@entity4018 ( @entity4018 ) usually affects older @entity1 and is associated with a median survival of 3.5-5 yr. Survival of @entity4018 @entity1 55 yr old or younger is longer, but there is no information on the youngest subset. The presenting features, evolution and survival were analyzed in 9 @entity1 with @entity4018 aged 30 yr or less, representing 2.8% of two series including 323 cases. Age ranged from 17 to 30 yr; 3 @entity1 were males and 6 females. Five @entity1 were asymptomatic and none had constitutional symptoms. @entity417 was observed in 4 @entity1 , being severe in only one. The WBC count was normal in 7 @entity1 and 2 had mild @entity491 ; moderate @entity1148 was observed in 7 @entity1 . No @entity1 showed blood blast cells or bone marrow @entity2008 . With a median follow-up of 6.8 (range 0.8-28) yr, 2 @entity1 died 10.7 and 9.9 yr from diagnosis, one from complications of bone marrow transplantation performed after progression of the disease and the other from @entity360 secondary to portal @entity101 . Among remaining @entity1 , one developed @entity3181 , another was lost to follow-up at 3 yr, and 5 remain asymptomatic and currently without treatment (one had been splenectomized at diagnosis). These results indicate that in most young adults with @entity4018 the disease presents without adverse prognostic factors and may remain stable for years, which may be of interest when considering the treatment of such @entity1 .

XXXX in adult individuals 30 years old or younger: presenting features, evolution and survival.

@entity1 :: ('9606', 'Species') :: ['patients', 'patient', 'people'] @entity1148 :: ('MESH:D013922', 'Disease') :: ['thrombocytosis'] @entity417 :: ('MESH:D000740', 'Disease') :: ['Anemia'] @entity101 :: ('MESH:D006973', 'Disease') :: ['hypertension'] @entity4018 :: ('MESH:D055728', 'Disease') :: ['Myelofibrosis with myeloid metaplasia', 'MMM'] @entity3181 :: ('MESH:D006502', 'Disease') :: ['Budd-Chiari syndrome'] @entity2008 :: ('MESH:D002869', 'Disease') :: ['cytogenetic abnormalities'] @entity360 :: ('MESH:D006471', 'Disease') :: ['gastrointestinal bleeding'] @entity491 :: ('MESH:D007964', 'Disease') :: ['leukocytosis']
@entity4018 :: (MESH:D055728,Disease) :: ['Myelofibrosis with myeloid metaplasia']
