Combined ketone body and glutamine supplementation restores aerobic energy production in AGC1-deficient neuronal progenitors
Year: 2025
Type: article
Language: en
Topic: Diet and metabolism studies
Authors and affiliations:
raw_author_name: Simona Nicole Barile
raw_affiliation_strings: CNR Institute of Biomembranes, Bioenergetics and Molecular Biotechnologies (IBIOM), Bari, Italy
raw_author_name: Maria Chiara Magnifico
raw_affiliation_strings: Department of Biosciences Biotechnologies and Environment, University of Bari "A. Moro", Bari, Italy
raw_author_name: Eleonora Poeta
raw_affiliation_strings: Department of Pharmacy and BioTechnology (FaBiT), Alma Mater Studiorum - University of Bologna, Bologna, Italy
IRCCS Istituto delle Scienze Neurologiche di Bologna, Bologna, Italy
raw_author_name: Felix Distelmaier
raw_affiliation_strings: Department of General Pediatrics, Neonatology and Pediatric Cardiology, University Children's Hospital, Heinrich-Heine University, Düsseldorf, Germany
raw_author_name: Luigi Viggiano
raw_affiliation_strings: Department of Biosciences Biotechnologies and Environment, University of Bari "A. Moro", Bari, Italy
raw_author_name: Nicola Balboni
raw_affiliation_strings: Department of Pharmacy and BioTechnology (FaBiT), Alma Mater Studiorum - University of Bologna, Bologna, Italy
raw_author_name: Michele Protti
raw_affiliation_strings: Department of Pharmacy and BioTechnology (FaBiT), Alma Mater Studiorum - University of Bologna, Bologna, Italy
raw_author_name: Sabrina Petralla
raw_affiliation_strings: Department of Pharmacy and BioTechnology (FaBiT), Alma Mater Studiorum - University of Bologna, Bologna, Italy
raw_author_name: Antonella Pignataro
raw_affiliation_strings: Department of Biosciences Biotechnologies and Environment, University of Bari "A. Moro", Bari, Italy
raw_author_name: Giacomo Volpe
raw_affiliation_strings: Hematology and Cell Therapy Unit, IRCCS Istituto Tumori "Giovanni Paolo II", Bari, Italy
raw_author_name: Monica De Luise
raw_affiliation_strings: Department of Medical and Surgical Sciences (DIMEC), Alma Mater Studiorum - University of Bologna, Bologna, Italy
raw_author_name: Massimo Bonora
raw_affiliation_strings: Department of Medical Sciences, University of Ferrara, Ferrara, Italy
raw_author_name: Marica Antonicelli
raw_affiliation_strings: Department of Biosciences Biotechnologies and Environment, University of Bari "A. Moro", Bari, Italy
raw_author_name: Giorgia Babini
raw_affiliation_strings: Department of Pharmacy and BioTechnology (FaBiT), Alma Mater Studiorum - University of Bologna, Bologna, Italy
raw_author_name: Francesca Massenzio
raw_affiliation_strings: Department of Pharmacy and BioTechnology (FaBiT), Alma Mater Studiorum - University of Bologna, Bologna, Italy
raw_author_name: Vito Porcelli
raw_affiliation_strings: Department of Biosciences Biotechnologies and Environment, University of Bari "A. Moro", Bari, Italy
raw_author_name: Eleonora Lama
raw_affiliation_strings: Department of Medical and Surgical Sciences (DIMEC), Alma Mater Studiorum - University of Bologna, Bologna, Italy
raw_author_name: Roberto Arrigoni
raw_affiliation_strings: CNR Institute of Biomembranes, Bioenergetics and Molecular Biotechnologies (IBIOM), Bari, Italy
raw_author_name: Isabella Pisano
raw_affiliation_strings: Department of Biosciences Biotechnologies and Environment, University of Bari "A. Moro", Bari, Italy
raw_author_name: Veronica Addabbo
raw_affiliation_strings: Department of Biosciences Biotechnologies and Environment, University of Bari "A. Moro", Bari, Italy
raw_author_name: Anna Campana
raw_affiliation_strings: Department of Biosciences Biotechnologies and Environment, University of Bari "A. Moro", Bari, Italy
raw_author_name: Francesca Begnozzi
raw_affiliation_strings: Department of Medical Sciences, University of Ferrara, Ferrara, Italy
raw_author_name: Stewart A. Anderson
raw_affiliation_strings: Department of Psychiatry, The Children's Hospital of Philadelphia and the University of Pennsylvania, Philadelphia, PA, USA
raw_author_name: Giuseppe Fiermonte
raw_affiliation_strings: Department of Biosciences Biotechnologies and Environment, University of Bari "A. Moro", Bari, Italy
raw_author_name: Federico Manuel Giorgi
raw_affiliation_strings: Department of Pharmacy and BioTechnology (FaBiT), Alma Mater Studiorum - University of Bologna, Bologna, Italy
raw_author_name: Paolo Pinton
raw_affiliation_strings: Biomedical Research Center, Kansai Medical University, Hirakata, Osaka, Japan
Department of Medical Sciences, University of Ferrara, Ferrara, Italy
raw_author_name: Ferdinando Palmieri
raw_affiliation_strings: Department of Biosciences Biotechnologies and Environment, University of Bari "A. Moro", Bari, Italy
raw_author_name: Giuseppe Gasparre
raw_affiliation_strings: Department of Medical and Surgical Sciences (DIMEC), Alma Mater Studiorum - University of Bologna, Bologna, Italy
raw_author_name: Laura Mercolini
raw_affiliation_strings: Department of Pharmacy and BioTechnology (FaBiT), Alma Mater Studiorum - University of Bologna, Bologna, Italy
raw_author_name: Luigi Palmieri
raw_affiliation_strings: CNR Institute of Biomembranes, Bioenergetics and Molecular Biotechnologies (IBIOM), Bari, Italy
Department of Biosciences Biotechnologies and Environment, University of Bari "A. Moro", Bari, Italy
raw_author_name: Douglas C. Wallace
raw_affiliation_strings: Center for Mitochon drial and Epigeno mic Medicine, Division of Human Genetics, Department of Pediatrics, The Children's Hospital of Philadelphia, Perelman School of Medicine, Philadelphia University of Pennsylvania, Pennsylvania, PA, USA
raw_author_name: Julia Hentschel
raw_affiliation_strings: Institute of Human Genetics, University Hospital Leipzig, Leipzig, Germany
raw_author_name: Barbara Monti
raw_affiliation_strings: Department of Pharmacy and BioTechnology (FaBiT), Alma Mater Studiorum - University of Bologna, Bologna, Italy. b.monti@unibo.it
IRCCS Istituto delle Scienze Neurologiche di Bologna, Bologna, Italy. b.monti@unibo.it
IRCCS Istituto delle Scienze Neurologiche di Bologna, Bologna, Italy
Department of Pharmacy and BioTechnology (FaBiT), Alma Mater Studiorum - University of Bologna, Bologna, Italy
raw_author_name: Francesco Massimo Lasorsa
raw_affiliation_strings: CNR Institute of Biomembranes, Bioenergetics and Molecular Biotechnologies (IBIOM), Bari, Italy. francesco.lasorsa@uniba.it
Department of Biosciences Biotechnologies and Environment, University of Bari "A. Moro", Bari, Italy. francesco.lasorsa@uniba.it
Department of Biosciences Biotechnologies and Environment, University of Bari "A. Moro", Bari, Italy
CNR Institute of Biomembranes, Bioenergetics and Molecular Biotechnologies (IBIOM), Bari, Italy