Samantha912/NLP_A2_WTH huggingface dataset:
Denys–Drash syndrome (DDS) or Drash syndrome is a rare disorder or syndrome characterized by gonadal dysgenesis, nephropathy, and Wilms' tumor.

Signs and symptoms

Clinically, Denys–Drash is characterized by the triad of pseudohermaphroditism, mesangial renal sclerosis, and Wilms' tumor. The condition first manifests as early nephrotic syndrome and progresses to mesangial renal sclerosis, and ultimately kidney failure—usually within the first three years of life.

Males with Denys-Drash syndrome exhibit gonadal dysgenesis and undescended testes. Females with Denys-Drash syndrome typically have normal genitalia.

The presenting characteristics of DDS include loss of playfulness, decreased appetite, weight loss, growth delay, abnormal skeletal development, insomnia, abdominal pain, constipation, and anuria.

Causes

The cause of DDS is most commonly (96% of patients) an abnormality in the WT1 gene (Wilms tumor suppressor gene). These abnormalities include changes in certain exons (9 and 8) and mutations in some alleles of the WT1 gene. Genetically, the syndrome is due to mutations in the Wilms tumor suppressor gene, WT1, which is on chromosome 11 (11p13). These mutations are usually found in exons 8 or 9, but at least one has been reported in exon 4.

The condition can be inherited in an autosomal dominant pattern, but most cases occur due to new genetic mutations in people with no family history of the disorder.

Mechanism

Prognosis 
A 1994 review of 150 cases reported in the literature found that 38% had died with a mean age of death of 2 years. 32% were still alive at the time of the report with a mean age of 4.65. No data were available for the remainder. The author described living with DDS as "walking a multidimensional tight rope".

History 
P. Denys and Allan L. Drash first described the syndrome.

See also
 Beckwith–Wiedemann syndrome
 WAGR syndrome
 Wilms' tumor

References

External links 
 

Transcription factor deficiencies
Rare diseases
Syndromes affecting the kidneys
Syndromes with tumors
Intersex variations
Danielli may refer to:

People 
 Given name
 Danielli Yuri-Barbosa (born 1984), judoka from Brazil

 Surname
 Donatella Danielli (born 1966), professor of mathematics
 James Frederic Danielli FRS (1911–1984), English biologist
 Maurizio Danielli (born 1949), Italian rower
 Simon Danielli (born 1979), English retired rugby union player

Other uses 
 Danielli Furton, human rare genetic disorder formed by Macrosomia, Obesity, Macrocephaly and Ocular abnormalities
 Davson–Danielli model, a model of the plasma membrane of a cell, proposed in 1935 by Hugh Davson and James Danielli. 
 Equus quagga danielli,  a plains zebra that lived in South Africa until becoming extinct late in the 19th century
 Thaumatococcus daniellii, a plant species from Africa, known for being the natural source of thaumatin

See also 
 Daniel (disambiguation)
 Danieli (disambiguation)
is a 1987 Japanese film directed by Shunichi Kajima.

Awards and nominations
9th Yokohama Film Festival 
 Won: Best Director - Shunichi Kajima
 Won: Best Supporting Actress - Eri Ishida
 5th Best Film

References

1987 films
Films directed by Shunichi Kajima
1980s Japanese-language films
1980s Japanese films
Gary Neville Nelson (born 15 May 1952) is an Australian Anglican bishop who served as Bishop of North West Australia (the largest diocese in geographical size in the Anglican Church of Australia, covering approximately a quarter of the Australian continent) from 26 May 2012 to 15 May 2022.

Early life
He grew up in Western Sydney and trained as a teacher at Sydney University. He spent two years with his wife in Papua New Guinea as missionary teachers.

Ministry
He was assistant curate in Dapto and later rector of Panania. 

Nelson served as Director of External Studies at Moore Theological College from 2006 until his appointment as Bishop of North West Australia in 2012.

Nelson stated that in the event that same-sex marriage was legalised in Australia, if he believes that religious freedom is not adequately protected,  he will refuse to register any marriages.

Nelson retired from the role of bishop on 15 May 2022, on reaching the retirement age of 70 years.

References

1952 births
21st-century Anglican bishops in Australia
Moore Theological College alumni
Clergy from Sydney
University of Sydney alumni
Anglican bishops of North West Australia
Living people
Evangelical Anglican bishops
El Guerrara () (also written al-Qarārah or Guerara) is a town and commune, coextensive with El Guerrara District, in Ghardaïa Province, Algeria. According to the 2008 census it has a population of 59,514, up from 48,313 in 1998, with an annual growth rate of 2.1%.

