OpenLLM-France/wikimedia huggingface dataset:
# Sly syndrome

Sly syndrome, also called mucopolysaccharidosis type VII (MPS-VII), is an autosomal recessive lysosomal storage disease caused by a deficiency of the enzyme β-glucuronidase. This enzyme is responsible for breaking down large sugar molecules called glycosaminoglycans (AKA GAGs, or mucopolysaccharides). The inability to break down GAGs leads to a buildup in many tissues and organs of the body. The severity of the disease can vary widely.

## Signs and symptoms

The most severe cases of Sly syndrome can result in hydrops fetalis, which results in fetal death or death soon after birth. Some people with Sly syndrome may begin to have symptoms in early childhood. Symptoms can include an enlarged head, fluid buildup in the brain, coarse facial features, enlarged tongue, enlarged liver, enlarged spleen, problems with the heart valves, and abdominal hernias. People with Sly syndrome may also have sleep apnea, frequent lung infections, and problems with vision secondary to cloudy corneas. Sly syndrome causes various musculoskeletal abnormalities that worsen with age. These can include short stature, joint deformities, dysostosis multiplex, spinal stenosis, and carpal tunnel syndrome.
While some individuals have developmental delay, others may have normal intelligence. However, the accumulation of GAGs in the brain usually leads to the slowing of development from ages 1–3, and then a loss of previously learned skills until death.

## Genetics

The defective gene responsible for Sly syndrome is located on chromosome 7.

## Diagnosis

Most people with Sly disease will have elevated levels of GAGs seen in the urine. A confirmatory test is necessary for diagnosis. Skin cells and red blood cells of affected people will have low levels of β-glucuronidase activity. Sly syndrome can also be diagnosed through prenatal testing.

## Treatment

Vestronidase alfa-vjbk (trade name Mepsevii), an enzyme replacement therapy which is a recombinant form of human β-glucuronidase, is approved by U.S. Food and Drug Administration for the treatment of Sly syndrome. Hematopoietic stem cell transplant (HSCT) has been used to treat other types of MPS diseases, but this is not yet available for MPS-VII. Animal experiments suggest that HSCT may be an effective treatment for MPS-VII in humans.

## Prognosis

The life expectancy of individuals with MPS VII varies depending on the symptoms. Some individuals are stillborn, while some may survive into adulthood.

## Epidemiology

MPS-VII is one of the rarest forms of MPS. It occurs in less than 1 in 250,000 births. As a family, MPS diseases occur in 1 in 25,000 births, and the larger family of lysosomal storage diseases occur in 1 out of 7,000 to 8,000 births.

## History

Sly syndrome was originally discovered in 1972. It was named after its discoverer William S. Sly, an American biochemist who has spent nearly his entire academic career at Saint Louis University.
# Jirgah

Jirgah (Persian: جيرگاه, also Romanized as Jīrgāh) is a village in Zalaqi-ye Sharqi Rural District, Besharat District, Aligudarz County, Lorestan Province, Iran. At the 2006 census, its population was 28, in 4 families.
# Odense Isstadion

Odense Isstadion ('Odense Ice Stadium'), also known as Spar Nord Arena for sponsorship reasons, is an ice hockey arena in Bolbro, Odense, Denmark. It has previously been known as VinMedKant Arena, Bryggeriet Vestfyen Arena, and Albani Arena for sponsorship reasons. The arena is used for ice hockey as well as figure skating and serves as the home ice of the Odense Bulldogs and Odense Ishockey Klub (OIK). Odense Isstadion has a 3,280 spectator capacity, of which 1,024 are seated.
The venue also features a secondary hall, commonly noted as Odense Hal 1, which is used for ice hockey, figure skating, and curling. The secondary rink has a total capacity of 1,250 spectators, of which 350 are seated.
# Semionotus

Semionotus (from Greek: σημιον semion, 'mark' and Greek: νῶτος nôtos, 'back') is an extinct genus of ray-finned fish found throughout Northern Pangaea (North America and Europe) during the late Triassic, becoming extinct in the Early Jurassic.
# Queen Street, Singapore

Queen Street (Chinese: 奎因街; Malay: Lebuh Queen) is one of the oldest streets in Singapore and once had a very strong Eurasian presence. Beginning at Arab Street, Queen Street forms major junctions with Ophir Road, Rochor Road, Middle Road and Bras Basah Road before ending at the junction of Stamford Road.

