OBJECTIVE: To investigate the location, staging, clinical symptoms, imaging features, and surgical treatment of the @entity7854 of @entity2172 (CCME). METHOD: This was a retrospective review of 20 CCME cases. RESULT: Of 20 cases with CCME, 2 cases were classified as Postic stage I, 0 as stage II, 13 as stage III, 5 as stage IV. Conductive @entity393 was the most common clinical symptom. The mean preoperative PTA was 54.1 dB, and the mean ABG was 41.7 dB. One case underwent a modified mastoidectomy and a second-stage ossicular reconstruction; 2 cases experienced a radical mastoidectomy without ossicular reconsturction for extensive @entity3540 ; 5 cases underwent modified mastoidectomy and a one-stage tympanoplasty, with one case diagnosed as @entity600 of ossicular chain (stapes hypoplasia); other 12 cases underwent a one-stage tympanoplasty. The @entity3540 localized to the posterior-epitympanum or mesotympanum in all @entity1 , mainly located in the incudostapedial joint. The mean postoperative PTA from 16 cases was 35.3 dB, and A-B gap was 20.2 dB. All @entity1 were followed-up for at least 1 year after operation and recurrence was found in 2 cases. Three cases were accompanied with @entity600 of ossicular chain. CONCLUSION: CCME is a rare entity and diagnosis is usually delayed in clinical practice due to the silent nature of disease in its early stage. The prognosis of CCME mainly depended on the stage of the lesions.

[Congenital XXXX of @entity2172 : 20 @entity1 ' clinical symptoms and imaging features].

@entity1 :: ('9606', 'Species') :: ['patients'] @entity2172 :: ('MESH:D010033', 'Disease') :: ['middle ear'] @entity600 :: ('MESH:D000014', 'Disease') :: ['congenital malformation'] @entity3540 :: ('MESH:D002781', 'Disease') :: ['cholesteatoma'] @entity393 :: ('MESH:D034381', 'Disease') :: ['hearing loss'] @entity7854 :: ('MESH:C562858', 'Disease') :: ['congenital cholesteatoma']
@entity3540 :: (MESH:D002781,Disease) :: ['cholesteatoma']