Climate 

El Guerrara has a hot desert climate (Köppen climate classification BWh), with very hot summers and mild winters, and very little precipitation throughout the year.

Transportation 

El Guerrara is on the W33, a regional road between Berriane on the N1 to the west, and the N3 about halfway between Touggourt and Ouargla to the east.

Education 

40% of the population has a tertiary education (the equal highest in the province), and another 80% has completed secondary education. The overall literacy rate is 5%, and is 1% among males and 4% among females.

Localities 
The commune of El Guerrara is composed of three localities:

 Vieux Ksar de El Guerrara
 Quartiers périphériques
 Palmeraie et village socialiste agricole

References 

Neighbouring towns and cities

Communes of Ghardaïa Province
Ioannis Sioutis (alternate spelling: Giannis) (; born July 27, 1973) is a Greek retired professional basketball player and current assistant coach, most recently for AEK Athens of the Greek Basket League, under head coach Ilias Kantzouris. He has also previously worked as an assistant for Panathinaikos. At a height of 1.84 m (6 ft ½ in), he played at the point guard position during his active basketball career.

Professional career
Sioutis started his playing career with the youth team of Milon in 1986. In 1995, he transferred to Aris. In 1997, he won the Korać Cup, and in 1998, he won the Greek Cup, both while playing with Aris. In 1999, he played with Panionios and in 2000, he returned to Aris. In 2002, he won the EuroLeague 2001–02 championship while playing with Panathinaikos.

He also played with Irakleio, Peristeri, Ilysiakos, Dafni, and ICBS. In 2007, Sioutis won the Greek 2nd Division with Sporting, and he then transferred to AEK Athens.

National team career
Sioutis also played in 11 games with the Greek national basketball team.

External links 
FIBA Profile
FIBA Europe Profile
Hellenic Federation Profile 
Eurobasket.com Profile

Greek men's basketball players
Greek Basket League players
1973 births
Living people
AEK B.C. players
Aris B.C. players
Dafnis B.C. players
ICBS B.C. players
Ilysiakos B.C. players
Irakleio B.C. players
Milon B.C. players
Panathinaikos B.C. players
Panionios B.C. players
Peristeri B.C. players
Sporting basketball players
Point guards
Basketball players from Athens
Tarff Rovers Football Club are a defunct football club from Kirkcowan in Wigtownshire, Scotland.

One of Scotland's oldest clubs, they were formed in 1874 and were full members of both the Scottish Football Association and the Southern Counties Football Association. Having full SFA status entitled Rovers to compete in the Scottish Qualifying Cup South competition and, on occasion, play in the Scottish Cup proper.

The club's finest hour came in 1969 when they faced Scottish League side Alloa Athletic in the Scottish Cup. This home tie saw Tarff triumph by one goal to nil. Despite belonging to a remote and sparsely populated part of Scotland – indeed Kirkcowan's current population is less than 400 – Tarff enjoyed certain periods of success.

During their final few years of the club's existence, a local businessman's financial assistance led to several titles, cup wins, and big name signings, including Chic Charnley and Rowan Alexander.

The club folded in 2003 when local interest quickly dwindled to the point where a committee could not be formed. The club's home ground of  Balgreen Park still exists, and is currently used by local Sunday league side Kirkcowan Wanderers.

References

Defunct football clubs in Scotland
Association football clubs established in 1874
Association football clubs disestablished in 2003
1874 establishments in Scotland
2003 disestablishments in Scotland
South of Scotland Football League teams
Football clubs in Dumfries and Galloway
South Channel is a small channel in the United States located in Massachusetts Bay near Boston, Massachusetts. It runs alongside Devils Back and Aldridge Ledge from northeast of Ram Head to the western coast of Commissioners Ledge.

Channels of the United States
Leski may refer to:

People 
 Andreja Leški (born 1997), Slovenian judoka
 Janusz Łęski (born 1930), Polish film director and screenwriter
 Kazimierz Leski (1912–2000), Polish engineer and spy

Places 
 Leski, Vinica, North Macedonia
 Lesko County, Subcarpathian Voivodeship, Poland
|-
|Džajići
|Konjic
|Herzegovina-Neretva Canton
|-
|Džanići
|Konjic
|Herzegovina-Neretva Canton
|-
|Džepi
|Konjic
|Herzegovina-Neretva Canton
|-
|Džindići
|Goražde
|Bosnian Podrinje Canton
|-
|Džuha
|Goražde
|Bosnian Podrinje Canton
|}

Lists of settlements in the Federation of Bosnia and Herzegovina (A-Ž)
Ole Laurits Olsen Søndergaard (24 May 1876 – 10 November 1958) was a Danish landscape painter. He also decorated a number of Danish churches with paintings and frescos.

