INTRODUCTION: @entity5043 ( @entity5043 ) and en coup de sabre (ECS) are variants of morphea. Although numerous findings on central nervous system (CNS) imaging of @entity5043 and ECS have been reported, the spectrum and frequency of CNS imaging findings and relation to cutaneous and @entity16 have not been fully characterized. METHODS: We retrospectively reviewed @entity1 younger than 50  years at our institution over a 16-year interval who had clinical diagnosis of @entity5043 and ECS by a skin or facial subspecialist. Two neuroradiologists evaluated available imaging and characterized CNS imaging findings. RESULTS: Eighty-eight @entity1 with @entity5043 or ECS were identified (62 @entity1 [70.4  %]; mean age 28.8  years). Of the 43 @entity1 with CNS imaging, 19 (44  %) had abnormal findings. The only finding in 1 of these 19 @entity1 was lateral ventricle asymmetry; of the other 18, findings were bilateral in 11 (61  %), ipsilateral to the side of facial involvement in 6 (33  %), and contralateral in 1 (6  %). Sixteen @entity1 had serial imaging examinations over an average of 632  days; 13 (81  %) had stable imaging findings, and 3 (19  %) had change over time. Of six @entity1 with progressive cutaneous findings, five (83  %) had stable imaging findings over time. Among the 23 @entity1 with clinical neurologic abnormality and imaging, 12 (52  %) had abnormal imaging findings. All seven @entity1 with @entity410 (100  %) had abnormal imaging studies. CONCLUSIONS: In @entity5043 and ECS, imaging findings often are bilateral and often do not progress, regardless of cutaneous disease activity. Findings are inconsistently associated with clinical abnormalities.

CNS imaging findings associated with XXXX and en coup de sabre: correlation to dermatologic and @entity16 .

@entity1 :: ('9606', 'Species') :: ['women', 'patients'] @entity16 :: ('MESH:D009422', 'Disease') :: ['neurologic abnormalities'] @entity410 :: ('MESH:D012640', 'Disease') :: ['seizures'] @entity5043 :: ('MESH:D005150', 'Disease') :: ['PRS', 'Parry-Romberg syndrome']
@entity5043 :: (MESH:D005150,Disease) :: ['Parry-Romberg syndrome']
