INTRODUCTION: @entity6017 , belonging to the group of the idiopathic inflammatory @entity121 , is characterized by bimodal pattern of age-specific incidence of rates, with peaks in age group from 5 to 14 years ( @entity8817 ) and in age group from 45 to 64 years ( @entity6017 ). THE AIM OF THIS STUDY: Is to evaluate the clinical characteristics of 12 @entity1 with @entity8817 followed by the 3rd Department of Internal Medicine, University of Debrecen and the 2nd Department of Pediatrics, Semmelweis University, Budapest. METHODS: The authors analyzed the medical records of the @entity1 with juvenile and adult form of @entity6017 retrospectively. RESULTS: All of the @entity1 had symmetrical weakness of the proximal muscles. The most frequent cutaneous features were facial erythema and Gottron papules (11/12). The extramuscular manifestations were also assessed. 7 @entity1 had @entity4841 . There were observed @entity3794 , @entity2407 , @entity1282 and @entity10632 in the same @entity1 , whose disease is overlapped with progressive @entity785 . In view of the clinical course, the authors found that prevalence of polycyclic (relapsing-remitting) and monophasic subtypes of the disease were similar (6/12 and 5/12). Finally, all of the @entity1 achieved remission, however, 2 @entity1 have to take low-dose @entity228 therapy permanently to maintain remission. One @entity1 's cutaneous symptoms proved to be persistent and in further 2 cases, regression of the @entity730 is slow, but continuous. DISCUSSION: The authors compare their data of juvenile @entity1 with the data of the relevant literature and to their experience with the management of adult @entity3918 @entity1 . It seems to be reasonable to treat the @entity1 in centres.

[Clinical characteristics of XXXX ].

@entity1 :: ('9606', 'Species') :: ['children', 'patients', 'patient'] @entity6017 :: ('MESH:D003882', 'Disease') :: ['Dermatomyositis', 'dermatomyositis', 'adult dermatomyositis'] @entity3918 :: ('MESH:D009223', 'Disease') :: ['DM'] @entity3794 :: ('MESH:D011658', 'Disease') :: ['pulmonary fibrosis'] @entity2407 :: ('MESH:D011928', 'Disease') :: ['Raynaud-syndrome'] @entity228 :: ('CHEBI:50858', 'Chemical') :: ['corticosteroid'] @entity8817 :: ('MESH:C538250', 'Disease') :: ['juvenile dermatomyositis'] @entity730 :: ('MESH:D002114', 'Disease') :: ['calcinosis'] @entity1282 :: ('MESH:D003680', 'Disease') :: ['dysphagia'] @entity4841 :: ('MESH:D018771', 'Disease') :: ['arthralgia'] @entity10632 :: ('MESH:D012859', 'Disease') :: ['sicca-syndrome'] @entity121 :: ('MESH:D009135', 'Disease') :: ['myopathies'] @entity785 :: ('MESH:D012595', 'Disease') :: ['systemic sclerosis']
@entity8817 :: (MESH:C538250,Disease) :: ['juvenile dermatomyositis']
