UNASSIGNED: @entity3986 is an @entity74 of unknown aetiology; it is a @entity209 primarily affecting proximal muscle groups leading to progressive @entity3986 . It later spreads to the muscles of the pelvic floor and lower extremities. The estimated incidence is 1:200,000. This paper describe a case of pregnancy and delivery in @entity1 with progressive @entity33921 . Cesarean section was performed due to progression of the underlying disease. First postoperative day DIC occure and surgical revision of abdominal cavity was performed. Although the uterine suture was strong, @entity548 was present. Blood was not coagulating. Supravaginal amputation of the uterus was performed including left-sided adnexectomy due to bleeding from the left ovarium. Due to the severity of the condition and assumed necessity of long-term controlled ventilation, the @entity1 was transferred to the intensive medicine department. She was dismissed home after 91 days of hospitalisation. Gravidity in advanced @entity3986 is rare and associated with a high risk. Due to @entity425 , @entity425 , @entity194 of individual muscle groups, spine deformities and often dislocation of thoracic organs, these @entity1 cannot avoid the caesarean section to end their pregnancy, followed by prolonged intubation and controlled ventilation. During pregnancy, the growing uterus elevates the diaphragm and impairs breathing. Therefore, pregnancies in such @entity1 will probably always have to be ended prematurely.

Pregnancy and delivery in XXXX . Case Report.

@entity1 :: ('9606', 'Species') :: ['woman', 'patients', 'patient'] @entity548 :: ('MESH:D006470', 'Disease') :: ['diffuse bleeding'] @entity3986 :: ('MESH:D009136', 'Disease') :: ['Leyden-M  bius muscular dystrophy', 'muscular dystrophy'] @entity425 :: ('MESH:D018908', 'Disease') :: ['diaphragm weakness', 'muscle weakness'] @entity33921 :: ('MESH:C535895', 'Disease') :: ['Leyden-Moebius muscular dystrophy'] @entity194 :: ('MESH:D001284', 'Disease') :: ['atrophy'] @entity74 :: ('MESH:D030342', 'Disease') :: ['autosomal recessive hereditary disease'] @entity209 :: ('MESH:D008659', 'Disease') :: ['congenital disorder of protein metabolism']
@entity3986 :: (MESH:D009136,Disease) :: ['Leyden-M  bius muscular dystrophy']
