ICD-10 Chapter II: Neoplasms; Chapter III: Diseases of the blood and blood-forming organs, and certain disorders involving the immune mechanism

# C00-D48 - Neoplasms

## (C00-C14) Malignant neoplasms, lip, oral cavity and pharynx
- (C00) Malignant neoplasm of lip
- (C01) Malignant neoplasm of base of tongue
- (C02) Malignant neoplasm of other and unspecified parts of tongue
- (C03) Malignant neoplasm of gum
- (C04) Malignant neoplasm of floor of mouth
- (C05) Malignant neoplasm of palate
- (C06) Malignant neoplasm of other and unspecified parts of mouth
- (C07) Malignant neoplasm of parotid gland
- (C08) Malignant neoplasm of other and unspecified major salivary glands
- (C09) Malignant neoplasm of tonsil
- (C10) Malignant neoplasm of oropharynx
- (C11) Malignant neoplasm of nasopharynx
- (C12) Malignant neoplasm of piriform sinus
- (C13) Malignant neoplasm of hypopharynx
- (C14) Malignant neoplasm of other and ill-defined sites in the lip, oral cavity and pharynx

## (C15-C26) Malignant neoplasms, digestive organs
- (C15) Malignant neoplasm of Esophagus
- (C16) Malignant neoplasm of Stomach
(C16.0) Cardia
(C16.1) Fundus of stomach
(C16.2) Body of stomach
(C16.3) Pyloric antrum
(C16.4) Pylorus
(C16.5) Lesser curvature of stomach, unspecified
(C16.6) Greater curvature of stomach, unspecified
(C16.8) Overlapping lesion of stomach
(C16.9) Stomach, unspecified
- (C16.0) Cardia
- (C16.1) Fundus of stomach
- (C16.2) Body of stomach
- (C16.3) Pyloric antrum
- (C16.4) Pylorus
- (C16.5) Lesser curvature of stomach, unspecified
- (C16.6) Greater curvature of stomach, unspecified
- (C16.8) Overlapping lesion of stomach
- (C16.9) Stomach, unspecified
- (C17) Malignant neoplasms of small intestine
(C17.0) Duodenum
(C17.1) Jejunum
(C17.2) Ileum
(C17.3) Meckel's diverticulum
(C17.8) Overlapping lesion of small intestine
(C17.9) Small intestine, unspecified
- (C17.0) Duodenum
- (C17.1) Jejunum
- (C17.2) Ileum
- (C17.3) Meckel's diverticulum
- (C17.8) Overlapping lesion of small intestine
- (C17.9) Small intestine, unspecified
- (C18) Malignant neoplasm of colon
- (C19) Malignant neoplasm of rectosigmoid junction
- (C20) Malignant neoplasm of rectum
- (C21) Malignant neoplasms of anus and anal canal
- (C22) Malignant neoplasms of liver and intrahepatic bile ducts
(C22.0) Liver cell carcinoma
(C22.1) Intrahepatic bile duct carcinoma
(C22.2) Hepatoblastoma
(C22.3) Angiosarcoma of liver
(C22.4) Other sarcomas of liver
(C22.7) Other specified carcinomas of liver
(C22.9) Liver, unspecified
- (C22.0) Liver cell carcinoma
- (C22.1) Intrahepatic bile duct carcinoma
- (C22.2) Hepatoblastoma
- (C22.3) Angiosarcoma of liver
- (C22.4) Other sarcomas of liver
- (C22.7) Other specified carcinomas of liver
- (C22.9) Liver, unspecified
- (C23) Malignant neoplasm of gallbladder
- (C24) Malignant neoplasm of other and unspecified parts of biliary tract
- (C25) Malignant neoplasm of pancreas
(C25.0) Head of pancreas
(C25.1) Body of pancreas
(C25.2) Tail of pancreas
(C25.3) Pancreatic duct
(C25.4) Endocrine pancreas
(C25.7) Other parts of pancreas
(C25.8) Overlapping lesion of pancreas
(C25.9) Pancreas, unspecified
- (C25.0) Head of pancreas
- (C25.1) Body of pancreas
- (C25.2) Tail of pancreas
- (C25.3) Pancreatic duct
- (C25.4) Endocrine pancreas
- (C25.7) Other parts of pancreas
- (C25.8) Overlapping lesion of pancreas
- (C25.9) Pancreas, unspecified
- (C26) Malignant neoplasms of other and ill-defined Digestive Organs

## (C30-C39) Malignant neoplasms, respiratory system and intrathoracic organs
- (C30) Malignant neoplasm of nasal cavity and middle ear
- (C31) Malignant neoplasm of accessory sinuses
- (C32) Malignant neoplasm of larynx
- (C33) Malignant neoplasm of trachea
- (C34) Malignant neoplasm of bronchus and lung
(C34.0) Main bronchus
(C34.1) Upper lobe, bronchus or lung
Pancoast tumor
(C34.2) Middle lobe, bronchus or lung
(C34.3) Lower lobe, bronchus or lung
(C34.8) Overlapping lesion of bronchus and lung
- (C34.0) Main bronchus
- (C34.1) Upper lobe, bronchus or lung
Pancoast tumor
- Pancoast tumor
- (C34.2) Middle lobe, bronchus or lung
- (C34.3) Lower lobe, bronchus or lung
- (C34.8) Overlapping lesion of bronchus and lung
- (C37) Malignant neoplasm of thymus
- (C38) Malignant neoplasm of heart, mediastinum and pleura
- (C39) Malignant neoplasms of other and ill-defined sites in respiratory system and intrathoracic organs

## (C40-C41) Malignant neoplasms, bone and articular cartilage
- (C40) Malignant neoplasm of bone and articular cartilage of limbs
- (C41) Malignant neoplasm of bone and articular cartilage of other and unspecified sites

## (C43-C44) Malignant neoplasms, skin
- (C43) Malignant melanoma of Skin
- (C44) Other malignant neoplasms of skin

## (C45-C49) Malignant neoplasms, connective and soft tissue
- (C45) Malignant neoplasm of Mesothelioma
- (C46) Malignant neoplasm of Kaposi's Sarcoma
- (C47) Malignant neoplasm of peripheral nerves and autonomic nervous system
- (C48) Malignant neoplasm of retroperitoneum and peritoneum
- (C49) Malignant neoplasm of other connective and soft tissue
C49.M10 Malignant fibrous histiocytoma
C49.M12 Atypical fibroxanthoma
C49.M20 Haemangiopericytoma
C49.M22 Angioendotheliomatosis, malignant
C49.M24 Dermatofibrosarcoma protruberans
C49.M30 Bednar tumour
C49.M40 Sarcoma of skin
C49.M42 Fibrosarcoma
C49.M44 Schwannoma, malignant
C49.M48 Leiomyosarcoma
C49.M50 Rhabdomyosarcoma
C49.M54 Myxofibrosarcoma
C49.M60 Angiosarcoma, cutaneous
C49.M70 Lymphangiosarcoma
- C49.M10 Malignant fibrous histiocytoma
- C49.M12 Atypical fibroxanthoma
- C49.M20 Haemangiopericytoma
- C49.M22 Angioendotheliomatosis, malignant
- C49.M24 Dermatofibrosarcoma protruberans
- C49.M30 Bednar tumour
- C49.M40 Sarcoma of skin
- C49.M42 Fibrosarcoma
- C49.M44 Schwannoma, malignant
- C49.M48 Leiomyosarcoma
- C49.M50 Rhabdomyosarcoma
- C49.M54 Myxofibrosarcoma
- C49.M60 Angiosarcoma, cutaneous
- C49.M70 Lymphangiosarcoma
(Alphanumeric subcodes are ILDS.)

