BACKGROUND: @entity600 ( @entity600 ) are rare benign congenital @entity5 appearing mainly in the head and neck with a considerably variable outcome. A need exists to validate a staging system, taking into account the prognosis of the @entity600 , including preoperative and @entity260 , long-term sequelae, and persistence of the disease to improve parental counseling and evaluate the outcome of a surgical treatment of such @entity5 . METHODS: Twenty-two @entity1 treated for @entity600 were selected from a series of 129 @entity1 operated on for @entity600 of the head and neck between 1986 and 1997 at St-Luc University Hospital, Brussels, Belgium. Their charts were reviewed retrospectively, with a special focus on the anatomic location of the lesions and all the complications reported. According to de Serres et al, @entity600 up to now have been divided into six possible categories according to their unilateral or bilateral infrahyoid and/or suprahyoid locations. RESULTS: Stage I (unilateral infrahyoid): nine @entity1 , 11% of complications (without mediastinal extension: 0%, with mediastinal extension: 50%); stage II (unilateral suprahyoid): three @entity1 , 33% of complications; stage III (unilateral suprahyoid and infrahyoid): eight @entity1 , 75% of complications; stage V (bilateral suprahyoid and infrahyoid): two @entity1 , 100% of complications. None of the @entity1 was initially seen with stage IV (bilateral suprahyoid) or stage VI (bilateral infrahyoid) @entity600 . Overall complications, preoperative complications, postoperative com- plications, and long-term morbidity showed a significant in- crease from stage I to V (p <.01, p =.002, p =.02, and p =.03, respectively). CONCLUSIONS: A staging system of cervicofacial @entity600 based on the anatomic location can be reliably used for prognostic purposes, allowing a more accurate assessment of the global risk of complications and determination of surgical outcome. Mediastinal extension in stage I @entity1 seems to be associated with a higher rate of complications. Such information can be used to inform parents more appropriately regarding the management and long-term prognosis of their @entity1 's @entity600 .

XXXX of the head and neck: a retrospective review and a support for staging.

@entity5 :: ('MESH:D009369', 'Disease') :: ['tumors'] @entity1 :: ('9606', 'Species') :: ['children', 'patients'] @entity260 :: ('MESH:D011183', 'Disease') :: ['postoperative complications'] @entity600 :: ('MESH:D000014', 'Disease') :: ['congenital malformations', 'LM', 'Lymphatic malformations', 'malformation']
@entity600 :: (MESH:D000014,Disease) :: ['Lymphatic malformations']
