease (>= IIb). Follicular papules were reported in 66% and alopecia in 59% of the cases. The most involved regions were limbs, followed by trunk and head. @entity111 was present in 81% of the @entity1 . The median time of @entity1 ' follow-up was 38 months. At the last follow-up visit, 67% of the @entity1 were alive with active disease, 27% deceased, and 6% were in complete remission. Four @entity1 had large cell transformation. At the time of diagnosis, 25% of the @entity1 showed @entity1712 . LIMITATIONS: Retrospective study with partial unavailable data. CONCLUSIONS: The characteristics of our @entity1 with @entity4888 correlated with aspects previously described in the literature, which were at a more advanced stage at diagnosis and had a less favorable outcome. @entity111 is a very common complaint. Large cell transformation should be monitored as it is implicated in poor prognosis.

XXXX : clinical and epidemiological evaluation in a single center in Brazil.

@entity4888 :: ('MESH:D009182', 'Disease') :: ['Folliculotropic mycosis fungoides', 'FMF'] @entity1 :: ('9606', 'Species') :: ['patients'] @entity1712 :: ('MESH:D004802', 'Disease') :: ['eosinophilia'] @entity706 :: ('MESH:D008223', 'Disease') :: ['Cutaneous Lymphoma'] @entity3217 :: ('MESH:D015821', 'Disease') :: ['mycosis'] @entity111 :: ('MESH:D011537', 'Disease') :: ['Pruritus']
@entity4888 :: (MESH:D009182,Disease) :: ['Folliculotropic mycosis fungoides']