## (C50-C58) Malignant neoplasms, breast and female genital organs
- (C50) Malignant neoplasm of breast
- (C51) Malignant neoplasm of vulva
- (C52) Malignant neoplasm of vagina
- (C53) Malignant neoplasm of cervix uteri
- (C54) Malignant neoplasm of corpus uteri
(C54.1) Endometrial cancer
- (C54.1) Endometrial cancer
- (C55) Malignant neoplasm of uterus, part unspecified
- (C56) Malignant neoplasm of ovary
- (C57) Malignant neoplasms of other and unspecified female and genital organs
- (C58) Malignant neoplasm of placenta
Choriocarcinoma NOS
Chorionepithelioma NOS
- Choriocarcinoma NOS
- Chorionepithelioma NOS

## (C60-C63) Malignant neoplasms, male genital organs
- (C60) Malignant neoplasm of penis
- (C61) Malignant neoplasm of prostate
- (C62) Malignant neoplasm of testis
- (C63) Malignant neoplasm of other and unspecified male genital organs

## (C64-C68) Malignant neoplasms, urinary organs
- (C64) Malignant neoplasm of kidney, except renal pelvis
Wilms' tumor
- Wilms' tumor
- (C65) Malignant neoplasm of renal pelvis
- (C66) Malignant neoplasm of ureter
- (C67) Malignant neoplasm of bladder
- (C68) Malignant neoplasm of other and unspecified urinary organs

## (C69-C72) Malignant neoplasms, nervous system
- (C69) Malignant neoplasms of eye and adnexa
(C69.0) Conjunctiva
(C69.1) Cornea
(C69.2) Retina
Retinoblastoma
(C69.3) Choroid
(C69.4) Ciliary body
(C69.5) Lacrimal gland and duct
(C69.6) Orbit
(C69.7) Overlapping lesion of eye and adnexa
- (C69.0) Conjunctiva
- (C69.1) Cornea
- (C69.2) Retina
Retinoblastoma
- Retinoblastoma
- (C69.3) Choroid
- (C69.4) Ciliary body
- (C69.5) Lacrimal gland and duct
- (C69.6) Orbit
- (C69.7) Overlapping lesion of eye and adnexa
- (C70) Malignant neoplasm of meninges
(C70.0) Cerebral meninges
(C70.1) Spinal meninges
- (C70.0) Cerebral meninges
- (C70.1) Spinal meninges
- (C71) Malignant neoplasm of brain
(C71.0) Cerebrum, except lobes and ventricles
(C71.1) Frontal lobe
(C71.2) Temporal lobe
(C71.3) Parietal lobe
(C71.4) Occipital lobe
(C71.5) Cerebral ventricle
(C71.6) Cerebellum
(C71.7) Brain stem
(C71.8) Overlapping lesion of brain
(C71.9) Brain, unspecified
- (C71.0) Cerebrum, except lobes and ventricles
- (C71.1) Frontal lobe
- (C71.2) Temporal lobe
- (C71.3) Parietal lobe
- (C71.4) Occipital lobe
- (C71.5) Cerebral ventricle
- (C71.6) Cerebellum
- (C71.7) Brain stem
- (C71.8) Overlapping lesion of brain
- (C71.9) Brain, unspecified
- (C72) Malignant neoplasm of spinal cord, cranial nerves and other parts of central nervous system
(C72.0) Spinal cord
(C72.1) Cauda equina
(C72.2) Olfactory nerve
(C72.3) Optic nerve
(C72.4) Acoustic nerve
(C72.5) Other and unspecified cranial nerves
(C72.8) Overlapping lesion of brain and other parts of central nervous system
(C72.9) Central nervous system, unspecified
- (C72.0) Spinal cord
- (C72.1) Cauda equina
- (C72.2) Olfactory nerve
- (C72.3) Optic nerve
- (C72.4) Acoustic nerve
- (C72.5) Other and unspecified cranial nerves
- (C72.8) Overlapping lesion of brain and other parts of central nervous system
- (C72.9) Central nervous system, unspecified

## (C73-C75) Malignant neoplasms, endocrine glands and related structures
- (C73) Malignant neoplasm of thyroid gland
- (C74) Malignant neoplasm of adrenal gland
(C74.0) Cortex of adrenal gland
(C74.1) Medulla of adrenal gland
Pheochromocytoma
(C74.9) Adrenal gland, unspecified
Neuroblastoma, NOS
- (C74.0) Cortex of adrenal gland
- (C74.1) Medulla of adrenal gland
Pheochromocytoma
- Pheochromocytoma
- (C74.9) Adrenal gland, unspecified
Neuroblastoma, NOS
- Neuroblastoma, NOS
- (C75) Malignant neoplasm of other endocrine glands and related structures

## (C76-C80) Malignant neoplasms, secondary and ill-defined
- (C76) Malignant neoplasm of other and ill-defined sites
(C76.0) Langerhans' cell histiocytosis, not elsewhere classified
(C76.1) Haemophagocytic lymphohistiocytosis
(C76.2) Haemophagocytic syndrome, infection-associated
(C76.3) Other histiocytosis syndromes
- (C76.0) Langerhans' cell histiocytosis, not elsewhere classified
- (C76.1) Haemophagocytic lymphohistiocytosis
- (C76.2) Haemophagocytic syndrome, infection-associated
- (C76.3) Other histiocytosis syndromes
- (C77) Secondary and unspecified malignant neoplasm of lymph nodes
- (C78) Secondary malignant neoplasm of respiratory and digestive organs
- (C79) Secondary malignant neoplasm of other sites
- (C80) Malignant neoplasm without specification of site

