# List of ICD-9 codes 740–759: congenital anomalies

ICD-9 chapters :
| Chapter | Block | Title |
| I | 001–139 | Infectious and Parasitic Diseases |
| II | 140–239 | Neoplasms |
| III | 240–279 | Endocrine, Nutritional and Metabolic Diseases, and Immunity Disorders |
| IV | 280–289 | Diseases of the Blood and Blood-forming Organs |
| V | 290–319 | Mental Disorders |
| VI | 320–389 | Diseases of the Nervous System and Sense Organs |
| VII | 390–459 | Diseases of the Circulatory System |
| VIII | 460–519 | Diseases of the Respiratory System |
| IX | 520–579 | Diseases of the Digestive System |
| X | 580–629 | Diseases of the Genitourinary System |
| XI | 630–679 | Complications of Pregnancy, Childbirth, and the Puerperium |
| XII | 680–709 | Diseases of the Skin and Subcutaneous Tissue |
| XIII | 710–739 | Diseases of the Musculoskeletal System and Connective Tissue |
| XIV | 740–759 | Congenital Anomalies |
| XV | 760–779 | Certain Conditions originating in the Perinatal Period |
| XVI | 780–799 | Symptoms, Signs and Ill-defined Conditions |
| XVII | 800–999 | Injury and Poisoning |
| | E800–E999 | Supplementary Classification of External Causes of Injury and Poisoning |
| | V01–V82 | Supplementary Classification of Factors influencing Health Status and Contact with Health Services |
| | M8000–M9970 | Morphology of Neoplasms |
This is a shortened version of the fourteenth chapter of the ICD-9: Congenital Anomalies. It covers ICD codes 740 to 759. The full chapter can be found on pages 417 to 437 of Volume 1, which contains all (sub)categories of the ICD-9. Volume 2 is an alphabetical index of Volume 1. Both volumes can be downloaded for free from the website of the World Health Organization.

## Nervous system (740–742)

* 740 Anencephalus and similar anomalies
** 740.0 Anencephalus
* 741 Spina bifida
* 742 Other congenital anomalies of nervous system
** 742.1 Microcephalus
** 742.3 Hydrocephalus

## Eye, ear, face and neck (743–744)

* 743 Congenital anomalies of eye
** 743.0 Anophthalmos
*** 743.00 Clinical anophthalmos unspecified
*** 743.03 Cystic eyeball congenital
*** 743.06 Cryptophthalmos
** 743.1 Microphthalmos
** 743.2 Buphthalmos
** 743.3 Congenital cataract and lens anomalies
** 743.4 Coloboma and other anomalies of anterior segment
*** 743.45 Aniridia
** 743.5 Congenital anomalies of posterior segment
** 743.6 Congenital anomalies of eyelids, lacrimal system, and orbit
* 744 Congenital anomalies of ear, face, and neck
** 744.0 Anomalies of ear causing impairment of hearing
** 744.1 Accessory auricle
** 744.2 Other specified congenital anomalies of ear
*** 744.22 Macrotia
*** 744.23 Microtia
** 744.3 Unspecified congenital anomaly of ear
** 744.4 Branchial cleft cyst or fistula; preauricular sinus
** 744.5 Webbing of neck
** 744.8 Other specified congenital anomalies of face and neck
*** 744.81 Macrocheilia
*** 744.82 Microcheilia
*** 744.83 Macrostomia
*** 744.84 Microstomia

