passages.id: split_6_test_1537_passage
passages.type: progene_text
passages.text: About 90 % of patients with congenital nephrogenic diabetes insipidus are males with the X - linked recessive form of the disease ( OMIM 304800 ) who have mutations in the arginine vasopressin receptor 2 gene ( AVPR2 ) , which codes for the vasopressin V2 receptor .