## (C81-C96) Malignant neoplasms, stated or presumed to be primary, of lymphoid, haematopoietic and related tissue
- (C81) Hodgkin's Disease
(C81.0) Lymphocytic predominance
(C81.1) Nodular sclerosis
(C81.2) Mixed cellularity
(C81.3) Lymphocytic depletion
- (C81.0) Lymphocytic predominance
- (C81.1) Nodular sclerosis
- (C81.2) Mixed cellularity
- (C81.3) Lymphocytic depletion
- (C82) Follicular non-Hodgkin's lymphoma (nodular)
(C82.0) Small cleaved cell, follicular
(C82.1) Mixed small cleaved and large cell, follicular
(C82.2) Large cell, follicular
- (C82.0) Small cleaved cell, follicular
- (C82.1) Mixed small cleaved and large cell, follicular
- (C82.2) Large cell, follicular
- (C83) Diffuse non-Hodgkin's lymphoma
(C83.0) Small cell (diffuse)
(C83.1) Small cleaved cell (diffuse)
(C83.2) Mixed small and large cell (diffuse)
(C83.3) Large cell (diffuse)
(C83.4) Immunoblastic (diffuse)
(C83.5) Lymphoblastic (diffuse)
(C83.6) Undifferentiated (diffuse)
(C83.7) Burkitt's tumour
- (C83.0) Small cell (diffuse)
- (C83.1) Small cleaved cell (diffuse)
- (C83.2) Mixed small and large cell (diffuse)
- (C83.3) Large cell (diffuse)
- (C83.4) Immunoblastic (diffuse)
- (C83.5) Lymphoblastic (diffuse)
- (C83.6) Undifferentiated (diffuse)
- (C83.7) Burkitt's tumour
- (C84) Peripheral and cutaneous T-cell lymphomas
(C84.0) Mycosis fungoides
(C84.1) Sezary's disease
(C84.2) T-zone lymphoma
(C84.3) Lymphoepithelioid lymphoma
(C84.4) Peripheral T-cell lymphoma
- (C84.0) Mycosis fungoides
- (C84.1) Sezary's disease
- (C84.2) T-zone lymphoma
- (C84.3) Lymphoepithelioid lymphoma
- (C84.4) Peripheral T-cell lymphoma
- (C85) Other and unspecified types of non-Hodgkin's lymphoma
(C85.0) Lymphosarcoma
(C85.1) B-cell lymphoma, unspecified
- (C85.0) Lymphosarcoma
- (C85.1) B-cell lymphoma, unspecified
- (C88) Malignant immunoproliferative diseases
(C88.0) Waldenstrom's macroglobulinaemia
(C88.1) Alpha heavy chain disease
(C88.2) Gamma heavy chain disease
(C88.3) Immunoproliferative small intestinal disease
- (C88.0) Waldenstrom's macroglobulinaemia
- (C88.1) Alpha heavy chain disease
- (C88.2) Gamma heavy chain disease
- (C88.3) Immunoproliferative small intestinal disease
- (C90) Multiple myeloma and malignant plasma cell neoplasms
(C90.0) Multiple myeloma
(C90.1) Plasma cell leukaemia
(C90.2) Plasmacytoma, extramedullary
- (C90.0) Multiple myeloma
- (C90.1) Plasma cell leukaemia
- (C90.2) Plasmacytoma, extramedullary
- (C91) Lymphoid leukaemia
(C91.0) Acute lymphoblastic leukaemia
(C91.1) Chronic lymphocytic leukaemia
(C91.4) Hairy-cell leukaemia
- (C91.0) Acute lymphoblastic leukaemia
- (C91.1) Chronic lymphocytic leukaemia
- (C91.4) Hairy-cell leukaemia
- (C92) Myeloid leukaemia
(C92.0) Acute myeloid leukaemia
(C92.1) Chronic myeloid leukaemia
(C92.2) Subacute myeloid leukaemia
(C92.3) Myeloid sarcoma
Chloroma
Granulocytic sarcoma
(C92.4) Acute promyelocytic leukaemia
(C92.5) Acute myelomonocytic leukaemia
- (C92.0) Acute myeloid leukaemia
- (C92.1) Chronic myeloid leukaemia
- (C92.2) Subacute myeloid leukaemia
- (C92.3) Myeloid sarcoma
Chloroma
Granulocytic sarcoma
- Chloroma
- Granulocytic sarcoma
- (C92.4) Acute promyelocytic leukaemia
- (C92.5) Acute myelomonocytic leukaemia
- (C93) Monocytic leukaemia
(C93.0) Acute monocytic leukaemia
(C93.1) Chronic monocytic leukaemia
(C93.2) Subacute monocytic leukaemia
- (C93.0) Acute monocytic leukaemia
- (C93.1) Chronic monocytic leukaemia
- (C93.2) Subacute monocytic leukaemia
- (C94) Other leukaemias of specified cell type
(C94.0) Acute erythraemia and erythroleukaemia
Di Guglielmo's disease
(C94.1) Chronic erythraemia
(C94.2) Acute megakaryoblastic leukaemia
(C94.3) Mast cell leukaemia
(C94.4) Acute panmyelosis
(C94.5) Acute myelofibrosis
(C94.7) Other specified leukaemias
- (C94.0) Acute erythraemia and erythroleukaemia
Di Guglielmo's disease
- Di Guglielmo's disease
- (C94.1) Chronic erythraemia
- (C94.2) Acute megakaryoblastic leukaemia
- (C94.3) Mast cell leukaemia
- (C94.4) Acute panmyelosis
- (C94.5) Acute myelofibrosis
- (C94.7) Other specified leukaemias
- (C95) Leukaemia of unspecified cell type
(C95.0) Acute leukaemia of unspecified cell type
(C95.1) Chronic leukaemia of unspecified cell type
(C95.2) Subacute leukaemia of unspecified cell type
(C95.7) Other leukaemia of unspecified cell type
(C95.9) Leukaemia, unspecified
- (C95.0) Acute leukaemia of unspecified cell type
- (C95.1) Chronic leukaemia of unspecified cell type
- (C95.2) Subacute leukaemia of unspecified cell type
- (C95.7) Other leukaemia of unspecified cell type
- (C95.9) Leukaemia, unspecified
- (C96) Other and unspecified malignant neoplasms of lymphoid, haematopoietic and related tissue
(C96.0) Letterer-Siwe disease
(C96.1) Malignant histiocytosis
(C96.2) Malignant mast cell tumour
Malignant mastocytosis
(C96.3) True histiocytic lymphoma
(C96.7) Other specified malignant neoplasms of lymphoid, haematopoietic and related tissue
(C96.9) Malignant neoplasm of lymphoid, haematopoietic and related tissue, unspecified
- (C96.0) Letterer-Siwe disease
- (C96.1) Malignant histiocytosis
- (C96.2) Malignant mast cell tumour
Malignant mastocytosis
- Malignant mastocytosis
- (C96.3) True histiocytic lymphoma
- (C96.7) Other specified malignant neoplasms of lymphoid, haematopoietic and related tissue
- (C96.9) Malignant neoplasm of lymphoid, haematopoietic and related tissue, unspecified

## (C97) Malignant neoplasms of independent (primary) multiple sites
- (C97) Malignant neoplasms of independent (primary) multiple sites

## (D00-D09) In situ neoplasms
- (D00) Carcinoma in situ of oral cavity, oesophagus and stomach
- (D01) Carcinoma in situ of other and unspecified digestive organs
- (D02) Carcinoma in situ of middle ear and respiratory system
- (D03) Melanoma in situ
- (D04) Carcinoma in situ of skin
- (D05) Carcinoma in situ of breast
- (D06) Carcinoma in situ of cervix uteri
- (D07) Carcinoma in situ of other and unspecified genital organs
- (D09) Carcinoma in situ of other and unspecified sites

