effectiveness of respiratory physiotherapy in children with neuromuscular disease

Conditions: Neuromuscular Diseases

Summary: the main objective of this study is to determine whether the respiratory physiotherapy allows improvement or maintenance of respiratory function in children with neuromuscular diseases, against respiratory deterioration that occurs in the group of subjects who did not receive this treatment. and to determine whether decreasing the number of respiratory infections and secondly the need for antibiotics and the number of emergency room visits and hospital admissions related to these.

background: many authors have demonstrated the efficacy of physiotherapy in respiratory attending respiratory difficulties associated with different types of pathologies (chronic obstructive pulmonary disease, cystic fibrosis, tumors), however the investigators did not find studies with scientific evidence demonstrating the effectiveness of these programs in children with neuromuscular diseases (nmd), whose quality and life expectancy depends largely on the proper handling of bronchial secretions and delay the deterioration of respiratory function. the main objective of this study focuses on determining the effectiveness of physiotherapy for the treatment of respiratory breathing difficulties in children with nmd. deducing other aspects such as the impact of this program on the number of visits to hospital emergencies department each year, hospital admissions and respiratory infections suffered by these children, and the need or not of antibiotics. material and method: this research is an analytical, longitudinal, prospective, experimental, evaluator blinded study. it is controlled with two parallel groups, randomized clinical trial. the sample consisted of children diagnosed with nmd. for the evolution of different variables spirometric test was used for variables related to the function respiratory, and a tracking sheet designed by the researchers to collect the number hospital emergency visits each year, as well as hospital admissions, respiratory infections and need of antibiotics. these assessments were made before and after the start of program and during every four months. patients were randomized to control or experimental group, no apply any respiratory physical therapy treatment in subjects in the first group and performing a respiratory physical therapy program in the second. this program was carried out once in week by the physiotherapist, and four times weekly at home, by family, during one year.

Eligibility criteria:
inclusion criteria: * being diagnosed with a disease of the neuromuscular junction, according to international classification of diseases 10. * be aged between 3 and 18 years. exclusion criteria: * being unable to perform spirometry, for physical or psychological difficulties. * be involved in another program respiratory physiotherapy. * present some kind of associated pathology (such as broken ribs, state epilepticus ...) in which it is contraindicated any maneuvers of the respiratory therapy protocol designed. * if researchers are informed of the existence of a serious illness of the father / mother / tutor that preclude to carrying out the program of respiratory physiotherapy at home.

Keywords: effectiveness physical therapy modalities neuromuscular diseases