PURPOSE: We strove to characterize the clinicopathologic features of a rare @entity5 involving the urogenital system. MATERIALS AND METHODS: Of 109 reported cases of @entity2269 , 25 have involved organs ordinarily evaluated and treated by urologists. Experience based on these cases plus 2 from our files forms the basis of this review. RESULTS: The term @entity2269 has been applied to a rare, highly malignant @entity5 that occurs most often in the abdominal cavity and is described in the nonurological literature. This @entity5 has distinctive histological, immunohistochemical and ultrastructural features. Several reports suggest a @entity74 . All reported @entity1 who have @entity5 involving the genitourinary structures have been treated with chemotherapy, but prognosis has been poor. CONCLUSIONS: The literature on @entity2269 indicates that a significant percentage of these rare @entity5 involve genitourinary organs. In most cases, @entity5 have been unresectable surgically and treatment has been multidrug chemotherapy. Response to treatment has been poor, with only 3 of 25 determinate cases free of disease when reported.

Urogenital involvement by XXXX .

@entity5 :: ('MESH:D009369', 'Disease') :: ['tumors', 'cancer', 'malignancies', 'malignant tumor', 'neoplasm'] @entity1 :: ('9606', 'Species') :: ['patients'] @entity74 :: ('MESH:D030342', 'Disease') :: ['characteristic genetic abnormality'] @entity2269 :: ('MESH:D058405', 'Disease') :: ['desmoplastic small round-cell tumor']
@entity2269 :: (MESH:D058405,Disease) :: ['desmoplastic small round-cell tumor']