## (D10-D36) Benign neoplasms
- (D10) Benign neoplasm of mouth and pharynx
- (D11) Benign neoplasm of major salivary glands
Warthin's tumor
Pleomorphic adenoma
(D11.0) Parotid gland
(D11.7) Other major salivary glands
Sublingual gland
Submandibular gland
(D11.9) Major salivary gland, unspecified
- Warthin's tumor
- Pleomorphic adenoma
- (D11.0) Parotid gland
- (D11.7) Other major salivary glands
Sublingual gland
Submandibular gland
- Sublingual gland
- Submandibular gland
- (D11.9) Major salivary gland, unspecified
- (D12) Benign neoplasm of colon, rectum, anus and anal canal
Familial adenomatous polyposis
(D12.0) Caecum
(D12.1) Appendix
(D12.2) Ascending colon
(D12.3) Transverse colon
(D12.4) Descending colon
(D12.5) Sigmoid colon
(D12.6) Colon, unspecified
Adenomatosis of colon
(D12.7) Rectosigmoid junction
(D12.8) Rectum
(D12.9) Anus and anal canal
- Familial adenomatous polyposis
- (D12.0) Caecum
- (D12.1) Appendix
- (D12.2) Ascending colon
- (D12.3) Transverse colon
- (D12.4) Descending colon
- (D12.5) Sigmoid colon
- (D12.6) Colon, unspecified
Adenomatosis of colon
- Adenomatosis of colon
- (D12.7) Rectosigmoid junction
- (D12.8) Rectum
- (D12.9) Anus and anal canal
- (D13) Benign neoplasm of other and ill-defined parts of digestive system
(D13.0) Oesophagus
(D13.1) Stomach
(D13.2) Duodenum
(D13.3) Other and unspecified parts of small intestine
(D13.4) Liver
Intrahepatic bile ducts
(D13.5) Extrahepatic bile ducts
(D13.6) Pancreas
(D13.7) Endocrine pancreas
Islet cell tumour
Islets of Langerhans
(D13.9) Ill-defined sites within the digestive system
Digestive system NOS
Intestine NOS
Spleen
- (D13.0) Oesophagus
- (D13.1) Stomach
- (D13.2) Duodenum
- (D13.3) Other and unspecified parts of small intestine
- (D13.4) Liver
Intrahepatic bile ducts
- Intrahepatic bile ducts
- (D13.5) Extrahepatic bile ducts
- (D13.6) Pancreas
- (D13.7) Endocrine pancreas
Islet cell tumour
Islets of Langerhans
- Islet cell tumour
- Islets of Langerhans
- (D13.9) Ill-defined sites within the digestive system
Digestive system NOS
Intestine NOS
Spleen
- Digestive system NOS
- Intestine NOS
- Spleen
- (D14) Benign neoplasm of middle ear and respiratory system
- (D15) Benign neoplasm of other and unspecified intrathoracic organs
(D15.0) Thymus
(D15.1) Heart
Myxoma
(D15.2) Mediastinum
- (D15.0) Thymus
- (D15.1) Heart
Myxoma
- Myxoma
- (D15.2) Mediastinum
- (D16) Benign neoplasm of bone and articular cartilage
(D16.0) Scapula and long bones of upper limb
(D16.1) Short bones of upper limb
(D16.2) Long bones of lower limb
(D16.3) Short bones of lower limb
(D16.4) Bones of skull and face
(D16.5) Lower jaw bone
(D16.6) Vertebral column
(D16.7) Ribs, sternum and clavicle
(D16.8) Pelvic bones, sacrum and coccyx
(D16.9) Bone and articular cartilage, unspecified
- (D16.0) Scapula and long bones of upper limb
- (D16.1) Short bones of upper limb
- (D16.2) Long bones of lower limb
- (D16.3) Short bones of lower limb
- (D16.4) Bones of skull and face
- (D16.5) Lower jaw bone
- (D16.6) Vertebral column
- (D16.7) Ribs, sternum and clavicle
- (D16.8) Pelvic bones, sacrum and coccyx
- (D16.9) Bone and articular cartilage, unspecified
- (D17) Benign lipomatous neoplasm
Lipoma (ILDS D17.910)
Lipomata, multiple (ILDS D17.920)
Angiolipoma (ILDS D17.930)
Lipoblastomatosis (ILDS D17.940)
Hibernoma (ILDS D17.950)
- Lipoma (ILDS D17.910)
- Lipomata, multiple (ILDS D17.920)
- Angiolipoma (ILDS D17.930)
- Lipoblastomatosis (ILDS D17.940)
- Hibernoma (ILDS D17.950)
- (D18) Haemangioma and lymphangioma, any site
(D18.0) Haemangioma, any site
Angioma NOS
(D18.1) Lymphangioma, any site
Cavernous haemangioma (ILDS D18.014)
- (D18.0) Haemangioma, any site
Angioma NOS
- Angioma NOS
- (D18.1) Lymphangioma, any site
Cavernous haemangioma (ILDS D18.014)
- Cavernous haemangioma (ILDS D18.014)
- (D19) Benign neoplasm of mesothelial tissue
- (D20) Benign neoplasm of soft tissue of retroperitoneum and peritoneum
- (D21) Other benign neoplasms of connective and other soft tissue
Chondroma
Masson's pseudoangiosarcoma (ILDS D21.M20)
Synovioma, giant-cell (ILDS D21.M30)
Leiomyoma (ILDS D21.M40)
Rhabdomyoma (ILDS D21.M50)
Angioleiomyoma (ILDS D21.M60)
- Chondroma
- Masson's pseudoangiosarcoma (ILDS D21.M20)
- Synovioma, giant-cell (ILDS D21.M30)
- Leiomyoma (ILDS D21.M40)
- Rhabdomyoma (ILDS D21.M50)
- Angioleiomyoma (ILDS D21.M60)
- (D22) Melanocytic naevi
- (D23) Other benign neoplasms of skin
- (D24) Benign neoplasm of breast
- (D25) Leiomyoma of uterus
Uterine fibroids
- Uterine fibroids
- (D26) Other benign neoplasms of uterus
- (D27) Benign neoplasm of ovary
- (D28) Benign neoplasm of other and unspecified female genital organs
- (D29) Benign neoplasm of male genital organs
- (D30) Benign neoplasm of urinary organs
(D30.0) Kidney
(D30.1) 
(D30.2) Ureter
(D30.3) Bladder
(D30.4) Urethra
(D30.7) Other urinary organs
(D30.9) Urinary organ, unspecified
- (D30.0) Kidney
- (D30.1) 
- (D30.2) Ureter
- (D30.3) Bladder
- (D30.4) Urethra
- (D30.7) Other urinary organs
- (D30.9) Urinary organ, unspecified
- (D31) Benign neoplasm of eye and adnexa
- (D32) Benign neoplasm of meninges
- (D33) Benign neoplasm of brain and other parts of central nervous system
- (D34) Benign neoplasm of thyroid gland
- (D35) Benign neoplasm of other and unspecified endocrine glands
(D35.0) Adrenal gland
(D35.1) Parathyroid gland
(D35.2) Pituitary gland
Pituitary adenoma
Prolactinoma
(D35.3) Craniopharyngeal duct
(D35.4) Pineal gland
(D35.5) Carotid body
(D35.6) Aortic body and other paraganglia
(D35.7) Other specified endocrine glands
(D35.8) Pluriglandular involvement
(D35.9) Endocrine gland, unspecified
- (D35.0) Adrenal gland
- (D35.1) Parathyroid gland
- (D35.2) Pituitary gland
Pituitary adenoma
Prolactinoma
- Pituitary adenoma
- Prolactinoma
- (D35.3) Craniopharyngeal duct
- (D35.4) Pineal gland
- (D35.5) Carotid body
- (D35.6) Aortic body and other paraganglia
- (D35.7) Other specified endocrine glands
- (D35.8) Pluriglandular involvement
- (D35.9) Endocrine gland, unspecified
- (D36) Benign neoplasm of other and unspecified sites

