The pulmonary vasculature: Achilles heel of the Fontan circulation
Journal: Heart
Year: 2019

The Authors’ reply: 

We thank Yalta and colleagues1 for their comments concerning our article reporting the relation between pulmonary artery size and functional capacity in patients with a Fontan circulation, recently published in this Journal.2 The emerging paradigm in Fontan physiology considers the pulmonary vasculature a key determinant of cardiac output.3 In the absence of obstructions in the cavo-pulmonary connection, both proximal pulmonary arteries and pulmonary vascular bed, in the ab