OBJECTIVE: To investigate the clinical cause, treatments and prognosis of @entity14361 in @entity12390 ( @entity12390 ). METHODS: Thirteen @entity1 of @entity12390 with @entity14361 were review retrospectively. RESULTS: From 1983 to 1998, 20 @entity1 with @entity12390 were managed in this hospital. Of them, 13 (65%) involving the laryngotracheobronchial region were observed. Respiratory tract lesions might be diffuse or localized and occurred in larynx (46%), @entity825 (69%) and bronchus (69%). @entity288 , immunosuppressive agents and @entity3761 were used in these @entity1 . Tracheotomy was performed in 4 @entity1 with @entity1224 . Montgomery T-tube or self-expanding metal stent were used in 2 @entity1 with @entity8276 . Of 13 case, 2 died from @entity1576 . The 5-years survival rate was 78.6%. CONCLUSION: Respiratory tract involvement is the most severe manifestation of the @entity12390 and the main cause of @entity204 despite aggressive medical therapy or tracheotomy.

[Laryngotracheobronchial involvement in XXXX ].

@entity1 :: ('9606', 'Species') :: ['patients'] @entity825 :: ('MESH:D055090', 'Disease') :: ['trachea'] @entity3761 :: ('MESH:D003622', 'Chemical') :: ['dapsone'] @entity12390 :: ('MESH:D011081', 'Disease') :: ['relapsing polychondritis', 'RP'] @entity14361 :: ('MESH:C566895', 'Disease') :: ['laryngotracheobronchial involvement'] @entity1576 :: ('MESH:D012131', 'Disease') :: ['respiratory complications'] @entity8276 :: ('MESH:D014133', 'Disease') :: ['tracheal collapse'] @entity204 :: ('MESH:D003643', 'Disease') :: ['death'] @entity1224 :: ('MESH:D000402', 'Disease') :: ['airway obstruction'] @entity288 :: ('MESH:D000305', 'Chemical') :: ['Corticosteroids']
@entity12390 :: (MESH:D011081,Disease) :: ['relapsing polychondritis']