## History

The area around Stamford Canal, Dhoby Ghaut and Selegie Road was known for the laundry services provided by the dhobies (laundrymen) from the colonial days. Many schools of high regard like the Raffles Girls' Secondary School, Saint Joseph's Institution and the Catholic High School used to be located here.

## Churches and hotels

Queen Street is known for the many churches that line it. The oldest Roman Catholic church still in existence, the Cathedral of the Good Shepherd, was built in 1847 with the churches of Saint Joseph's, Saints Peter and Paul and Our Lady of Lourdes following after. Other churches on this street include Kum Yan Methodist Church and Grace Singapore Chinese Church. The Central Sikh temple, the oldest in Singapore, which was built on Queen Street in the 1930s, was pulled down in the 1980s to make way for new development and moved to Towner Road. Flats and shops were built on its original site of Queen Street.
In June 2016, the Church of Saints Peter and Paul re-opened after completion of a one-year, $8 million restoration. The church, which was listed as a national monument in 2003, had cracks in the walls, a leaking roof, and termites. Because of the historic status of the church, the roof had to be repaired according to the original design; hundreds of nuts and bolts were used rather than welding.
Other buildings on this street include the Oxford Hotel, BOC Plaza, Mercure Singapore Bugis, Bugis+, Albert Centre Market and Food Centre, Fu Lu Shou Complex and some shophouses. Queen Street Bus Terminal, which hosts cross-border services to and from Johor Bahru, is also located there. On 7 November 2015, an 11-storey China Cultural Centre opened. The building is part of an effort to encourage exchanges of art and culture between China and Singapore.

## Arts and culture district

In 2014, the section of Queen Street between Bras Basah Road and Middle Road underwent substantial renovation as part of a project to develop the area into an arts and cultural district. Parking spots were removed, sidewalks were widened and benches installed in an effort to create space for holding public events, including in front of the Singapore Art Museum and the Waterloo Centre.

## Variant names

* Chinese names
** Sek-a-ni Koi. Sekani in Hokkien (Min Nan) means Eurasian, reflecting the presence of Eurasians in the area.
** San Ma Lu, which means "the third horseway".
** Se Zai Nian Jie, meaning "Eurasian street", referring to the fact that the street was a part of the Eurasian enclave.
* Tamil names
** Dhoby Kampam and Vannan Teruvu, both mean "street of dhobies".
* Malay name
** Kampong Dhobi, a reference to the laundrymen that dominated the area.
# Dwitiyo Manob

Dwitiyo Manob or Ditiyo Manob (English: The second generation) is a Bengali science fiction written by Bangladeshi writer Humayun Ahmed. This novel deals with the super natural powers of Homo superior (the next generation of Homo sapiens) and it is inspired by 1911 science fiction novel The Hampdenshire Wonder.

