We report two cases with complete form of @entity473 (CAVCD) accompanied by @entity1467 whose pulmonary vascular resistance (Rp) were more than 10 Wood unit.m2 at the age of less than 6 months. One @entity1 was 3-month-old @entity1 whose Rp was 12 Wood unit.m2. The open lung biopsy at 3 months old showed histopathological change of Heath-Edwards grade I. He underwent intracardiac repair at the age of 4 months. He is doing well at 30 months of postoperative period. Another @entity1 was 5-month-old @entity1 whose Rp was 15.5 Wood unit.m2. Histopathological change of lung at 5 months old demonstrated Heath-Edwards grade III. She underwent intracardiac repair at the age of 7 months, 2 months after lung biopsy. However, she died of @entity120 7 days after surgery. The postmortem examination revealed that @entity3885 progressed during 2 months interval between the lung biopsy and the operation. In conclusion, cardiac catheterization with estimation of Rp should be performed in the cases of CAVCD, especially in those with @entity1467 , in early infancy. If Rp is more than 10 Wood unit.m2 and lung biopsy indicates the surgical indication, surgical intervention should be done as soon as possible since the @entity3885 may progress in a short period.

[Two cases of complete XXXX whose pulmonary vascular resistance were over 10 wood unit.m2 before 6 months of age].

@entity1 :: ('9606', 'Species') :: ['girl', 'boy', 'child'] @entity473 :: ('MESH:C563240', 'Disease') :: ['atrioventricular canal defect'] @entity120 :: ('MESH:D006976', 'Disease') :: ['oversystemic pulmonary hypertension and low output syndrome'] @entity3885 :: ('MESH:D008173', 'Disease') :: ['pulmonary vascular obstructive disease'] @entity1467 :: ('MESH:D004314', 'Disease') :: ["Down's syndrome"]
@entity473 :: (MESH:C563240,Disease) :: ['atrioventricular canal defect']