## Circulatory system (745–747)

* 745 Bulbus cordis anomalies and anomalies of cardiac septal closure
** 745.0 Common truncus
** 745.1 Transposition of great vessels
** 745.2 Tetralogy of fallot
** 745.3 Common ventricle
** 745.4 Ventricular septal defect
** 745.5 Atrial septal defect
** 745.6 Endocardial cushion defects
** 745.7 Cor biloculare
* 746 Other congenital anomalies of heart
** 746.1 Tricuspid atresia and stenosis congenital
** 746.2 Ebstein's anomaly
** 746.3 Congenital stenosis of aortic valve
** 746.4 Congenital insufficiency of aortic valve
** 746.5 Congenital mitral stenosis
** 746.6 Congenital mitral insufficiency
** 746.7 Hypoplastic left heart syndrome
** 746.8 Other specified congenital anomalies of heart
*** 746.81 Subaortic stenosis congenital
*** 746.82 Cor triatriatum
*** 746.83 Infundibular pulmonic stenosis congenital
*** 746.84 Congenital obstructive anomalies of heart not elsewhere classified
*** 746.85 Coronary artery anomaly congenital
*** 746.86 Congenital heart block
*** 746.87 Malposition of heart and cardiac apex
*** 746.89 Other specified congenital anomalies of heart
**** Brugada syndrome
* 747 Other congenital anomalies of circulatory system
** 747.1 Coarctation of aorta
*** 747.11 Interruption of aortic arch
** 747.2 Other congenital anomalies of aorta
** 747.3 Congenital anomalies of pulmonary artery
** 747.4 Congenital anomalies of great veins
** 747.5 Absence or hypoplasia of umbilical artery
** 747.6 Arteriovenous malformation, unspec.
** 747.8 Other specified anomalies of circulatory system
*** 747.81 Congenital anomalies of cerebrovascular system
*** 747.82 Spinal vessel anomaly
*** 747.83 Persistent fetal circulation
** 747.9 Unspecified congenital anomaly of circulatory system

## Respiratory system (748–748)

* 748 Congenital anomalies of respiratory system
** 748.0 Choanal atresia

## Digestive system (749–751)

* 749 Cleft palate
** 749.0 Cleft palate, unspec.
** 749.2 Cleft palate w/ cleft lip
* 750 Other congenital anomalies of upper alimentary tract
** 750.0 Tongue tie
** 750.1 Other congenital anomalies of tongue
** 750.2 Other specified congenital anomalies of mouth and pharynx
** 750.3 Congenital tracheoesophageal fistula esophageal atresia and stenosis
** 750.4 Other specified congenital anomalies of esophagus
** 750.5 Congenital hypertrophic pyloric stenosis
** 750.6 Congenital hiatus hernia
** 750.7 Other specified congenital anomalies of stomach
** 750.8 Other specified congenital anomalies of upper alimentary tract
** 750.9 Unspecified congenital anomaly of upper alimentary tract
* 751 Other congenital anomalies of digestive system
** 751.0 Meckel's diverticulum
** 751.1 Congenital atresia and stenosis of small intestine
** 751.2 Imperforate anus
** 751.3 Hirschsprung's disease
** 751.4 Congenital anomalies of intestinal fixation
** 751.5 Other congenital anomalies of intestine
** 751.6 Anomalies of gallbladder bile ducts and liver
** 751.7 Congenital anomalies of pancreas
** 751.8 Other specified congenital anomalies of digestive system
** 751.9 Unspecified congenital anomaly of digestive system

## Genital organs (752–752)

* 752 Congenital anomalies of genital organs
** 752.0 Congenital anomalies of ovaries
** 752.1 Congenital anomalies of fallopian tubes and broad ligaments
** 752.2 Doubling of uterus
** 752.3 Other congenital anomalies of uterus
** 752.4 Anomalies of cervix, vagina, and external female genitalia
*** 752.42 Imperforate hymen
*** 752.43 Cervical agenesis
** 752.5 Undescended testicle
** 752.6 Hypospadias and epispadias
*** 752.61 Hypospadias
*** 752.62 Epispadias
*** 752.63 Congenital chordee
*** 752.64 Micropenis
** 752.7 Indeterminate sex and pseudohermaphroditism

