have been diagnosed with Pulmonary langerhans Histiocytosis X. 63 y/o white male and have been told my only hope for the future is a lung transplant. My PFT shows 26% lung capacity and my carbon dioxide/oxygen exchange last year was 51%, this year 41%. My doctor expects a continuing degradation and under pressure admitted that I have probably 4 years left. Should I obtain a second opinion? What are my chances of obtaining a lung transplant? Should I even bother to pursue this option?

Summarized question: What is pulmonary langerhans histiocytosis?