## Synopsis

Mehtabuddin is a successful businessman living in Dhaka with his daughter. He has problem of anger management, and has promised his daughter Tuntuni that he will keep his cool for a week. A school teacher from Netrokona, Mehtabuddin's native place, sends a man named Khalilullah to meet Mehtabuddin; Khalilullah supposedly has "special power". Khalilullah appears very simple and rustic. However he astonishes them by staying under water without oxygen for several hours, and fixing electronic equipment with no tools and no training. Mehtabuddin, clueless on how to solve Khalilullah's mysterious power, seeks help from his knowledgeable and bookworm friend Jalal. Despite their strict examination of Khalilullah's exhibition of special power, the mystery remains unresolved.
Meanwhile, Tuntuni, an otherwise loner, strikes friendship with Khalilullah. Khalilullah reminisces that he grew his special power following a heavy bout of high fever in his childhood; he does not remember anything before. The school teacher from Netrokona further informs Mehtabuddin that Khalilullah may be a jinn. Mehtabuddin becomes increasingly restless and uncomfortable by Khalilullah's unresolved mystery. Jalal suggests that he could be "Homo superior", the next evolutionary stage of Homo sapiens. Mehtabuddin locks Khalilullah in a room.
Moved by Tuntuni's telling of her mother's untimely death, Khalilullah endeavours to create a machine that would help reconnect with the dead. Tuntuni questions why Mehtabuddin locked Khalilullah. Growing emotional connection between Khalilullah and Tuntuni further unsettles Mehtabuddin; he arranges for killing Khalilullah while Tuntuni suffers from heavy fever.

## Characters

* Mehtabuddin
* Tuntuni
* Khalilluah/Aranya
* Jalal Khan
* Barek
* Habibur Rehman (retired Headmaster of a village school)
# Aleksandr Dedushkin

Aleksandr Dedushkin (born 1981 in Ulyanovsk, Russia) is a Russian professional basketball player. He is a center. He is 2.07 m (6 ft 9 ½ in) in height and 120 kg (265 pounds) in weight.

## Professional career

He has played with the pro clubs Khimki BC, Spartak Saint Petersburg, Ural Great, Proteas EKA AEL and BC Krasnye Krylia.
# Cabbie Richards

Cabral Richards, better known as Cabbie Richards, is a Canadian sports television personality who is best known for his time on SportsCentre on TSN, a Canadian sports cable television network.

## Broadcasting career

Originally an intern at The Score, Richards hosted five-minute segments called Cabbie on the Street from 2001 to 2002. After leaving The Score, he joined Sportsnet to produce and host the programs NBAXL and J-Zone, before moving back to The Score in 2005, where he again hosted Cabbie on the Street segments, along with Cabbie Unlimited and Cabbie All Stars. Richards also hosted NBA Court Surfing, before leaving the network again on November 30, 2010. Since 2011, Richards began hosting a weekly segment on TSN's SportsCentre entitled "Cabbie Presents".
Richards was a special correspondent on The Marilyn Denis Show on CTV from 2011 to 2012, where he brought a male perspective to conversations about relationships, while also filing reports with Hollywood actors, musicians and everyday Canadians on the street.
According to Richards, his particular style of journalism – entertain first, inform second – has allowed him to carve out a unique identity. He often initiates physical contact with the people he interviews, a technique that has gotten mixed reactions from interviewees.
His unorthodox and animated style however, has endeared him to many of the A-List athletes he's interviewed. These include stars such as Michael Jordan, Kobe Bryant, Stephen Curry, Aaron Rodgers, Alexander Ovechkin, Derek Jeter and Alex Rodriguez. Richards' atypical interviews with Kobe Bryant have garnered particular attention. Their frequent collaborations had resulted in the two developing a friendly relationship. Richards' interviews have also spanned into the world of entertainment with celebrities such as Will Smith, Hugh Jackman, Will Ferrell, Kevin Hart, Drake, Wiz Khalifa, A$AP Rocky & Kendrick Lamar.

### Cabbie Presents

Richards hosted and produced Cabbie Presents, a weekly segment which aired Fridays on "Sportscentre" on TSN. "Cabbie Presents" offered a light-hearted slice of life look at professional athletes, with a sketch-based format to the segment.
From 2012 to 2019, Richards also hosted a podcast, "Cabbie Presents: The Podcast", where he interviewed a variety of sports and entertainment stars.

### Departure from TSN

Cabbie left TSN on September 6, 2019 to pursue other career aspirations. Thereafter, he began co-hosting Bleacher Report's B/R Betting Show alongside expert Kelly Stewart.