Biography
Born in Allerslev near Lejre in northwestern Zealand, Søndergaard studied painting at the Royal Danish Academy of Fine Arts from 1898 to 1900. He completed his education at Kunstnernes Frie Studieskoler under Kristian Zahrtmann in 1902.

Søndergaard was a versatile artist, remembered for his portraits and landscapes of the countryside around Roskilde. His paintings reveal his association with his friend L.A. Ring, especially his winter scenes with stooping figures shovelling snow. For his Roskilde Fjord ved Marbæk, he received the Eckersberg Medal in 1945. Other notable works are Kirken og smedjen i Jystrup and Snekasten, Jystrup, both painted in the early 1930s.

Another important aspect of Søndergaard's work was church decoration. On assignments for the National Museum of Denmark, he participated in the restoration of frescos in the churches of Lyngby, Ballerup, Måløv, Vallensved and Vallensbæk, as well as the cathedrals of Aarhus and Roskilde. He also decorated a number of Danish churches including the Church of Our Saviour, Esbjerg, (1929), St John's, Vejle, (1934), Jerslev Church (1944), and the apse vault of Sct Nikolai Church in Holbæk (1930).

Awards
In 1945, Søndergaard was awarded the Eckersberg Medal and, in 1952, the Thorvaldsen Medal.

References

1876 births
1958 deaths
20th-century Danish painters
Danish landscape painters
People from Lejre Municipality
Recipients of the Thorvaldsen Medal
Recipients of the Eckersberg Medal
Royal Danish Academy of Fine Arts alumni
Julián Besteiro  is a station on Line 12 of the Madrid Metro, located next to the Civic Center Julián Besteiro in Leganés, which is named for the socialist politician Julián Besteiro (1870–1940). It is located in fare Zone B1.

References 

Line 12 (Madrid Metro) stations
Buildings and structures in Leganés
Railway stations in Spain opened in 2003
Esther Morgan McCullough (1888 – June 14, 1957) was an American novelist and anthologist.

Biography
Esther Morgan Park McCullough was born in North Bennington, Vermont, to Eliza Hall (Park) McCullough and John G. McCullough, an attorney and future governor of Vermont. She and her siblings Hall, Eliza, and Ella were raised in their mother's family mansion, now known as the Park-McCullough Historic House.

McCullough wrote novels such as Archangel House (1935) and The Five Devils of Kilmainham (1955). The latter, which was about the effect of murder on families living on the fringes of Dublin in the 1880s, was praised by critics as a masterpiece of suspense. Her largest project was As I Pass, O Manhattan (1956), a 1200-page anthology of writing about life in New York from its earliest days that encompassed some 200 authors and ranged from poetry to biography. Hailed as a "magnificent tribute to a mighty city", this compendium of "literary New Yorkiana" is still being used by other writers.

Her unpublished biography of painter Harriet Blackstone is among the Harriet Blackstone Papers in the Smithsonian Institution.

McCullough was also a musician and served for a time as director of the Vermont Symphony Orchestra.

Personal life
Her longtime companion was the pianist Stell Andersen.

Publications
—And Forever (1935)
Archangel House (1939)
The Five Devils of Kilmainham (1955)
 As I Pass, O Manhattan: An Anthology of Life in New York (1956)

References

1888 births
1957 deaths
American women novelists
20th-century American novelists
20th-century American women writers
Novelists from Vermont
American historical novelists
Burials in Vermont
Les Valls de Valira is a municipality in the comarca of the Alt Urgell in Catalonia, that surrounds the south and south-west border of Andorra. It includes a small exclave to the south-east.

Landmarks
Sant Serni de Tavèrnoles

References

External links
 Government data pages 

Municipalities in Alt Urgell
George Robert Crawford (13 January 1926 – 7 August 2012) was an Australian politician.

