@entity2846 ( @entity2846 ) and @entity189 (CPCs) are rare @entity5 that affect mostly @entity1 . Due to their rarity, their epidemiology and outcomes are incompletely understood. The National @entity5 Institute's Surveillance, Epidemiology and End Results (SEER) Program is a well-established population-based group of registries that collects and publishes @entity5 incidence and survival data representing approximately 28  % of the US population. SEER-STAT v8.1.2 was used to identify @entity1 with ICD-O-3 codes for @entity5683 in @entity1 aged 0-19. Demographics, initial treatment, and follow-up data were collected. Statistical methods including Kaplan-Meier curves, log rank tests, and Cox proportional hazards regression were used to estimate associations between independent variables and survival. The SEER registries contained 107 @entity2846 (2004-2010) and 95 CPCs (1978-2010). Median follow-up was 38 and 40  months, respectively. More than 75  % of CPCs were diagnosed before the age of 5  years, versus 48  % for @entity2846 . Sixty-five percent of CPCs and 57  % of @entity2846 occurred in males. In both groups at least 90  % of @entity1 underwent surgical resection. Gross total resection (GTR) was achieved in 67.0  % of CPCs and 63.6  % of @entity2846 . Almost 17  % of CPCs were treated with radiation versus only 0.9  % of @entity2846 . More than 98  % of @entity1 with CPP were alive at the last follow-up, versus 62  % of @entity2846 @entity1 . For @entity2846 , surgery was significantly associated with increased overall survival, but contrary to previous reports, extent of surgical resection was not associated with survival. Age, sex, race, and radiation treatment also had no effect on survival. This report, using the SEER datasets, corroborates many findings of previous smaller studies on CPTs. @entity2846 occurs in younger @entity1 , with a male predominance, and a much worse prognosis than CPP. As such, these @entity5 have been treated aggressively with high rates of GTR and radiation treatment. Despite these treatments, overall survival for @entity2846 remains poor.

Pediatric XXXX : epidemiology, treatments, and outcome analysis on 202 @entity1 from the SEER database.

@entity1 :: ('9606', 'Species') :: ['children', 'patients'] @entity5683 :: ('MESH:D016545', 'Disease') :: ['choroid plexus tumors'] @entity5 :: ('MESH:D009369', 'Disease') :: ['cancer', 'Cancer', 'neoplasms', 'tumors'] @entity189 :: ('MESH:D002277', 'Disease') :: ['carcinomas'] @entity2846 :: ('MESH:D020288', 'Disease') :: ['Choroid plexus papillomas', 'CPPs', 'CPC']
@entity5683 :: (MESH:D016545,Disease) :: ['choroid plexus tumors']