### Sportsnet

Richards rejoined Sportsnet, which acquired The Score Television Network back in 2012, as its executive producer of sports betting content in 2021.

## Voice acting

Richards voiced Zeus and Talbot in the video game, Heavy Metal: Geomatrix.

## Personal life

Richards grew up in Toronto, Ontario and attended Galt Collegiate Institute in Cambridge, Ontario. He attended Ryerson University's Radio and Television Art's (RTA) program for three years, leaving before completing his degree.
# Igla (spacecraft docking system)

The Igla (Russian: Игла, "Needle") docking system was a Soviet radio telemetry system for automated docking of Soyuz spacecraft. The first prototypes were made in late 1965. On 30 October 1967, the first automated docking of Soyuz uncrewed spacecraft took place.

## Problems

* The Soyuz 15 mission was aborted when the system failed to dock to the Salyut 3, on 26 August 1974. There was no manual backup system.
* Salyut 5, launched on June 22, 1976, was equipped with an improved radio system. On July 6, 1976, Soyuz 21 had problems undocking automatically, but was able to undock manually. Soyuz 23 failed to dock, ran out of fuel to manual dock, and returned to Earth.
* The Igla docking system suffered an engine failure on Soyuz 33 on 10 April, 1979. After consideration by ground crews, the mission was aborted by firing the back up engines and initiating a ballistic reentry.

## Kurs

In 1986 Igla was succeeded by the Kurs docking system, first used on Soyuz TM-1.
# Queen of the Night (2001 film)

Queen of the Night (Croatian: Kraljica noći) is a 2001 Croatian film directed by Branko Schmidt. It was Croatia's submission to the 74th Academy Awards for the Academy Award for Best Foreign Language Film, but was not accepted as a nominee.
# Tony Stewart (politician)

Anthony Paul Stewart (born 23 November 1956), a former Australian politician, was a Member of the New South Wales Legislative Assembly representing the electorates of Bankstown and Lakemba between 1995 and 2011 for the Labor Party.
He was the Minister for Small Business, Minister for Science and Medical Research and Minister Assisting the Minister for Health (Cancer) in the New South Wales State Government from 8 September 2008 until 11 November 2008. He was dismissed by Premier Nathan Rees after allegations that he had verbally and physically harassed a staff member. Stewart later sought to challenge these allegations in the Court of Appeal which held that the decision to withdraw his commission as a minister was not subject to judicial review. In January 2010, he was appointed secretary assisting the minister for sport and recreation.
Stewart was elected to the NSW Legislative Assembly on 25 March 1995, representing the electorate Lakemba. He was elected as Member for Bankstown at a general election in March 1999 and re-elected to this district in March 2003 and March 2007.
Stewart decided to not contest the 2011 state election. The Labor Party endorsed Bankstown Mayor, Tania Mihailuk, as its candidate for the election held in March 2011.
# Mueang Phang Nga district

Mueang Phang Nga (Thai: เมืองพังงา, RTGS: Mueang Phang Nga, pronounced) is the capital district (amphoe mueang) of Phang Nga province in southern Thailand.

## Geography

The district is bordered by several neighboring districts, arranged geographically. To the east, it shares borders with Thap Put and Phanom districts of Surat Thani province. Moving clockwise, the adjacent districts within Phang Nga province include Kapong, Thai Mueang, and Takua Thung. To the south, the district overlooks Phang Nga Bay and is adjacent to the insular district of Ko Yao.
Several protected natural areas are located within or near the district. Ao Phang Nga National Park encompasses the islands to the south of the district, known for their distinctive landscapes and marine biodiversity. Sa Nang Manora Forest Park, covering an area of 0.29 km$^2$ (0.11 sq mi), is dedicated to protecting the Khao Toy Nang Hong Forest, which includes the Sa Nang Manora waterfall. In the northern part of the district, the Ton Pariwat Wildlife Sanctuary, aim to provide a protected habitat for local wildlife. The district also features a variety of caves situated within its limestone hills, which are notable for their geological formations.

