Conclusion: Head and neck paragangliomas account for 0,12 % of the tumors in this region, and are mainly located in the carotid bodies. Paragangliomas arising in the nasal cavity are rare, only 23 cases reported so far. They affect the middle or upper turbinates, and also the etmoid, maxillary and sphenoidal sinuses. We report the third case in literature of a ACTH producing paraganglioma in the nasal cavity.