## (D37-D48) Neoplasms of uncertain or unknown behaviour
- (D37) Neoplasm of uncertain or unknown behaviour of oral cavity and digestive organs
- (D38) Neoplasm of uncertain or unknown behaviour of middle ear and respiratory and intrathoracic organs
- (D39) Neoplasm of uncertain or unknown behaviour of female genital organs
(D39.0) Uterus
(D39.1) Ovary
(D39.2) Placenta
(D39.7) Other female genital organs
(D39.9) Female genital organ, unspecified
- (D39.0) Uterus
- (D39.1) Ovary
- (D39.2) Placenta
- (D39.7) Other female genital organs
- (D39.9) Female genital organ, unspecified
- (D40) Neoplasm of uncertain or unknown behaviour of male genital organs
- (D41) Neoplasm of uncertain or unknown behaviour of urinary organs
- (D42) Neoplasm of uncertain or unknown behaviour of meninges
- (D43) Neoplasm of uncertain or unknown behaviour of brain and central nervous system
- (D44) Neoplasm of uncertain or unknown behaviour of endocrine glands
(D44.0) Thyroid gland
(D44.1) Adrenal gland
(D44.2) Parathyroid gland
(D44.3) Pituitary gland
(D44.4) Craniopharyngeal duct
(D44.5) Pineal gland
(D44.6) Carotid body
(D44.7) Aortic body and other paraganglia
(D44.8) Pluriglandular involvement
Multiple endocrine adenomatosis
(D44.9) Endocrine gland, unspecified
- (D44.0) Thyroid gland
- (D44.1) Adrenal gland
- (D44.2) Parathyroid gland
- (D44.3) Pituitary gland
- (D44.4) Craniopharyngeal duct
- (D44.5) Pineal gland
- (D44.6) Carotid body
- (D44.7) Aortic body and other paraganglia
- (D44.8) Pluriglandular involvement
Multiple endocrine adenomatosis
- Multiple endocrine adenomatosis
- (D44.9) Endocrine gland, unspecified
- (D45) Polycythaemia vera
- (D46) Myelodysplastic syndromes
- (D47) Other neoplasms of uncertain or unknown behaviour of lymphoid, haematopoietic and related tissue
(D47.0) Histiocytic and mast cell tumours of uncertain and unknown behaviour
Mast cell tumour NOS
Mastocytoma NOS
(D47.1) Chronic myeloproliferative disease
Myelofibrosis (with myeloid metaplasia)
Myeloproliferative disease, unspecified
Myelosclerosis (megakaryocytic) with myeloid metaplasia
(D47.2) Monoclonal gammopathy
(D47.3) Essential (haemorrhagic) thrombocythaemia
(D47.7) Other specified neoplasms of uncertain or unknown behaviour of lymphoid, haematopoietic and related tissue
(D47.9) Neoplasm of uncertain or unknown behaviour of lymphoid, haematopoietic and related tissue, unspecified
- (D47.0) Histiocytic and mast cell tumours of uncertain and unknown behaviour
Mast cell tumour NOS
Mastocytoma NOS
- Mast cell tumour NOS
- Mastocytoma NOS
- (D47.1) Chronic myeloproliferative disease
Myelofibrosis (with myeloid metaplasia)
Myeloproliferative disease, unspecified
Myelosclerosis (megakaryocytic) with myeloid metaplasia
- Myelofibrosis (with myeloid metaplasia)
- Myeloproliferative disease, unspecified
- Myelosclerosis (megakaryocytic) with myeloid metaplasia
- (D47.2) Monoclonal gammopathy
- (D47.3) Essential (haemorrhagic) thrombocythaemia
- (D47.7) Other specified neoplasms of uncertain or unknown behaviour of lymphoid, haematopoietic and related tissue
- (D47.9) Neoplasm of uncertain or unknown behaviour of lymphoid, haematopoietic and related tissue, unspecified
- (D48) Neoplasm of uncertain or unknown behaviour of other and unspecified sites
(D48.0) Bone and articular cartilage
(D48.1) Connective and other soft tissue
(D48.2) Peripheral nerves and autonomic nervous system
(D48.3) Retroperitoneum
(D48.4) Peritoneum
(D48.5) Skin
(D48.6) Breast
(D48.7) Other specified sites
(D48.9) Neoplasm of uncertain or unknown behaviour, unspecified
- (D48.0) Bone and articular cartilage
- (D48.1) Connective and other soft tissue
- (D48.2) Peripheral nerves and autonomic nervous system
- (D48.3) Retroperitoneum
- (D48.4) Peritoneum
- (D48.5) Skin
- (D48.6) Breast
- (D48.7) Other specified sites
- (D48.9) Neoplasm of uncertain or unknown behaviour, unspecified

# D50-D89 - Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism

## (D50-D53) Nutritional anemias
- (D50) Iron deficiency anaemia
(D50.0) Iron deficiency anaemia secondary to blood loss (chronic)
(D50.1) Sideropenic dysphagia
Kelly-Paterson syndrome
Plummer-Vinson syndrome
(D50.8) Other iron deficiency anaemias
(D50.9) Iron deficiency anaemia, unspecified
- (D50.0) Iron deficiency anaemia secondary to blood loss (chronic)
- (D50.1) Sideropenic dysphagia
Kelly-Paterson syndrome
Plummer-Vinson syndrome
- Kelly-Paterson syndrome
- Plummer-Vinson syndrome
- (D50.8) Other iron deficiency anaemias
- (D50.9) Iron deficiency anaemia, unspecified
- (D51) Vitamin B12 deficiency anaemia
(D51.0) Vitamin B12 deficiency anaemia due to intrinsic factor deficiency
Pernicious anemia
(D51.1) Vitamin B 12 deficiency anaemia due to selective vitamin B 12 malabsorption with proteinuria
Megaloblastic hereditary anaemia
(D51.2) Transcobalamin II deficiency
(D51.3) Other dietary vitamin B 12 deficiency anaemia
(D51.8) Other vitamin B 12 deficiency anaemias
(D51.9) Vitamin B 12 deficiency anaemia, unspecified
- (D51.0) Vitamin B12 deficiency anaemia due to intrinsic factor deficiency
Pernicious anemia
- Pernicious anemia
- (D51.1) Vitamin B 12 deficiency anaemia due to selective vitamin B 12 malabsorption with proteinuria
Megaloblastic hereditary anaemia
- Megaloblastic hereditary anaemia
- (D51.2) Transcobalamin II deficiency
- (D51.3) Other dietary vitamin B 12 deficiency anaemia
- (D51.8) Other vitamin B 12 deficiency anaemias
- (D51.9) Vitamin B 12 deficiency anaemia, unspecified
- (D52) Folate deficiency anaemia
(D52.0) Dietary folate deficiency anaemia
Nutritional megaloblastic anaemia
(D52.1) Drug-induced folate deficiency anaemia
(D52.8) Other folate deficiency anaemias
(D52.9) Folate deficiency anaemia, unspecified
- (D52.0) Dietary folate deficiency anaemia
Nutritional megaloblastic anaemia
- Nutritional megaloblastic anaemia
- (D52.1) Drug-induced folate deficiency anaemia
- (D52.8) Other folate deficiency anaemias
- (D52.9) Folate deficiency anaemia, unspecified
- (D53) Other nutritional anaemias
(D53.0) Protein deficiency anaemia
(D53.1) Other megaloblastic anaemias, not elsewhere classified
(D53.2) Scorbutic anaemia
(D53.8) Other specified nutritional anaemias
(D53.9) Nutritional anaemia, unspecified
- (D53.0) Protein deficiency anaemia
- (D53.1) Other megaloblastic anaemias, not elsewhere classified
- (D53.2) Scorbutic anaemia
- (D53.8) Other specified nutritional anaemias
- (D53.9) Nutritional anaemia, unspecified