He was born in Prahran and was an official with the Plumbers and Gasfitters Employees Union of Australia, serving more than twenty years as general secretary and Victorian branch secretary. He joined the Labor Party in 1944 and sat on the State Executive from 1960 to 1975 and in 1979. From 1965 to 1969 he was state vice-president, rising to president from 1969 to 1973 and from 1983 to 1985. In 1985 he was elected to the Victorian Legislative Council as a member for Jika Jika, serving until his retirement in 1992. Crawford died in 2012.

References

1926 births
2012 deaths
Australian socialists
Members of the Victorian Legislative Council
Australian Labor Party members of the Parliament of Victoria
Vato () (Spanish "guy") may refer to:

Geography
 Vätö, island in the Norrtälje archipelago
 Vätö Church medieval church in Vätö in Stockholm County, Sweden
 Port Vato village at the south coast of the island of Ambrym in Vanuatu

Entertainment
 "Vato" (song), a song by Snoop Dogg
 "Vato", a song by Dj Mustard (featuring YG, Jeezy and Que)
 "Vatos", an episode of The Walking Dead
 El Vato, a television series based on the life of Mexican singer El Dasa

Other
 Swamini Vato sayings of Gunatitanand Swami
 Vatos Locos, gangs

See also
 Cholo (subculture)
Emerson Point Preserve is a  preserve in Manatee County, Florida, located west of Palmetto and at the western end of Snead Island.

History 
The majority of Emerson Point was undeveloped until preliminary site plans were submitted to the County in the early 1980s for an eight-story condo on a three-acre site at the tip of Emerson Point. Due to local opposition, the County suspended the condo project after considering to seek public acquisition of the land. The initial portion of what was then referred to as "Emerson Point Park” was acquired by the State in 1991, with approximately 195 acres acquired under the Conservation and Recreation Lands (CARL) program (exists today as the Florida Forever program) on October 23, 1991, under a 70% State, 30% County funding initiative.

Features 
The preserve is home to several Native American mounds in the Portavant Mound Site. The preserve also has an observation tower that provides views of Terra Ceia Bay, Tampa Bay, and the Sunshine Skyway Bridge.

References

Nature reserves in Florida
Geography of Manatee County, Florida
Protected areas of Manatee County, Florida
Landforms of Manatee County, Florida
1991 establishments in Florida
The arbelas (plural arbelai) was a type of ancient Roman gladiator. The word is a hapax legomenon, occurring only in the Oneirocritica of Artemidorus, a Greek work on dream interpretation that discusses the symbolism of various gladiator types. It may be related to the Greek word arbelos (ἄρβηλος), a cobbler's semicircular blade used to cut leather similar to an ulu. 

A few reliefs show gladiators armed with a curved blade fighting each other; it has been argued that these (possibly also fighting retiarii, the net-fighters) are arbelai; however, they have also been seen as the scissores who likewise may have been matched against retiarii. 

Artemidorus lists the arbelas among gladiators who might appear in dreams advising a man about what sort of woman he is to marry. Both the dimachaerus, who fought with two curved blades, and the "so-called" arbelas signify that the woman will either be a poisoner, malicious, or ugly.

See also 
 List of Roman gladiator types

References

Gladiator types
Gladiatorial combat
"Heaven Is a Halfpipe" (also known as "Heaven Is a Halfpipe (If I Die)") is the debut single of American rock band OPM. It was included on their debut studio album, Menace to Sobriety (2000), and was released on June 27, 2000.

The song peaked at number 18 on the US Billboard Modern Rock Tracks chart and was a top-40 hit in several other nations, including the United Kingdom, where it reached number four on the UK Singles Chart. It was the 33rd-best-selling single of 2001 in the UK, earning a gold certification from the British Phonographic Industry (BPI) for sales and streams of over 400,000. The song was re-recorded in 2012 for the Heaven Can Wait EP.

Content

"Heaven Is a Halfpipe" is about a man who loves skateboarding, getting high and being free. He imagines Heaven being like a half-pipe, where he does not have to worry about the police ruining his good time ("'Cause right now on Earth I can't do jack / without the man upon my back"). The trick skills of professional skateboarders Christian Hosoi and Mike McGill are mentioned during the bridge ("Like Christian Hosoi way back in '87" / "We'll be busting Christ airs until we get to heaven" / "With all your rules, you gots to chill" / "I'm gonna twist out like Mike McGill" / "I'm gonna twist out cos I got the skills''").

Music video
The music video features OPM doing skateboarding tricks on a large half-pipe and flying around. At the end of the video, they perform to a crowd. One man in the audience also wears a white T-shirt that says "FREE CHRISTIAN HOSOI", in reference to Hosoi's arrest in January 2000 for attempting to transport nearly 1.5 lb of crystal methamphetamine from Los Angeles to Honolulu.

