respiratory muscle training in scleroderma

Conditions: Scleroderma (Limited and Diffuse)

Summary: the aim of this study is to investigate the effects of imt on respiratory muscle strength, pulmonary function tests, quality of life aerobic capacity, dyspnea, fatigue and physical activity level in scleroderma patients with ild. the study will include 30 scleroderma + ild patients who are under follow-up in fırat university rheumatology department. patients will be randomly divided into two groups. high intensity intermittent inspiratory muscle training (h-imt) will be applied to the respiratory muscle training group in addition to the exercise program. respiratory muscle strength will be assessed by maximal inspiratory pressure (mip) and maximal expiratory pressure (mep); aerobic capacity will be assessed by exercise test and vo2max. dyspnea will be assessed with the modified medical research council scale; fatigue with the fatigue severity scale; quality of life with the scleroderma health assessment questionnaire; physical activity level with the international physical activity scale - short form

inspiratory muscle training (imt) is performed by inspiring against an external load provided by a device. it is easy to implement, low cost and can be easily integrated into rehabilitation programs. pulmonary rehabilitation and inspiratory muscle training have been applied as an effective method in ild. however, there are no studies investigating the effects of imt in individuals with ild. the aim of this study was to investigate the effects of imt on respiratory muscle strength, pulmonary function tests, quality of life, aerobic capacity, dyspnea, fatigue and physical activity level in scleroderma patients with ild. the study will include 30 scleroderma + ild patients who are under follow-up in fırat university rheumatology department. patients will be randomly divided into two groups. high intensity intermittent inspiratory muscle training (h-imt) will be applied to the respiratory muscle training group in addition to the exercise program. this training will be performed with power breath (powerbreathe classic light resistance, powerbreath, imt technologies ltd, birmingham, uk) respiratory muscle training device. in the control group, only stretching, strengthening and posture exercises will be applied as a home program. respiratory muscle strength will be assessed by maximal inspiratory pressure (mip) and maximal expiratory pressure (mep); aerobic capacity will be assessed by vo2max with exercise test. dyspnea will be assessed using the modified medical research council scale; fatigue will be assessed using the fatigue severity scale; quality of life will be assessed using the scleroderma health assessment questionnaire; physical activity level will be assessed using the international physical activity scale - short form.

Eligibility criteria:
inclusion criteria: * 18-65 years old * patients whose medical treatment has not changed in the last three months * patients who volunteered to participate in the study and were cooperative * literate patients * patients followed with a diagnosis of ssc exclusion criteria: * patients who are pregnant * patients with a diagnosis of malignancy * patients with other concomitant systemic inflammatory rheumatic diseases * patients with neurological, orthopedic or congenital problems that prevent physical activity

Keywords: scleroderma inspiratory muscle training pulmonary functions