BACKGROUND: @entity5409 develop after hepatic portoenterostomy in some @entity1 with @entity2876 and have been regarded as an indication of poor prognosis; however, there is confusion about the terminology and concepts of the lesions. We investigated whether the @entity5409 constituted a single entity. @entity1 AND METHODS: From 1980 to 2005, we encountered 80 @entity1 with @entity2876 . Abdominal ultrasonography disclosed intrahepatic @entity5409 in 20 (25%) @entity1 after hepatic portoenterostomy. The @entity5409 were analyzed morphologically with radiologic imaging studies and histologically in 13 @entity1 who underwent liver transplantation. RESULTS: Fifteen @entity1 had solitary simple @entity5409 , and 5 @entity1 had multiple continuous oval or beaded lesions. @entity75 had a fibrotic cyst wall and lacked epithelia. Continuous lesions had a cyst wall covered with biliary epithelia. Thirteen @entity1 with solitary cysts died or required liver transplantation. In 2 @entity1 with continuous lesions, surgical reboring of the porta hepatis could eliminate @entity5409 and @entity1087 . CONCLUSIONS: @entity5409 include 2 different conditions. @entity2001 are @entity6112 , which should be referred to as a bile lake, and are associated with poor prognosis. Continuous beaded cysts are dilated bile ducts, which may be reversed. This distinction is important when considering the treatment strategy.

Intrahepatic cystic lesions after hepatic portoenterostomy for XXXX with bile lake and dilated bile ducts.

@entity1 :: ('9606', 'Species') :: ['patients', 'PATIENTS'] @entity5409 :: ('MESH:D052177', 'Disease') :: ['Intrahepatic cystic lesions', 'cystic lesions'] @entity1087 :: ('MESH:D007565', 'Disease') :: ['jaundice'] @entity6112 :: ('MESH:D016055', 'Disease') :: ['retention pseudocysts'] @entity75 :: ('MESH:D001927', 'Disease') :: ['Solitary lesions'] @entity2001 :: ('MESH:D001845', 'Disease') :: ['Solitary cysts'] @entity2876 :: ('MESH:D001656', 'Disease') :: ['biliary atresia']
@entity2876 :: (MESH:D001656,Disease) :: ['biliary atresia']
