To evaluate the long-term results of atriopulmonary Fontan connection, we reviewed the outcome of 20 consecutive @entity1 (single ventricle 8, double outlet right ventricle 8, @entity1145 3, mitral @entity1146 1; mean age, 13 +/- 11) who underwent this operation between 1981 and 1997 at our institution. Glenn shunt preceded Fontan operation in 1 @entity1 . Four @entity1 had a concomitant bidirectional Glenn anastomosis at the time of the Fontan operation. Follow-up was 100% complete, and total cumulative follow-up of all @entity1 was 241 @entity1 -years (maximum, 20 years). Three hospital deaths and 5 late deaths were observed, resulting in 58 +/- 11% of cumulative survival at 20 years after the operation. @entity944 probably due to @entity943 was the major cause of the late death, and occurred in 3 @entity1 . Reoperation was required in 5 @entity1 (2%/ @entity1 -year) at 1 to 17 years postoperatively. Re-closure of an atrioventricular valve was performed for failure of the valve closure in 3 @entity1 at 1 to 6 years postoperatively. Reconstruction of the stenotic @entity2597 ( @entity2597 ) was concomitantly required in 2 of the 3 @entity1 . Pacemaker implantation was required for @entity1168 with @entity955 in 1 @entity1 at 17 years. One @entity1 with @entity956 developed intraright @entity715 at 12 years after the initial Fontan operation, and this @entity1 underwent conversion to extracardiac conduit cavopulmonary connection with right atrial maze procedure. @entity4710 are most common complications, and occurred in 12 @entity1 (5.0%/ @entity1 -year), resulting in 40 +/- 13% of the cumulative free rate at 15 years after the operation. Thus, failure of the @entity340 and stenosis of @entity2597 were important early to intermediate complications after the atriopulmonary Fontan connection. On the other hand, @entity4710 were inevitable, and were most common late complications leading to intra-right @entity715 , which was successfully resolved by conversion of the conventional atriopulmonary Fontan anastomosis to extracardiac conduit cavopulmonary connection.

[Long-term results of XXXX for complex cardiac anomalies].

@entity1 :: ('9606', 'Species') :: ['patients', 'patient'] @entity4710 :: ('MESH:D013617', 'Disease') :: ['Atrial tachyarrhythmias', 'atrial tachyarrhythmias'] @entity2597 :: ('MESH:D003240', 'Disease') :: ['APC', 'atriopulmonary connection'] @entity944 :: ('MESH:D003645', 'Disease') :: ['Sudden death'] @entity1145 :: ('MESH:D018785', 'Disease') :: ['tricuspid atresia'] @entity956 :: ('MESH:D001282', 'Disease') :: ['atrial flutter'] @entity955 :: ('MESH:D001281', 'Disease') :: ['atrial fibrillation'] @entity1146 :: ('MESH:D018633', 'Disease') :: ['atresia'] @entity715 :: ('MESH:D013927', 'Disease') :: ['atrial thrombosis'] @entity340 :: ('MESH:D006349', 'Disease') :: ['atrioventricular valve closure'] @entity943 :: ('MESH:D001145', 'Disease') :: ['arrhythmias'] @entity1168 :: ('MESH:D001919', 'Disease') :: ['bradycardia']
@entity2597 :: (MESH:D003240,Disease) :: ['atriopulmonary fontan connection']