## Administration

The district is divided into nine sub-districts (tambons), which are further subdivided into 42 villages (mubans). Phang Nga itself is a town (thesaban mueang) and covers tambon Thai Chang. There are a further seven tambon administrative organizations (TAO).
| No. | Name | Thai name | Villages | Pop. |
| 1. | Thai Chang | ท้ายช้าง | - | 9,559 |
| 2. | Nop Pring | นบปริง | 8 | 6,184 |
| 3. | Tham Nam Phut | ถ้ำน้ำผุด | 4 | 3,218 |
| 4. | Bang Toei | บางเตย | 9 | 6,667 |
| 5. | Tak Daet | ตากแดด | 4 | 2,886 |
| 6. | Song Phraek | สองแพรก | 3 | 555 |
| 7. | Thung Kha Ngok | ทุ่งคาโงก | 5 | 2,535 |
| 8. | Ko Panyi | เกาะปันหยี | 4 | 4,218 |
| 9. | Pa Ko | ป่ากอ | 5 | 2,604 |
# Nina Fyodorova

Nina Viktorovna Baldycheva (Russian: Нина Викторовна Балдычёва; also known as Baldychova, Fedorova, Baldycheva-Fedorova or Fyodorova; 18 July 1947 – 27 January 2019) was a Russian cross-country skier who competed from 1970 to 1980. She won three medals at the Winter Olympics with a gold in the 4 × 5 km relay (1976), a silver in the 4 × 5 km relay (1980), and a bronze in the 5 km (1976). In the relay in 1976, she injured her left hand in a fall at the start, but completed the race.
At the FIS Nordic World Ski Championships Fyodorova earned two gold (3 × 5 km relay: 1970, 4 × 5 km: 1974) and one bronze medals (5 km: 1970). Domestically she won one individual Soviet title, over 5 km in 1971, and eight relay titles (1969–73, 1975–76, 1979). After retiring from competitions she worked as a cross-country skiing coach in Saint Petersburg. In 1976 she was awarded the Order of the Badge of Honor.

## Cross-country skiing results

All results are sourced from the International Ski Federation (FIS).

### Olympic Games

* 3 medals – (1 gold, 1 silver, 1 bronze)
| Year | Age | 5 km | 10 km | 3/4 × 5 km  relay |
| 1972 | 24 | 10 | — | — |
| 1976 | 28 | Bronze | 4 | Gold |
| 1980 | 32 | 5 | 6 | Silver |

### World Championships

* 3 medals – (2 gold, 1 bronze)
| Year | Age | 5 km | 10 km | 20 km | 3/4 × 5 km  relay |
| 1970 | 22 | Bronze | — | — | Gold |
| 1974 | 26 | 5 | — | — | Gold |
| 1980 | 32 | — | — | 5 | — |
# M. N. R. Balan

M.N.R. Balan is an Indian politician who served as Deputy Speaker of 14th Puducherry Assembly and Member of 14th Puducherry Assembly from Ozhukarai Assembly constituency. He is the son-in law of R. V. Janakiraman.
# Diveria

The Diveria (Walliser German: Churumm Bach; German: KrummBach) is an Alpine river which flows through Switzerland (Canton Valais) and Italy (Province of Verbano Cusio Ossola). It is a tributary of the Toce and therefore, via Lake Maggiore and the Ticino, of the Po. The valley crossed by the Diveria, the Val Divedro, is the only one in the Valais to form part of the Po basin rather than that of the Rhône.

