Nutritional Management in Severe Methylmalonic and Propionic Acidemias: How Much Medical Food Is Too Much?
Year: 2025
Type: article
Language: en
Topic: Metabolism and Genetic Disorders
Authors and affiliations:
raw_author_name: Diane Margoses
raw_affiliation_strings: Reference Centre for Inborn Errors of Metabolism Necker‐Enfants Malades Hospital, APHP, Filière G2m, MetabERN  Paris France
raw_author_name: Apolline Imbard
raw_affiliation_strings: Biochemistry Laboratory Necker‐Enfants Malades Hospital, APHP  Paris France
Département Médicaments et Technologies Pour la Santé (DMTS) Université Paris‐Saclay, CEA, INRAE, MetaboHUB  Gif‐sur‐Yvette France
Faculty of Pharmacy Université Paris‐Saclay  Orsay France
Biochemistry Laboratory, Necker-Enfants Malades Hospital, APHP, Paris, France
raw_author_name: Clément Pontoizeau
raw_affiliation_strings: Biochemistry Laboratory Necker‐Enfants Malades Hospital, APHP  Paris France
INSERM UMR_S1163 Institut Imagine  Paris France
Université Paris Cité  Paris France
INSERM UMR_S1163, Institut Imagine, Paris, France
Biochemistry Laboratory, Necker-Enfants Malades Hospital, APHP, Paris, France
raw_author_name: Anaïs Brassier
raw_affiliation_strings: Reference Centre for Inborn Errors of Metabolism Necker‐Enfants Malades Hospital, APHP, Filière G2m, MetabERN  Paris France
raw_author_name: Jean‐Baptiste Arnoux
raw_affiliation_strings: Reference Centre for Inborn Errors of Metabolism Necker‐Enfants Malades Hospital, APHP, Filière G2m, MetabERN  Paris France
raw_author_name: Juliette Bouchereau
raw_affiliation_strings: Reference Centre for Inborn Errors of Metabolism Necker‐Enfants Malades Hospital, APHP, Filière G2m, MetabERN  Paris France
raw_author_name: Claire‐Marine Bérat
raw_affiliation_strings: Reference Centre for Inborn Errors of Metabolism Necker‐Enfants Malades Hospital, APHP, Filière G2m, MetabERN  Paris France
raw_author_name: Murielle Assoun
raw_affiliation_strings: Reference Centre for Inborn Errors of Metabolism Necker‐Enfants Malades Hospital, APHP, Filière G2m, MetabERN  Paris France
raw_author_name: Claire Belloche
raw_affiliation_strings: Reference Centre for Inborn Errors of Metabolism Necker‐Enfants Malades Hospital, APHP, Filière G2m, MetabERN  Paris France
raw_author_name: Sabine Dewulf
raw_affiliation_strings: Reference Centre for Inborn Errors of Metabolism Necker‐Enfants Malades Hospital, APHP, Filière G2m, MetabERN  Paris France
raw_author_name: Sandrine Dubois
raw_affiliation_strings: Reference Centre for Inborn Errors of Metabolism Necker‐Enfants Malades Hospital, APHP, Filière G2m, MetabERN  Paris France
raw_author_name: Bénédicte Samba
raw_affiliation_strings: Reference Centre for Inborn Errors of Metabolism Necker‐Enfants Malades Hospital, APHP, Filière G2m, MetabERN  Paris France
raw_author_name: Aude Servais
raw_affiliation_strings: Department of Adult Nephrology Necker‐Enfants Malades Hospital, APHP, Filière G2m, MetabERN  Paris France
Reference Centre for Inborn Errors of Metabolism Necker‐Enfants Malades Hospital, APHP, Filière G2m, MetabERN  Paris France
raw_author_name: Myriam Dao
raw_affiliation_strings: Department of Adult Nephrology Necker‐Enfants Malades Hospital, APHP, Filière G2m, MetabERN  Paris France
Reference Centre for Inborn Errors of Metabolism Necker‐Enfants Malades Hospital, APHP, Filière G2m, MetabERN  Paris France
raw_author_name: Edouard Le Guillou
raw_affiliation_strings: Biochemistry Laboratory Necker‐Enfants Malades Hospital, APHP  Paris France
Biochemistry Laboratory, Necker-Enfants Malades Hospital, APHP, Paris, France
raw_author_name: Amélie de Colnet
raw_affiliation_strings: Biochemistry Laboratory Necker‐Enfants Malades Hospital, APHP  Paris France
Biochemistry Laboratory, Necker-Enfants Malades Hospital, APHP, Paris, France
raw_author_name: Chris Ottolenghi
raw_affiliation_strings: Biochemistry Laboratory Necker‐Enfants Malades Hospital, APHP  Paris France
INSERM UMR_S1163 Institut Imagine  Paris France
Université Paris Cité  Paris France
Biochemistry Laboratory, Necker-Enfants Malades Hospital, APHP, Paris, France
INSERM UMR_S1163, Institut Imagine, Paris, France
raw_author_name: Pascale de Lonlay
raw_affiliation_strings: INSERM U1151 Institut Necker‐Enfants Malades (INEM)  Paris France
Reference Centre for Inborn Errors of Metabolism Necker‐Enfants Malades Hospital, APHP, Filière G2m, MetabERN  Paris France
Université Paris Cité  Paris France
raw_author_name: Jean‐François Benoist
raw_affiliation_strings: Biochemistry Laboratory Necker‐Enfants Malades Hospital, APHP  Paris France
Département Médicaments et Technologies Pour la Santé (DMTS) Université Paris‐Saclay, CEA, INRAE, MetaboHUB  Gif‐sur‐Yvette France
Faculty of Pharmacy Université Paris‐Saclay  Orsay France
Biochemistry Laboratory, Necker-Enfants Malades Hospital, APHP, Paris, France
raw_author_name: Manuel Schiff
raw_affiliation_strings: INSERM UMR_S1163 Institut Imagine  Paris France
Reference Centre for Inborn Errors of Metabolism Necker‐Enfants Malades Hospital, APHP, Filière G2m, MetabERN  Paris France
Université Paris Cité  Paris France
Reference Centre for Inborn Errors of Metabolism Necker‐Enfants Malades Hospital, APHP, Filière G2m, MetabERN Paris France