PURPOSE: To evaluate the disease-free and overall survival of pediatric @entity1 with nonrhabdomyosarcoma soft-tissue @entity242 . METHODS: We retrospectively analyzed the records of 67 pediatric @entity1 with a diagnosis of @entity242 treated with curative intent between 1970 and 1992. Median follow-up time for the 52 survivors was 120 months (range, 7 to 277 months). Fifty-nine @entity1 received external beam radiotherapy, in a median dose of 5400 cGy (range, 1800 to 6660 cGy.) All @entity1 underwent an initial surgical procedure. Eighteen @entity1 had gross @entity66 , and 15 had gross total excision with microscopic @entity66 or positive margins. Adjuvant chemotherapy was administered to 44 @entity1 (65%). RESULTS: The actuarial 10-year freedom from progression or recurrence and overall survival rates were 76% and 75%, and the 20-year rates were the same. Of 18 @entity1 with gross @entity66 , 9 (50%) had local progression and 6 died of @entity66 . By contrast, only one @entity1 with microscopic @entity66 who received postoperative radiotherapy had a local recurrence. The disease-free survival rate also correlated with histologic grade. CONCLUSIONS: As with adult soft tissue @entity242 , gross @entity66 predicts @entity177 . Our results suggest that pediatric @entity1 with soft tissue @entity242 treated with surgery and postoperative radiotherapy generally have a favorable overall survival rate.

XXXX : a 20-year experience.

@entity1 :: ('9606', 'Species') :: ['patients', 'patient'] @entity177 :: ('MESH:D051437', 'Disease') :: ['local failure'] @entity66 :: ('MESH:D004194', 'Disease') :: ['residual disease', 'local-only disease'] @entity242 :: ('MESH:D012509', 'Disease') :: ['sarcomas', 'nonrhabdomyosarcoma soft tissue sarcoma']
@entity242 :: (MESH:D012509,Disease) :: ['Childhood soft tissue sarcoma']
