PURPOSE: @entity1636 ( @entity1636 ) is a rare @entity5 in @entity1 with important distinctions from the @entity66 . We reviewed the National Cancer Data Base (NCDB) to determine factors associated with long-term survival. METHODS: The NCDB was queried for @entity1 less than 18years of age who were diagnosed with @entity1636 between 1998 and 2011. Kaplan-Meier analysis was utilized to determine factors significantly associated with overall survival. RESULTS: A total of 111 @entity1 were included (median age: 4years, 69% female). @entity1636 was more common in the youngest cohort, with 48% of cases occurring in @entity1 younger than the age of 3. Median @entity5 size was 9.5cm (IQR: 6.5-13.0), and 87% of @entity1 underwent some form of surgical resection. Among @entity1 with available data, 19 of 62 presented with @entity3 . Overall 1- and 3-year survival was 70% and 64%, respectively. Age, @entity5 size, extension of @entity5 into surrounding tissue, and @entity3 were all found to be significantly associated with survival. Among @entity1 who underwent a surgical procedure, margin status was also found to be significantly associated with survival. CONCLUSION: Age, @entity5 size, extension of @entity5 , @entity3 , and margin status are significantly associated with long-term survival in @entity1 with @entity1636 .

Factors associated with survival in pediatric XXXX : An analysis of the National Cancer Data Base (NCDB).

@entity1 :: ('9606', 'Species') :: ['children', 'patients'] @entity66 :: ('MESH:D004194', 'Disease') :: ['adult disease'] @entity5 :: ('MESH:D009369', 'Disease') :: ['tumor'] @entity1636 :: ('MESH:D018268', 'Disease') :: ['Adrenocortical carcinoma', 'ACC', 'adrenocortical carcinoma'] @entity3 :: ('MESH:D009362', 'Disease') :: ['metastases', 'metastatic disease']
@entity1636 :: (MESH:D018268,Disease) :: ['adrenocortical carcinoma']
