Objective: Appendiceal carcinoids are usually located at the tip of the appendix and occur as incidental findings. Epithelial neoplasms of the appendix are uncommon and consist of mucinous adenomas, carcinomas and neoplasms with features of both carcinoid and adenocarcinomas. Method: A case of dual mucinous cystadenoma and carcinoid of the appendix is reported. Results: The patient, a 57-year old-asymptomatic female presented with a cystic right iliac fossa mass. The excised specimen was appendix cystically dilated measuring up to 8,5 cm in diameter. The luminal content consisted of viscid mucin. The base of the appendix was thickened (up to 1,5 cm) and firm. Microscopically the cystic part of the specimen had features of mucinous cystadenoma with adenomatous epithelium extending as well over the thickened appendiceal wall. At that area the wall was involved by a well differentiated neuroendocrine neoplasm WHO gr I (carcinoid). The neoplastic cells infiltrated the entire thickness of the appendiceal wall, the mesoappendix and reached the serosal surface. The two neoplasms where separate and there was no transitional zone between them. Conclusion: Dual carcinoid/epithelial neoplasia is a rare occurrence in the appendix. The prognosis appears to be no worse than for either of the two components alone.