## Course

From its source at an elevation of 2,005 metres (6,578 ft) in Swiss territory near the Simplon Pass it flows through the hamlet Egga to the village of Simplon. From here it follows a south-easterly course through the Gondo gorge to the hamlet of Gondo in the municipality of Zwischbergen. Turning to the east it enters Italy and passes the villages of Paglino, Iselle di Trasquera, Bertonio and Varzo; turning south it passes Ricegno, Mognata, Campeglia and Crevoladossola where it enters the Toce.
# Aljmir Murati

Aljmir Murati (born 18 September 1985) is a Swiss football player of Kosovar Albanian descent.
# Aleksandr Katyshev

Aleksandr Katyshev (born 2 January 1996) is a Russian male BMX rider, representing his nation at international competitions. He competed in the time trial event at the 2015 UCI BMX World Championships.
# Duchess potatoes

Duchess potatoes (French: pommes de terre duchesse) consist of a purée of mashed potato, egg yolk, and butter, which is forced from a piping bag or hand-moulded into various shapes which are then baked in a high temperature oven until golden. They are typically seasoned similarly to mashed potatoes with, for example, salt, pepper, and nutmeg. They are a classic item of French cuisine, and are found in historic French cookbooks.

## History

The first known recipe for the dish was published in La Nouvelle Cuisinière Bourgeoise in 1746. The phrase à la duchesse became an appellation in French cuisine for any dish incorporating a mashed potato/egg yolk mixture. Recipes for duchess potatoes have been published in American cookbooks since at least 1878. In her 1896 cookbook, Fannie Farmer described the creative potential of duchess potatoes, writing: "Shape, using pastry bag and tube, in form of baskets, pyramids, crowns, leaves, roses, etc. Brush over with beaten egg diluted with one teaspoon water, and brown in a hot oven." In 1902, the Boston Cooking School published a duchess potatoes recipe in its magazine. French cookbook author Auguste Escoffier described duchesse potatoes in his highly influential cookbook Le Guide Culinaire, first published in 1903.
During the Great Depression, the U.S. federal government cooperated with a dozen state agricultural agencies to improve potato breeding. The U.S. Bureau of Home Economics encouraged consumers to try less common potato dishes, such as duchess potatoes. World War II led to domestic food shortages in the U.S., especially of butter, meat and canned foods. In January 1943, first lady Eleanor Roosevelt released menus for nine family meals served at the White House. One dinner included meatloaf and duchess potatoes. In 1949, the New York Times was promoting duchess potatoes surrounding roast chicken or roast fish as an elegant but inexpensive dining alternative to beef. When Craig Claiborne graduated eighth in his class from the École hôtelière de Lausanne in 1954, his final examination included preparing fish in white wine, with velouté sauce, hollandaise sauce and duchess potatoes.
In September 1959, US President Dwight Eisenhower had a meeting with Soviet Premier Nikita Khrushchev at Camp David. The dinner included prime rib and baked red snapper. Duchess potatoes were among the side dishes. When Mohammad Reza Pahlavi, the Shah of Iran, visited Washington, D.C., in April 1962, he hosted a six-course dinner for President John F. Kennedy at the Iranian embassy. The main course was pheasant, and duchess potatoes were also part of the meal. In June 1966, King Faisal of Saudi Arabia visited Washington, D.C. President Lyndon Johnson hosted a state dinner at the White House, and the menu included filet of sole almondine, roast sirloin and duchess potatoes.
# Dzielin

Dzielin is a village in the administrative district of Gmina Czernice Borowe, within Przasnysz County, Masovian Voivodeship, in east-central Poland. It lies approximately 3 kilometres (2 mi) east of Czernice Borowe, 10 km (6 mi) west of Przasnysz, and 93 km (58 mi) north of Warsaw.
# Herstedøster Church

Herstedøster Church (Danish: Herstedøster Kirke) is a church in the northern outskirts of Albertslund, Albertslund Municipality, Denmark. In medieval times, the Romanesque church was dedicated to Saint Nicholas. The tower is of late-Gothic origin. The church interior was given a major renovation in 1994 by Alan Havsteen-Mikkelsen. In 1973, R. Smalley discovered frescoes dated to around 1175, probably the date of origin of the church. On 1 February 2009 a major fire broke out at the church.