BACKGROUND: @entity19865 is so named because Kikuchi and Fujimoto were the first scientists to describe it in Japan in 1972. Although the disease has been reported from all over the world and more so from Asia, it is rare. To date only eight cases have been reported from Nepal. @entity3799 , @entity221 and raised Erythrocyte Sedimentation Rate are usual presenting features of this disease. We describe a case which presented with @entity882 and @entity3329 in addition to the usual features. Out of the total eight cases that have been reported from Nepal so far, no @entity1 had @entity882 and only one @entity1 had @entity3329 . CASE PRESENTATION: A 24-year-old Nepali female presented with a 3-week history of low-grade @entity221 , @entity10 , and @entity158 , discrete, unilateral left-sided cervical and @entity3329 . Among the multitude of tests that were carried out, Erythrocyte Sedimentation Rate was raised and there was @entity882 while other tests were normal. Painful @entity3329 pointed to bacterial @entity3298 while chronic low-grade @entity221 suggested @entity378 . A cervical lymph node was excised for histopathological examination to reach an accurate diagnosis. On the basis of pathognomonic features viz., paracortical foci composed of various types of histiocytes including crescentic type in the background of abundant apoptotic karyorrhectic debris, a diagnosis of @entity19865 was made. On follow-up evaluation after 6  weeks, the @entity1 had no systemic symptoms, enlarged lymph nodes had regressed in size significantly, and Erythrocyte Sedimentation Rate and platelet count had become normal. CONCLUSION: @entity19865 should be kept in the differential diagnosis of @entity3329 in young @entity1 , female or male even in @entity378 -endemic countries and even in @entity1 who have unusual features; for example @entity882 and involvement of axillary lymph nodes in addition to cervical lymph nodes as in this case.

An uncommon presentation of XXXX : a case report with literature review.

@entity1 :: ('9606', 'Species') :: ['patients', 'patient'] @entity3329 :: ('MESH:D008206', 'Disease') :: ['lymphadenopathy', 'axillary lymphadenopathy'] @entity882 :: ('MESH:D013921', 'Disease') :: ['thrombocytopenia'] @entity3298 :: ('MESH:D008199', 'Disease') :: ['lymphadenitis'] @entity3799 :: ('MESH:D002575', 'Disease') :: ['Cervical lymphadenopathy'] @entity158 :: ('MESH:D010146', 'Disease') :: ['painful'] @entity19865 :: ('MESH:D020042', 'Disease') :: ['Kikuchi-Fujimoto disease'] @entity10 :: ('MESH:D006261', 'Disease') :: ['headache'] @entity378 :: ('MESH:D014376', 'Disease') :: ['tuberculosis'] @entity221 :: ('MESH:D005334', 'Disease') :: ['fever']
@entity19865 :: (MESH:D020042,Disease) :: ['Kikuchi Fujimoto disease']
