The objective of the study was to explore clinical, electroencephalography (EEG), neuropsychological features and prognosis of @entity3148 ( @entity3148 ). Of 327 @entity1 aged between 1 and 9 years with a diagnosis of @entity6191 followed between 2000 and 2008, 18 (5.5%) had @entity3148 . Male significantly predominated (88.9%). Age at onset ranged from 2.3 to 4.9 years (mean 3.6 years). Median follow-up period was 6.3 years. In addition to @entity410 @entity1 had @entity410 (66.7%), drop attacks (72.2%), head drops (77.8%) absences (88.9%), tonic-clonic generalized @entity410 (77.8%), tonic @entity410 (38.9%), @entity159 (16.7%). Seven @entity1 (38.9%) had an @entity302 . At onset, @entity302 and @entity73 were recorded, respectively, in 100% and 77.8% of @entity1 . EEG @entity2402 in all @entity1 within 4 years since the onset. At long-term follow-up, two @entity1 developed focal abnormalities typical of @entity1654 and two @entity1 photosensitivity. On neuropsychological testing 66.7% of @entity1 had a normal IQ (mean 81.2  17.0, range 47-105, median 84.5) after a mean period of 4.4 years since the last @entity410 . Sixteen out of 18 @entity1 remitted within 3.5 years since the onset and in two @entity1 tonic @entity410 persisted. @entity3148 is generalized childhood @entity302 : although cognitive functions might deteriorate, outcome is good regarding @entity410 .

XXXX : an age-dependent @entity302 with favorable @entity410 outcome but variable cognitive evolution.

@entity1 :: ('9606', 'Species') :: ['children', 'patients'] @entity410 :: ('MESH:D012640', 'Disease') :: ['seizure', 'seizures', 'myoclonic seizures', 'myoclonic-astatic seizures'] @entity2402 :: ('MESH:D010015', 'Disease') :: ['abnormalities disappeared'] @entity73 :: ('MESH:D003072', 'Disease') :: ['slow abnormalities'] @entity1654 :: ('MESH:D019305', 'Disease') :: ['rolandic epilepsy'] @entity302 :: ('MESH:D004827', 'Disease') :: ['epileptic encephalopathy', 'epilepsy', 'interictal epileptiform'] @entity6191 :: ('MESH:D004829', 'Disease') :: ['generalized epilepsy'] @entity3148 :: ('MESH:D004831', 'Disease') :: ['myoclonic-astatic epilepsy', 'MAE'] @entity159 :: ('MESH:D013226', 'Disease') :: ['non-convulsive status epilepticus']
@entity3148 :: (MESH:D004831,Disease) :: ['Myoclonic astatic epilepsy']