## (D55-D59) Haemolytic anaemias
- (D55) Anaemia due to enzyme disorders
(D55.0) Anaemia due to glucose-6-phosphate dehydrogenase (G6PD) deficiency
Favism
G6PD deficiency anaemia
(D55.1) Anaemia due to other disorders of glutathione metabolism
(D55.2) Anaemia due to disorders of glycolytic enzymes
(D55.3) Anaemia due to disorders of nucleotide metabolism
(D55.8) Other anaemias due to enzyme disorders
(D55.9) Anaemia due to enzyme disorder, unspecified
- (D55.0) Anaemia due to glucose-6-phosphate dehydrogenase (G6PD) deficiency
Favism
G6PD deficiency anaemia
- Favism
- G6PD deficiency anaemia
- (D55.1) Anaemia due to other disorders of glutathione metabolism
- (D55.2) Anaemia due to disorders of glycolytic enzymes
- (D55.3) Anaemia due to disorders of nucleotide metabolism
- (D55.8) Other anaemias due to enzyme disorders
- (D55.9) Anaemia due to enzyme disorder, unspecified
- (D56) Thalassaemia
(D56.0) Alpha thalassaemia
(D56.1) Beta thalassaemia
(D56.2) Delta-beta thalassaemia
(D56.3) Thalassaemia trait
(D56.4) Hereditary persistence of fetal haemoglobin (HPFH)
(D56.8) Other thalassaemias
(D56.9) Thalassaemia, unspecified
- (D56.0) Alpha thalassaemia
- (D56.1) Beta thalassaemia
- (D56.2) Delta-beta thalassaemia
- (D56.3) Thalassaemia trait
- (D56.4) Hereditary persistence of fetal haemoglobin (HPFH)
- (D56.8) Other thalassaemias
- (D56.9) Thalassaemia, unspecified
- (D57) Sickle-cell disorders
(D57.0) Sickle-cell anaemia with crisis
(D57.1) Sickle-cell anaemia without crisis
(D57.2) Double heterozygous sickling disorders
(D57.3) Sickle-cell trait
(D57.8) Other sickle-cell disorders
- (D57.0) Sickle-cell anaemia with crisis
- (D57.1) Sickle-cell anaemia without crisis
- (D57.2) Double heterozygous sickling disorders
- (D57.3) Sickle-cell trait
- (D57.8) Other sickle-cell disorders
- (D58) Other hereditary haemolytic anaemias
(D58.0) Hereditary spherocytosis
(D58.1) Hereditary elliptocytosis
(D58.2) Other haemoglobinopathies
(D58.8) Other specified hereditary haemolytic anaemias
Stomatocytosis
- (D58.0) Hereditary spherocytosis
- (D58.1) Hereditary elliptocytosis
- (D58.2) Other haemoglobinopathies
- (D58.8) Other specified hereditary haemolytic anaemias
Stomatocytosis
- Stomatocytosis
- (D59) Acquired haemolytic anaemia
(D59.0) Drug-induced autoimmune haemolytic anaemia
(D59.1) Other autoimmune haemolytic anaemias
Warm autoimmune hemolytic anemia
(D59.2) Drug-induced nonautoimmune haemolytic anaemia
(D59.3) Haemolytic-uraemic syndrome
(D59.4) Other nonautoimmune haemolytic anaemias
Microangiopathic hemolytic anemia
(D59.5) Paroxysmal nocturnal haemoglobinuria (Marchiafava-Micheli)
(D59.6) Haemoglobinuria due to haemolysis from other external causes
(D59.8) Other acquired haemolytic anaemias
(D59.9) Acquired haemolytic anaemia, unspecified
- (D59.0) Drug-induced autoimmune haemolytic anaemia
- (D59.1) Other autoimmune haemolytic anaemias
Warm autoimmune hemolytic anemia
- Warm autoimmune hemolytic anemia
- (D59.2) Drug-induced nonautoimmune haemolytic anaemia
- (D59.3) Haemolytic-uraemic syndrome
- (D59.4) Other nonautoimmune haemolytic anaemias
Microangiopathic hemolytic anemia
- Microangiopathic hemolytic anemia
- (D59.5) Paroxysmal nocturnal haemoglobinuria (Marchiafava-Micheli)
- (D59.6) Haemoglobinuria due to haemolysis from other external causes
- (D59.8) Other acquired haemolytic anaemias
- (D59.9) Acquired haemolytic anaemia, unspecified

## (D60-D64) Aplastic and other anaemias
- (D60) Acquired pure red cell aplasia (erythroblastopenia)
- (D61) Other aplastic anaemias
(D61.0) Constitutional aplastic anaemia
Fanconi anemia
- (D61.0) Constitutional aplastic anaemia
Fanconi anemia
- Fanconi anemia
- (D62) Acute posthaemorrhagic anaemia
- (D63) Anaemia in chronic diseases classified elsewhere
- (D64) Other anaemias
(D64.0) Hereditary sideroblastic anaemia
(D64.1) Secondary sideroblastic anaemia due to disease
(D64.2) Secondary sideroblastic anaemia due to drugs and toxins
(D64.3) Other sideroblastic anaemias
(D64.4) Congenital dyserythropoietic anaemia
(D64.8) Other specified anaemias
(D64.9) Anaemia, unspecified
- (D64.0) Hereditary sideroblastic anaemia
- (D64.1) Secondary sideroblastic anaemia due to disease
- (D64.2) Secondary sideroblastic anaemia due to drugs and toxins
- (D64.3) Other sideroblastic anaemias
- (D64.4) Congenital dyserythropoietic anaemia
- (D64.8) Other specified anaemias
- (D64.9) Anaemia, unspecified