## Urinary system (753–753)

* 753 Congenital anomalies of urinary system
** 753.0 Renal agenesis and dysgenesis
** 753.1 Cystic kidney disease
** 753.2 Obstructive defects of renal pelvis and ureter
** 753.3 Other specified anomalies of kidney
*** Renal ectopia
*** Horseshoe kidney
** 753.4 Other specified anomalies of ureter
*** Ectopic ureter
** 753.5 Exstrophy of urinary bladder
** 753.6 Atresia and stenosis of urethra and bladder neck
** 753.7 Anomalies of urachus
*** Urachal cyst
** 753.8 Other specified anomalies of bladder and urethra
** 753.9 Unspecified anomaly of urinary system

## Musculoskeletal system (754–756)

* 754 Certain congenital musculoskeletal deformities
** 754.1 Torticollis, sternomastoid
** 754.3 Dislocation of hip, unilateral
** 754.5 Varus deformities of feet
*** 754.51 Talipes equinovarus
** 754.6 Valgus deformities of feet
** 754.8 Other specified nonteratogenic anomalies
*** 754.81 Pectus excavatum
* 755 Other congenital anomalies of limbs
** 755.0 Polydactyly
** 755.1 Syndactyly
** 755.5 Other congenital anomalies of upper limb including shoulder girdle
*** 755.54 Madelung's deformity
*** 755.55 Acrocephalosyndactyly
**** Apert syndrome
** 755.9 Limb anomaly, unspec.
* 756 Other congenital musculoskeletal anomalies
** 756.1 Anomalies of spine
*** 756.12 Spondylolisthesis
*** 756.16 Klippel–Feil syndrome
*** 756.17 Spina bifida occulta
** 756.2 Cervical rib
** 756.3 Other congenital anomalies of ribs and sternum
** 756.4 Chondrodystrophy
** 756.5 Osteodystrophies
*** 756.51 Osteogenesis imperfecta
** 756.6 Congenital anomalies of diaphragm
** 756.7 Congenital anomalies of abdominal wall
** 756.8 Other specified congenital anomalies of muscle tendon fascia and connective tissue
*** 756.81 Congenital absence of muscle and tendon
*** 756.82 Accessory muscle
*** 756.83 Ehlers–Danlos syndrome

## Integument (757–757)

* 757 Congenital anomalies of the integument
** 757.3 Other specified anomalies of skin
*** 757.32 Birthmarks
*** 757.39 Other specified congenital anomalies of skin
**** Bloom syndrome
**** Epidermolysis bullosa
**** Pseudoxanthoma elasticum
** 757.6 Supernumerary nipple

## Chromosomal anomalies (758–758)

* 758 Chromosomal anomalies
** 758.0 Down syndrome
** 758.1 Patau's syndrome
** 758.2 Edward's syndrome
** 758.3 Autosomal deletion syndromes
*** 758.31 Cri du chat syndrome
*** 758.32 Velo-cardio-facial syndrome
*** 758.33 Other microdeletions
**** Miller–Dieker syndrome
**** Smith–Magenis syndrome
** 758.4 Balanced autosomal translocation in normal individual
** 758.5 Other conditions due to autosomal anomalies
** 758.6 Gonadal dysgenesis
*** Turner syndrome
*** XO syndrome
** 758.7 Klinefelter syndrome
** 758.8 Other conditions due to sex chromosome anomalies
*** Snyder–Robinson syndrome (SRS)
** 758.9 Conditions due to anomaly of unspecified chromosome

## Other (759–759)

* 759 Other and unspecified congenital anomalies
** 759.0 Anomalies of spleen, congenital
** 759.1 Anomalies of adrenal gland, congenital
** 759.2 Anomalies of other endocrine glands, congenital
** 759.3 Situs inversus
** 759.4 Conjoined twins
** 759.5 Tuberous sclerosis
** 759.6 Other congenital hamartoses, not elsewhere classified
*** Cowden syndrome
** 759.7 Multiple congenital anomalies, so described
** 759.8 Other specified congenital anomalies
*** 759.81 Prader-Willi syndrome
*** 759.82 Marfan syndrome
*** 759.83 Fragile X syndrome
*** 759.89 Other specified congenital anomalies
** 759.9 Congenital anomaly, unspecified