PURPOSE: To report the clinical features and surgical management of @entity82 using the type I Boston Keratoprosthesis (KPro). DESIGN: Interventional case series. METHODS: Retrospective chart review of 9 eyes in 9 @entity1 with @entity6716 that developed @entity82 . RESULTS: All @entity1 had clinical diagnosis of @entity6716 . Previously, all @entity1 had undergone @entity231 surgery with posterior chamber intraocular lens (IOL) implantation and 7 @entity1 had existing tube shunts. In all cases, @entity82 presented as progressive retrocorneal and retrolenticular membrane formation causing displacement of the @entity2790 . Two eyes had tractional folds in the retina with posterior extension of the membrane. The management included IOL explantation in 7 of 9 cases, @entity82 with pars plana vitrectomy in all 9 @entity1 , and implantation of a type I Boston KPro in all eyes. At a mean final follow-up of 26.1 months (range 6 to 48 months), vision remained improved in all @entity1 . No @entity1 had recurrence of the fibrotic membrane after KPro implantation. CONCLUSION: This study represents another case series describing @entity82 and the largest study to report utilization of the type I Boston KPro in such @entity1 . As the @entity82 can cause @entity2790 , @entity2687 , @entity8814 , and @entity1713 , monitoring for @entity82 in @entity6716 with early surgical intervention is recommended. Type I Boston KPro may be considered in the surgical treatment of this condition.

Surgical and visual outcomes of the type I Boston Keratoprosthesis for the management of XXXX in @entity6716 .

@entity1 :: ('9606', 'Species') :: ['patients', 'patient'] @entity82 :: ('MESH:D005355', 'Disease') :: ['removal of fibrosis', 'fibrosis', 'aniridic fibrosis syndrome'] @entity231 :: ('MESH:D002386', 'Disease') :: ['cataract'] @entity1713 :: ('MESH:D012163', 'Disease') :: ['retinal detachment'] @entity6716 :: ('MESH:D015783', 'Disease') :: ['congenital aniridia'] @entity8814 :: ('MESH:D015814', 'Disease') :: ['hypotony'] @entity2790 :: ('MESH:D009798', 'Disease') :: ['IOL and secondary corneal decompensation', 'IOL dislocation'] @entity2687 :: ('MESH:D003316', 'Disease') :: ['corneal decompensation']
@entity82 :: (MESH:D005355,Disease) :: ['aniridic fibrosis syndrome']