## (D65-D69) Coagulation defects, purpura and other haemorrhagic conditions
- (D65) Disseminated intravascular coagulation (defibrination syndrome)
- (D66) Hereditary factor VIII deficiency
Haemophilia A
- Haemophilia A
- (D67) Hereditary factor IX deficiency
Christmas disease
- Christmas disease
- (D68) Other coagulation defects
(D68.0) Von Willebrand's disease
(D68.1) Hereditary factor XI deficiency
Haemophilia C
(D68.2) Hereditary deficiency of other clotting factors
(D68.3) Haemorrhagic disorder due to circulating anticoagulants
(D68.4) Acquired coagulation factor deficiency
(D68.8) Other specified coagulation defects
(D68.9) Coagulation defect, unspecified
- (D68.0) Von Willebrand's disease
- (D68.1) Hereditary factor XI deficiency
Haemophilia C
- Haemophilia C
- (D68.2) Hereditary deficiency of other clotting factors
- (D68.3) Haemorrhagic disorder due to circulating anticoagulants
- (D68.4) Acquired coagulation factor deficiency
- (D68.8) Other specified coagulation defects
- (D68.9) Coagulation defect, unspecified
- (D69) Purpura and other haemorrhagic conditions
(D69.0) Allergic purpura
anaphylactoid purpura
Henoch-Schonlein purpura
(D69.1) Qualitative platelet defects
Bernard-Soulier syndrome (giant platelet)
Glanzmann's disease
Grey platelet syndrome
Thromboasthenia (haemorrhagic)(hereditary)
Thrombocytopathy
(D69.2) Other nonthrombocytopenic purpura
(D69.3) Idiopathic thrombocytopenic purpura
(D69.4) Other primary thrombocytopenia
(D69.5) Secondary thrombocytopenia
(D69.6) Thrombocytopenia, unspecified
(D69.8) Other specified haemorrhagic conditions
(D69.9) Haemorrhagic condition, unspecified
- (D69.0) Allergic purpura
anaphylactoid purpura
Henoch-Schonlein purpura
- anaphylactoid purpura
- Henoch-Schonlein purpura
- (D69.1) Qualitative platelet defects
Bernard-Soulier syndrome (giant platelet)
Glanzmann's disease
Grey platelet syndrome
Thromboasthenia (haemorrhagic)(hereditary)
Thrombocytopathy
- Bernard-Soulier syndrome (giant platelet)
- Glanzmann's disease
- Grey platelet syndrome
- Thromboasthenia (haemorrhagic)(hereditary)
- Thrombocytopathy
- (D69.2) Other nonthrombocytopenic purpura
- (D69.3) Idiopathic thrombocytopenic purpura
- (D69.4) Other primary thrombocytopenia
- (D69.5) Secondary thrombocytopenia
- (D69.6) Thrombocytopenia, unspecified
- (D69.8) Other specified haemorrhagic conditions
- (D69.9) Haemorrhagic condition, unspecified

## (D70-D77) Other diseases of blood and blood-forming organs
- (D70) Agranulocytosis
Neutropenia
- Neutropenia
- (D71) Functional disorders of polymorphonuclear neutrophils
- (D72) Other disorders of white blood cells
(D72.1) Eosinophilia
(D72.8) Other specified disorders of white blood cells
Leukocytosis
Lymphocytosis (symptomatic)
Lymphopenia
Monocytosis (symptomatic)
Plasmacytosis
- (D72.1) Eosinophilia
- (D72.8) Other specified disorders of white blood cells
Leukocytosis
Lymphocytosis (symptomatic)
Lymphopenia
Monocytosis (symptomatic)
Plasmacytosis
- Leukocytosis
- Lymphocytosis (symptomatic)
- Lymphopenia
- Monocytosis (symptomatic)
- Plasmacytosis
- (D73) Diseases of spleen
(D73.0) Hyposplenism
(D73.1) Hypersplenism
(D73.2) Chronic congestive splenomegaly
(D73.3) Abscess of spleen
(D73.4) Cyst of spleen
(D73.5) Infarction of spleen
(D73.8) Other diseases of spleen
(D73.9) Disease of spleen, unspecified
- (D73.0) Hyposplenism
- (D73.1) Hypersplenism
- (D73.2) Chronic congestive splenomegaly
- (D73.3) Abscess of spleen
- (D73.4) Cyst of spleen
- (D73.5) Infarction of spleen
- (D73.8) Other diseases of spleen
- (D73.9) Disease of spleen, unspecified
- (D74) Methaemoglobinaemia
- (D75) Other diseases of blood and blood-forming organs
(D75.0) Familial erythrocytosis
(D75.1) Secondary polycythaemia
(D75.2) Essential thrombocytosis
(D75.8) Other specified diseases of blood and blood-forming organs
Basophilia
(D75.9) Disease of blood and blood-forming organs, unspecified
- (D75.0) Familial erythrocytosis
- (D75.1) Secondary polycythaemia
- (D75.2) Essential thrombocytosis
- (D75.8) Other specified diseases of blood and blood-forming organs
Basophilia
- Basophilia
- (D75.9) Disease of blood and blood-forming organs, unspecified
- (D76) Certain diseases involving lymphoreticular tissue and reticulohistiocytic system
(D76.0) Langerhans' cell histiocytosis, not elsewhere classified
Eosinophilic granuloma
Hand-Schuller-Christian disease
Histiocytosis X (chronic)
(D76.1) Haemophagocytic lymphohistiocytosis
Familial haemophagocytic reticulosis
(D76.2) Haemophagocytic syndrome, infection-associated
(D76.3) Other histiocytosis syndromes
Reticulohistiocytoma (giant-cell)
Sinus histiocytosis with massive lymphadenopathy
Xanthogranuloma
- (D76.0) Langerhans' cell histiocytosis, not elsewhere classified
Eosinophilic granuloma
Hand-Schuller-Christian disease
Histiocytosis X (chronic)
- Eosinophilic granuloma
- Hand-Schuller-Christian disease
- Histiocytosis X (chronic)
- (D76.1) Haemophagocytic lymphohistiocytosis
Familial haemophagocytic reticulosis
- Familial haemophagocytic reticulosis
- (D76.2) Haemophagocytic syndrome, infection-associated
- (D76.3) Other histiocytosis syndromes
Reticulohistiocytoma (giant-cell)
Sinus histiocytosis with massive lymphadenopathy
Xanthogranuloma
- Reticulohistiocytoma (giant-cell)
- Sinus histiocytosis with massive lymphadenopathy
- Xanthogranuloma
- (D77) Other disorders of blood and blood-forming organs in diseases classified elsewhere

