INTRODUCTION: Accessory breast tissue is a very rare finding in the general population with an incidence of one to two percent. An even rarer occurrence is accessory mammary-like tissue which developed @entity0 . The authors present a case of aggressive and @entity189 of vulvar originating from mammary-like tissue. CASE: A 73-year-old Caucasian female presented with a lesion in her left vulva. The lesion was ulcerated and fragile. A dermatologist had evaluated the lesion and took a punch biopsy. Result was @entity189 . She was admitted to the gynecologic oncology clinic then after and was operated. After a radical vulvectomy and bilateral inguinal lymphadenectomy she received adjuvant radiotherapy because of lymph node @entity3 . One year after the finish of radiotherapy @entity1 was found to have lung and femur @entity3 . She began to receive systemic chemotherapy for @entity3 . CONCLUSION: Primary mammary-like @entity420 is exceedingly rare. There is no consensus about the diagnosis, treatment, and follow up of these @entity1 in literature. However, given that histological data confirms these @entity5 are behaving like @entity0 instead of known patterns of @entity5 , the best treatment practices for @entity0 may be applied to treat these @entity189 @entity1 .

An unusual case of mammary gland-like XXXX : case report and review of literature.

@entity1 :: ('9606', 'Species') :: ['patients', 'patient'] @entity0 :: ('MESH:D001943', 'Disease') :: ['breast carcinoma', 'breast cancers', 'breast cancer'] @entity5 :: ('MESH:D009369', 'Disease') :: ['vulva cancer', 'cancers'] @entity189 :: ('MESH:D002277', 'Disease') :: ['vulvar carcinoma', 'metastatic carcinoma'] @entity3 :: ('MESH:D009362', 'Disease') :: ['metastasis'] @entity420 :: ('MESH:D000230', 'Disease') :: ['adenocarcinoma of the vulva']
@entity189 :: (MESH:D002277,Disease) :: ['carcinoma of vulva']