Track listings
UK CD and cassette single; Australian CD single
 "Heaven Is a Halfpipe" (album version) – 4:18
 "Space People" – 3:45
 "Group Therapy" – 2:21

German CD single
 "Heaven Is a Halfpipe" (clean album version) – 4:18
 "Space People" – 3:45

Charts

Weekly charts

Year-end charts

Certifications

Release history

References

2000 debut singles
2000 songs
Atlantic Records singles
Music videos directed by David Slade
OPM (band) songs
Songs about death
Songs about drugs
Ville Koski (born 27 January 2002) is a Finnish professional footballer who plays for Veikkausliiga club Honka.

Club career 
After playing in Kakkonen for three seasons with PKKU and Honka II, he made his Veikkausliiga debut on 12 Sep 2020 for Honka, when he came in from the bench for the final minutes, in 1–3 away victory against RoPS.

Career statistics

References 

Living people
2002 births
Finnish men's footballers
Men's association football defenders
Finland men's youth international footballers
Finland men's under-21 international footballers
Finland men's international footballers
Kakkonen players
FC Honka players
Veikkausliiga players
Peter McCabe (born Peter Henry McCabe; 7 November 1945 – April 1998) was an English author and music journalist, who wrote in a variety of genres. He was an editor at Rolling Stone and Oui magazine, and is the former editor-in-chief of Country Music magazine and a nationally syndicated country music columnist.

McCabe wrote an article in the 28 February 1972 issue of New York magazine in which he alleged financial impropriety on the part of Allen Klein, manager of the Beatles' Apple Corps organisation, with regard to the dispersal of funds raised through US sales of George Harrison's The Concert for Bangladesh live album. The funds were intended for distribution to Bangladeshi refugees via UNICEF yet, according to McCabe, Klein's ABKCO company had withheld an amount of $1.14 per album. Klein responded with a $150 million libel suit, which he later withdrew.

Later in 1972, McCabe's book Apple to the Core: The Unmaking of the Beatles, with co-writer Robert D. Schonfeld, was published by Pocket Books. The book focuses on the business problems that led to the group's break-up and again presented Klein in an unfavourable light. It was subsequently translated into Japanese as ビートルズの不思議な旅 /
Bītoruzu no fushigina tabi, and into Dutch as "Apple" tot op het klokhuis; Wat er met de Beatles gebeurde.

In 1984, he and Schonfeld co-authored a work containing interviews with John Lennon, titled John Lennon: For the Record. McCabe also wrote the 1975 book Honkytonk Heroes: A photo album of country music. His most widely known work, with 600 copies in US libraries, is Bad News at Black Rock: The Sell-out of CBS News (1987). He has also written several novels, including Cities of Lies (1993) and Wasteland (1994).

References

1945 births
Living people
Rolling Stone people
American magazine editors
American male non-fiction writers
"When It's Springtime in Alaska (It's Forty Below)" is a 1959 single by Johnny Horton, written by Tillman Franks and released through Columbia Records. The single was Johnny Horton's sixth release on the country chart and the first of three number ones on the country chart.  The single spent twenty-three weeks on the chart. The song was a marginally successful crossover, reaching #85 on the Music Vendor Pop Top 100.

The song takes place in Fairbanks, Alaska in the springtime. The narrator/singer is a prospector making a trip to Fairbanks after two years in the wilderness; he decides to visit a saloon and hears "redheaded Lil" singing the title words. He and Lil spend the evening dancing, but the singer is unaware that Lil is "Big Ed's wife-to-be." Big Ed discovers the two dancing and throws his knife at the singer, who predicts that he will not survive his wound: "When it's springtime in Alaska, I'll be six feet below." 

The lyrics say the temperature outside is . While it is very rare for the temperature to actually be that low in the springtime in Fairbanks, it has happened. A low temperature of  was recorded at the Fairbanks International Airport on March 30, 1970. The coldest time of the year in Fairbanks is around January 13 of each year, with night-time low temperatures at this time averaging around  and daytime high temperatures averaging around . The coldest-ever low temperature recorded there was , on December 28 and 29, 1961.  A temperature of  was recorded in Fairbanks on January 14, 1934.

References

1959 singles
Johnny Horton songs
Columbia Records singles
1959 songs
Murder ballads
Songs about Alaska
Song articles with missing songwriters