## (D80-D89) Certain disorders involving the immune mechanism
- (D80) Immunodeficiency with predominantly antibody defects
(D80.0) Hereditary hypogammaglobulinaemia
Autosomal recessive agammaglobulinaemia (Swiss type)
X-linked agammaglobulinaemia (Bruton) (with growth hormone deficiency)
(D80.1) Nonfamilial hypogammaglobulinaemia
Agammaglobulinaemia with immunoglobulin-bearing B-lymphocytes
Common variable agammaglobulinaemia (CVAgamma)
Hypogammaglobulinaemia NOS
(D80.2) Selective deficiency of immunoglobulin A (IgA)
(D80.3) Selective deficiency of immunoglobulin G (IgG) subclasses
(D80.4) Selective deficiency of immunoglobulin M (IgM)
(D80.5) Immunodeficiency with increased immunoglobulin M (IgM)
(D80.6) Antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinaemia
(D80.7) Transient hypogammaglobulinaemia of infancy
(D80.8) Other immunodeficiencies with predominantly antibody defects
Kappa light chain deficiency
(D80.8) Immunodeficiency with predominantly antibody defects, unspecified
- (D80.0) Hereditary hypogammaglobulinaemia
Autosomal recessive agammaglobulinaemia (Swiss type)
X-linked agammaglobulinaemia (Bruton) (with growth hormone deficiency)
- Autosomal recessive agammaglobulinaemia (Swiss type)
- X-linked agammaglobulinaemia (Bruton) (with growth hormone deficiency)
- (D80.1) Nonfamilial hypogammaglobulinaemia
Agammaglobulinaemia with immunoglobulin-bearing B-lymphocytes
Common variable agammaglobulinaemia (CVAgamma)
Hypogammaglobulinaemia NOS
- Agammaglobulinaemia with immunoglobulin-bearing B-lymphocytes
- Common variable agammaglobulinaemia (CVAgamma)
- Hypogammaglobulinaemia NOS
- (D80.2) Selective deficiency of immunoglobulin A (IgA)
- (D80.3) Selective deficiency of immunoglobulin G (IgG) subclasses
- (D80.4) Selective deficiency of immunoglobulin M (IgM)
- (D80.5) Immunodeficiency with increased immunoglobulin M (IgM)
- (D80.6) Antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinaemia
- (D80.7) Transient hypogammaglobulinaemia of infancy
- (D80.8) Other immunodeficiencies with predominantly antibody defects
Kappa light chain deficiency
- Kappa light chain deficiency
- (D80.8) Immunodeficiency with predominantly antibody defects, unspecified
- (D81) Combined immunodeficiencies
(D81.0) Severe combined immunodeficiency (SCID) with reticular dysgenesis
(D81.1) Severe combined immunodeficiency (SCID) with low T-cell and B-cell numbers
(D81.2) Severe combined immunodeficiency (SCID) with low or normal B-cell numbers
(D81.3) Adenosine deaminase deficiency (ADA)
(D81.4) Nezelof's syndrome
(D81.5) Purine nucleoside phosphorylase deficiency (PNP)
(D81.6) Major histocompatibility complex class I deficiency
Bare lymphocyte syndrome
(D81.7) Major histocompatibility complex class II deficiency
(D81.8) Other combined immunodeficiencies
Biotin-dependent carboxylase deficiency
(D81.9) Combined immunodeficiency, unspecified
Severe combined immunodeficiency disorder (SCID) NOS
- (D81.0) Severe combined immunodeficiency (SCID) with reticular dysgenesis
- (D81.1) Severe combined immunodeficiency (SCID) with low T-cell and B-cell numbers
- (D81.2) Severe combined immunodeficiency (SCID) with low or normal B-cell numbers
- (D81.3) Adenosine deaminase deficiency (ADA)
- (D81.4) Nezelof's syndrome
- (D81.5) Purine nucleoside phosphorylase deficiency (PNP)
- (D81.6) Major histocompatibility complex class I deficiency
Bare lymphocyte syndrome
- Bare lymphocyte syndrome
- (D81.7) Major histocompatibility complex class II deficiency
- (D81.8) Other combined immunodeficiencies
Biotin-dependent carboxylase deficiency
- Biotin-dependent carboxylase deficiency
- (D81.9) Combined immunodeficiency, unspecified
Severe combined immunodeficiency disorder (SCID) NOS
- Severe combined immunodeficiency disorder (SCID) NOS
- (D82) Immunodeficiency associated with other major defects
(D82.0) Wiskott-Aldrich syndrome
Immunodeficiency with thrombocytopenia and eczema
(D82.1) Di George's syndrome
(D82.2) Immunodeficiency with short-limbed stature
(D82.3) Immunodeficiency following hereditary defective response to Epstein-Barr virus
X-linked lymphoproliferative disease
(D82.4) Hyperimmunoglobulin E syndrome (IgE)
- (D82.0) Wiskott-Aldrich syndrome
Immunodeficiency with thrombocytopenia and eczema
- Immunodeficiency with thrombocytopenia and eczema
- (D82.1) Di George's syndrome
- (D82.2) Immunodeficiency with short-limbed stature
- (D82.3) Immunodeficiency following hereditary defective response to Epstein-Barr virus
X-linked lymphoproliferative disease
- X-linked lymphoproliferative disease
- (D82.4) Hyperimmunoglobulin E syndrome (IgE)
- (D83) Common variable immunodeficiency
- (D84) Other immunodeficiencies
(D84.0) Lymphocyte function antigen-1 (LFA-1) defect
(D84.1) Defects in the complement system
C1 esterase inhibitor deficiency (C1-INH)
(D84.8) Other specified immunodeficiencies
(D84.9) Immunodeficiency, unspecified
- (D84.0) Lymphocyte function antigen-1 (LFA-1) defect
- (D84.1) Defects in the complement system
C1 esterase inhibitor deficiency (C1-INH)
- C1 esterase inhibitor deficiency (C1-INH)
- (D84.8) Other specified immunodeficiencies
- (D84.9) Immunodeficiency, unspecified
- (D86) Sarcoidosis
(D86.0) Sarcoidosis of lung
(D86.1) Sarcoidosis of lymph nodes
(D86.2) Sarcoidosis of lung with sarcoidosis of lymph nodes
(D86.3) Sarcoidosis of skin
(D86.8) Sarcoidosis of other and combined sites
- (D86.0) Sarcoidosis of lung
- (D86.1) Sarcoidosis of lymph nodes
- (D86.2) Sarcoidosis of lung with sarcoidosis of lymph nodes
- (D86.3) Sarcoidosis of skin
- (D86.8) Sarcoidosis of other and combined sites
- (D89) Other disorders involving the immune mechanism, not elsewhere classified
(D89.0) Polyclonal hypergammaglobulinaemia
Benign hypergammaglobulinaemic purpura
Polyclonal gammopathy NOS
(D89.1) Cryoglobulinaemia
(D89.2) Hypergammaglobulinaemia, unspecified
(D89.8) Other specified disorders involving the immune mechanism, not elsewhere classified
(D89.9) Disorder involving the immune mechanism, unspecified
- (D89.0) Polyclonal hypergammaglobulinaemia
Benign hypergammaglobulinaemic purpura
Polyclonal gammopathy NOS
- Benign hypergammaglobulinaemic purpura
- Polyclonal gammopathy NOS
- (D89.1) Cryoglobulinaemia
- (D89.2) Hypergammaglobulinaemia, unspecified
- (D89.8) Other specified disorders involving the immune mechanism, not elsewhere classified
- (D89.9) Disorder involving the immune mechanism, unspecified