Objective: Female patient with chronic sinusitis and hypertension presents with lipothymia, dizziness, polyuria and polydipsia. Laboratory studies showed hyperglicemia, leucocytosis, hypokalemia, hypercortisoluria and elevated serum ACTH levels. Head MRI revealed tumor in the right nasal cavity with implantation at the cribiform plate of the ethmoid bone. Method: Microscopically the tumor had lobular architecture with big, round cells and with eosinophilic granular cytoplasm. These cells were NSE+, synaptophysin+, CD56+, CD57+ and ACTH+. Surrounding the tumor lobules were several spindle cells S-100+ (sustentacular cells).