UNASSIGNED: We present our experience with seven cases of epithelioid @entity980 ( @entity980 ) to further characterise its clinicopathological features. There were five males and two females with ages ranging from 19 to 84 years (mean 56 years). Four @entity5 occurred in the somatic soft tissue, two in organs and one in the bone. The mean @entity5 size was 10.7cm (range 3.5-15cm). Histologically, six @entity5 were characterised by sheet-like growth of uniform epithelioid cells with large vesicular nuclei, prominent nucleoli, high mitotic activity and moderate to abundant amphophilic-to-eosinophilic cytoplasm. One @entity5 was composed of dyscohesive cells with rhabdoid appearance embedded in a myxoid matrix. Features suggestive of rhabdomyoblastic differentiation were absent. However, immunohistochemical study revealed skeletal muscle differentiation in all cases. Of note, focal expression of epithelial markers with co-expression of neuroendocrine markers was noted in five and three cases, respectively. Of six @entity1 with follow-up, one experienced local recurrence and three developed @entity3 . To date, three @entity1 have died of disease within 14 months. This study further demonstrates that epithelioid @entity980 represents a distinct variant of @entity980 with an @entity146 . It may be misdiagnosed as poorly differentiated @entity3270 due to co-expression of epithelial and neuroendocrine markers.

Epithelioid XXXX : a clinicopathological study of seven additional cases supporting a distinctive variant with aggressive biological behaviour.

@entity1 :: ('9606', 'Species') :: ['patients'] @entity146 :: ('MESH:D001523', 'Disease') :: ['aggressive behaviour'] @entity5 :: ('MESH:D009369', 'Disease') :: ['tumours', 'tumour'] @entity3 :: ('MESH:D009362', 'Disease') :: ['metastases'] @entity980 :: ('MESH:D012208', 'Disease') :: ['RMS', 'rhabdomyosarcoma'] @entity3270 :: ('MESH:D018278', 'Disease') :: ['neuroendocrine carcinoma']
@entity980 :: (MESH:D012208,Disease) :: ['rhabdomyosarcoma']
